Multiple Genes Core to ERAD, Macroautophagy and Lysosomal Degradation Pathways Participate in the Proteostasis Response in α1-Antitrypsin Deficiency.
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| Title: | Multiple Genes Core to ERAD, Macroautophagy and Lysosomal Degradation Pathways Participate in the Proteostasis Response in α1-Antitrypsin Deficiency. |
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| Authors: | Li J; Department of Pediatrics, Washington University School of Medicine, St. Louis, Missouri., Moretti F; Novartis Biomedical Research, Basel, Switzerland., Hidvegi T; Department of Pediatrics, Washington University School of Medicine, St. Louis, Missouri., Sviben S; Center for Cellular Imaging, Washington University School of Medicine, St. Louis, Missouri., Fitzpatrick JAJ; Center for Cellular Imaging, Washington University School of Medicine, St. Louis, Missouri; Department of Cell Biology, Washington University School of Medicine, St. Louis, Missouri; Department of Neuroscience, Washington University School of Medicine, St. Louis, Missouri., Sundaramoorthi H; Department of Pediatrics, Washington University School of Medicine, St. Louis, Missouri., Pak SC; Department of Pediatrics, Washington University School of Medicine, St. Louis, Missouri., Silverman GA; Department of Pediatrics, Washington University School of Medicine, St. Louis, Missouri., Knapp B; Novartis Biomedical Research, Basel, Switzerland., Filipuzzi I; Novartis Biomedical Research, Basel, Switzerland., Alford J; Novartis Biomedical Research, Cambridge, Massachusetts., Reece-Hoyes J; Novartis Biomedical Research, Cambridge, Massachusetts., Nigsch F; Novartis Biomedical Research, Basel, Switzerland., Murphy LO; Novartis Biomedical Research, Cambridge, Massachusetts., Nyfeler B; Novartis Biomedical Research, Basel, Switzerland., Perlmutter DH; Department of Pediatrics, Washington University School of Medicine, St. Louis, Missouri. Electronic address: perlmutterd@wustl.edu. |
| Source: | Cellular and molecular gastroenterology and hepatology [Cell Mol Gastroenterol Hepatol] 2024; Vol. 17 (6), pp. 1007-1024. Date of Electronic Publication: 2024 Feb 07. |
| Publication Type: | Journal Article |
| Journal Info: | Publisher: American Gastroenterological Association Country of Publication: United States NLM ID: 101648302 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 2352-345X (Electronic) Linking ISSN: 2352345X NLM ISO Abbreviation: Cell Mol Gastroenterol Hepatol Subsets: MEDLINE |
| Database: | MEDLINE Ultimate |
| FullText | Text: Availability: 0 |
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| Header | DbId: mdl DbLabel: MEDLINE Ultimate An: 38336172 AccessLevel: 2 PubType: Academic Journal PubTypeId: academicJournal PreciseRelevancyScore: 0 |
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| Items | – Name: Title Label: Title Group: Ti Data: Multiple Genes Core to ERAD, Macroautophagy and Lysosomal Degradation Pathways Participate in the Proteostasis Response in α1-Antitrypsin Deficiency. – Name: Author Label: Authors Group: Au Data: <searchLink fieldCode="AU" term="%22Li+J%22">Li J</searchLink>; Department of Pediatrics, Washington University School of Medicine, St. Louis, Missouri.<br /><searchLink fieldCode="AU" term="%22Moretti+F%22">Moretti F</searchLink>; Novartis Biomedical Research, Basel, Switzerland.<br /><searchLink fieldCode="AU" term="%22Hidvegi+T%22">Hidvegi T</searchLink>; Department of Pediatrics, Washington University School of Medicine, St. Louis, Missouri.<br /><searchLink fieldCode="AU" term="%22Sviben+S%22">Sviben S</searchLink>; Center for Cellular Imaging, Washington University School of Medicine, St. Louis, Missouri.<br /><searchLink fieldCode="AU" term="%22Fitzpatrick+JAJ%22">Fitzpatrick JAJ</searchLink>; Center for Cellular Imaging, Washington University School of Medicine, St. Louis, Missouri; Department of Cell Biology, Washington University School of Medicine, St. Louis, Missouri; Department of Neuroscience, Washington University School of Medicine, St. Louis, Missouri.