Upper limb progression in Duchenne muscular dystrophy: Insights from a 36-month longitudinal study using the PUL 20.

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Title: Upper limb progression in Duchenne muscular dystrophy: Insights from a 36-month longitudinal study using the PUL 20.
Authors: Coratti G; Pediatric Neurology, Università Cattolica del Sacro Cuore, Rome, Italy.; Centro Clinico Nemo, Neuropsichiatria Infantile, Fondazione Agostino Gemelli IRCCS, Rome, Italy., Pane M; Pediatric Neurology, Università Cattolica del Sacro Cuore, Rome, Italy.; Centro Clinico Nemo, Neuropsichiatria Infantile, Fondazione Agostino Gemelli IRCCS, Rome, Italy., Paolucci S; Centro Clinico Nemo, Neuropsichiatria Infantile, Fondazione Agostino Gemelli IRCCS, Rome, Italy., Bello L; Neurology Unit, Azienda Ospedale Padova Università Padova, Padua, Italy., D'Amico A; Department of Neurosciences, Unit of Neuromuscular and Neurodegenerative Disorders, Bambino Gesù Children's Hospital, IRCCS, Rome, Italy., Berardinelli A; C. Mondino Foundation, Pavia, Italy., Catteruccia M; Department of Neurosciences, Unit of Neuromuscular and Neurodegenerative Disorders, Bambino Gesù Children's Hospital, IRCCS, Rome, Italy., De Luca G; Department of Neurosciences, Unit of Neuromuscular and Neurodegenerative Disorders, Bambino Gesù Children's Hospital, IRCCS, Rome, Italy., Masson R; Developmental Neurology Unit, Fondazione IRCCS Istituto Neurologico Carlo Besta, Milan, Italy., Zanin R; Developmental Neurology Unit, Fondazione IRCCS Istituto Neurologico Carlo Besta, Milan, Italy., Battini R; Department Neuroscience, IRCCS Stella Maris Foundation, Pisa, Italy.; Department Clinical and Experimental Medicine, University of Pisa, Pisa, Italy., Dosi C; Developmental Neurology Unit, Fondazione IRCCS Istituto Neurologico Carlo Besta, Milan, Italy., Frosini S; Department Neuroscience, IRCCS Stella Maris Foundation, Pisa, Italy., Gardani A; C. Mondino Foundation, Pavia, Italy., Buchignani B; Department Neuroscience, IRCCS Stella Maris Foundation, Pisa, Italy.; Department of Translational Research and of New Surgical, Medical Technologies Pisa University, Pisa, Italy., Capasso A; Pediatric Neurology, Università Cattolica del Sacro Cuore, Rome, Italy.; Centro Clinico Nemo, Neuropsichiatria Infantile, Fondazione Agostino Gemelli IRCCS, Rome, Italy., Ricci F; Child Neuropsychiatry Unit, Department of Public Health and Paediatric Sciences, University of Turin, Turin, Italy., Cicala G; Pediatric Neurology, Università Cattolica del Sacro Cuore, Rome, Italy.; Centro Clinico Nemo, Neuropsichiatria Infantile, Fondazione Agostino Gemelli IRCCS, Rome, Italy., Cavallina I; Child Neuropsychiatry Unit, Department of Public Health and Paediatric Sciences, University of Turin, Turin, Italy., Rolle E; Neuromuscular Unit, Department of Neurosciences, University of Turin, Turin, Italy., Mongini TE; Neuromuscular Unit, Department of Neurosciences, University of Turin, Turin, Italy., Sansone VA; Neurorehabilitation Unit, The NEMO Center in Milan, University of Milan, ASST Niguarda Hospital, Milan, Italy., Albamonte E; Neurorehabilitation Unit, The NEMO Center in Milan, University of Milan, ASST Niguarda Hospital, Milan, Italy., Pini A; Pediatric Neuromuscular Unit, IRCCS Institute of the Neurological Sciences of Bologna, Bologna, Italy., Giannotta M; Pediatric Neuromuscular Unit, IRCCS Institute of the Neurological Sciences of Bologna, Bologna, Italy., Panicucci C; Department of Neuroscience, Rehabilitation, Ophtalmology, Genetics, Maternal and Child Health, Center of Translational and Experimental Myology, University of Genova, IRCCS Istituto Giannina Gaslini, Genova, Italy., Not R; Pediatric Neuromuscular Unit, IRCCS Institute of the Neurological Sciences of Bologna, Bologna, Italy., Bruno C; Department of Neuroscience, Rehabilitation, Ophtalmology, Genetics, Maternal and Child Health, Center of Translational and Experimental Myology, University of Genova, IRCCS Istituto Giannina Gaslini, Genova, Italy., Nigro V; Medical Genetics and Cardiomyology Unit, Department of Precision Medicine, Università degli Studi della Campania 'Luigi Vanvitelli', Napoli, Italy.; TIGEM, Pozzuoli, Italy., Picillo E; Medical Genetics and Cardiomyology Unit, Department of Precision Medicine, Università degli Studi della Campania 'Luigi Vanvitelli', Napoli, Italy., Pegoraro E; Neurology Unit, Azienda Ospedale Padova Università Padova, Padua, Italy., Mercuri E; Pediatric Neurology, Università Cattolica del Sacro Cuore, Rome, Italy.; Centro Clinico Nemo, Neuropsichiatria Infantile, Fondazione Agostino Gemelli IRCCS, Rome, Italy.
