Characteristics, treatment and lung function outcomes of pulmonary exacerbations in cystic fibrosis: insights from the BEAT-CF cohort.

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Title: Characteristics, treatment and lung function outcomes of pulmonary exacerbations in cystic fibrosis: insights from the BEAT-CF cohort.
Authors: Fathima P; Health and Clinical Analytics, Sydney School of Public Health, The University of Sydney, Sydney, Australia parveen.fathima@sydney.edu.au.; Wesfarmers Centre of Vaccines and Infectious Diseases, The Kids Research Institute Australia, Perth, Australia.; Sydney Institute of Infectious Diseases (Sydney ID), Sydney, Australia., Pan E; Wesfarmers Centre of Vaccines and Infectious Diseases, The Kids Research Institute Australia, Perth, Australia., Marsh J; Wesfarmers Centre of Vaccines and Infectious Diseases, The Kids Research Institute Australia, Perth, Australia., Shanthikumar S; Infection, Immunity and Global Health Theme, Murdoch Children's Research Institute, Royal Children's Hospital, Melbourne, Australia.; Department of Paediatrics, The University of Melbourne, Melbourne, Australia.; Respiratory and Sleep Medicine, Royal Children's Hospital, Melbourne, Australia., Sivam S; Royal Prince Alfred Hospital, The University of Sydney, Sydney, Australia., Jaffe A; School of Clinical Medicine, The University of New South Wales, Randwick, Australia.; Sydney Children's Hospital Network, Randwick, Australia., Selvadurai H; The Children's Hospital, Westmead, Australia.; Discipline of Paediatrics and Child Health, The University of Sydney, Sydney, Australia., Khatami A; The Children's Hospital, Westmead, Australia.; Discipline of Paediatrics and Child Health, The University of Sydney, Sydney, Australia., Jayasuriya G; The Children's Hospital, Westmead, Australia.; Respiratory and Sleep Medicine, John Hunter Children's Hospital, Newcastle, Australia., Norman R; School of Population Health, Curtin University, Perth, Australia., Tai A; Department of Paediatric Respiratory and Sleep Medicine, Women's and Children's Hospital, Adelaide, Australia.; Adelaide Medical School, The University of Adelaide, Adelaide, Australia., Burr L; Department of Respiratory and Sleep Medicine, Mater Health, South Brisbane, Australia.; Mater Research, The University of Queensland, Brisbane, Australia., Mulrennan S; Department of Respiratory Medicine, Sir Charles Gairdner Hospital, Nedlands, Australia.; Institute for Respiratory Health, Perth, Australia.; UWA Medical School, The University of Western Australia, Perth, Australia., Snelling T; Health and Clinical Analytics, Sydney School of Public Health, The University of Sydney, Sydney, Australia.; Wesfarmers Centre of Vaccines and Infectious Diseases, The Kids Research Institute Australia, Perth, Australia.; Sydney Institute of Infectious Diseases (Sydney ID), Sydney, Australia.; Joint senior authors., Schultz A; Walyan Respiratory Research Centre, The Kids Research Institute Australia, The University of Western Australia, Perth, Australia.; Department of Respiratory and Sleep Medicine, Perth Children's Hospital, Perth, Australia.; Joint senior authors.
Source: The European respiratory journal [Eur Respir J] 2026 Jan 08; Vol. 67 (1). Date of Electronic Publication: 2026 Jan 08 (Print Publication: 2026).
Publication Type: Journal Article; Multicenter Study
Journal Info: Publisher: European Respiratory Society Country of Publication: England NLM ID: 8803460 Publication Model: Electronic-Print Cited Medium: Internet ISSN: 1399-3003 (Electronic) Linking ISSN: 09031936 NLM ISO Abbreviation: Eur Respir J Subsets: MEDLINE
Database: MEDLINE Ultimate
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  Data: Characteristics, treatment and lung function outcomes of pulmonary exacerbations in cystic fibrosis: insights from the BEAT-CF cohort.