<br /><searchLink fieldCode="AU" term="%22Sundaramoorthi+H%22">Sundaramoorthi H</searchLink>; Department of Pediatrics, Washington University School of Medicine, St. Louis, Missouri.<br /><searchLink fieldCode="AU" term="%22Pak+SC%22">Pak SC</searchLink>; Department of Pediatrics, Washington University School of Medicine, St. Louis, Missouri.<br /><searchLink fieldCode="AU" term="%22Silverman+GA%22">Silverman GA</searchLink>; Department of Pediatrics, Washington University School of Medicine, St. Louis, Missouri.<br /><searchLink fieldCode="AU" term="%22Knapp+B%22">Knapp B</searchLink>; Novartis Biomedical Research, Basel, Switzerland.<br /><searchLink fieldCode="AU" term="%22Filipuzzi+I%22">Filipuzzi I</searchLink>; Novartis Biomedical Research, Basel, Switzerland.<br /><searchLink fieldCode="AU" term="%22Alford+J%22">Alford J</searchLink>; Novartis Biomedical Research, Cambridge, Massachusetts.<br /><searchLink fieldCode="AU" term="%22Reece-Hoyes+J%22">Reece-Hoyes J</searchLink>; Novartis Biomedical Research, Cambridge, Massachusetts.<br /><searchLink fieldCode="AU" term="%22Nigsch+F%22">Nigsch F</searchLink>; Novartis Biomedical Research, Basel, Switzerland.<br /><searchLink fieldCode="AU" term="%22Murphy+LO%22">Murphy LO</searchLink>; Novartis Biomedical Research, Cambridge, Massachusetts.<br /><searchLink fieldCode="AU" term="%22Nyfeler+B%22">Nyfeler B</searchLink>; Novartis Biomedical Research, Basel, Switzerland.<br /><searchLink fieldCode="AU" term="%22Perlmutter+DH%22">Perlmutter DH</searchLink>; Department of Pediatrics, Washington University School of Medicine, St. Louis, Missouri. Electronic address: perlmutterd@wustl.edu. – Name: TitleSource Label: Source Group: Src Data: <searchLink fieldCode="JN" term="%22101648302%22">Cellular and molecular gastroenterology and hepatology</searchLink> [Cell Mol Gastroenterol Hepatol] 2024; Vol. 17 (6), pp. 1007-1024. <i>Date of Electronic Publication: </i>2024 Feb 07. – Name: TypePub Label: Publication Type Group: TypPub Data: Journal Article – Name: TitleSource Label: Journal Info Group: Src Data: <i>Publisher: </i><searchLink fieldCode="PB" term="%22American+Gastroenterological+Association%22">American Gastroenterological Association </searchLink><i>Country of Publication: </i>United States <i>NLM ID: </i>101648302 <i>Publication Model: </i>Print-Electronic <i>Cited Medium: </i>Internet <i>ISSN: </i>2352-345X (Electronic) <i>Linking ISSN: </i><searchLink fieldCode="IS" term="%222352345X%22">2352345X </searchLink><i>NLM ISO Abbreviation: </i>Cell Mol Gastroenterol Hepatol <i>Subsets: </i>MEDLINE |
| PLink | https://search.ebscohost.com/login.aspx?direct=true&site=eds-live&db=mdl&AN=38336172 |
| RecordInfo | BibRecord: BibEntity: Identifiers: – Type: doi Value: 10.1016/j.jcmgh.2024.02.006 Languages: – Code: eng Text: English PhysicalDescription: Pagination: StartPage: 1007 Titles: – TitleFull: Multiple Genes Core to ERAD, Macroautophagy and Lysosomal Degradation Pathways Participate in the Proteostasis Response in α1-Antitrypsin Deficiency. Type: main BibRelationships: HasContributorRelationships: – PersonEntity: Name: NameFull: Li J – PersonEntity: Name: NameFull: Moretti F – PersonEntity: Name: NameFull: Hidvegi T – PersonEntity: Name: NameFull: Sviben S – PersonEntity: Name: NameFull: Fitzpatrick JAJ – PersonEntity: Name: NameFull: Sundaramoorthi H – PersonEntity: Name: NameFull: Pak SC – PersonEntity: Name: NameFull: Silverman GA – PersonEntity: Name: NameFull: Knapp B – PersonEntity: Name: NameFull: Filipuzzi I – PersonEntity: Name: NameFull: Alford J – PersonEntity: Name: NameFull: Reece-Hoyes J – PersonEntity: Name: NameFull: Nigsch F – PersonEntity: Name: NameFull: Murphy LO – PersonEntity: Name: NameFull: Nyfeler B – PersonEntity: Name: NameFull: Perlmutter DH IsPartOfRelationships: – BibEntity: Dates: – D: 01 M: 01 Text: 2024 Type: published Y: 2024 Identifiers: – Type: issn-electronic Value: 2352-345X Numbering: – Type: volume Value: 17 – Type: issue Value: 6 Titles: – TitleFull: Cellular and molecular gastroenterology and hepatology Type: main |
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