Decreasing ganglioside synthesis delays motor and cognitive symptom onset in Spg11 knockout mice.

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Title: Decreasing ganglioside synthesis delays motor and cognitive symptom onset in Spg11 knockout mice.
Authors: Fortier M; Sorbonne Université, Paris Brain Institute (ICM Institut du Cerveau), INSERM U1127, CNRS UMR 7225, Assistance Publique-Hôpitaux de Paris (AP-HP), Paris, France., Cauhapé M; Sorbonne Université, Paris Brain Institute (ICM Institut du Cerveau), INSERM U1127, CNRS UMR 7225, Assistance Publique-Hôpitaux de Paris (AP-HP), Paris, France., Buono S; Dynacure SA (now Flamingo Therapeutics NV), Illkirch, France., Becker J; Dynacure SA (now Flamingo Therapeutics NV), Illkirch, France., Menuet A; Dynacure SA (now Flamingo Therapeutics NV), Illkirch, France., Branchu J; Sorbonne Université, Paris Brain Institute (ICM Institut du Cerveau), INSERM U1127, CNRS UMR 7225, Assistance Publique-Hôpitaux de Paris (AP-HP), Paris, France., Ricca I; Molecular Medicine, IRCCS Fondazione Stella Maris, 56128 Pisa, Italy., Mero S; Molecular Medicine, IRCCS Fondazione Stella Maris, 56128 Pisa, Italy., Dorgham K; Sorbonne Université, INSERM, Centre d'Immunologie et des Maladies Infectieuses-Paris (CIMI-Paris), Paris, France., El Hachimi KH; Sorbonne Université, Paris Brain Institute (ICM Institut du Cerveau), INSERM U1127, CNRS UMR 7225, Assistance Publique-Hôpitaux de Paris (AP-HP), Paris, France; EPHE, PSL Research University, Paris, France., Dobrenis K; Dominick P. Purpura Department of Neuroscience, Albert Einstein College of Medicine, Bronx, NY 10461, USA., Colsch B; Université Paris-Saclay, CEA, INRAE, Département Médicaments et Technologies pour la Santé, MetaboHUB, Gif sur Yvette, France., Samaroo D; Sorbonne Université, Paris Brain Institute (ICM Institut du Cerveau), INSERM U1127, CNRS UMR 7225, Assistance Publique-Hôpitaux de Paris (AP-HP), Paris, France., Devaux M; Sorbonne Université, Paris Brain Institute (ICM Institut du Cerveau), INSERM U1127, CNRS UMR 7225, Assistance Publique-Hôpitaux de Paris (AP-HP), Paris, France., Durr A; Sorbonne Université, Paris Brain Institute (ICM Institut du Cerveau), INSERM U1127, CNRS UMR 7225, Assistance Publique-Hôpitaux de Paris (AP-HP), Paris, France., Stevanin G; Sorbonne Université, Paris Brain Institute (ICM Institut du Cerveau), INSERM U1127, CNRS UMR 7225, Assistance Publique-Hôpitaux de Paris (AP-HP), Paris, France; EPHE, PSL Research University, Paris, France; University of Bordeaux, CNRS, INCIA, UMR 5287, NRGen Team, Bordeaux, France., Santorelli FM; Molecular Medicine, IRCCS Fondazione Stella Maris, 56128 Pisa, Italy., Colombo S; Dynacure SA (now Flamingo Therapeutics NV), Illkirch, France., Cowling B; Dynacure SA (now Flamingo Therapeutics NV), Illkirch, France., Darios F; Sorbonne Université, Paris Brain Institute (ICM Institut du Cerveau), INSERM U1127, CNRS UMR 7225, Assistance Publique-Hôpitaux de Paris (AP-HP), Paris, France. Electronic address: frederic.darios@icm-institute.org.
Source: Neurobiology of disease [Neurobiol Dis] 2024 Sep; Vol. 199, pp. 106564. Date of Electronic Publication: 2024 Jun 12.
Publication Type: Journal Article; Research Support, Non-U.S. Gov't
Journal Info: Publisher: Academic Press Country of Publication: United States NLM ID: 9500169 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1095-953X (Electronic) Linking ISSN: 09699961 NLM ISO Abbreviation: Neurobiol Dis Subsets: MEDLINE
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  Data: Decreasing ganglioside synthesis delays motor and cognitive symptom onset in Spg11 knockout mice.
