Associations between respiratory pathogens and lung function in primary ciliary dyskinesia: cross-sectional analysis from the PROVALF-PCD cohort.

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Title: Associations between respiratory pathogens and lung function in primary ciliary dyskinesia: cross-sectional analysis from the PROVALF-PCD cohort.
Authors: Rubbo B; Clinical and Experimental Sciences, University of Southampton Faculty of Medicine, Southampton, UK.; Primary Ciliary Dyskinesia Centre, University Hospital Southampton NHS Foundation Trust, Southampton, UK., Kant A; Clinical and Experimental Sciences, University of Southampton Faculty of Medicine, Southampton, UK.; Primary Ciliary Dyskinesia Centre, University Hospital Southampton NHS Foundation Trust, Southampton, UK., Zhang K; Clinical and Experimental Sciences, University of Southampton Faculty of Medicine, Southampton, UK.; Primary Ciliary Dyskinesia Centre, University Hospital Southampton NHS Foundation Trust, Southampton, UK., Allegorico A; Respiratory and Cystic Fibrosis Unit, Academic Pediatric Department, Bambino Gesù Children Hospital, IRCCS, Rome, Italy., Basilicata S; Department of Translational Medical Sciences, Pediatric Pulmonology, Federico II University, Naples, Italy., Boon M; Department of Pediatrics, University Hospital Leuven, Leuven, Belgium., Borrelli M; Department of Translational Medical Sciences, Pediatric Pulmonology, Federico II University, Naples, Italy., Calogero C; Azienda Ospedaliero Universitaria Ospedale Pediatrico Meyer, Florence, Italy., Carr SB; Royal Brompton and Harefield NHS Foundation Trust, Department of Paediatrics, Primary Ciliary Dyskinesia Centre, London, UK., Carroll M; Primary Ciliary Dyskinesia Centre, University Hospital Southampton NHS Foundation Trust, Southampton, UK., Constant C; Department of Pediatrics, Hospital de Santa Maria, Centro Hospitalar Universitário Lisboa Norte and Faculty of Medicine, University of Lisbon, Lisbon, Portugal., Castillo Corullón S; FE Pediatría y Neumología Infantil, Unidad de Neumología Infantil y Fibrosis Quística, Hospital Clínico de Valencia, Valencia, Spain., Corvol H; AP-HP, Sorbonne Université, Unité d'Exploration Fonctionnelle Respiratoire, Hôpital Armand-Trousseau, and Sorbonne Université, INSERM U938, Paris, France., Cutrera R; Respiratory and Cystic Fibrosis Unit, Academic Pediatric Department, Bambino Gesù Children Hospital, IRCCS, Rome, Italy., Dillenhöfer S; Department of Paediatric Pulmonology, University Children's Hospital, Ruhr University Bochum, Katholisches Klinikum Bochum, Bochum, Germany.; Children's Hospital and Research Institute, Marienhospital Wesel, Wesel, Germany., Emiralioglu N; Department of Pediatric Pulmonology, Hacettepe University Faculty of Medicine, Ankara, Turkey., Eralp E; Department of Pediatric Pulmonology, Marmara Universitesi, Istanbul, Turkey., Eryilmaz Polat S; Department of Pediatrics, Division of Pediatric Pulmonology, Ankara City Hospital, Ankara, Turkey., Gardner L; Royal Brompton and Harefield NHS Foundation Trust, Department of Paediatrics, Primary Ciliary Dyskinesia Centre, London, UK., Gokdemir Y; Department of Pediatric Pulmonology, Marmara Universitesi, Istanbul, Turkey., Harris A; Clinical and Experimental Sciences, University of Southampton Faculty of Medicine, Southampton, UK.; Primary Ciliary Dyskinesia Centre, University Hospital Southampton NHS Foundation Trust, Southampton, UK., Hogg C; Royal Brompton and Harefield NHS Foundation Trust, Department of Paediatrics, Primary Ciliary Dyskinesia Centre, London, UK., Karadag B; Department of Pediatric Pulmonology, Marmara Universitesi, Istanbul, Turkey., Kobbernagel H; Danish PCD Centre, Danish Paediatric Pulmonary Service, Department of Paediatrics and Adolescent Medicine, Copenhagen University Hospital, Rigshospitalet, Copenhagen, Denmark.; Department of Clinical Medicine, Faculty of Health and Medical Sciences, University of Copenhagen, Copenhagen, Denmark., Koerner-Rettberg C; Department of Paediatric Pulmonology, University Children's Hospital, Ruhr