A Specific Activity-Based Probe to Monitor Family GH59 Galactosylceramidase, the Enzyme Deficient in Krabbe Disease.

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Title: A Specific Activity-Based Probe to Monitor Family GH59 Galactosylceramidase, the Enzyme Deficient in Krabbe Disease.
Authors: Marques AR; Department of Biochemistry, Academic Medical Center, University of Amsterdam, Meibergdreef 15, 1105 AZ, Amsterdam, The Netherlands.; Present address: Institute of Biochemistry, Christian-Albrechts-University of Kiel, Otto-Hahn-Platz 9, 24098, Kiel, Germany., Willems LI; Department of Bio-organic Synthesis, Leiden Institute of Chemistry, Leiden University, Einsteeinweg 55, 2300 RA, Leiden, The Netherlands.; Present address: Department of Chemistry, Simon Fraser University, 8888 University Drive, Burnaby, V5A 1S6, BC, Canada., Herrera Moro D; Department of Biochemistry, Academic Medical Center, University of Amsterdam, Meibergdreef 15, 1105 AZ, Amsterdam, The Netherlands., Florea BI; Department of Bio-organic Synthesis, Leiden Institute of Chemistry, Leiden University, Einsteeinweg 55, 2300 RA, Leiden, The Netherlands., Scheij S; Department of Biochemistry, Academic Medical Center, University of Amsterdam, Meibergdreef 15, 1105 AZ, Amsterdam, The Netherlands., Ottenhoff R; Department of Biochemistry, Academic Medical Center, University of Amsterdam, Meibergdreef 15, 1105 AZ, Amsterdam, The Netherlands., van Roomen CP; Department of Biochemistry, Academic Medical Center, University of Amsterdam, Meibergdreef 15, 1105 AZ, Amsterdam, The Netherlands., Verhoek M; Department of Biochemistry, Leiden Institute of Chemistry, Leiden University, Einsteinweg 55, 2300 RA, Leiden, The Netherlands., Nelson JK; Department of Biochemistry, Academic Medical Center, University of Amsterdam, Meibergdreef 15, 1105 AZ, Amsterdam, The Netherlands., Kallemeijn WW; Department of Biochemistry, Leiden Institute of Chemistry, Leiden University, Einsteinweg 55, 2300 RA, Leiden, The Netherlands., Biela-Banas A; Institute of Organic and Analytical Chemistry, Université D'Orléans, Rue de Chartres, B. P. 6759, 45100, Orléans, France., Martin OR; Institute of Organic and Analytical Chemistry, Université D'Orléans, Rue de Chartres, B. P. 6759, 45100, Orléans, France., Cachón-González MB; Department of Medicine, University of Cambridge, Addenbrooke's Hospital, Hills Road, Cambridge, CB2 2QQ, UK., Kim NN; Department of Medicine, University of Cambridge, Addenbrooke's Hospital, Hills Road, Cambridge, CB2 2QQ, UK., Cox TM; Department of Medicine, University of Cambridge, Addenbrooke's Hospital, Hills Road, Cambridge, CB2 2QQ, UK., Boot RG; Department of Biochemistry, Leiden Institute of Chemistry, Leiden University, Einsteinweg 55, 2300 RA, Leiden, The Netherlands., Overkleeft HS; Department of Bio-organic Synthesis, Leiden Institute of Chemistry, Leiden University, Einsteeinweg 55, 2300 RA, Leiden, The Netherlands., Aerts JM; Department of Biochemistry, Academic Medical Center, University of Amsterdam, Meibergdreef 15, 1105 AZ, Amsterdam, The Netherlands.; Department of Biochemistry, Leiden Institute of Chemistry, Leiden University, Einsteinweg 55, 2300 RA, Leiden, The Netherlands.
Source: Chembiochem : a European journal of chemical biology [Chembiochem] 2017 Feb 16; Vol. 18 (4), pp. 402-412. Date of Electronic Publication: 2017 Jan 31.
Publication Type: Journal Article; Research Support, Non-U.S. Gov't
Journal Info: Publisher: Wiley-VCH Verlag Country of Publication: Germany NLM ID: 100937360 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1439-7633 (Electronic) Linking ISSN: 14394227 NLM ISO Abbreviation: Chembiochem Subsets: MEDLINE
Database: MEDLINE Ultimate
Description
ISSN:1439-7633
DOI:10.1002/cbic.201600561