ADHD Symptoms and Insistence on Sameness in Prader-Willi Syndrome

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Bibliographic Details
Title: ADHD Symptoms and Insistence on Sameness in Prader-Willi Syndrome
Language: English
Authors: Wigren, M., Hansen, S.
Source: Journal of Intellectual Disability Research. Jun 2005 49(6):449-456.
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Peer Reviewed: Y
Page Count: 8
Publication Date: 2005
Document Type: Journal Articles
Reports - Research
Education Level: Elementary Secondary Education
Descriptors: Profiles, Eating Disorders, Symptoms (Individual Disorders), Attention Deficit Disorders, Hyperactivity, Disabilities, Antisocial Behavior, Children, Adolescents, Rating Scales
DOI: 10.1111/j.1365-2788.2005.00690.x
ISSN: 0964-2633
Abstract: Background: Apart from a pervasive eating disorder, the Prader-Willi (PWS) syndrome is characterized by a distinct behavioural profile comprising maladaptive behaviours, obsessive-compulsive traits and skin picking, all included in the PWS behavioural phenotype. In this study, we present a further delineation of this characteristic behavioural profile by screening for indices of executive dysfunctions related to attention-deficit hyperactivity disorder (ADHD), immature compulsive-like adherence to sameness and skin picking, and how these features aggregate into symptom constellations in children and adolescents with PWS. Method: Parents of 58 individuals with PWS (aged 5-18 years) participated by completing Childhood Routines Inventory (CRI) and Conners Parent Rating Scale (CPRS-48). Results: Results showed that indices of ADHD and excessive insistence on sameness were common, comorbid and of early onset. They were both associated with conduct problems. Skin picking, appearing as a single and comorbid symptom, was less associated with childlike compulsions and ADHD-related problems. Conclusions: Findings are discussed in terms of further research in executive dysfunctions in PWS.
Abstractor: Author
Number of References: 39
Entry Date: 2005
Accession Number: EJ718421
Database: ERIC
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Abstract:Background: Apart from a pervasive eating disorder, the Prader-Willi (PWS) syndrome is characterized by a distinct behavioural profile comprising maladaptive behaviours, obsessive-compulsive traits and skin picking, all included in the PWS behavioural phenotype. In this study, we present a further delineation of this characteristic behavioural profile by screening for indices of executive dysfunctions related to attention-deficit hyperactivity disorder (ADHD), immature compulsive-like adherence to sameness and skin picking, and how these features aggregate into symptom constellations in children and adolescents with PWS. Method: Parents of 58 individuals with PWS (aged 5-18 years) participated by completing Childhood Routines Inventory (CRI) and Conners Parent Rating Scale (CPRS-48). Results: Results showed that indices of ADHD and excessive insistence on sameness were common, comorbid and of early onset. They were both associated with conduct problems. Skin picking, appearing as a single and comorbid symptom, was less associated with childlike compulsions and ADHD-related problems. Conclusions: Findings are discussed in terms of further research in executive dysfunctions in PWS.
ISSN:0964-2633
DOI:10.1111/j.1365-2788.2005.00690.x