Prolonged treatment with open-label pirfenidone in Hermansky-Pudlak syndrome pulmonary fibrosis.

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Title: Prolonged treatment with open-label pirfenidone in Hermansky-Pudlak syndrome pulmonary fibrosis.
Authors: O'Brien KJ; Office of the Clinical Director, National Human Genome Research Institute, National Institutes of Health, Bethesda, MD, USA., Introne WJ; Office of the Clinical Director, National Human Genome Research Institute, National Institutes of Health, Bethesda, MD, USA., Akal O; Department of Mathematics, Florida State University, Tallahassee, FL, USA., Akal T; Department of Statistics, Middle East Technical University, Ankara, Turkey., Barbu A; Department of Statistics, Florida State University, Tallahassee, FL, USA., McGowan MP; Medical Genetics Branch, National Human Genome Research Institute, National Institutes of Health, Bethesda, MD, USA., Merideth MA; Medical Genetics Branch, National Human Genome Research Institute, National Institutes of Health, Bethesda, MD, USA., Seward SL Jr; Department of Medicine, Mount Sinai St. Luke's and Mount Sinai West, New York, NY, USA., Gahl WA; Office of the Clinical Director, National Human Genome Research Institute, National Institutes of Health, Bethesda, MD, USA; Medical Genetics Branch, National Human Genome Research Institute, National Institutes of Health, Bethesda, MD, USA., Gochuico BR; Medical Genetics Branch, National Human Genome Research Institute, National Institutes of Health, Bethesda, MD, USA. Electronic address: gochuicb@mail.nih.gov.
Source: Molecular genetics and metabolism [Mol Genet Metab] 2018 Sep; Vol. 125 (1-2), pp. 168-173. Date of Electronic Publication: 2018 Jul 23.
Publication Type: Journal Article; Research Support, N.I.H., Intramural
Journal Info: Publisher: Academic Press Country of Publication: United States NLM ID: 9805456 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1096-7206 (Electronic) Linking ISSN: 10967192 NLM ISO Abbreviation: Mol Genet Metab Subsets: MEDLINE
Database: MEDLINE Ultimate
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  Data: Prolonged treatment with open-label pirfenidone in Hermansky-Pudlak syndrome pulmonary fibrosis.
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  Data: <searchLink fieldCode="AU" term="%22O'Brien+KJ%22">O'Brien KJ</searchLink>; Office of the Clinical Director, National Human Genome Research Institute, National Institutes of Health, Bethesda, MD, USA.<br /><searchLink fieldCode="AU" term="%22Introne+WJ%22">Introne WJ</searchLink>; Office of the Clinical Director, National Human Genome Research Institute, National Institutes of Health, Bethesda, MD, USA.<br /><searchLink fieldCode="AU" term="%22Akal+O%22">Akal O</searchLink>; Department of Mathematics, Florida State University, Tallahassee, FL, USA.<br /><searchLink fieldCode="AU" term="%22Akal+T%22">Akal T</searchLink>; Department of Statistics, Middle East Technical University, Ankara, Turkey.<br /><searchLink fieldCode="AU" term="%22Barbu+A%22">Barbu A</searchLink>; Department of Statistics, Florida State University, Tallahassee, FL, USA.<br /><searchLink fieldCode="AU" term="%22McGowan+MP%22">McGowan MP</searchLink>; Medical Genetics Branch, National Human Genome Research Institute, National Institutes of Health, Bethesda, MD, USA.<br /><searchLink fieldCode="AU" term="%22Merideth+MA%22">Merideth MA</searchLink>; Medical Genetics Branch, National Human Genome Research Institute, National Institutes of Health, Bethesda, MD, USA.<br /><searchLink fieldCode="AU" term="%22Seward+SL+Jr%22">Seward SL Jr</searchLink>; Department of Medicine, Mount Sinai St. Luke's and Mount Sinai West, New York, NY, USA.<br /><searchLink fieldCode="AU" term="%22Gahl+WA%22">Gahl WA</searchLink>; Office of the Clinical Director, National Human Genome Research Institute, National Institutes of Health, Bethesda, MD, USA; Medical Genetics Branch, National Human Genome Research Institute, National Institutes of Health, Bethesda, MD, USA.<br /><searchLink fieldCode="AU" term="%22Gochuico+BR%22">Gochuico BR</searchLink>; Medical Genetics Branch, National Human Genome Research Institute, National Institutes of Health, Bethesda, MD, USA. Electronic address: gochuicb@mail.nih.gov.
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  Data: <i>Publisher: </i><searchLink fieldCode="PB" term="%22Academic+Press%22">Academic Press </searchLink><i>Country of Publication: </i>United States <i>NLM ID: </i>9805456 <i>Publication Model: </i>Print-Electronic <i>Cited Medium: </i>Internet <i>ISSN: </i>1096-7206 (Electronic) <i>Linking ISSN: </i><searchLink fieldCode="IS" term="%2210967192%22">10967192 </searchLink><i>NLM ISO Abbreviation: </i>Mol Genet Metab <i>Subsets: </i>MEDLINE
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              Text: 2018 Sep
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