University Bochum, Katholisches Klinikum Bochum, Bochum, Germany.; Children's Hospital and Research Institute, Marienhospital Wesel, Wesel, Germany., Kouis P; Medical School, University of Cyprus, Nicosia, Cyprus., Lorent N; Department of Respiratory Diseases, University Hospitals Leuven, Leuven, Belgium.; Department of CHROMETA, Laboratory for Respiratory Diseases and Thoracic Surgery, KU Leuven, Leuven, Belgium., Marcou M; Medical School, University of Cyprus, Nicosia, Cyprus., Mathin JK; Danish PCD Centre, Danish Paediatric Pulmonary Service, Department of Paediatrics and Adolescent Medicine, Copenhagen University Hospital, Rigshospitalet, Copenhagen, Denmark.; Department of Clinical Medicine, Faculty of Health and Medical Sciences, University of Copenhagen, Copenhagen, Denmark., Martinu V; Department of Paediatrics, Charles University, 2nd Faculty of Medicine, University Hospital in Motol, Prague, Czech Republic., Moreno-Galdó A; Hospital Vall d'Hebron, Neumología Infantil, Barcelona, Spain., Morgan L; Concord Hospital, Concord Clinical School, University of Sydney, Department of Respiratory Medicine, Sydney, Australia., Nielsen KG; Danish PCD Centre, Danish Paediatric Pulmonary Service, Department of Paediatrics and Adolescent Medicine, Copenhagen University Hospital, Rigshospitalet, Copenhagen, Denmark.; Department of Clinical Medicine, Faculty of Health and Medical Sciences, University of Copenhagen, Copenhagen, Denmark., Omran H; Department of General Pediatrics, University Hospital Muenster, Muenster, Germany., Ozcelik U; Department of Pediatric Pulmonology, Hacettepe University Faculty of Medicine, Ankara, Turkey., Pohunek P; Department of Paediatrics, Charles University, 2nd Faculty of Medicine, University Hospital in Motol, Prague, Czech Republic., Raidt J; Department of General Pediatrics, University Hospital Muenster, Muenster, Germany., Robinson P; Royal Children's Hospital, Respiratory Medicine, Melbourne, Australia.; Faculty of Medicine Dentistry and Health Sciences, Paediatrics, University of Melbourne, Melbourne, Australia., Rovira-Amigo S; Hospital Vall d'Hebron, Neumología Infantil, Barcelona, Spain., Santamaria F; Department of Translational Medical Sciences, Pediatric Pulmonology, Federico II University, Naples, Italy., Schlegtendal A; Department of Paediatric Pulmonology, University Children's Hospital, Ruhr University Bochum, Katholisches Klinikum Bochum, Bochum, Germany.; Children's Hospital and Research Institute, Marienhospital Wesel, Wesel, Germany., Tamalet A; AP-HP, Sorbonne Université, Unité d'Exploration Fonctionnelle Respiratoire, Hôpital Armand-Trousseau, and Sorbonne Université, INSERM U938, Paris, France., Thouvenin G; AP-HP, Sorbonne Université, Unité d'Exploration Fonctionnelle Respiratoire, Hôpital Armand-Trousseau, and Sorbonne Université, INSERM U938, Paris, France., Ullmann N; Respiratory and Cystic Fibrosis Unit, Academic Pediatric Department, Bambino Gesù Children Hospital, IRCCS, Rome, Italy., Walker W; Primary Ciliary Dyskinesia Centre, University Hospital Southampton NHS Foundation Trust, Southampton, UK., Yiallouros P; Medical School, University of Cyprus, Nicosia, Cyprus., Kuehni CE; Institute of Social and Preventive Medicine, University of Bern, Bern, Switzerland.; Division of Paediatric Respiratory Medicine and Allergology, Department of Paediatrics, Inselspital, University Hospital, University of Bern, Bern, Switzerland., Latzin P; Institute of Social and Preventive Medicine, University of Bern, Bern, Switzerland.; Division of Paediatric Respiratory Medicine and Allergology, Department of Paediatrics, Inselspital, University Hospital, University of Bern, Bern, Switzerland., Beydon N; AP-HP, Sorbonne Université, Unité d'Exploration Fonctionnelle Respiratoire, Hôpital Armand-Trousseau, and Sorbonne Université, INSERM U938, Paris, France., Lucas JS; Clinical and Experimental Sciences, University of Southampton Faculty of Medicine, Southampton, UK.; Primary Ciliary Dyskinesia Centre, University Hospital Southampton NHS Foundation Trust, Southampton, UK.
