Global frequency, diagnosis, and treatment of hereditary angioedema with normal C1 inhibitor.

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Title: Global frequency, diagnosis, and treatment of hereditary angioedema with normal C1 inhibitor.
Authors: Magerl M; Angioedema Center of Reference and Excellence (ACARE), Institute of Allergology, Charité-Universitätsmedizin Berlin, corporate member of Freie Universität Berlin and Humboldt-Universität zu Berlin, Berlin, Germany.; Fraunhofer Institute for Translational Medicine and Pharmacology ITMP, Allergology and Immunology, Berlin, Germany., Riedl MA; Division of Allergy and Immunology, University of California-San Diego, La Jolla, Calif., Arruda LK; Clinical Hospital of Ribeirão Preto Medical School, University of São Paulo, São Paulo, Brazil., Bauer A; Department of Dermatology, University Allergy Center, University Hospital Carl Gustav Carus, Technical University Dresden, Dresden, Germany., Berardi A; Instituto de Asma, Alergia y Enfermedades Respiratorias, Corrientes, Argentina., Bernstein JA; University of Cincinnati College of Medicine, Division of Rheumatology, Allergy and Immunology and Bernstein Allergy Group and Clinical Research Center, Cincinnati, Ohio., Bouillet L; French National Reference Center for Angioedema (CREAK), Grenoble Alpes University, Grenoble, France., Buckland M; Barts Health NHS Trust, London, United Kingdom., Buttgereit T; Angioedema Center of Reference and Excellence (ACARE), Institute of Allergology, Charité-Universitätsmedizin Berlin, corporate member of Freie Universität Berlin and Humboldt-Universität zu Berlin, Berlin, Germany.; Fraunhofer Institute for Translational Medicine and Pharmacology ITMP, Allergology and Immunology, Berlin, Germany., Cohn DM; Amsterdam UMC Location AMC, Amsterdam, The Netherlands., Craig T; Penn State University, University Park, Pa., Criado RF; Alergo Skin, Santo André, Brazil., Du-Thanh A; Montpellier University Hospital, Montpelier, France., Fain O; Sorbonne Université, service de médecine interne, AP-HP, Hôpital St Antoine, Paris, France., Gonçalo M; Clínica de Dermatologia, University Hospital, Coimbra Local Health Unit, and Faculty of Medicine, University of Coimbra, Coimbra, Portugal., Greve J; Department of Otorhinolaryngology, Head and Neck Surgery, Ulm University Medical Center, Ulm, Germany., Grumach AS; Clinical Immunology, University Center Faculty of Medicine ABC, Santo André, Brazil., Guilarte M; Allergy Department, Hereditary Angioedema Reference Center (CSUR-74), Vall d'Hebron Research Unit (VHIR), Hospital Universitari Vall d'Hebron, Barcelona, Spain., Katelaris C; Campbelltown Hospital and Western Sydney University, Campbelltown, Australia., Kinaciyan T; Department of Dermatology, ACARE, Medical University of Vienna, Vienna, Austria., Latysheva EA; Pirogov Russian National Research Medical University, Moscow, Russia., Lleonart R; Hospital Universitari de Bellvitge, Barcelona, Spain., Llosa OC; SANNA-Clínica el Golf, San Isidro, Peru., Mansour E; Universidade Estadual de Campinas (UNICAMP), Campinas, Brazil., Grivcheva-Panovska V; ACARE North Macedonia, PHI University Clinic of Dermatology, Ss Cyril and Methodius Skopje University, Skopje, Republic of North Macedonia., Parisi C; Hospital Italiano de Buenos Aires, Buenos Aires, Argentina., Rosario Filho NA; Federal University of Parana, Curitiba, Brazil., Santos AS; ACARE, Hereditary Angioedema Unit, Immunoallergology Department, Unidade Local de Saúde de Santa Maria, Faculdade de Medicina da Universidade de Lisboa, Lisbon, Portugal., Staubach P; Hautklinik und Poliklinik Universitätsmedizin der Johannes Gutenberg-Universität Mainz, Mainz, Germany., Valerieva A; Department of Allergology, Medical University of Sofia, University Hospital 'Alexandrovska,' Sofia, Bulgaria., Rodrigues Valle SO; Clementino Fraga Filho University Hospital Federal University of Rio de Janeiro, Rio de Janeiro, Brazil., Danese S; Outcomes Insights, Agoura Hills, Calif., Ulloa J; Outcomes Insights, Agoura Hills, Calif., Audhya PK; KalVista Pharmaceuticals Inc, Cambridge, Mass., Maurer M; Angioedema Center of Reference and Excellence (ACARE), Institute of Allergology, Charité-Universitätsmedizin Berlin, corporate member of Freie Universität Berlin and Humboldt-Universität zu Berlin, Berlin, Germany.; Fraunhofer Institute for Translational Medicine and Pharmacology ITMP, Allergology and Immunology, Berlin, Germany.
Source: The journal of allergy and clinical immunology. Global [J Allergy Clin Immunol Glob] 2025 Feb 27; Vol. 4 (3), pp. 100446. Date of Electronic Publication: 2025 Feb 27 (Print Publication: 2025).
Publication Type: Journal Article
Journal Info: Publisher: Elsevier Inc Country of Publication: United States NLM ID: 9918453488706676 Publication Model: eCollection Cited Medium: Internet ISSN: 2772-8293 (Electronic) Linking ISSN: 27728293 NLM ISO Abbreviation: J Allergy Clin Immunol Glob Subsets: PubMed not MEDLINE
Database: MEDLINE Ultimate
Description
ISSN:2772-8293
DOI:10.1016/j.jacig.2025.100446