The displacement of frataxin from the mitochondrial cristae correlates with abnormal respiratory supercomplexes formation and bioenergetic defects in cells of Friedreich ataxia patients.

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Title: The displacement of frataxin from the mitochondrial cristae correlates with abnormal respiratory supercomplexes formation and bioenergetic defects in cells of Friedreich ataxia patients.
Authors: Doni D; Department of Biology, University of Padova, Padova, Italy., Rigoni G; Department of Biology, University of Padova, Padova, Italy., Palumbo E; Department of Molecular Medicine, University of Padova, Padova, Italy., Baschiera E; Clinical Genetics Unit, Department of Women's and Children's Health, University of Padova, Padova, Italy.; Istituto di Ricerca Pediatrica (IRP) Città della Speranza, Padova, Italy., Peruzzo R; Department of Biology, University of Padova, Padova, Italy., De Rosa E; Department of Biology, University of Padova, Padova, Italy., Caicci F; Department of Biology, University of Padova, Padova, Italy., Passerini L; Department of Biology, University of Padova, Padova, Italy., Bettio D; Clinical Genetics Unit, Department of Women's and Children's Health, University of Padova, Padova, Italy.; Istituto di Ricerca Pediatrica (IRP) Città della Speranza, Padova, Italy., Russo A; Department of Molecular Medicine, University of Padova, Padova, Italy., Szabò I; Department of Biology, University of Padova, Padova, Italy., Soriano ME; Department of Biology, University of Padova, Padova, Italy., Salviati L; Clinical Genetics Unit, Department of Women's and Children's Health, University of Padova, Padova, Italy.; Istituto di Ricerca Pediatrica (IRP) Città della Speranza, Padova, Italy.; Myology Center, University of Padova, Padova, Italy., Costantini P; Department of Biology, University of Padova, Padova, Italy.
Source: FASEB journal : official publication of the Federation of American Societies for Experimental Biology [FASEB J] 2021 Mar; Vol. 35 (3), pp. e21362.
Publication Type: Journal Article; Research Support, Non-U.S. Gov't
Journal Info: Publisher: Federation of American Societies for Experimental Biology Country of Publication: United States NLM ID: 8804484 Publication Model: Print Cited Medium: Internet ISSN: 1530-6860 (Electronic) Linking ISSN: 08926638 NLM ISO Abbreviation: FASEB J Subsets: MEDLINE
Database: MEDLINE Ultimate
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  Data: The displacement of frataxin from the mitochondrial cristae correlates with abnormal respiratory supercomplexes formation and bioenergetic defects in cells of Friedreich ataxia patients.
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  Data: <searchLink fieldCode="AU" term="%22Doni+D%22">Doni D</searchLink>; Department of Biology, University of Padova, Padova, Italy.<br /><searchLink fieldCode="AU" term="%22Rigoni+G%22">Rigoni G</searchLink>; Department of Biology, University of Padova, Padova, Italy.<br /><searchLink fieldCode="AU" term="%22Palumbo+E%22">Palumbo E</searchLink>; Department of Molecular Medicine, University of Padova, Padova, Italy.<br /><searchLink fieldCode="AU" term="%22Baschiera+E%22">Baschiera E</searchLink>; Clinical Genetics Unit, Department of Women's and Children's Health, University of Padova, Padova, Italy.; Istituto di Ricerca Pediatrica (IRP) Città della Speranza, Padova, Italy.<br /><searchLink fieldCode="AU" term="%22Peruzzo+R%22">Peruzzo R</searchLink>; Department of Biology, University of Padova, Padova, Italy.<br /><searchLink fieldCode="AU" term="%22De+Rosa+E%22">De Rosa E</searchLink>; Department of Biology, University of Padova, Padova, Italy.<br /><searchLink fieldCode="AU" term="%22Caicci+F%22">Caicci F</searchLink>; Department of Biology, University of Padova, Padova, Italy.<br /><searchLink fieldCode="AU" term="%22Passerini+L%22">Passerini L</searchLink>; Department of Biology, University of Padova, Padova, Italy.<br /><searchLink fieldCode="AU" term="%22Bettio+D%22">Bettio D</searchLink>; Clinical Genetics Unit, Department of Women's and Children's Health, University of Padova, Padova, Italy.; Istituto di Ricerca Pediatrica (IRP) Città della Speranza, Padova, Italy.<br /><searchLink fieldCode="AU" term="%22Russo+A%22">Russo A</searchLink>; Department of Molecular Medicine, University of Padova, Padova, Italy.<br /><searchLink fieldCode="AU" term="%22Szabò+I%22">Szabò I</searchLink>; Department of Biology, University of Padova, Padova, Italy.<br /><searchLink fieldCode="AU" term="%22Soriano+ME%22">Soriano ME</searchLink>; Department of Biology, University of Padova, Padova, Italy.<br /><searchLink fieldCode="AU" term="%22Salviati+L%22">Salviati L</searchLink>; Clinical Genetics Unit, Department of Women's and Children's Health, University of Padova, Padova, Italy.; Istituto di Ricerca Pediatrica (IRP) Città della Speranza, Padova, Italy.; Myology Center, University of Padova, Padova, Italy.<br /><searchLink fieldCode="AU" term="%22Costantini+P%22">Costantini P</searchLink>; Department of Biology, University of Padova, Padova, Italy.
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              Text: 2021 Mar
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