Compromised repolarization reserve in a murine model of catecholaminergic polymorphic ventricular tachycardia caused by RyR2-R420Q mutation.

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Title: Compromised repolarization reserve in a murine model of catecholaminergic polymorphic ventricular tachycardia caused by RyR2-R420Q mutation.
Authors: Zissimopoulos S; Institute of Life Science, Swansea University Medical School, Swansea University, Swansea SA2 8PP, UK., Kirilenko P; School of Biosciences, College of Biomedical and Life Sciences, Cardiff University, Cardiff CF10 3AX, UK., Braza-Boïls A; CAFAMUSME Research Group, Instituto de Investigación Sanitaria La Fe de Valencia, Spain; CIBERCV, Center for Biomedical Network Research on Cardiovascular Diseases, Madrid, Spain., Zorio E; CAFAMUSME Research Group, Instituto de Investigación Sanitaria La Fe de Valencia, Spain; CIBERCV, Center for Biomedical Network Research on Cardiovascular Diseases, Madrid, Spain; Inherited Cardiac Diseases Unit, Cardiology Department at the Hospital Universitario y Politécnico La Fe de Valencia, Spain; Department of Medicine, Faculty of Medicine and Dentistry, Universitat de València, 46010, Valencia, Spain., Wang Y; Inserm, UMR-S 1180, Signalling and Cardiovascular Pathophysiology, Faculté de Pharmacie, Université Paris-Saclay, 17 Avenue des Sciences, 91400 Orsay, France., Gomez AM; Inserm, UMR-S 1180, Signalling and Cardiovascular Pathophysiology, Faculté de Pharmacie, Université Paris-Saclay, 17 Avenue des Sciences, 91400 Orsay, France., Cannell MB; School of Physiology, Pharmacology & Neuroscience, Faculty of Biomedical Sciences, University of Bristol, University Walk, Bristol BS8 1TD, UK., Latinkic B; School of Biosciences, College of Biomedical and Life Sciences, Cardiff University, Cardiff CF10 3AX, UK., Fowler ED; School of Biosciences, College of Biomedical and Life Sciences, Cardiff University, Cardiff CF10 3AX, UK. Electronic address: FowlerED@Cardiff.ac.uk.
Source: Journal of molecular and cellular cardiology [J Mol Cell Cardiol] 2025 Sep; Vol. 206, pp. 127-140. Date of Electronic Publication: 2025 Jul 24.
Publication Type: Journal Article
Journal Info: Publisher: Academic Press Country of Publication: England NLM ID: 0262322 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1095-8584 (Electronic) Linking ISSN: 00222828 NLM ISO Abbreviation: J Mol Cell Cardiol Subsets: MEDLINE
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  Data: Compromised repolarization reserve in a murine model of catecholaminergic polymorphic ventricular tachycardia caused by RyR2-R420Q mutation.
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  Data: <searchLink fieldCode="AU" term="%22Zissimopoulos+S%22">Zissimopoulos S</searchLink>; Institute of Life Science, Swansea University Medical School, Swansea University, Swansea SA2 8PP, UK.<br /><searchLink fieldCode="AU" term="%22Kirilenko+P%22">Kirilenko P</searchLink>; School of Biosciences, College of Biomedical and Life Sciences, Cardiff University, Cardiff CF10 3AX, UK.<br /><searchLink fieldCode="AU" term="%22Braza-Boïls+A%22">Braza-Boïls A</searchLink>; CAFAMUSME Research Group, Instituto de Investigación Sanitaria La Fe de Valencia, Spain; CIBERCV, Center for Biomedical Network Research on Cardiovascular Diseases, Madrid, Spain.<br /><searchLink fieldCode="AU" term="%22Zorio+E%22">Zorio E</searchLink>; CAFAMUSME Research Group, Instituto de Investigación Sanitaria La Fe de Valencia, Spain; CIBERCV, Center for Biomedical Network Research on Cardiovascular Diseases, Madrid, Spain; Inherited Cardiac Diseases Unit, Cardiology Department at the Hospital Universitario y Politécnico La Fe de Valencia, Spain; Department of Medicine, Faculty of Medicine and Dentistry, Universitat de València, 46010, Valencia, Spain.<br /><searchLink fieldCode="AU" term="%22Wang+Y%22">Wang Y</searchLink>; Inserm, UMR-S 1180, Signalling and Cardiovascular Pathophysiology, Faculté de Pharmacie, Université Paris-Saclay, 17 Avenue des Sciences, 91400 Orsay, France.<br /><searchLink fieldCode="AU" term="%22Gomez+AM%22">Gomez AM</searchLink>; Inserm, UMR-S 1180, Signalling and Cardiovascular Pathophysiology, Faculté de Pharmacie, Université Paris-Saclay, 17 Avenue des Sciences, 91400 Orsay, France.<br /><searchLink fieldCode="AU" term="%22Cannell+MB%22">Cannell MB</searchLink>; School of Physiology, Pharmacology & Neuroscience, Faculty of Biomedical Sciences, University of Bristol, University Walk, Bristol BS8 1TD, UK.<br /><searchLink fieldCode="AU" term="%22Latinkic+B%22">Latinkic B</searchLink>; School of Biosciences, College of Biomedical and Life Sciences, Cardiff University, Cardiff CF10 3AX, UK.<br /><searchLink fieldCode="AU" term="%22Fowler+ED%22">Fowler ED</searchLink>; School of Biosciences, College of Biomedical and Life Sciences, Cardiff University, Cardiff CF10 3AX, UK. Electronic address: FowlerED@Cardiff.ac.uk.
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  Data: <searchLink fieldCode="JN" term="%220262322%22">Journal of molecular and cellular cardiology</searchLink> [J Mol Cell Cardiol] 2025 Sep; Vol. 206, pp. 127-140. <i>Date of Electronic Publication: </i>2025 Jul 24.
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  Data: <i>Publisher: </i><searchLink fieldCode="PB" term="%22Academic+Press%22">Academic Press </searchLink><i>Country of Publication: </i>England <i>NLM ID: </i>0262322 <i>Publication Model: </i>Print-Electronic <i>Cited Medium: </i>Internet <i>ISSN: </i>1095-8584 (Electronic) <i>Linking ISSN: </i><searchLink fieldCode="IS" term="%2200222828%22">00222828 </searchLink><i>NLM ISO Abbreviation: </i>J Mol Cell Cardiol <i>Subsets: </i>MEDLINE
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        Value: 10.1016/j.yjmcc.2025.07.014
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              Text: 2025 Sep
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