Corporate Authors: Italian DMD group
Source: Journal of neuromuscular diseases [J Neuromuscul Dis] 2026 May; Vol. 13 (3), pp. 293-303. Date of Electronic Publication: 2025 Sep 18.
Publication Type: Journal Article
Journal Info: Publisher: IOS Press Country of Publication: United States NLM ID: 101649948 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 2214-3602 (Electronic) Linking ISSN: 22143599 NLM ISO Abbreviation: J Neuromuscul Dis Subsets: MEDLINE
Database: MEDLINE Ultimate
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  Data: Upper limb progression in Duchenne muscular dystrophy: Insights from a 36-month longitudinal study using the PUL 20.
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  Data: <searchLink fieldCode="AU" term="%22Coratti+G%22">Coratti G</searchLink>; Pediatric Neurology, Università Cattolica del Sacro Cuore, Rome, Italy.; Centro Clinico Nemo, Neuropsichiatria Infantile, Fondazione Agostino Gemelli IRCCS, Rome, Italy.<br /><searchLink fieldCode="AU" term="%22Pane+M%22">Pane M</searchLink>; Pediatric Neurology, Università Cattolica del Sacro Cuore, Rome, Italy.; Centro Clinico Nemo, Neuropsichiatria Infantile, Fondazione Agostino Gemelli IRCCS, Rome, Italy.<br /><searchLink fieldCode="AU" term="%22Paolucci+S%22">Paolucci S</searchLink>; Centro Clinico Nemo, Neuropsichiatria Infantile, Fondazione Agostino Gemelli IRCCS, Rome, Italy.<br /><searchLink fieldCode="AU" term="%22Bello+L%22">Bello L</searchLink>; Neurology Unit, Azienda Ospedale Padova Università Padova, Padua, Italy.<br /><searchLink fieldCode="AU" term="%22D'Amico+A%22">D'Amico A</searchLink>; Department of Neurosciences, Unit of Neuromuscular and Neurodegenerative Disorders, Bambino Gesù Children's Hospital, IRCCS, Rome, Italy.<br /><searchLink fieldCode="AU" term="%22Berardinelli+A%22">Berardinelli A</searchLink>; C. Mondino Foundation, Pavia, Italy.<br /><searchLink fieldCode="AU" term="%22Catteruccia+M%22">Catteruccia M</searchLink>; Department of Neurosciences, Unit of Neuromuscular and Neurodegenerative Disorders, Bambino Gesù Children's Hospital, IRCCS, Rome, Italy.<br /><searchLink fieldCode="AU" term="%22De+Luca+G%22">De Luca G</searchLink>; Department of Neurosciences, Unit of Neuromuscular and Neurodegenerative Disorders, Bambino Gesù Children's Hospital, IRCCS, Rome, Italy.<br /><searchLink fieldCode="AU" term="%22Masson+R%22">Masson R</searchLink>; Developmental Neurology Unit, Fondazione IRCCS Istituto Neurologico Carlo Besta, Milan, Italy.<br /><searchLink fieldCode="AU" term="%22Zanin+R%22">Zanin R</searchLink>; Developmental Neurology Unit, Fondazione IRCCS Istituto Neurologico Carlo Besta, Milan, Italy.<br /><searchLink fieldCode="AU" term="%22Battini+R%22">Battini R</searchLink>; Department Neuroscience, IRCCS Stella Maris Foundation, Pisa, Italy.; Department Clinical and Experimental Medicine, University of Pisa, Pisa, Italy.<br /><searchLink fieldCode="AU" term="%22Dosi+C%22">Dosi C</searchLink>; Developmental Neurology Unit, Fondazione IRCCS Istituto Neurologico Carlo Besta, Milan, Italy.<br /><searchLink fieldCode="AU" term="%22Frosini+S%22">Frosini S</searchLink>; Department Neuroscience, IRCCS Stella Maris Foundation, Pisa, Italy.<br /><searchLink fieldCode="AU" term="%22Gardani+A%22">Gardani A</searchLink>; C. Mondino Foundation, Pavia, Italy.<br /><searchLink fieldCode="AU" term="%22Buchignani+B%22">Buchignani B</searchLink>; Department Neuroscience, IRCCS Stella Maris Foundation, Pisa, Italy.; Department of Translational Research and of New Surgical, Medical Technologies Pisa University, Pisa, Italy.