Mitochondrial creatine sensitivity is lost in the D2.mdx model of Duchenne muscular dystrophy and rescued by the mitochondrial-enhancing compound Olesoxime.

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Title: Mitochondrial creatine sensitivity is lost in the D2.mdx model of Duchenne muscular dystrophy and rescued by the mitochondrial-enhancing compound Olesoxime.
Authors: Bellissimo CA; School of Kinesiology & Health Science, Muscle Health Research Centre, York University, Toronto, Ontario, Canada., Delfinis LJ; School of Kinesiology & Health Science, Muscle Health Research Centre, York University, Toronto, Ontario, Canada., Hughes MC; School of Kinesiology & Health Science, Muscle Health Research Centre, York University, Toronto, Ontario, Canada., Turnbull PC; School of Kinesiology & Health Science, Muscle Health Research Centre, York University, Toronto, Ontario, Canada., Gandhi S; School of Kinesiology & Health Science, Muscle Health Research Centre, York University, Toronto, Ontario, Canada., DiBenedetto SN; School of Kinesiology & Health Science, Muscle Health Research Centre, York University, Toronto, Ontario, Canada., Rahman FA; Faculty of Health, Department of Kinesiology and Health Sciences, University of Waterloo, Waterloo, Ontario, Canada., Tadi P; School of Kinesiology & Health Science, Muscle Health Research Centre, York University, Toronto, Ontario, Canada., Amaral CA; School of Kinesiology & Health Science, Muscle Health Research Centre, York University, Toronto, Ontario, Canada., Dehghani A; School of Kinesiology & Health Science, Muscle Health Research Centre, York University, Toronto, Ontario, Canada., Cobley JN; Redox Biology Group, Centre for Health Sciences, University of the Highlands and Islands, Inverness, United Kingdom., Quadrilatero J; Faculty of Health, Department of Kinesiology and Health Sciences, University of Waterloo, Waterloo, Ontario, Canada., Schlattner U; Laboratory of Fundamental and Applied Bioenergetics, University Grenoble Alpes, Inserm U1055, Grenoble, France and Institut Universiatire de France Paris, France., Perry CGR; School of Kinesiology & Health Science, Muscle Health Research Centre, York University, Toronto, Ontario, Canada.
Source: American journal of physiology. Cell physiology [Am J Physiol Cell Physiol] 2023 May 01; Vol. 324 (5), pp. C1141-C1157. Date of Electronic Publication: 2023 Jan 23.
Publication Type: Journal Article; Research Support, Non-U.S. Gov't
Journal Info: Publisher: American Physiological Society Country of Publication: United States NLM ID: 100901225 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1522-1563 (Electronic) Linking ISSN: 03636143 NLM ISO Abbreviation: Am J Physiol Cell Physiol Subsets: MEDLINE
Database: MEDLINE Ultimate
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ISSN:1522-1563
DOI:10.1152/ajpcell.00377.2022