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  Data: <searchLink fieldCode="AU" term="%22Fortier+M%22">Fortier M</searchLink>; Sorbonne Université, Paris Brain Institute (ICM Institut du Cerveau), INSERM U1127, CNRS UMR 7225, Assistance Publique-Hôpitaux de Paris (AP-HP), Paris, France.<br /><searchLink fieldCode="AU" term="%22Cauhapé+M%22">Cauhapé M</searchLink>; Sorbonne Université, Paris Brain Institute (ICM Institut du Cerveau), INSERM U1127, CNRS UMR 7225, Assistance Publique-Hôpitaux de Paris (AP-HP), Paris, France.<br /><searchLink fieldCode="AU" term="%22Buono+S%22">Buono S</searchLink>; Dynacure SA (now Flamingo Therapeutics NV), Illkirch, France.<br /><searchLink fieldCode="AU" term="%22Becker+J%22">Becker J</searchLink>; Dynacure SA (now Flamingo Therapeutics NV), Illkirch, France.<br /><searchLink fieldCode="AU" term="%22Menuet+A%22">Menuet A</searchLink>; Dynacure SA (now Flamingo Therapeutics NV), Illkirch, France.<br /><searchLink fieldCode="AU" term="%22Branchu+J%22">Branchu J</searchLink>; Sorbonne Université, Paris Brain Institute (ICM Institut du Cerveau), INSERM U1127, CNRS UMR 7225, Assistance Publique-Hôpitaux de Paris (AP-HP), Paris, France.<br /><searchLink fieldCode="AU" term="%22Ricca+I%22">Ricca I</searchLink>; Molecular Medicine, IRCCS Fondazione Stella Maris, 56128 Pisa, Italy.<br /><searchLink fieldCode="AU" term="%22Mero+S%22">Mero S</searchLink>; Molecular Medicine, IRCCS Fondazione Stella Maris, 56128 Pisa, Italy.<br /><searchLink fieldCode="AU" term="%22Dorgham+K%22">Dorgham K</searchLink>; Sorbonne Université, INSERM, Centre d'Immunologie et des Maladies Infectieuses-Paris (CIMI-Paris), Paris, France.<br /><searchLink fieldCode="AU" term="%22El+Hachimi+KH%22">El Hachimi KH</searchLink>; Sorbonne Université, Paris Brain Institute (ICM Institut du Cerveau), INSERM U1127, CNRS UMR 7225, Assistance Publique-Hôpitaux de Paris (AP-HP), Paris, France; EPHE, PSL Research University, Paris, France.<br /><searchLink fieldCode="AU" term="%22Dobrenis+K%22">Dobrenis K</searchLink>; Dominick P. Purpura Department of Neuroscience, Albert Einstein College of Medicine, Bronx, NY 10461, USA.<br /><searchLink fieldCode="AU" term="%22Colsch+B%22">Colsch B</searchLink>; Université Paris-Saclay, CEA, INRAE, Département Médicaments et Technologies pour la Santé, MetaboHUB, Gif sur Yvette, France.<br /><searchLink fieldCode="AU" term="%22Samaroo+D%22">Samaroo D</searchLink>; Sorbonne Université, Paris Brain Institute (ICM Institut du Cerveau), INSERM U1127, CNRS UMR 7225, Assistance Publique-Hôpitaux de Paris (AP-HP), Paris, France.<br /><searchLink fieldCode="AU" term="%22Devaux+M%22">Devaux M</searchLink>; Sorbonne Université, Paris Brain Institute (ICM Institut du Cerveau), INSERM U1127, CNRS UMR 7225, Assistance Publique-Hôpitaux de Paris (AP-HP), Paris, France.<br /><searchLink fieldCode="AU" term="%22Durr+A%22">Durr A</searchLink>; Sorbonne Université, Paris Brain Institute (ICM Institut du Cerveau), INSERM U1127, CNRS UMR 7225, Assistance Publique-Hôpitaux de Paris (AP-HP), Paris, France.<br /><searchLink fieldCode="AU" term="%22Stevanin+G%22">Stevanin G</searchLink>; Sorbonne Université, Paris Brain Institute (ICM Institut du Cerveau), INSERM U1127, CNRS UMR 7225, Assistance Publique-Hôpitaux de Paris (AP-HP), Paris, France; EPHE, PSL Research University, Paris, France; University of Bordeaux, CNRS, INCIA, UMR 5287, NRGen Team, Bordeaux, France.<br /><searchLink fieldCode="AU" term="%22Santorelli+FM%22">Santorelli FM</searchLink>; Molecular Medicine, IRCCS Fondazione Stella Maris, 56128 Pisa, Italy.<br /><searchLink fieldCode="AU" term="%22Colombo+S%22">Colombo S</searchLink>; Dynacure SA (now Flamingo Therapeutics NV), Illkirch, France.<br /><searchLink fieldCode="AU" term="%22Cowling+B%22">Cowling B</searchLink>; Dynacure SA (now Flamingo Therapeutics NV), Illkirch, France.<br /><searchLink fieldCode="AU" term="%22Darios+F%22">Darios F</searchLink>; Sorbonne Université, Paris Brain Institute (ICM Institut du Cerveau), INSERM U1127, CNRS UMR 7225, Assistance Publique-Hôpitaux de Paris (AP-HP), Paris, France. Electronic address: frederic.darios@icm-institute.org.
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  Data: <searchLink fieldCode="JN" term="%229500169%22">Neurobiology of disease</searchLink> [Neurobiol Dis] 2024 Sep; Vol. 199, pp. 106564. <i>Date of Electronic Publication: </i>2024 Jun 12.
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  Data: <i>Publisher: </i><searchLink fieldCode="PB" term="%22Academic+Press%22">Academic Press </searchLink><i>Country of Publication: </i>United States <i>NLM ID: </i>9500169 <i>Publication Model: </i>Print-Electronic <i>Cited Medium: </i>Internet <i>ISSN: </i>1095-953X (Electronic) <i>Linking ISSN: </i><searchLink fieldCode="IS" term="%2209699961%22">09699961 </searchLink><i>NLM ISO Abbreviation: </i>Neurobiol Dis <i>Subsets: </i>MEDLINE
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