Source: ERJ open research [ERJ Open Res] 2024 Sep 30; Vol. 10 (5). Date of Electronic Publication: 2024 Sep 30 (Print Publication: 2024).
Publication Type: Journal Article
Journal Info: Publisher: European Respiratory Society Country of Publication: England NLM ID: 101671641 Publication Model: eCollection Cited Medium: Print ISSN: 2312-0541 (Print) Linking ISSN: 23120541 NLM ISO Abbreviation: ERJ Open Res Subsets: PubMed not MEDLINE
Database: MEDLINE Ultimate
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PubType: Academic Journal
PubTypeId: academicJournal
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  Data: Associations between respiratory pathogens and lung function in primary ciliary dyskinesia: cross-sectional analysis from the PROVALF-PCD cohort.
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  Data: <searchLink fieldCode="AU" term="%22Rubbo+B%22">Rubbo B</searchLink>; Clinical and Experimental Sciences, University of Southampton Faculty of Medicine, Southampton, UK.; Primary Ciliary Dyskinesia Centre, University Hospital Southampton NHS Foundation Trust, Southampton, UK.<br /><searchLink fieldCode="AU" term="%22Kant+A%22">Kant A</searchLink>; Clinical and Experimental Sciences, University of Southampton Faculty of Medicine, Southampton, UK.; Primary Ciliary Dyskinesia Centre, University Hospital Southampton NHS Foundation Trust, Southampton, UK.<br /><searchLink fieldCode="AU" term="%22Zhang+K%22">Zhang K</searchLink>; Clinical and Experimental Sciences, University of Southampton Faculty of Medicine, Southampton, UK.; Primary Ciliary Dyskinesia Centre, University Hospital Southampton NHS Foundation Trust, Southampton, UK.<br /><searchLink fieldCode="AU" term="%22Allegorico+A%22">Allegorico A</searchLink>; Respiratory and Cystic Fibrosis Unit, Academic Pediatric Department, Bambino Gesù Children Hospital, IRCCS, Rome, Italy.<br /><searchLink fieldCode="AU" term="%22Basilicata+S%22">Basilicata S</searchLink>; Department of Translational Medical Sciences, Pediatric Pulmonology, Federico II University, Naples, Italy.<br /><searchLink fieldCode="AU" term="%22Boon+M%22">Boon M</searchLink>; Department of Pediatrics, University Hospital Leuven, Leuven, Belgium.<br /><searchLink fieldCode="AU" term="%22Borrelli+M%22">Borrelli M</searchLink>; Department of Translational Medical Sciences, Pediatric Pulmonology, Federico II University, Naples, Italy.<br /><searchLink fieldCode="AU" term="%22Calogero+C%22">Calogero C</searchLink>; Azienda Ospedaliero Universitaria Ospedale Pediatrico Meyer, Florence, Italy.<br /><searchLink fieldCode="AU" term="%22Carr+SB%22">Carr SB</searchLink>; Royal Brompton and Harefield NHS Foundation Trust, Department of Paediatrics, Primary Ciliary Dyskinesia Centre, London, UK.<br /><searchLink fieldCode="AU" term="%22Carroll+M%22">Carroll M</searchLink>; Primary Ciliary Dyskinesia Centre, University Hospital Southampton NHS Foundation Trust, Southampton, UK.<br /><searchLink fieldCode="AU" term="%22Constant+C%22">Constant C</searchLink>; Department of Pediatrics, Hospital de Santa Maria, Centro Hospitalar Universitário Lisboa Norte and Faculty of Medicine, University of Lisbon, Lisbon, Portugal.