PKD1 mutation perturbs morphogenesis in tubular epithelial organoids derived from human pluripotent stem cells.
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| Title: | PKD1 mutation perturbs morphogenesis in tubular epithelial organoids derived from human pluripotent stem cells. |
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| Authors: | Scarlat A; Istituto di Ricerche Farmacologiche Mario Negri IRCCS, Centro Anna Maria Astori, Science and Technology Park Kilometro Rosso, Bergamo, Italy., Trionfini P; Istituto di Ricerche Farmacologiche Mario Negri IRCCS, Centro Anna Maria Astori, Science and Technology Park Kilometro Rosso, Bergamo, Italy., Rizzo P; Istituto di Ricerche Farmacologiche Mario Negri IRCCS, Centro Anna Maria Astori, Science and Technology Park Kilometro Rosso, Bergamo, Italy., Conti S; Istituto di Ricerche Farmacologiche Mario Negri IRCCS, Centro Anna Maria Astori, Science and Technology Park Kilometro Rosso, Bergamo, Italy., Longaretti L; Istituto di Ricerche Farmacologiche Mario Negri IRCCS, Centro Anna Maria Astori, Science and Technology Park Kilometro Rosso, Bergamo, Italy., Breno M; Istituto di Ricerche Farmacologiche Mario Negri IRCCS, Centro Anna Maria Astori, Science and Technology Park Kilometro Rosso, Bergamo, Italy., Longhi L; Istituto di Ricerche Farmacologiche Mario Negri IRCCS, Centro Anna Maria Astori, Science and Technology Park Kilometro Rosso, Bergamo, Italy., Xinaris C; Istituto di Ricerche Farmacologiche Mario Negri IRCCS, Centro Anna Maria Astori, Science and Technology Park Kilometro Rosso, Bergamo, Italy., Remuzzi G; Istituto di Ricerche Farmacologiche Mario Negri IRCCS, Centro Anna Maria Astori, Science and Technology Park Kilometro Rosso, Bergamo, Italy., Benigni A; Istituto di Ricerche Farmacologiche Mario Negri IRCCS, Centro Anna Maria Astori, Science and Technology Park Kilometro Rosso, Bergamo, Italy. ariela.benigni@marionegri.it., Tomasoni S; Istituto di Ricerche Farmacologiche Mario Negri IRCCS, Centro Anna Maria Astori, Science and Technology Park Kilometro Rosso, Bergamo, Italy. |
| Source: | Scientific reports [Sci Rep] 2025 Mar 26; Vol. 15 (1), pp. 10375. Date of Electronic Publication: 2025 Mar 26. |
| Publication Type: | Journal Article |
| Journal Info: | Publisher: Nature Publishing Group Country of Publication: England NLM ID: 101563288 Publication Model: Electronic Cited Medium: Internet ISSN: 2045-2322 (Electronic) Linking ISSN: 20452322 NLM ISO Abbreviation: Sci Rep Subsets: MEDLINE |
| Database: | MEDLINE Ultimate |
| FullText | Text: Availability: 0 |
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| Header | DbId: mdl DbLabel: MEDLINE Ultimate An: 40140667 AccessLevel: 2 PubType: Academic Journal PubTypeId: academicJournal PreciseRelevancyScore: 0 |
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| Items | – Name: Title Label: Title Group: Ti Data: PKD1 mutation perturbs morphogenesis in tubular epithelial organoids derived from human pluripotent stem cells. – Name: Author Label: Authors Group: Au Data: <searchLink fieldCode="AU" term="%22Scarlat+A%22">Scarlat A</searchLink>; Istituto di Ricerche Farmacologiche Mario Negri IRCCS, Centro Anna Maria Astori, Science and Technology Park Kilometro Rosso, Bergamo, Italy.<br /><searchLink fieldCode="AU" term="%22Trionfini+P%22">Trionfini P</searchLink>; Istituto di Ricerche Farmacologiche Mario Negri IRCCS, Centro Anna Maria Astori, Science and Technology Park Kilometro Rosso, Bergamo, Italy.<br /><searchLink fieldCode="AU" term="%22Rizzo+P%22">Rizzo P</searchLink>; Istituto di Ricerche Farmacologiche Mario Negri IRCCS, Centro Anna Maria Astori, Science and Technology Park Kilometro Rosso, Bergamo, Italy.