Nuclear Protein Aggregates Disrupt RNA Processing and Alter Biomechanics in a Muscle Cell Model of OPMD.
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| Title: | Nuclear Protein Aggregates Disrupt RNA Processing and Alter Biomechanics in a Muscle Cell Model of OPMD. |
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| Authors: | Shademan M; Leiden University Medical Centre, Leiden, Leiden, The Netherlands., Flannery S; Target Discovery Institute, Centre for Medicines Discovery, Nuffield Department of Medicine, University of Oxford, Oxford UK., Bos E; Leiden University Medical Centre, Leiden, Leiden, The Netherlands., Evers TMJ; Medical Systems Biophysics and Bioengineering Laboratory, Leiden Academic Centre for Drug Research, Leiden University, Leiden, the Netherlands., Sheikhhassani V; Medical Systems Biophysics and Bioengineering Laboratory, Leiden Academic Centre for Drug Research, Leiden University, Leiden, the Netherlands., Mashaghi A; Medical Systems Biophysics and Bioengineering Laboratory, Leiden Academic Centre for Drug Research, Leiden University, Leiden, the Netherlands., Kusters B; Radboud University Medical Center, Nijmegen, The Netherlands., van Engelen B; Radboud University Medical Center, Nijmegen, The Netherlands., Sharp TH; School of Biochemistry, Bristol University, Bristol, UK., Fischer R; Target Discovery Institute, Centre for Medicines Discovery, Nuffield Department of Medicine, University of Oxford, Oxford UK., Kessler BM; Target Discovery Institute, Centre for Medicines Discovery, Nuffield Department of Medicine, University of Oxford, Oxford UK., Raz V; Leiden University Medical Centre, Leiden, Leiden, The Netherlands. |
| Source: | Aging and disease [Aging Dis] 2025 Aug 28. Date of Electronic Publication: 2025 Aug 28. |
| Publication Type: | Journal Article |
| Journal Info: | Publisher: JKL International Country of Publication: United States NLM ID: 101540533 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 2152-5250 (Electronic) Linking ISSN: 21525250 NLM ISO Abbreviation: Aging Dis Subsets: MEDLINE |
| Database: | MEDLINE Ultimate |
| FullText | Text: Availability: 0 |
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| Header | DbId: mdl DbLabel: MEDLINE Ultimate An: 40901980 AccessLevel: 2 PubType: Academic Journal PubTypeId: academicJournal PreciseRelevancyScore: 0 |
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| Items | – Name: Title Label: Title Group: Ti Data: Nuclear Protein Aggregates Disrupt RNA Processing and Alter Biomechanics in a Muscle Cell Model of OPMD. – Name: Author Label: Authors Group: Au Data: <searchLink fieldCode="AU" term="%22Shademan+M%22">Shademan M</searchLink>; Leiden University Medical Centre, Leiden, Leiden, The Netherlands.<br /><searchLink fieldCode="AU" term="%22Flannery+S%22">Flannery S</searchLink>; Target Discovery Institute, Centre for Medicines Discovery, Nuffield Department of Medicine, University of Oxford, Oxford UK.<br /><searchLink fieldCode="AU" term="%22Bos+E%22">Bos E</searchLink>; Leiden University Medical Centre, Leiden, Leiden, The Netherlands.<br /><searchLink fieldCode="AU" term="%22Evers+TMJ%22">Evers TMJ</searchLink>; Medical Systems Biophysics and Bioengineering Laboratory, Leiden Academic Centre for Drug Research, Leiden University, Leiden, the Netherlands.<br /><searchLink fieldCode="AU" term="%22Sheikhhassani+V%22">Sheikhhassani V</searchLink>; Medical Systems Biophysics and Bioengineering Laboratory, Leiden Academic Centre for Drug Research, Leiden University, Leiden, the Netherlands.<br /><searchLink fieldCode="AU" term="%22Mashaghi+A%22">Mashaghi A</searchLink>; Medical Systems Biophysics and Bioengineering Laboratory, Leiden Academic Centre for Drug Research, Leiden University, Leiden, the Netherlands.<br /><searchLink fieldCode="AU" term="%22Kusters+B%22">Kusters B</searchLink>; Radboud University Medical Center, Nijmegen, The Netherlands.<br /><searchLink fieldCode="AU" term="%22van+Engelen+B%22">van Engelen B</searchLink>; Radboud University Medical Center, Nijmegen, The Netherlands.<br /><searchLink fieldCode="AU" term="%22Sharp+TH%22">Sharp TH</searchLink>; School of Biochemistry, Bristol University, Bristol, UK.<br /><searchLink fieldCode="AU" term="%22Fischer+R%22">Fischer R</searchLink>; Target Discovery Institute, Centre for Medicines Discovery, Nuffield Department of Medicine, University of Oxford, Oxford UK.<br /><searchLink fieldCode="AU" term="%22Kessler+BM%22">Kessler BM</searchLink>; Target Discovery Institute, Centre for Medicines Discovery, Nuffield Department of Medicine, University of Oxford, Oxford UK.<br /><searchLink fieldCode="AU" term="%22Raz+V%22">Raz V</searchLink>; Leiden University Medical Centre, Leiden, Leiden, The Netherlands. – Name: TitleSource Label: Source Group: Src Data: <searchLink fieldCode="JN" term="%22101540533%22">Aging and disease</searchLink> [Aging Dis] 2025 Aug 28. <i>Date of Electronic Publication: </i>2025 Aug 28. – Name: TypePub Label: Publication Type Group: TypPub Data: Journal Article – Name: TitleSource Label: Journal Info Group: Src Data: <i>Publisher: </i><searchLink fieldCode="PB" term="%22JKL+International%22">JKL International </searchLink><i>Country of Publication: </i>United States <i>NLM ID: </i>101540533 <i>Publication Model: </i>Print-Electronic <i>Cited Medium: </i>Internet <i>ISSN: </i>2152-5250 (Electronic) <i>Linking ISSN: </i><searchLink fieldCode="IS" term="%2221525250%22">21525250 </searchLink><i>NLM ISO Abbreviation: </i>Aging Dis <i>Subsets: </i>MEDLINE |
| PLink | https://search.ebscohost.com/login.aspx?direct=true&site=eds-live&db=mdl&AN=40901980 |
| RecordInfo | BibRecord: BibEntity: Identifiers: – Type: doi Value: 10.14336/AD.2025.0699 Languages: – Code: eng Text: English Titles: – TitleFull: Nuclear Protein Aggregates Disrupt RNA Processing and Alter Biomechanics in a Muscle Cell Model of OPMD. Type: main BibRelationships: HasContributorRelationships: – PersonEntity: Name: NameFull: Shademan M – PersonEntity: Name: NameFull: Flannery S – PersonEntity: Name: NameFull: Bos E – PersonEntity: Name: NameFull: Evers TMJ – PersonEntity: Name: NameFull: Sheikhhassani V – PersonEntity: Name: NameFull: Mashaghi A – PersonEntity: Name: NameFull: Kusters B – PersonEntity: Name: NameFull: van Engelen B – PersonEntity: Name: NameFull: Sharp TH – PersonEntity: Name: NameFull: Fischer R – PersonEntity: Name: NameFull: Kessler BM – PersonEntity: Name: NameFull: Raz V IsPartOfRelationships: – BibEntity: Dates: – D: 28 M: 08 Text: 2025 Aug 28 Type: published Y: 2025 Identifiers: – Type: issn-electronic Value: 2152-5250 Titles: – TitleFull: Aging and disease Type: main |
| ResultId | 1 |