Complement drives glucosylceramide accumulation and tissue inflammation in Gaucher disease.

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Title: Complement drives glucosylceramide accumulation and tissue inflammation in Gaucher disease.
Authors: Pandey MK; Division of Human Genetics, Cincinnati Children's Hospital Medical Center, Cincinnati, Ohio 45229, USA., Burrow TA; Division of Human Genetics, Cincinnati Children's Hospital Medical Center, Cincinnati, Ohio 45229, USA., Rani R; Division of Immunobiology and Center for Systems Immunology, Cincinnati Children's Hospital Medical Center, Cincinnati, Ohio 45229, USA., Martin LJ; Division of Human Genetics, Cincinnati Children's Hospital Medical Center, Cincinnati, Ohio 45229, USA., Witte D; Division of Pathology, Cincinnati Children's Hospital Medical Center, Cincinnati, Ohio 45229, USA., Setchell KD; Laboratory of Mass Spectroscopy, Cincinnati Children's Hospital Medical Center, Cincinnati, Ohio 45229, USA., Mckay MA; Division of Human Genetics, Cincinnati Children's Hospital Medical Center, Cincinnati, Ohio 45229, USA., Magnusen AF; Division of Immunobiology and Center for Systems Immunology, Cincinnati Children's Hospital Medical Center, Cincinnati, Ohio 45229, USA., Zhang W; Laboratory of Mass Spectroscopy, Cincinnati Children's Hospital Medical Center, Cincinnati, Ohio 45229, USA., Liou B; Division of Human Genetics, Cincinnati Children's Hospital Medical Center, Cincinnati, Ohio 45229, USA., Köhl J; Division of Immunobiology and Center for Systems Immunology, Cincinnati Children's Hospital Medical Center, Cincinnati, Ohio 45229, USA.; Institute for Systemic Inflammation Research, University of Lübeck, 23562 Lübeck, Germany., Grabowski GA; Division of Human Genetics, Cincinnati Children's Hospital Medical Center, Cincinnati, Ohio 45229, USA.
Source: Nature [Nature] 2017 Mar 02; Vol. 543 (7643), pp. 108-112. Date of Electronic Publication: 2017 Feb 22.
Publication Type: Journal Article; Research Support, Non-U.S. Gov't
Journal Info: Publisher: Nature Publishing Group Country of Publication: England NLM ID: 0410462 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1476-4687 (Electronic) Linking ISSN: 00280836 NLM ISO Abbreviation: Nature Subsets: MEDLINE
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  Data: <searchLink fieldCode="AU" term="%22Pandey+MK%22">Pandey MK</searchLink>; Division of Human Genetics, Cincinnati Children's Hospital Medical Center, Cincinnati, Ohio 45229, USA.<br /><searchLink fieldCode="AU" term="%22Burrow+TA%22">Burrow TA</searchLink>; Division of Human Genetics, Cincinnati Children's Hospital Medical Center, Cincinnati, Ohio 45229, USA.<br /><searchLink fieldCode="AU" term="%22Rani+R%22">Rani R</searchLink>; Division of Immunobiology and Center for Systems Immunology, Cincinnati Children's Hospital Medical Center, Cincinnati, Ohio 45229, USA.<br /><searchLink fieldCode="AU" term="%22Martin+LJ%22">Martin LJ</searchLink>; Division of Human Genetics, Cincinnati Children's Hospital Medical Center, Cincinnati, Ohio 45229, USA.<br /><searchLink fieldCode="AU" term="%22Witte+D%22">Witte D</searchLink>; Division of Pathology, Cincinnati Children's Hospital Medical Center, Cincinnati, Ohio 45229, USA.<br /><searchLink fieldCode="AU" term="%22Setchell+KD%22">Setchell KD</searchLink>; Laboratory of Mass Spectroscopy, Cincinnati Children's Hospital Medical Center, Cincinnati, Ohio 45229, USA.<br /><searchLink fieldCode="AU" term="%22Mckay+MA%22">Mckay MA</searchLink>; Division of Human Genetics, Cincinnati Children's Hospital Medical Center, Cincinnati, Ohio 45229, USA.<br /><searchLink fieldCode="AU" term="%22Magnusen+AF%22">Magnusen AF</searchLink>; Division of Immunobiology and Center for Systems Immunology, Cincinnati Children's Hospital Medical Center, Cincinnati, Ohio 45229, USA.<br /><searchLink fieldCode="AU" term="%22Zhang+W%22">Zhang W</searchLink>; Laboratory of Mass Spectroscopy, Cincinnati Children's Hospital Medical Center, Cincinnati, Ohio 45229, USA.<br /><searchLink fieldCode="AU" term="%22Liou+B%22">Liou B</searchLink>; Division of Human Genetics, Cincinnati Children's Hospital Medical Center, Cincinnati, Ohio 45229, USA.<br /><searchLink fieldCode="AU" term="%22Köhl+J%22">Köhl J</searchLink>; Division of Immunobiology and Center for Systems Immunology, Cincinnati Children's Hospital Medical Center, Cincinnati, Ohio 45229, USA.; Institute for Systemic Inflammation Research, University of Lübeck, 23562 Lübeck, Germany.<br /><searchLink fieldCode="AU" term="%22Grabowski+GA%22">Grabowski GA</searchLink>; Division of Human Genetics, Cincinnati Children's Hospital Medical Center, Cincinnati, Ohio 45229, USA.
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  Data: <searchLink fieldCode="JN" term="%220410462%22">Nature</searchLink> [Nature] 2017 Mar 02; Vol. 543 (7643), pp. 108-112. <i>Date of Electronic Publication: </i>2017 Feb 22.
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