From Biogenesis to Breakdown: How Protein Biogenesis and Quality Control Failures Drive Mitochondrial Disease.

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Title: From Biogenesis to Breakdown: How Protein Biogenesis and Quality Control Failures Drive Mitochondrial Disease.
Authors: Leeming PJ; Department of Biochemistry and Pharmacology, The University of Melbourne, Parkville, Victoria, Australia.; The Bio21 Molecular Science and Biotechnology Institute, The University of Melbourne, Parkville, Victoria, Australia., Mercuri-Svik J; Department of Biochemistry and Pharmacology, The University of Melbourne, Parkville, Victoria, Australia.; The Bio21 Molecular Science and Biotechnology Institute, The University of Melbourne, Parkville, Victoria, Australia., Stojanovski D; Department of Biochemistry and Pharmacology, The University of Melbourne, Parkville, Victoria, Australia.; The Bio21 Molecular Science and Biotechnology Institute, The University of Melbourne, Parkville, Victoria, Australia.
Source: Molecular and cellular biology [Mol Cell Biol] 2026 Jan; Vol. 46 (1), pp. 21-47. