Dietary intake remains unchanged while nutritional status improves in children and adults with cystic fibrosis on Elexacaftor/Tezacaftor/Ivacaftor.

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Title: Dietary intake remains unchanged while nutritional status improves in children and adults with cystic fibrosis on Elexacaftor/Tezacaftor/Ivacaftor.
Authors: Enaud R; University of Bordeaux, INSERM U1045, Centre de Recherche Cardio-thoracique de Bordeaux, U1045, Bordeaux, France; Bordeaux University Hospital, CRCM pédiatrique, CIC 1401, Bordeaux, France., Languepin J; Limoges University Hospital, Paediatric Cystic Fibrosis Reference Center (CRCM), Limoges, France., Lagarrigue M; Centre de ressources et de compétences pour la mucoviscidose, Hôpital des Enfants, CHU de Toulouse, Toulouse, France., Arrouy A; Centre de ressources et de compétences pour la mucoviscidose, Hôpital des Enfants, CHU de Toulouse, Toulouse, France; Service de Gastroentérologie, Hépatologie, Nutrition et Maladies Héréditaires du Métabolisme, Hôpital des Enfants, CHU de Toulouse, Toulouse, France., Macey J; Bordeaux University Hospital, Adult CF center, France., Bui S; Bordeaux University Hospital, CRCM pédiatrique, CIC 1401, Bordeaux, France., Dupuis M; Adult Cystic Fibrosis Center, Pulmonology, CHU Toulouse, France., Roditis L; Centre de ressources et de compétences pour la mucoviscidose, Hôpital des Enfants, CHU de Toulouse, Toulouse, France., Flumian C; Centre d'Investigation Clinique 1436, CHU de Toulouse, Toulouse, France., Mas E; Centre de ressources et de compétences pour la mucoviscidose, Hôpital des Enfants, CHU de Toulouse, Toulouse, France; Service de Gastroentérologie, Hépatologie, Nutrition et Maladies Héréditaires du Métabolisme, Hôpital des Enfants, CHU de Toulouse, Toulouse, France; Centre d'Investigation Clinique 1436, CHU de Toulouse, Toulouse, France; Institut de Recherche en Santé Digestive (IRSD), Université de Toulouse, INSERM, INRAE, ENVT, UPS, Toulouse, France. Electronic address: mas.e@chu-toulouse.fr., Mittaine M; Centre de ressources et de compétences pour la mucoviscidose, Hôpital des Enfants, CHU de Toulouse, Toulouse, France.
Source: Clinical nutrition (Edinburgh, Scotland) [Clin Nutr] 2025 Jul; Vol. 50, pp. 76-82. Date of Electronic Publication: 2025 Apr 30.
Publication Type: Journal Article; Multicenter Study; Observational Study
Journal Info: Publisher: Elsevier Country of Publication: England NLM ID: 8309603 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1532-1983 (Electronic) Linking ISSN: 02615614 NLM ISO Abbreviation: Clin Nutr Subsets: MEDLINE
Database: MEDLINE Ultimate
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  Data: Dietary intake remains unchanged while nutritional status improves in children and adults with cystic fibrosis on Elexacaftor/Tezacaftor/Ivacaftor.
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  Data: <searchLink fieldCode="AU" term="%22Enaud+R%22">Enaud R</searchLink>; University of Bordeaux, INSERM U1045, Centre de Recherche Cardio-thoracique de Bordeaux, U1045, Bordeaux, France; Bordeaux University Hospital, CRCM pédiatrique, CIC 1401, Bordeaux, France.<br /><searchLink fieldCode="AU" term="%22Languepin+J%22">Languepin J</searchLink>; Limoges University Hospital, Paediatric Cystic Fibrosis Reference Center (CRCM), Limoges, France.<br /><searchLink fieldCode="AU" term="%22Lagarrigue+M%22">Lagarrigue M</searchLink>; Centre de ressources et de compétences pour la mucoviscidose, Hôpital des Enfants, CHU de Toulouse, Toulouse, France.<br /><searchLink fieldCode="AU" term="%22Arrouy+A%22">Arrouy A</searchLink>; Centre de ressources et de compétences pour la mucoviscidose, Hôpital des Enfants, CHU de Toulouse, Toulouse, France; Service de Gastroentérologie, Hépatologie, Nutrition et Maladies Héréditaires du Métabolisme, Hôpital des Enfants, CHU de Toulouse, Toulouse, France.<br /><searchLink fieldCode="AU" term="%22Macey+J%22">Macey J</searchLink>; Bordeaux University Hospital, Adult CF center, France.<br /><searchLink fieldCode="AU" term="%22Bui+S%22">Bui S</searchLink>; Bordeaux University Hospital, CRCM pédiatrique, CIC 1401, Bordeaux, France.<br /><searchLink fieldCode="AU" term="%22Dupuis+M%22">Dupuis M</searchLink>; Adult Cystic Fibrosis Center, Pulmonology, CHU Toulouse, France.<br /><searchLink fieldCode="AU" term="%22Roditis+L%22">Roditis L</searchLink>; Centre de ressources et de compétences pour la mucoviscidose, Hôpital des Enfants, CHU de Toulouse, Toulouse, France.<br /><searchLink fieldCode="AU" term="%22Flumian+C%22">Flumian C</searchLink>; Centre d'Investigation Clinique 1436, CHU de Toulouse, Toulouse, France.<br /><searchLink fieldCode="AU" term="%22Mas+E%22">Mas E</searchLink>; Centre de ressources et de compétences pour la mucoviscidose, Hôpital des Enfants, CHU de Toulouse, Toulouse, France; Service de Gastroentérologie, Hépatologie, Nutrition et Maladies Héréditaires du Métabolisme, Hôpital des Enfants, CHU de Toulouse, Toulouse, France; Centre d'Investigation Clinique 1436, CHU de Toulouse, Toulouse, France; Institut de Recherche en Santé Digestive (IRSD), Université de Toulouse, INSERM, INRAE, ENVT, UPS, Toulouse, France. Electronic address: mas.e@chu-toulouse.fr.<br /><searchLink fieldCode="AU" term="%22Mittaine+M%22">Mittaine M</searchLink>; Centre de ressources et de compétences pour la mucoviscidose, Hôpital des Enfants, CHU de Toulouse, Toulouse, France.
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      – TitleFull: Dietary intake remains unchanged while nutritional status improves in children and adults with cystic fibrosis on Elexacaftor/Tezacaftor/Ivacaftor.
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              Text: 2025 Jul
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