<br /><searchLink fieldCode="AU" term="%22Castillo+Corullón+S%22">Castillo Corullón S</searchLink>; FE Pediatría y Neumología Infantil, Unidad de Neumología Infantil y Fibrosis Quística, Hospital Clínico de Valencia, Valencia, Spain.<br /><searchLink fieldCode="AU" term="%22Corvol+H%22">Corvol H</searchLink>; AP-HP, Sorbonne Université, Unité d'Exploration Fonctionnelle Respiratoire, Hôpital Armand-Trousseau, and Sorbonne Université, INSERM U938, Paris, France.<br /><searchLink fieldCode="AU" term="%22Cutrera+R%22">Cutrera R</searchLink>; Respiratory and Cystic Fibrosis Unit, Academic Pediatric Department, Bambino Gesù Children Hospital, IRCCS, Rome, Italy.<br /><searchLink fieldCode="AU" term="%22Dillenhöfer+S%22">Dillenhöfer S</searchLink>; Department of Paediatric Pulmonology, University Children's Hospital, Ruhr University Bochum, Katholisches Klinikum Bochum, Bochum, Germany.; Children's Hospital and Research Institute, Marienhospital Wesel, Wesel, Germany.<br /><searchLink fieldCode="AU" term="%22Emiralioglu+N%22">Emiralioglu N</searchLink>; Department of Pediatric Pulmonology, Hacettepe University Faculty of Medicine, Ankara, Turkey.<br /><searchLink fieldCode="AU" term="%22Eralp+E%22">Eralp E</searchLink>; Department of Pediatric Pulmonology, Marmara Universitesi, Istanbul, Turkey.<br /><searchLink fieldCode="AU" term="%22Eryilmaz+Polat+S%22">Eryilmaz Polat S</searchLink>; Department of Pediatrics, Division of Pediatric Pulmonology, Ankara City Hospital, Ankara, Turkey.<br /><searchLink fieldCode="AU" term="%22Gardner+L%22">Gardner L</searchLink>; Royal Brompton and Harefield NHS Foundation Trust, Department of Paediatrics, Primary Ciliary Dyskinesia Centre, London, UK.<br /><searchLink fieldCode="AU" term="%22Gokdemir+Y%22">Gokdemir Y</searchLink>; Department of Pediatric Pulmonology, Marmara Universitesi, Istanbul, Turkey.<br /><searchLink fieldCode="AU" term="%22Harris+A%22">Harris A</searchLink>; Clinical and Experimental Sciences, University of Southampton Faculty of Medicine, Southampton, UK.; Primary Ciliary Dyskinesia Centre, University Hospital Southampton NHS Foundation Trust, Southampton, UK.<br /><searchLink fieldCode="AU" term="%22Hogg+C%22">Hogg C</searchLink>; Royal Brompton and Harefield NHS Foundation Trust, Department of Paediatrics, Primary Ciliary Dyskinesia Centre, London, UK.<br /><searchLink fieldCode="AU" term="%22Karadag+B%22">Karadag B</searchLink>; Department of Pediatric Pulmonology, Marmara Universitesi, Istanbul, Turkey.<br /><searchLink fieldCode="AU" term="%22Kobbernagel+H%22">Kobbernagel H</searchLink>; Danish PCD Centre, Danish Paediatric Pulmonary Service, Department of Paediatrics and Adolescent Medicine, Copenhagen University Hospital, Rigshospitalet, Copenhagen, Denmark.; Department of Clinical Medicine, Faculty of Health and Medical Sciences, University of Copenhagen, Copenhagen, Denmark.<br /><searchLink fieldCode="AU" term="%22Koerner-Rettberg+C%22">Koerner-Rettberg C</searchLink>; Department of Paediatric Pulmonology, University Children's Hospital, Ruhr University Bochum, Katholisches Klinikum Bochum, Bochum, Germany.; Children's Hospital and Research Institute, Marienhospital Wesel, Wesel, Germany.<br /><searchLink fieldCode="AU" term="%22Kouis+P%22">Kouis P</searchLink>; Medical School, University of Cyprus, Nicosia, Cyprus.