Progressive pulmonary fibrosis in a murine model of Hermansky-Pudlak syndrome.

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Title: Progressive pulmonary fibrosis in a murine model of Hermansky-Pudlak syndrome.
Authors: Abudi-Sinreich S; Human Biochemical Genetics Section, National Human Genome Research Institute (NHGRI), National Institute of Health (NIH), Bethesda, MD, 20892, USA.; The Sackler School of Medicine, Tel Aviv University, Tel Aviv, Israel., Bodine SP; Human Biochemical Genetics Section, National Human Genome Research Institute (NHGRI), National Institute of Health (NIH), Bethesda, MD, 20892, USA., Yokoyama T; Human Biochemical Genetics Section, National Human Genome Research Institute (NHGRI), National Institute of Health (NIH), Bethesda, MD, 20892, USA., Tolman NJ; UDP Translational Laboratory, NIH Undiagnosed Diseases Program, National Human Genome Research Institute (NHGRI), National Institutes of Health (NIH), Bethesda, MD, 20892, USA., Tyrlik M; Human Biochemical Genetics Section, National Human Genome Research Institute (NHGRI), National Institute of Health (NIH), Bethesda, MD, 20892, USA., Testa LC; UDP Translational Laboratory, NIH Undiagnosed Diseases Program, National Human Genome Research Institute (NHGRI), National Institutes of Health (NIH), Bethesda, MD, 20892, USA., Han CG; Human Biochemical Genetics Section, National Human Genome Research Institute (NHGRI), National Institute of Health (NIH), Bethesda, MD, 20892, USA., Dorward HM; Human Biochemical Genetics Section, National Human Genome Research Institute (NHGRI), National Institute of Health (NIH), Bethesda, MD, 20892, USA., Wincovitch SM; National Human Genome Research Institute (NHGRI) Cytogenetics and Microscopy Core, National Institute of Health (NIH), Bethesda, MD, 20892, USA., Anikster Y; The Sackler School of Medicine, Tel Aviv University, Tel Aviv, Israel.; Edmond and Lily Safra Children's Hospital, Sheba Medical Center, Ramat Gan, Israel., Gahl WA; Human Biochemical Genetics Section, National Human Genome Research Institute (NHGRI), National Institute of Health (NIH), Bethesda, MD, 20892, USA.; UDP Translational Laboratory, NIH Undiagnosed Diseases Program, National Human Genome Research Institute (NHGRI), National Institutes of Health (NIH), Bethesda, MD, 20892, USA., Cinar R; Laboratory of Physiologic Studies, National Institute on Alcohol Abuse and Alcoholism (NIAAA), National Institute of Health (NIH), Rockville, MD, 20852, USA., Gochuico BR; Human Biochemical Genetics Section, National Human Genome Research Institute (NHGRI), National Institute of Health (NIH), Bethesda, MD, 20892, USA., Malicdan MCV; Human Biochemical Genetics Section, National Human Genome Research Institute (NHGRI), National Institute of Health (NIH), Bethesda, MD, 20892, USA. malicdanm@mail.nih.gov.; UDP Translational Laboratory, NIH Undiagnosed Diseases Program, National Human Genome Research Institute (NHGRI), National Institutes of Health (NIH), Bethesda, MD, 20892, USA. malicdanm@mail.nih.gov.
Source: Respiratory research [Respir Res] 2022 May 04; Vol. 23 (1), pp. 112. Date of Electronic Publication: 2022 May 04.
Publication Type: Journal Article
Journal Info: Publisher: BioMed Central Ltd Country of Publication: England NLM ID: 101090633 Publication Model: Electronic Cited Medium: Internet ISSN: 1465-993X (Electronic) Linking ISSN: 14659921 NLM ISO Abbreviation: Respir Res Subsets: MEDLINE
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  Data: Progressive pulmonary fibrosis in a murine model of Hermansky-Pudlak syndrome.
