Generation of mice with combined Hexa Gly269Ser KI or KO and Neu3 KO alleles to create new models of GM2 gangliosidoses.
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| Title: | Generation of mice with combined Hexa Gly269Ser KI or KO and Neu3 KO alleles to create new models of GM2 gangliosidoses. |
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| Authors: | Barker EN; Department of Biochemistry and Medical Genetics, University of Manitoba, Winnipeg, CanadaR3T 2N2., Ashiri M; Department of Biochemistry and Medical Genetics, University of Manitoba, Winnipeg, CanadaR3T 2N2., Saville JT; Genetics and Molecular Pathology, SA Pathology at Women's and Children's Hospital, 72 King William Road, North Adelaide 5006, Australia.; School of Medicine, University of Adelaide, Adelaide 5005, Australia., Hemming R; Department of Biochemistry and Medical Genetics, University of Manitoba, Winnipeg, CanadaR3T 2N2., Furletti N; Department of Biochemistry and Medical Genetics, University of Manitoba, Winnipeg, CanadaR3T 2N2., Dhume SH; Physiology & Pathophysiology, University of Manitoba, Winnipeg, CanadaR3T 2N2.; PrairieNeuro Research Centre, Kleysen Institute for Advanced Medicine, Health Sciences Centre, Winnipeg, CanadaR3E 0Z3., Yu S; Department of Biochemistry and Medical Genetics, University of Manitoba, Winnipeg, CanadaR3T 2N2., Anjos E; Department of Biochemistry and Medical Genetics, University of Manitoba, Winnipeg, CanadaR3T 2N2., Wu X; Department of Biochemistry and Medical Genetics, University of Manitoba, Winnipeg, CanadaR3T 2N2., Fresnoza A; Department of Biochemistry and Medical Genetics, University of Manitoba, Winnipeg, CanadaR3T 2N2., Merz DC; Department of Biochemistry and Medical Genetics, University of Manitoba, Winnipeg, CanadaR3T 2N2., Jackson M; Department of Biochemistry and Medical Genetics, University of Manitoba, Winnipeg, CanadaR3T 2N2., Del Bigio MR; Pathology, University of Manitoba, Winnipeg, CanadaR3T 2N2.; Children's Hospital Research Institute of Manitoba, 715 McDermot Ave, Winnipeg, CanadaR3E 3P4., Siddiqui TJ; Physiology & Pathophysiology, University of Manitoba, Winnipeg, CanadaR3T 2N2.; PrairieNeuro Research Centre, Kleysen Institute for Advanced Medicine, Health Sciences Centre, Winnipeg, CanadaR3E 0Z3.; Children's Hospital Research Institute of Manitoba, 715 McDermot Ave, Winnipeg, CanadaR3E 3P4., Fuller M; Genetics and Molecular Pathology, SA Pathology at Women's and Children's Hospital, 72 King William Road, North Adelaide 5006, Australia.; School of Medicine, University of Adelaide, Adelaide 5005, Australia.; School of Biological Sciences, University of Adelaide, Adelaide 5005, Australia., Mark BL; Department of Biochemistry and Medical Genetics, University of Manitoba, Winnipeg, CanadaR3T 2N2.; Children's Hospital Research Institute of Manitoba, 715 McDermot Ave, Winnipeg, CanadaR3E 3P4.; Department of Microbiology, University of Manitoba, Winnipeg, CanadaR3T 2N2., Triggs-Raine B; Department of Biochemistry and Medical Genetics, University of Manitoba, Winnipeg, CanadaR3T 2N2.; Children's Hospital Research Institute of Manitoba, 715 McDermot Ave, Winnipeg, CanadaR3E 3P4. |
| Source: | Biology open [Biol Open] 2025 Sep 15; Vol. 14 (9). Date of Electronic Publication: 2025 Sep 30. |
| Publication Type: | Journal Article |
