Increased phosphorylation of HexM improves lysosomal uptake and potential for managing GM2 gangliosidoses.

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Title: Increased phosphorylation of HexM improves lysosomal uptake and potential for managing GM2 gangliosidoses.
Authors: Benzie G; Department of Microbiology, University of Manitoba, Winnipeg, MB R3T 2N2, Canada., Bouma K; Department of Microbiology, University of Manitoba, Winnipeg, MB R3T 2N2, Canada., Battellino T; Department of Chemistry, University of Manitoba, Winnipeg R3T 2N2, Canada., Cooper S; Biochemistry and Medical Genetics, University of Manitoba, Canada., Hemming R; Biochemistry and Medical Genetics, University of Manitoba, Canada., Kammouni W; Biochemistry and Medical Genetics, University of Manitoba, Canada., Liu L; M6P Therapeutics, 20 S. Sarah St., St. Louis, MO 63018, United States., Do C; M6P Therapeutics, 20 S. Sarah St., St. Louis, MO 63018, United States., Khajehpour M; Department of Chemistry, University of Manitoba, Winnipeg R3T 2N2, Canada., Perreault H; Department of Chemistry, University of Manitoba, Winnipeg R3T 2N2, Canada., Kornfeld S; Washington University School of Medicine in St. Louis, Department of Biochemistry & Molecular Biophysics, United States., Triggs-Raine B; Biochemistry and Medical Genetics, University of Manitoba, Canada., Mark BL; Department of Microbiology, University of Manitoba, Winnipeg, MB R3T 2N2, Canada.
Source: BBA advances [BBA Adv] 2021 Dec 13; Vol. 2, pp. 100032. Date of Electronic Publication: 2021 Dec 13 (Print Publication: 2022).
Publication Type: Journal Article
Journal Info: Publisher: Elsevier B.V Country of Publication: Netherlands NLM ID: 9918227371406676 Publication Model: eCollection Cited Medium: Internet ISSN: 2667-1603 (Electronic) Linking ISSN: 26671603 NLM ISO Abbreviation: BBA Adv Subsets: PubMed not MEDLINE
Database: MEDLINE Ultimate
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  Data: Increased phosphorylation of HexM improves lysosomal uptake and potential for managing GM2 gangliosidoses.
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  Data: <searchLink fieldCode="AU" term="%22Benzie+G%22">Benzie G</searchLink>; Department of Microbiology, University of Manitoba, Winnipeg, MB R3T 2N2, Canada.<br /><searchLink fieldCode="AU" term="%22Bouma+K%22">Bouma K</searchLink>; Department of Microbiology, University of Manitoba, Winnipeg, MB R3T 2N2, Canada.<br /><searchLink fieldCode="AU" term="%22Battellino+T%22">Battellino T</searchLink>; Department of Chemistry, University of Manitoba, Winnipeg R3T 2N2, Canada.<br /><searchLink fieldCode="AU" term="%22Cooper+S%22">Cooper S</searchLink>; Biochemistry and Medical Genetics, University of Manitoba, Canada.<br /><searchLink fieldCode="AU" term="%22Hemming+R%22">Hemming R</searchLink>; Biochemistry and Medical Genetics, University of Manitoba, Canada.<br /><searchLink fieldCode="AU" term="%22Kammouni+W%22">Kammouni W</searchLink>; Biochemistry and Medical Genetics, University of Manitoba, Canada.<br /><searchLink fieldCode="AU" term="%22Liu+L%22">Liu L</searchLink>; M6P Therapeutics, 20 S. Sarah St., St. Louis, MO 63018, United States.<br /><searchLink fieldCode="AU" term="%22Do+C%22">Do C</searchLink>; M6P Therapeutics, 20 S. Sarah St., St. Louis, MO 63018, United States.<br /><searchLink fieldCode="AU" term="%22Khajehpour+M%22">Khajehpour M</searchLink>; Department of Chemistry, University of Manitoba, Winnipeg R3T 2N2, Canada.<br /><searchLink fieldCode="AU" term="%22Perreault+H%22">Perreault H</searchLink>; Department of Chemistry, University of Manitoba, Winnipeg R3T 2N2, Canada.<br /><searchLink fieldCode="AU" term="%22Kornfeld+S%22">Kornfeld S</searchLink>; Washington University School of Medicine in St. Louis, Department of Biochemistry & Molecular Biophysics, United States.<br /><searchLink fieldCode="AU" term="%22Triggs-Raine+B%22">Triggs-Raine B</searchLink>; Biochemistry and Medical Genetics, University of Manitoba, Canada.<br /><searchLink fieldCode="AU" term="%22Mark+BL%22">Mark BL</searchLink>; Department of Microbiology, University of Manitoba, Winnipeg, MB R3T 2N2, Canada.
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  Data: <searchLink fieldCode="JN" term="%229918227371406676%22">BBA advances</searchLink> [BBA Adv] 2021 Dec 13; Vol. 2, pp. 100032. <i>Date of Electronic Publication: </i>2021 Dec 13 (<i>Print Publication: </i>2022).
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  Data: <i>Publisher: </i><searchLink fieldCode="PB" term="%22Elsevier+B%2EV%22">Elsevier B.V </searchLink><i>Country of Publication: </i>Netherlands <i>NLM ID: </i>9918227371406676 <i>Publication Model: </i>eCollection <i>Cited Medium: </i>Internet <i>ISSN: </i>2667-1603 (Electronic) <i>Linking ISSN: </i><searchLink fieldCode="IS" term="%2226671603%22">26671603 </searchLink><i>NLM ISO Abbreviation: </i>BBA Adv <i>Subsets: </i>PubMed not MEDLINE
PLink https://search.ebscohost.com/login.aspx?direct=true&site=eds-live&db=mdl&AN=37082581
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        Value: 10.1016/j.bbadva.2021.100032
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