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  Data: <searchLink fieldCode="AU" term="%22Fathima+P%22">Fathima P</searchLink>; Health and Clinical Analytics, Sydney School of Public Health, The University of Sydney, Sydney, Australia parveen.fathima@sydney.edu.au.; Wesfarmers Centre of Vaccines and Infectious Diseases, The Kids Research Institute Australia, Perth, Australia.; Sydney Institute of Infectious Diseases (Sydney ID), Sydney, Australia.<br /><searchLink fieldCode="AU" term="%22Pan+E%22">Pan E</searchLink>; Wesfarmers Centre of Vaccines and Infectious Diseases, The Kids Research Institute Australia, Perth, Australia.<br /><searchLink fieldCode="AU" term="%22Marsh+J%22">Marsh J</searchLink>; Wesfarmers Centre of Vaccines and Infectious Diseases, The Kids Research Institute Australia, Perth, Australia.<br /><searchLink fieldCode="AU" term="%22Shanthikumar+S%22">Shanthikumar S</searchLink>; Infection, Immunity and Global Health Theme, Murdoch Children's Research Institute, Royal Children's Hospital, Melbourne, Australia.; Department of Paediatrics, The University of Melbourne, Melbourne, Australia.; Respiratory and Sleep Medicine, Royal Children's Hospital, Melbourne, Australia.<br /><searchLink fieldCode="AU" term="%22Sivam+S%22">Sivam S</searchLink>; Royal Prince Alfred Hospital, The University of Sydney, Sydney, Australia.<br /><searchLink fieldCode="AU" term="%22Jaffe+A%22">Jaffe A</searchLink>; School of Clinical Medicine, The University of New South Wales, Randwick, Australia.; Sydney Children's Hospital Network, Randwick, Australia.<br /><searchLink fieldCode="AU" term="%22Selvadurai+H%22">Selvadurai H</searchLink>; The Children's Hospital, Westmead, Australia.; Discipline of Paediatrics and Child Health, The University of Sydney, Sydney, Australia.<br /><searchLink fieldCode="AU" term="%22Khatami+A%22">Khatami A</searchLink>; The Children's Hospital, Westmead, Australia.; Discipline of Paediatrics and Child Health, The University of Sydney, Sydney, Australia.<br /><searchLink fieldCode="AU" term="%22Jayasuriya+G%22">Jayasuriya G</searchLink>; The Children's Hospital, Westmead, Australia.; Respiratory and Sleep Medicine, John Hunter Children's Hospital, Newcastle, Australia.<br /><searchLink fieldCode="AU" term="%22Norman+R%22">Norman R</searchLink>; School of Population Health, Curtin University, Perth, Australia.<br /><searchLink fieldCode="AU" term="%22Tai+A%22">Tai A</searchLink>; Department of Paediatric Respiratory and Sleep Medicine, Women's and Children's Hospital, Adelaide, Australia.; Adelaide Medical School, The University of Adelaide, Adelaide, Australia.<br /><searchLink fieldCode="AU" term="%22Burr+L%22">Burr L</searchLink>; Department of Respiratory and Sleep Medicine, Mater Health, South Brisbane, Australia.; Mater Research, The University of Queensland, Brisbane, Australia.<br /><searchLink fieldCode="AU" term="%22Mulrennan+S%22">Mulrennan S</searchLink>; Department of Respiratory Medicine, Sir Charles Gairdner Hospital, Nedlands, Australia.; Institute for Respiratory Health, Perth, Australia.; UWA Medical School, The University of Western Australia, Perth, Australia.<br /><searchLink fieldCode="AU" term="%22Snelling+T%22">Snelling T</searchLink>; Health and Clinical Analytics, Sydney School of Public Health, The University of Sydney, Sydney, Australia.; Wesfarmers Centre of Vaccines and Infectious Diseases, The Kids Research Institute Australia, Perth, Australia.; Sydney Institute of Infectious Diseases (Sydney ID), Sydney, Australia.; Joint senior authors.<br /><searchLink fieldCode="AU" term="%22Schultz+A%22">Schultz A</searchLink>; Walyan Respiratory Research Centre, The Kids Research Institute Australia, The University of Western Australia, Perth, Australia.; Department of Respiratory and Sleep Medicine, Perth Children's Hospital, Perth, Australia.; Joint senior authors.
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  Data: <searchLink fieldCode="JN" term="%228803460%22">The European respiratory journal</searchLink> [Eur Respir J] 2026 Jan 08; Vol. 67 (1). <i>Date of Electronic Publication: </i>2026 Jan 08 (<i>Print Publication: </i>2026).
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  Data: <i>Publisher: </i><searchLink fieldCode="PB" term="%22European+Respiratory+Society%22">European Respiratory Society </searchLink><i>Country of Publication: </i>England <i>NLM ID: </i>8803460 <i>Publication Model: </i>Electronic-Print <i>Cited Medium: </i>Internet <i>ISSN: </i>1399-3003 (Electronic) <i>Linking ISSN: </i><searchLink fieldCode="IS" term="%2209031936%22">09031936 </searchLink><i>NLM ISO Abbreviation: </i>Eur Respir J <i>Subsets: </i>MEDLINE
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        Value: 10.1183/13993003.01349-2025
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        Text: English
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      – TitleFull: Characteristics, treatment and lung function outcomes of pulmonary exacerbations in cystic fibrosis: insights from the BEAT-CF cohort.
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              Text: 2026 Jan 08
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