Novel gain-of-function mutants identify a critical region within CFTR membrane-spanning domain 2 controlling cAMP-dependent and ATP-independent channel activation.

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Title: Novel gain-of-function mutants identify a critical region within CFTR membrane-spanning domain 2 controlling cAMP-dependent and ATP-independent channel activation.
Authors: Castanier S; Université Paris Cité, CNRS, INSERM, Institut Necker Enfants Malades-INEM, Paris, F-75015, France., Elbahnsi A; Sorbonne Université, Muséum National d'Histoire Naturelle, UMR CNRS 7590, Institut de Minéralogie, de Physique des Matériaux et de Cosmochimie, IMPMC, Paris, 75005, France.; Université Paris Cité, Inserm U1268 MCTR, CiTCoM UMR 8038 CNRS, Paris, 75006, France., Chevalier B; Université Paris Cité, CNRS, INSERM, Institut Necker Enfants Malades-INEM, Paris, F-75015, France., Baatallah N; Université Paris Cité, CNRS, INSERM, Institut Necker Enfants Malades-INEM, Paris, F-75015, France., Pranke I; Université Paris Cité, CNRS, INSERM, Institut Necker Enfants Malades-INEM, Paris, F-75015, France., Berri L; Université Paris Cité, CNRS, INSERM, Institut Necker Enfants Malades-INEM, Paris, F-75015, France., Edelman A; Université Paris Cité, CNRS, INSERM, Institut Necker Enfants Malades-INEM, Paris, F-75015, France., Sermet-Gaudelus I; Université Paris Cité, CNRS, INSERM, Institut Necker Enfants Malades-INEM, Paris, F-75015, France., Mornon JP; Sorbonne Université, Muséum National d'Histoire Naturelle, UMR CNRS 7590, Institut de Minéralogie, de Physique des Matériaux et de Cosmochimie, IMPMC, Paris, 75005, France., Callebaut I; Sorbonne Université, Muséum National d'Histoire Naturelle, UMR CNRS 7590, Institut de Minéralogie, de Physique des Matériaux et de Cosmochimie, IMPMC, Paris, 75005, France., Hinzpeter A; Université Paris Cité, CNRS, INSERM, Institut Necker Enfants Malades-INEM, Paris, F-75015, France. alexandre.hinzpeter@inserm.fr.
Source: Cellular and molecular life sciences : CMLS [Cell Mol Life Sci] 2024 Oct 07; Vol. 81 (1), pp. 426. Date of Electronic Publication: 2024 Oct 07.
Publication Type: Journal Article
Journal Info: Publisher: Springer Country of Publication: Switzerland NLM ID: 9705402 Publication Model: Electronic Cited Medium: Internet ISSN: 1420-9071 (Electronic) Linking ISSN: 1420682X NLM ISO Abbreviation: Cell Mol Life Sci Subsets: MEDLINE
Database: MEDLINE Ultimate
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  Data: Novel gain-of-function mutants identify a critical region within CFTR membrane-spanning domain 2 controlling cAMP-dependent and ATP-independent channel activation.
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  Data: <searchLink fieldCode="AU" term="%22Castanier+S%22">Castanier S</searchLink>; Université Paris Cité, CNRS, INSERM, Institut Necker Enfants Malades-INEM, Paris, F-75015, France.<br /><searchLink fieldCode="AU" term="%22Elbahnsi+A%22">Elbahnsi A</searchLink>; Sorbonne Université, Muséum National d'Histoire Naturelle, UMR CNRS 7590, Institut de Minéralogie, de Physique des Matériaux et de Cosmochimie, IMPMC, Paris, 75005, France.; Université Paris Cité, Inserm U1268 MCTR, CiTCoM UMR 8038 CNRS, Paris, 75006, France.<br /><searchLink fieldCode="AU" term="%22Chevalier+B%22">Chevalier B</searchLink>; Université Paris Cité, CNRS, INSERM, Institut Necker Enfants Malades-INEM, Paris, F-75015, France.<br /><searchLink fieldCode="AU" term="%22Baatallah+N%22">Baatallah N</searchLink>; Université Paris Cité, CNRS, INSERM, Institut Necker Enfants Malades-INEM, Paris, F-75015, France.<br /><searchLink fieldCode="AU" term="%22Pranke+I%22">Pranke I</searchLink>; Université Paris Cité, CNRS, INSERM, Institut Necker Enfants Malades-INEM, Paris, F-75015, France.<br /><searchLink fieldCode="AU" term="%22Berri+L%22">Berri L</searchLink>; Université Paris Cité, CNRS, INSERM, Institut Necker Enfants Malades-INEM, Paris, F-75015, France.<br /><searchLink fieldCode="AU" term="%22Edelman+A%22">Edelman A</searchLink>; Université Paris Cité, CNRS, INSERM, Institut Necker Enfants Malades-INEM, Paris, F-75015, France.<br /><searchLink fieldCode="AU" term="%22Sermet-Gaudelus+I%22">Sermet-Gaudelus I</searchLink>; Université Paris Cité, CNRS, INSERM, Institut Necker Enfants Malades-INEM, Paris, F-75015, France.<br /><searchLink fieldCode="AU" term="%22Mornon+JP%22">Mornon JP</searchLink>; Sorbonne Université, Muséum National d'Histoire Naturelle, UMR CNRS 7590, Institut de Minéralogie, de Physique des Matériaux et de Cosmochimie, IMPMC, Paris, 75005, France.<br /><searchLink fieldCode="AU" term="%22Callebaut+I%22">Callebaut I</searchLink>; Sorbonne Université, Muséum National d'Histoire Naturelle, UMR CNRS 7590, Institut de Minéralogie, de Physique des Matériaux et de Cosmochimie, IMPMC, Paris, 75005, France.<br /><searchLink fieldCode="AU" term="%22Hinzpeter+A%22">Hinzpeter A</searchLink>; Université Paris Cité, CNRS, INSERM, Institut Necker Enfants Malades-INEM, Paris, F-75015, France. alexandre.hinzpeter@inserm.fr.
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  Data: <searchLink fieldCode="JN" term="%229705402%22">Cellular and molecular life sciences : CMLS</searchLink> [Cell Mol Life Sci] 2024 Oct 07; Vol. 81 (1), pp. 426. <i>Date of Electronic Publication: </i>2024 Oct 07.
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