| Journal Info: | Publisher: Company of Biologists Ltd Country of Publication: England NLM ID: 101578018 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 2046-6390 (Electronic) Linking ISSN: 20466390 NLM ISO Abbreviation: Biol Open Subsets: MEDLINE |
| Database: | MEDLINE Ultimate |
| FullText | Text: Availability: 0 |
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| Header | DbId: mdl DbLabel: MEDLINE Ultimate An: 40916664 AccessLevel: 2 PubType: Academic Journal PubTypeId: academicJournal PreciseRelevancyScore: 0 |
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| Items | – Name: Title Label: Title Group: Ti Data: Generation of mice with combined Hexa Gly269Ser KI or KO and Neu3 KO alleles to create new models of GM2 gangliosidoses. – Name: Author Label: Authors Group: Au Data: <searchLink fieldCode="AU" term="%22Barker+EN%22">Barker EN</searchLink>; Department of Biochemistry and Medical Genetics, University of Manitoba, Winnipeg, CanadaR3T 2N2.<br /><searchLink fieldCode="AU" term="%22Ashiri+M%22">Ashiri M</searchLink>; Department of Biochemistry and Medical Genetics, University of Manitoba, Winnipeg, CanadaR3T 2N2.<br /><searchLink fieldCode="AU" term="%22Saville+JT%22">Saville JT</searchLink>; Genetics and Molecular Pathology, SA Pathology at Women's and Children's Hospital, 72 King William Road, North Adelaide 5006, Australia.; School of Medicine, University of Adelaide, Adelaide 5005, Australia.<br /><searchLink fieldCode="AU" term="%22Hemming+R%22">Hemming R</searchLink>; Department of Biochemistry and Medical Genetics, University of Manitoba, Winnipeg, CanadaR3T 2N2.<br /><searchLink fieldCode="AU" term="%22Furletti+N%22">Furletti N</searchLink>; Department of Biochemistry and Medical Genetics, University of Manitoba, Winnipeg, CanadaR3T 2N2.<br /><searchLink fieldCode="AU" term="%22Dhume+SH%22">Dhume SH</searchLink>; Physiology & Pathophysiology, University of Manitoba, Winnipeg, CanadaR3T 2N2.; PrairieNeuro Research Centre, Kleysen Institute for Advanced Medicine, Health Sciences Centre, Winnipeg, CanadaR3E 0Z3.<br /><searchLink fieldCode="AU" term="%22Yu+S%22">Yu S</searchLink>; Department of Biochemistry and Medical Genetics, University of Manitoba, Winnipeg, CanadaR3T 2N2.<br /><searchLink fieldCode="AU" term="%22Anjos+E%22">Anjos E</searchLink>; Department of Biochemistry and Medical Genetics, University of Manitoba, Winnipeg, CanadaR3T 2N2.<br /><searchLink fieldCode="AU" term="%22Wu+X%22">Wu X</searchLink>; Department of Biochemistry and Medical Genetics, University of Manitoba, Winnipeg, CanadaR3T 2N2.<br /><searchLink fieldCode="AU" term="%22Fresnoza+A%22">Fresnoza A</searchLink>; Department of Biochemistry and Medical Genetics, University of Manitoba, Winnipeg, CanadaR3T 2N2.<br /><searchLink fieldCode="AU" term="%22Merz+DC%22">Merz DC</searchLink>; Department of Biochemistry and Medical Genetics, University of Manitoba, Winnipeg, CanadaR3T 2N2.<br /><searchLink fieldCode="AU" term="%22Jackson+M%22">Jackson M</searchLink>; Department of Biochemistry and Medical Genetics, University of Manitoba, Winnipeg, CanadaR3T 2N2.<br /><searchLink fieldCode="AU" term="%22Del+Bigio+MR%22">Del Bigio MR</searchLink>; Pathology, University of Manitoba, Winnipeg, CanadaR3T 2N2.; Children's Hospital Research Institute of Manitoba, 715 McDermot Ave, Winnipeg, CanadaR3E 3P4.<br /><searchLink fieldCode="AU" term="%22Siddiqui+TJ%22">Siddiqui TJ</searchLink>; Physiology & Pathophysiology, University of Manitoba, Winnipeg, CanadaR3T 2N2.; PrairieNeuro Research Centre, Kleysen Institute for Advanced Medicine, Health Sciences Centre, Winnipeg, CanadaR3E 0Z3.; Children's Hospital Research Institute of Manitoba, 715 McDermot Ave, Winnipeg, CanadaR3E 3P4.