The displacement of frataxin from the mitochondrial cristae correlates with abnormal respiratory supercomplexes formation and bioenergetic defects in cells of Friedreich ataxia patients.
Saved in:
| Title: | The displacement of frataxin from the mitochondrial cristae correlates with abnormal respiratory supercomplexes formation and bioenergetic defects in cells of Friedreich ataxia patients. |
|---|---|
| Authors: | Doni D; Department of Biology, University of Padova, Padova, Italy., Rigoni G; Department of Biology, University of Padova, Padova, Italy., Palumbo E; Department of Molecular Medicine, University of Padova, Padova, Italy., Baschiera E; Clinical Genetics Unit, Department of Women's and Children's Health, University of Padova, Padova, Italy.; Istituto di Ricerca Pediatrica (IRP) Città della Speranza, Padova, Italy., Peruzzo R; Department of Biology, University of Padova, Padova, Italy., De Rosa E; Department of Biology, University of Padova, Padova, Italy., Caicci F; Department of Biology, University of Padova, Padova, Italy., Passerini L; Department of Biology, University of Padova, Padova, Italy., Bettio D; Clinical Genetics Unit, Department of Women's and Children's Health, University of Padova, Padova, Italy.; Istituto di Ricerca Pediatrica (IRP) Città della Speranza, Padova, Italy., Russo A; Department of Molecular Medicine, University of Padova, Padova, Italy., Szabò I; Department of Biology, University of Padova, Padova, Italy., Soriano ME; Department of Biology, University of Padova, Padova, Italy., Salviati L; Clinical Genetics Unit, Department of Women's and Children's Health, University of Padova, Padova, Italy.; Istituto di Ricerca Pediatrica (IRP) Città della Speranza, Padova, Italy.; Myology Center, University of Padova, Padova, Italy., Costantini P; Department of Biology, University of Padova, Padova, Italy. |
| Source: | FASEB journal : official publication of the Federation of American Societies for Experimental Biology [FASEB J] 2021 Mar; Vol. 35 (3), pp. e21362. |
| Publication Type: | Journal Article; Research Support, Non-U.S. Gov't |
| Journal Info: | Publisher: Federation of American Societies for Experimental Biology Country of Publication: United States NLM ID: 8804484 Publication Model: Print Cited Medium: Internet ISSN: 1530-6860 (Electronic) Linking ISSN: 08926638 NLM ISO Abbreviation: FASEB J Subsets: MEDLINE |
| Database: | MEDLINE Ultimate |
| FullText | Links: – Type: pdflink Text: Availability: 0 |
|---|---|
| Header | DbId: mdl DbLabel: MEDLINE Ultimate An: 33629768 AccessLevel: 2 PubType: Academic Journal PubTypeId: academicJournal PreciseRelevancyScore: 0 |
| IllustrationInfo | |
| Items | – Name: Title Label: Title Group: Ti Data: The displacement of frataxin from the mitochondrial cristae correlates with abnormal respiratory supercomplexes formation and bioenergetic defects in cells of Friedreich ataxia patients. – Name: Author Label: Authors Group: Au Data: <searchLink fieldCode="AU" term="%22Doni+D%22">Doni D</searchLink>; Department of Biology, University of Padova, Padova, Italy.<br /><searchLink fieldCode="AU" term="%22Rigoni+G%22">Rigoni G</searchLink>; Department of Biology, University of Padova, Padova, Italy.<br /><searchLink fieldCode="AU" term="%22Palumbo+E%22">Palumbo E</searchLink>; Department of Molecular Medicine, University of Padova, Padova, Italy.<br /><searchLink fieldCode="AU" term="%22Baschiera+E%22">Baschiera E</searchLink>; Clinical Genetics Unit, Department of Women's and Children's Health, University of Padova, Padova, Italy.; Istituto di Ricerca Pediatrica (IRP) Città della Speranza, Padova, Italy.<br /><searchLink fieldCode="AU" term="%22Peruzzo+R%22">Peruzzo R</searchLink>; Department of Biology, University of Padova, Padova, Italy.<br /><searchLink fieldCode="AU" term="%22De+Rosa+E%22">De Rosa E</searchLink>; Department of Biology, University of Padova, Padova, Italy.