<br /><searchLink fieldCode="AU" term="%22Conti+S%22">Conti S</searchLink>; Istituto di Ricerche Farmacologiche Mario Negri IRCCS, Centro Anna Maria Astori, Science and Technology Park Kilometro Rosso, Bergamo, Italy.<br /><searchLink fieldCode="AU" term="%22Longaretti+L%22">Longaretti L</searchLink>; Istituto di Ricerche Farmacologiche Mario Negri IRCCS, Centro Anna Maria Astori, Science and Technology Park Kilometro Rosso, Bergamo, Italy.<br /><searchLink fieldCode="AU" term="%22Breno+M%22">Breno M</searchLink>; Istituto di Ricerche Farmacologiche Mario Negri IRCCS, Centro Anna Maria Astori, Science and Technology Park Kilometro Rosso, Bergamo, Italy.<br /><searchLink fieldCode="AU" term="%22Longhi+L%22">Longhi L</searchLink>; Istituto di Ricerche Farmacologiche Mario Negri IRCCS, Centro Anna Maria Astori, Science and Technology Park Kilometro Rosso, Bergamo, Italy.<br /><searchLink fieldCode="AU" term="%22Xinaris+C%22">Xinaris C</searchLink>; Istituto di Ricerche Farmacologiche Mario Negri IRCCS, Centro Anna Maria Astori, Science and Technology Park Kilometro Rosso, Bergamo, Italy.<br /><searchLink fieldCode="AU" term="%22Remuzzi+G%22">Remuzzi G</searchLink>; Istituto di Ricerche Farmacologiche Mario Negri IRCCS, Centro Anna Maria Astori, Science and Technology Park Kilometro Rosso, Bergamo, Italy.<br /><searchLink fieldCode="AU" term="%22Benigni+A%22">Benigni A</searchLink>; Istituto di Ricerche Farmacologiche Mario Negri IRCCS, Centro Anna Maria Astori, Science and Technology Park Kilometro Rosso, Bergamo, Italy. ariela.benigni@marionegri.it.<br /><searchLink fieldCode="AU" term="%22Tomasoni+S%22">Tomasoni S</searchLink>; Istituto di Ricerche Farmacologiche Mario Negri IRCCS, Centro Anna Maria Astori, Science and Technology Park Kilometro Rosso, Bergamo, Italy. – Name: TitleSource Label: Source Group: Src Data: <searchLink fieldCode="JN" term="%22101563288%22">Scientific reports</searchLink> [Sci Rep] 2025 Mar 26; Vol. 15 (1), pp. 10375. <i>Date of Electronic Publication: </i>2025 Mar 26. – Name: TypePub Label: Publication Type Group: TypPub Data: Journal Article – Name: TitleSource Label: Journal Info Group: Src Data: <i>Publisher: </i><searchLink fieldCode="PB" term="%22Nature+Publishing+Group%22">Nature Publishing Group </searchLink><i>Country of Publication: </i>England <i>NLM ID: </i>101563288 <i>Publication Model: </i>Electronic <i>Cited Medium: </i>Internet <i>ISSN: </i>2045-2322 (Electronic) <i>Linking ISSN: </i><searchLink fieldCode="IS" term="%2220452322%22">20452322 </searchLink><i>NLM ISO Abbreviation: </i>Sci Rep <i>Subsets: </i>MEDLINE |
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| RecordInfo | BibRecord: BibEntity: Identifiers: – Type: doi Value: 10.1038/s41598-025-94855-9 Languages: – Code: eng Text: English PhysicalDescription: Pagination: StartPage: 10375 Titles: – TitleFull: PKD1 mutation perturbs morphogenesis in tubular epithelial organoids derived from human pluripotent stem cells. Type: main BibRelationships: HasContributorRelationships: – PersonEntity: Name: NameFull: Scarlat A – PersonEntity: Name: NameFull: Trionfini P – PersonEntity: Name: NameFull: Rizzo P – PersonEntity: Name: NameFull: Conti S – PersonEntity: Name: NameFull: Longaretti L – PersonEntity: Name: NameFull: Breno M – PersonEntity: Name: NameFull: Longhi L – PersonEntity: Name: NameFull: Xinaris C – PersonEntity: Name: NameFull: Remuzzi G – PersonEntity: Name: NameFull: Benigni A – PersonEntity: Name: NameFull: Tomasoni S IsPartOfRelationships: – BibEntity: Dates: – D: 26 M: 03 Text: 2025 Mar 26 Type: published Y: 2025 Identifiers: – Type: issn-electronic Value: 2045-2322 Numbering: – Type: volume Value: 15 – Type: issue Value: 1 Titles: – TitleFull: Scientific reports Type: main |
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