Multiple Genes Core to ERAD, Macroautophagy and Lysosomal Degradation Pathways Participate in the Proteostasis Response in α1-Antitrypsin Deficiency.

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Title: Multiple Genes Core to ERAD, Macroautophagy and Lysosomal Degradation Pathways Participate in the Proteostasis Response in α1-Antitrypsin Deficiency.
Authors: Li J; Department of Pediatrics, Washington University School of Medicine, St. Louis, Missouri., Moretti F; Novartis Biomedical Research, Basel, Switzerland., Hidvegi T; Department of Pediatrics, Washington University School of Medicine, St. Louis, Missouri., Sviben S; Center for Cellular Imaging, Washington University School of Medicine, St. Louis, Missouri., Fitzpatrick JAJ; Center for Cellular Imaging, Washington University School of Medicine, St. Louis, Missouri; Department of Cell Biology, Washington University School of Medicine, St. Louis, Missouri; Department of Neuroscience, Washington University School of Medicine, St. Louis, Missouri., Sundaramoorthi H; Department of Pediatrics, Washington University School of Medicine, St. Louis, Missouri., Pak SC; Department of Pediatrics, Washington University School of Medicine, St. Louis, Missouri., Silverman GA; Department of Pediatrics, Washington University School of Medicine, St. Louis, Missouri., Knapp B; Novartis Biomedical Research, Basel, Switzerland., Filipuzzi I; Novartis Biomedical Research, Basel, Switzerland., Alford J; Novartis Biomedical Research, Cambridge, Massachusetts., Reece-Hoyes J; Novartis Biomedical Research, Cambridge, Massachusetts., Nigsch F; Novartis Biomedical Research, Basel, Switzerland., Murphy LO; Novartis Biomedical Research, Cambridge, Massachusetts., Nyfeler B; Novartis Biomedical Research, Basel, Switzerland., Perlmutter DH; Department of Pediatrics, Washington University School of Medicine, St. Louis, Missouri. Electronic address: perlmutterd@wustl.edu.
Source: Cellular and molecular gastroenterology and hepatology [Cell Mol Gastroenterol Hepatol] 2024; Vol. 17 (6), pp. 1007-1024. Date of Electronic Publication: 2024 Feb 07.
Publication Type: Journal Article
Journal Info: Publisher: American Gastroenterological Association Country of Publication: United States NLM ID: 101648302 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 2352-345X (Electronic) Linking ISSN: 2352345X NLM ISO Abbreviation: Cell Mol Gastroenterol Hepatol Subsets: MEDLINE
Database: MEDLINE Ultimate
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  Data: Multiple Genes Core to ERAD, Macroautophagy and Lysosomal Degradation Pathways Participate in the Proteostasis Response in α1-Antitrypsin Deficiency.
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  Data: <searchLink fieldCode="AU" term="%22Li+J%22">Li J</searchLink>; Department of Pediatrics, Washington University School of Medicine, St. Louis, Missouri.<br /><searchLink fieldCode="AU" term="%22Moretti+F%22">Moretti F</searchLink>; Novartis Biomedical Research, Basel, Switzerland.<br /><searchLink fieldCode="AU" term="%22Hidvegi+T%22">Hidvegi T</searchLink>; Department of Pediatrics, Washington University School of Medicine, St. Louis, Missouri.<br /><searchLink fieldCode="AU" term="%22Sviben+S%22">Sviben S</searchLink>; Center for Cellular Imaging, Washington University School of Medicine, St. Louis, Missouri.<br /><searchLink fieldCode="AU" term="%22Fitzpatrick+JAJ%22">Fitzpatrick JAJ</searchLink>; Center for Cellular Imaging, Washington University School of Medicine, St. Louis, Missouri; Department of Cell Biology, Washington University School of Medicine, St. Louis, Missouri; Department of Neuroscience, Washington University School of Medicine, St. Louis, Missouri.<br /><searchLink fieldCode="AU" term="%22Sundaramoorthi+H%22">Sundaramoorthi H</searchLink>; Department of Pediatrics, Washington University School of Medicine, St. Louis, Missouri.<br /><searchLink fieldCode="AU" term="%22Pak+SC%22">Pak SC</searchLink>; Department of Pediatrics, Washington University School of Medicine, St. Louis, Missouri.<br /><searchLink fieldCode="AU" term="%22Silverman+GA%22">Silverman GA</searchLink>; Department of Pediatrics, Washington University School of Medicine, St. Louis, Missouri.<br /><searchLink fieldCode="AU" term="%22Knapp+B%22">Knapp B</searchLink>; Novartis Biomedical Research, Basel, Switzerland.<br /><searchLink fieldCode="AU" term="%22Filipuzzi+I%22">Filipuzzi I</searchLink>; Novartis Biomedical Research, Basel, Switzerland.<br /><searchLink fieldCode="AU" term="%22Alford+J%22">Alford J</searchLink>; Novartis Biomedical Research, Cambridge, Massachusetts.<br /><searchLink fieldCode="AU" term="%22Reece-Hoyes+J%22">Reece-Hoyes J</searchLink>; Novartis Biomedical Research, Cambridge, Massachusetts.<br /><searchLink fieldCode="AU" term="%22Nigsch+F%22">Nigsch F</searchLink>; Novartis Biomedical Research, Basel, Switzerland.<br /><searchLink fieldCode="AU" term="%22Murphy+LO%22">Murphy LO</searchLink>; Novartis Biomedical Research, Cambridge, Massachusetts.<br /><searchLink fieldCode="AU" term="%22Nyfeler+B%22">Nyfeler B</searchLink>; Novartis Biomedical Research, Basel, Switzerland.<br /><searchLink fieldCode="AU" term="%22Perlmutter+DH%22">Perlmutter DH</searchLink>; Department of Pediatrics, Washington University School of Medicine, St. Louis, Missouri. Electronic address: perlmutterd@wustl.edu.
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  Data: <searchLink fieldCode="JN" term="%22101648302%22">Cellular and molecular gastroenterology and hepatology</searchLink> [Cell Mol Gastroenterol Hepatol] 2024; Vol. 17 (6), pp. 1007-1024. <i>Date of Electronic Publication: </i>2024 Feb 07.
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