<br /><searchLink fieldCode="AU" term="%22Lorent+N%22">Lorent N</searchLink>; Department of Respiratory Diseases, University Hospitals Leuven, Leuven, Belgium.; Department of CHROMETA, Laboratory for Respiratory Diseases and Thoracic Surgery, KU Leuven, Leuven, Belgium.<br /><searchLink fieldCode="AU" term="%22Marcou+M%22">Marcou M</searchLink>; Medical School, University of Cyprus, Nicosia, Cyprus.<br /><searchLink fieldCode="AU" term="%22Mathin+JK%22">Mathin JK</searchLink>; Danish PCD Centre, Danish Paediatric Pulmonary Service, Department of Paediatrics and Adolescent Medicine, Copenhagen University Hospital, Rigshospitalet, Copenhagen, Denmark.; Department of Clinical Medicine, Faculty of Health and Medical Sciences, University of Copenhagen, Copenhagen, Denmark.<br /><searchLink fieldCode="AU" term="%22Martinu+V%22">Martinu V</searchLink>; Department of Paediatrics, Charles University, 2nd Faculty of Medicine, University Hospital in Motol, Prague, Czech Republic.<br /><searchLink fieldCode="AU" term="%22Moreno-Galdó+A%22">Moreno-Galdó A</searchLink>; Hospital Vall d'Hebron, Neumología Infantil, Barcelona, Spain.<br /><searchLink fieldCode="AU" term="%22Morgan+L%22">Morgan L</searchLink>; Concord Hospital, Concord Clinical School, University of Sydney, Department of Respiratory Medicine, Sydney, Australia.<br /><searchLink fieldCode="AU" term="%22Nielsen+KG%22">Nielsen KG</searchLink>; Danish PCD Centre, Danish Paediatric Pulmonary Service, Department of Paediatrics and Adolescent Medicine, Copenhagen University Hospital, Rigshospitalet, Copenhagen, Denmark.; Department of Clinical Medicine, Faculty of Health and Medical Sciences, University of Copenhagen, Copenhagen, Denmark.<br /><searchLink fieldCode="AU" term="%22Omran+H%22">Omran H</searchLink>; Department of General Pediatrics, University Hospital Muenster, Muenster, Germany.<br /><searchLink fieldCode="AU" term="%22Ozcelik+U%22">Ozcelik U</searchLink>; Department of Pediatric Pulmonology, Hacettepe University Faculty of Medicine, Ankara, Turkey.<br /><searchLink fieldCode="AU" term="%22Pohunek+P%22">Pohunek P</searchLink>; Department of Paediatrics, Charles University, 2nd Faculty of Medicine, University Hospital in Motol, Prague, Czech Republic.<br /><searchLink fieldCode="AU" term="%22Raidt+J%22">Raidt J</searchLink>; Department of General Pediatrics, University Hospital Muenster, Muenster, Germany.<br /><searchLink fieldCode="AU" term="%22Robinson+P%22">Robinson P</searchLink>; Royal Children's Hospital, Respiratory Medicine, Melbourne, Australia.; Faculty of Medicine Dentistry and Health Sciences, Paediatrics, University of Melbourne, Melbourne, Australia.<br /><searchLink fieldCode="AU" term="%22Rovira-Amigo+S%22">Rovira-Amigo S</searchLink>; Hospital Vall d'Hebron, Neumología Infantil, Barcelona, Spain.<br /><searchLink fieldCode="AU" term="%22Santamaria+F%22">Santamaria F</searchLink>; Department of Translational Medical Sciences, Pediatric Pulmonology, Federico II University, Naples, Italy.<br /><searchLink fieldCode="AU" term="%22Schlegtendal+A%22">Schlegtendal A</searchLink>; Department of Paediatric Pulmonology, University Children's Hospital, Ruhr University Bochum, Katholisches Klinikum Bochum, Bochum, Germany.; Children's Hospital and Research Institute, Marienhospital Wesel, Wesel, Germany.