<br /><searchLink fieldCode="AU" term="%22Fuller+M%22">Fuller M</searchLink>; Genetics and Molecular Pathology, SA Pathology at Women's and Children's Hospital, 72 King William Road, North Adelaide 5006, Australia.; School of Medicine, University of Adelaide, Adelaide 5005, Australia.; School of Biological Sciences, University of Adelaide, Adelaide 5005, Australia.<br /><searchLink fieldCode="AU" term="%22Mark+BL%22">Mark BL</searchLink>; Department of Biochemistry and Medical Genetics, University of Manitoba, Winnipeg, CanadaR3T 2N2.; Children's Hospital Research Institute of Manitoba, 715 McDermot Ave, Winnipeg, CanadaR3E 3P4.; Department of Microbiology, University of Manitoba, Winnipeg, CanadaR3T 2N2.<br /><searchLink fieldCode="AU" term="%22Triggs-Raine+B%22">Triggs-Raine B</searchLink>; Department of Biochemistry and Medical Genetics, University of Manitoba, Winnipeg, CanadaR3T 2N2.; Children's Hospital Research Institute of Manitoba, 715 McDermot Ave, Winnipeg, CanadaR3E 3P4. – Name: TitleSource Label: Source Group: Src Data: <searchLink fieldCode="JN" term="%22101578018%22">Biology open</searchLink> [Biol Open] 2025 Sep 15; Vol. 14 (9). <i>Date of Electronic Publication: </i>2025 Sep 30. – Name: TypePub Label: Publication Type Group: TypPub Data: Journal Article – Name: TitleSource Label: Journal Info Group: Src Data: <i>Publisher: </i><searchLink fieldCode="PB" term="%22Company+of+Biologists+Ltd%22">Company of Biologists Ltd </searchLink><i>Country of Publication: </i>England <i>NLM ID: </i>101578018 <i>Publication Model: </i>Print-Electronic <i>Cited Medium: </i>Internet <i>ISSN: </i>2046-6390 (Electronic) <i>Linking ISSN: </i><searchLink fieldCode="IS" term="%2220466390%22">20466390 </searchLink><i>NLM ISO Abbreviation: </i>Biol Open <i>Subsets: </i>MEDLINE |
| PLink | https://search.ebscohost.com/login.aspx?direct=true&site=eds-live&db=mdl&AN=40916664 |
| RecordInfo | BibRecord: BibEntity: Identifiers: – Type: doi Value: 10.1242/bio.062045 Languages: – Code: eng Text: English Titles: – TitleFull: Generation of mice with combined Hexa Gly269Ser KI or KO and Neu3 KO alleles to create new models of GM2 gangliosidoses. Type: main BibRelationships: HasContributorRelationships: – PersonEntity: Name: NameFull: Barker EN – PersonEntity: Name: NameFull: Ashiri M – PersonEntity: Name: NameFull: Saville JT – PersonEntity: Name: NameFull: Hemming R – PersonEntity: Name: NameFull: Furletti N – PersonEntity: Name: NameFull: Dhume SH – PersonEntity: Name: NameFull: Yu S – PersonEntity: Name: NameFull: Anjos E – PersonEntity: Name: NameFull: Wu X – PersonEntity: Name: NameFull: Fresnoza A – PersonEntity: Name: NameFull: Merz DC – PersonEntity: Name: NameFull: Jackson M – PersonEntity: Name: NameFull: Del Bigio MR – PersonEntity: Name: NameFull: Siddiqui TJ – PersonEntity: Name: NameFull: Fuller M – PersonEntity: Name: NameFull: Mark BL – PersonEntity: Name: NameFull: Triggs-Raine B IsPartOfRelationships: – BibEntity: Dates: – D: 15 M: 09 Text: 2025 Sep 15 Type: published Y: 2025 Identifiers: – Type: issn-electronic Value: 2046-6390 Numbering: – Type: volume Value: 14 – Type: issue Value: 9 Titles: – TitleFull: Biology open Type: main |
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