<br /><searchLink fieldCode="AU" term="%22Capasso+A%22">Capasso A</searchLink>; Pediatric Neurology, Università Cattolica del Sacro Cuore, Rome, Italy.; Centro Clinico Nemo, Neuropsichiatria Infantile, Fondazione Agostino Gemelli IRCCS, Rome, Italy.<br /><searchLink fieldCode="AU" term="%22Ricci+F%22">Ricci F</searchLink>; Child Neuropsychiatry Unit, Department of Public Health and Paediatric Sciences, University of Turin, Turin, Italy.<br /><searchLink fieldCode="AU" term="%22Cicala+G%22">Cicala G</searchLink>; Pediatric Neurology, Università Cattolica del Sacro Cuore, Rome, Italy.; Centro Clinico Nemo, Neuropsichiatria Infantile, Fondazione Agostino Gemelli IRCCS, Rome, Italy.<br /><searchLink fieldCode="AU" term="%22Cavallina+I%22">Cavallina I</searchLink>; Child Neuropsychiatry Unit, Department of Public Health and Paediatric Sciences, University of Turin, Turin, Italy.<br /><searchLink fieldCode="AU" term="%22Rolle+E%22">Rolle E</searchLink>; Neuromuscular Unit, Department of Neurosciences, University of Turin, Turin, Italy.<br /><searchLink fieldCode="AU" term="%22Mongini+TE%22">Mongini TE</searchLink>; Neuromuscular Unit, Department of Neurosciences, University of Turin, Turin, Italy.<br /><searchLink fieldCode="AU" term="%22Sansone+VA%22">Sansone VA</searchLink>; Neurorehabilitation Unit, The NEMO Center in Milan, University of Milan, ASST Niguarda Hospital, Milan, Italy.<br /><searchLink fieldCode="AU" term="%22Albamonte+E%22">Albamonte E</searchLink>; Neurorehabilitation Unit, The NEMO Center in Milan, University of Milan, ASST Niguarda Hospital, Milan, Italy.<br /><searchLink fieldCode="AU" term="%22Pini+A%22">Pini A</searchLink>; Pediatric Neuromuscular Unit, IRCCS Institute of the Neurological Sciences of Bologna, Bologna, Italy.<br /><searchLink fieldCode="AU" term="%22Giannotta+M%22">Giannotta M</searchLink>; Pediatric Neuromuscular Unit, IRCCS Institute of the Neurological Sciences of Bologna, Bologna, Italy.<br /><searchLink fieldCode="AU" term="%22Panicucci+C%22">Panicucci C</searchLink>; Department of Neuroscience, Rehabilitation, Ophtalmology, Genetics, Maternal and Child Health, Center of Translational and Experimental Myology, University of Genova, IRCCS Istituto Giannina Gaslini, Genova, Italy.<br /><searchLink fieldCode="AU" term="%22Not+R%22">Not R</searchLink>; Pediatric Neuromuscular Unit, IRCCS Institute of the Neurological Sciences of Bologna, Bologna, Italy.<br /><searchLink fieldCode="AU" term="%22Bruno+C%22">Bruno C</searchLink>; Department of Neuroscience, Rehabilitation, Ophtalmology, Genetics, Maternal and Child Health, Center of Translational and Experimental Myology, University of Genova, IRCCS Istituto Giannina Gaslini, Genova, Italy.<br /><searchLink fieldCode="AU" term="%22Nigro+V%22">Nigro V</searchLink>; Medical Genetics and Cardiomyology Unit, Department of Precision Medicine, Università degli Studi della Campania 'Luigi Vanvitelli', Napoli, Italy.; TIGEM, Pozzuoli, Italy.<br /><searchLink fieldCode="AU" term="%22Picillo+E%22">Picillo E</searchLink>; Medical Genetics and Cardiomyology Unit, Department of Precision Medicine, Università degli Studi della Campania 'Luigi Vanvitelli', Napoli, Italy.<br /><searchLink fieldCode="AU" term="%22Pegoraro+E%22">Pegoraro E</searchLink>; Neurology Unit, Azienda Ospedale Padova Università Padova, Padua, Italy.<br /><searchLink fieldCode="AU" term="%22Mercuri+E%22">Mercuri E</searchLink>; Pediatric Neurology, Università Cattolica del Sacro Cuore, Rome, Italy.; Centro Clinico Nemo, Neuropsichiatria Infantile, Fondazione Agostino Gemelli IRCCS, Rome, Italy.
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