<br /><searchLink fieldCode="AU" term="%22Tamalet+A%22">Tamalet A</searchLink>; AP-HP, Sorbonne Université, Unité d'Exploration Fonctionnelle Respiratoire, Hôpital Armand-Trousseau, and Sorbonne Université, INSERM U938, Paris, France.<br /><searchLink fieldCode="AU" term="%22Thouvenin+G%22">Thouvenin G</searchLink>; AP-HP, Sorbonne Université, Unité d'Exploration Fonctionnelle Respiratoire, Hôpital Armand-Trousseau, and Sorbonne Université, INSERM U938, Paris, France.<br /><searchLink fieldCode="AU" term="%22Ullmann+N%22">Ullmann N</searchLink>; Respiratory and Cystic Fibrosis Unit, Academic Pediatric Department, Bambino Gesù Children Hospital, IRCCS, Rome, Italy.<br /><searchLink fieldCode="AU" term="%22Walker+W%22">Walker W</searchLink>; Primary Ciliary Dyskinesia Centre, University Hospital Southampton NHS Foundation Trust, Southampton, UK.<br /><searchLink fieldCode="AU" term="%22Yiallouros+P%22">Yiallouros P</searchLink>; Medical School, University of Cyprus, Nicosia, Cyprus.<br /><searchLink fieldCode="AU" term="%22Kuehni+CE%22">Kuehni CE</searchLink>; Institute of Social and Preventive Medicine, University of Bern, Bern, Switzerland.; Division of Paediatric Respiratory Medicine and Allergology, Department of Paediatrics, Inselspital, University Hospital, University of Bern, Bern, Switzerland.<br /><searchLink fieldCode="AU" term="%22Latzin+P%22">Latzin P</searchLink>; Institute of Social and Preventive Medicine, University of Bern, Bern, Switzerland.; Division of Paediatric Respiratory Medicine and Allergology, Department of Paediatrics, Inselspital, University Hospital, University of Bern, Bern, Switzerland.<br /><searchLink fieldCode="AU" term="%22Beydon+N%22">Beydon N</searchLink>; AP-HP, Sorbonne Université, Unité d'Exploration Fonctionnelle Respiratoire, Hôpital Armand-Trousseau, and Sorbonne Université, INSERM U938, Paris, France.<br /><searchLink fieldCode="AU" term="%22Lucas+JS%22">Lucas JS</searchLink>; Clinical and Experimental Sciences, University of Southampton Faculty of Medicine, Southampton, UK.; Primary Ciliary Dyskinesia Centre, University Hospital Southampton NHS Foundation Trust, Southampton, UK.
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  Data: <searchLink fieldCode="JN" term="%22101671641%22">ERJ open research</searchLink> [ERJ Open Res] 2024 Sep 30; Vol. 10 (5). <i>Date of Electronic Publication: </i>2024 Sep 30 (<i>Print Publication: </i>2024).
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            NameFull: Yiallouros P
      – PersonEntity:
          Name:
            NameFull: Kuehni CE
      – PersonEntity:
          Name:
            NameFull: Latzin P
      – PersonEntity:
          Name:
            NameFull: Beydon N
      – PersonEntity:
          Name:
            NameFull: Lucas JS
    IsPartOfRelationships:
      – BibEntity:
          Dates:
            – D: 30
              M: 09
              Text: 2024 Sep 30
              Type: published
              Y: 2024
          Identifiers:
            – Type: issn-print
              Value: 2312-0541
          Numbering:
            – Type: volume
              Value: 10
            – Type: issue
              Value: 5
          Titles:
            – TitleFull: ERJ open research
              Type: main
ResultId 1