<br /><searchLink fieldCode="AU" term="%22Caicci+F%22">Caicci F</searchLink>; Department of Biology, University of Padova, Padova, Italy.<br /><searchLink fieldCode="AU" term="%22Passerini+L%22">Passerini L</searchLink>; Department of Biology, University of Padova, Padova, Italy.<br /><searchLink fieldCode="AU" term="%22Bettio+D%22">Bettio D</searchLink>; Clinical Genetics Unit, Department of Women's and Children's Health, University of Padova, Padova, Italy.; Istituto di Ricerca Pediatrica (IRP) Città della Speranza, Padova, Italy.<br /><searchLink fieldCode="AU" term="%22Russo+A%22">Russo A</searchLink>; Department of Molecular Medicine, University of Padova, Padova, Italy.<br /><searchLink fieldCode="AU" term="%22Szabò+I%22">Szabò I</searchLink>; Department of Biology, University of Padova, Padova, Italy.<br /><searchLink fieldCode="AU" term="%22Soriano+ME%22">Soriano ME</searchLink>; Department of Biology, University of Padova, Padova, Italy.<br /><searchLink fieldCode="AU" term="%22Salviati+L%22">Salviati L</searchLink>; Clinical Genetics Unit, Department of Women's and Children's Health, University of Padova, Padova, Italy.; Istituto di Ricerca Pediatrica (IRP) Città della Speranza, Padova, Italy.; Myology Center, University of Padova, Padova, Italy.<br /><searchLink fieldCode="AU" term="%22Costantini+P%22">Costantini P</searchLink>; Department of Biology, University of Padova, Padova, Italy. – Name: TitleSource Label: Source Group: Src Data: <searchLink fieldCode="JN" term="%228804484%22">FASEB journal : official publication of the Federation of American Societies for Experimental Biology</searchLink> [FASEB J] 2021 Mar; Vol. 35 (3), pp. e21362. – Name: TypePub Label: Publication Type Group: TypPub Data: Journal Article; Research Support, Non-U.S. Gov't – Name: TitleSource Label: Journal Info Group: Src Data: <i>Publisher: </i><searchLink fieldCode="PB" term="%22Federation+of+American+Societies+for+Experimental+Biology%22">Federation of American Societies for Experimental Biology </searchLink><i>Country of Publication: </i>United States <i>NLM ID: </i>8804484 <i>Publication Model: </i>Print <i>Cited Medium: </i>Internet <i>ISSN: </i>1530-6860 (Electronic) <i>Linking ISSN: </i><searchLink fieldCode="IS" term="%2208926638%22">08926638 </searchLink><i>NLM ISO Abbreviation: </i>FASEB J <i>Subsets: </i>MEDLINE |
| PLink | https://search.ebscohost.com/login.aspx?direct=true&site=eds-live&db=mdl&AN=33629768 |
| RecordInfo | BibRecord: BibEntity: Identifiers: – Type: doi Value: 10.1096/fj.202000524RR Languages: – Code: eng Text: English PhysicalDescription: Pagination: StartPage: e21362 Titles: – TitleFull: The displacement of frataxin from the mitochondrial cristae correlates with abnormal respiratory supercomplexes formation and bioenergetic defects in cells of Friedreich ataxia patients. Type: main BibRelationships: HasContributorRelationships: – PersonEntity: Name: NameFull: Doni D – PersonEntity: Name: NameFull: Rigoni G – PersonEntity: Name: NameFull: Palumbo E – PersonEntity: Name: NameFull: Baschiera E – PersonEntity: Name: NameFull: Peruzzo R – PersonEntity: Name: NameFull: De Rosa E – PersonEntity: Name: NameFull: Caicci F – PersonEntity: Name: NameFull: Passerini L – PersonEntity: Name: NameFull: Bettio D – PersonEntity: Name: NameFull: Russo A – PersonEntity: Name: NameFull: Szabò I – PersonEntity: Name: NameFull: Soriano ME – PersonEntity: Name: NameFull: Salviati L – PersonEntity: Name: NameFull: Costantini P IsPartOfRelationships: – BibEntity: Dates: – D: 01 M: 03 Text: 2021 Mar Type: published Y: 2021 Identifiers: – Type: issn-electronic Value: 1530-6860 Numbering: – Type: volume Value: 35 – Type: issue Value: 3 Titles: – TitleFull: FASEB journal : official publication of the Federation of American Societies for Experimental Biology Type: main |
| ResultId | 1 |