Nuclear Protein Aggregates Disrupt RNA Processing and Alter Biomechanics in a Muscle Cell Model of OPMD.

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Title: Nuclear Protein Aggregates Disrupt RNA Processing and Alter Biomechanics in a Muscle Cell Model of OPMD.
Authors: Shademan M; Leiden University Medical Centre, Leiden, Leiden, The Netherlands., Flannery S; Target Discovery Institute, Centre for Medicines Discovery, Nuffield Department of Medicine, University of Oxford, Oxford UK., Bos E; Leiden University Medical Centre, Leiden, Leiden, The Netherlands., Evers TMJ; Medical Systems Biophysics and Bioengineering Laboratory, Leiden Academic Centre for Drug Research, Leiden University, Leiden, the Netherlands., Sheikhhassani V; Medical Systems Biophysics and Bioengineering Laboratory, Leiden Academic Centre for Drug Research, Leiden University, Leiden, the Netherlands., Mashaghi A; Medical Systems Biophysics and Bioengineering Laboratory, Leiden Academic Centre for Drug Research, Leiden University, Leiden, the Netherlands., Kusters B; Radboud University Medical Center, Nijmegen, The Netherlands., van Engelen B; Radboud University Medical Center, Nijmegen, The Netherlands., Sharp TH; School of Biochemistry, Bristol University, Bristol, UK., Fischer R; Target Discovery Institute, Centre for Medicines Discovery, Nuffield Department of Medicine, University of Oxford, Oxford UK., Kessler BM; Target Discovery Institute, Centre for Medicines Discovery, Nuffield Department of Medicine, University of Oxford, Oxford UK., Raz V; Leiden University Medical Centre, Leiden, Leiden, The Netherlands.
Source: Aging and disease [Aging Dis] 2025 Aug 28. Date of Electronic Publication: 2025 Aug 28.
Publication Type: Journal Article
Journal Info: Publisher: JKL International Country of Publication: United States NLM ID: 101540533 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 2152-5250 (Electronic) Linking ISSN: 21525250 NLM ISO Abbreviation: Aging Dis Subsets: MEDLINE
Database: MEDLINE Ultimate
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  Data: Nuclear Protein Aggregates Disrupt RNA Processing and Alter Biomechanics in a Muscle Cell Model of OPMD.
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  Data: <searchLink fieldCode="AU" term="%22Shademan+M%22">Shademan M</searchLink>; Leiden University Medical Centre, Leiden, Leiden, The Netherlands.<br /><searchLink fieldCode="AU" term="%22Flannery+S%22">Flannery S</searchLink>; Target Discovery Institute, Centre for Medicines Discovery, Nuffield Department of Medicine, University of Oxford, Oxford UK.<br /><searchLink fieldCode="AU" term="%22Bos+E%22">Bos E</searchLink>; Leiden University Medical Centre, Leiden, Leiden, The Netherlands.<br /><searchLink fieldCode="AU" term="%22Evers+TMJ%22">Evers TMJ</searchLink>; Medical Systems Biophysics and Bioengineering Laboratory, Leiden Academic Centre for Drug Research, Leiden University, Leiden, the Netherlands.<br /><searchLink fieldCode="AU" term="%22Sheikhhassani+V%22">Sheikhhassani V</searchLink>; Medical Systems Biophysics and Bioengineering Laboratory, Leiden Academic Centre for Drug Research, Leiden University, Leiden, the Netherlands.<br /><searchLink fieldCode="AU" term="%22Mashaghi+A%22">Mashaghi A</searchLink>; Medical Systems Biophysics and Bioengineering Laboratory, Leiden Academic Centre for Drug Research, Leiden University, Leiden, the Netherlands.<br /><searchLink fieldCode="AU" term="%22Kusters+B%22">Kusters B</searchLink>; Radboud University Medical Center, Nijmegen, The Netherlands.<br /><searchLink fieldCode="AU" term="%22van+Engelen+B%22">van Engelen B</searchLink>; Radboud University Medical Center, Nijmegen, The Netherlands.<br /><searchLink fieldCode="AU" term="%22Sharp+TH%22">Sharp TH</searchLink>; School of Biochemistry, Bristol University, Bristol, UK.<br /><searchLink fieldCode="AU" term="%22Fischer+R%22">Fischer R</searchLink>; Target Discovery Institute, Centre for Medicines Discovery, Nuffield Department of Medicine, University of Oxford, Oxford UK.<br /><searchLink fieldCode="AU" term="%22Kessler+BM%22">Kessler BM</searchLink>; Target Discovery Institute, Centre for Medicines Discovery, Nuffield Department of Medicine, University of Oxford, Oxford UK.<br /><searchLink fieldCode="AU" term="%22Raz+V%22">Raz V</searchLink>; Leiden University Medical Centre, Leiden, Leiden, The Netherlands.
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  Data: <i>Publisher: </i><searchLink fieldCode="PB" term="%22JKL+International%22">JKL International </searchLink><i>Country of Publication: </i>United States <i>NLM ID: </i>101540533 <i>Publication Model: </i>Print-Electronic <i>Cited Medium: </i>Internet <i>ISSN: </i>2152-5250 (Electronic) <i>Linking ISSN: </i><searchLink fieldCode="IS" term="%2221525250%22">21525250 </searchLink><i>NLM ISO Abbreviation: </i>Aging Dis <i>Subsets: </i>MEDLINE
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        Value: 10.14336/AD.2025.0699
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        Text: English
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      – TitleFull: Nuclear Protein Aggregates Disrupt RNA Processing and Alter Biomechanics in a Muscle Cell Model of OPMD.
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            – D: 28
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              Text: 2025 Aug 28
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