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  Data: <searchLink fieldCode="AU" term="%22Abudi-Sinreich+S%22">Abudi-Sinreich S</searchLink>; Human Biochemical Genetics Section, National Human Genome Research Institute (NHGRI), National Institute of Health (NIH), Bethesda, MD, 20892, USA.; The Sackler School of Medicine, Tel Aviv University, Tel Aviv, Israel.<br /><searchLink fieldCode="AU" term="%22Bodine+SP%22">Bodine SP</searchLink>; Human Biochemical Genetics Section, National Human Genome Research Institute (NHGRI), National Institute of Health (NIH), Bethesda, MD, 20892, USA.<br /><searchLink fieldCode="AU" term="%22Yokoyama+T%22">Yokoyama T</searchLink>; Human Biochemical Genetics Section, National Human Genome Research Institute (NHGRI), National Institute of Health (NIH), Bethesda, MD, 20892, USA.<br /><searchLink fieldCode="AU" term="%22Tolman+NJ%22">Tolman NJ</searchLink>; UDP Translational Laboratory, NIH Undiagnosed Diseases Program, National Human Genome Research Institute (NHGRI), National Institutes of Health (NIH), Bethesda, MD, 20892, USA.<br /><searchLink fieldCode="AU" term="%22Tyrlik+M%22">Tyrlik M</searchLink>; Human Biochemical Genetics Section, National Human Genome Research Institute (NHGRI), National Institute of Health (NIH), Bethesda, MD, 20892, USA.<br /><searchLink fieldCode="AU" term="%22Testa+LC%22">Testa LC</searchLink>; UDP Translational Laboratory, NIH Undiagnosed Diseases Program, National Human Genome Research Institute (NHGRI), National Institutes of Health (NIH), Bethesda, MD, 20892, USA.<br /><searchLink fieldCode="AU" term="%22Han+CG%22">Han CG</searchLink>; Human Biochemical Genetics Section, National Human Genome Research Institute (NHGRI), National Institute of Health (NIH), Bethesda, MD, 20892, USA.<br /><searchLink fieldCode="AU" term="%22Dorward+HM%22">Dorward HM</searchLink>; Human Biochemical Genetics Section, National Human Genome Research Institute (NHGRI), National Institute of Health (NIH), Bethesda, MD, 20892, USA.<br /><searchLink fieldCode="AU" term="%22Wincovitch+SM%22">Wincovitch SM</searchLink>; National Human Genome Research Institute (NHGRI) Cytogenetics and Microscopy Core, National Institute of Health (NIH), Bethesda, MD, 20892, USA.<br /><searchLink fieldCode="AU" term="%22Anikster+Y%22">Anikster Y</searchLink>; The Sackler School of Medicine, Tel Aviv University, Tel Aviv, Israel.; Edmond and Lily Safra Children's Hospital, Sheba Medical Center, Ramat Gan, Israel.<br /><searchLink fieldCode="AU" term="%22Gahl+WA%22">Gahl WA</searchLink>; Human Biochemical Genetics Section, National Human Genome Research Institute (NHGRI), National Institute of Health (NIH), Bethesda, MD, 20892, USA.; UDP Translational Laboratory, NIH Undiagnosed Diseases Program, National Human Genome Research Institute (NHGRI), National Institutes of Health (NIH), Bethesda, MD, 20892, USA.<br /><searchLink fieldCode="AU" term="%22Cinar+R%22">Cinar R</searchLink>; Laboratory of Physiologic Studies, National Institute on Alcohol Abuse and Alcoholism (NIAAA), National Institute of Health (NIH), Rockville, MD, 20852, USA.<br /><searchLink fieldCode="AU" term="%22Gochuico+BR%22">Gochuico BR</searchLink>; Human Biochemical Genetics Section, National Human Genome Research Institute (NHGRI), National Institute of Health (NIH), Bethesda, MD, 20892, USA.<br /><searchLink fieldCode="AU" term="%22Malicdan+MCV%22">Malicdan MCV</searchLink>; Human Biochemical Genetics Section, National Human Genome Research Institute (NHGRI), National Institute of Health (NIH), Bethesda, MD, 20892, USA. malicdanm@mail.nih.gov.; UDP Translational Laboratory, NIH Undiagnosed Diseases Program, National Human Genome Research Institute (NHGRI), National Institutes of Health (NIH), Bethesda, MD, 20892, USA. malicdanm@mail.nih.gov.
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  Data: <searchLink fieldCode="JN" term="%22101090633%22">Respiratory research</searchLink> [Respir Res] 2022 May 04; Vol. 23 (1), pp. 112. <i>Date of Electronic Publication: </i>2022 May 04.
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  Data: <i>Publisher: </i><searchLink fieldCode="PB" term="%22BioMed+Central+Ltd%22">BioMed Central Ltd </searchLink><i>Country of Publication: </i>England <i>NLM ID: </i>101090633 <i>Publication Model: </i>Electronic <i>Cited Medium: </i>Internet <i>ISSN: </i>1465-993X (Electronic) <i>Linking ISSN: </i><searchLink fieldCode="IS" term="%2214659921%22">14659921 </searchLink><i>NLM ISO Abbreviation: </i>Respir Res <i>Subsets: </i>MEDLINE
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        Value: 10.1186/s12931-022-02002-z
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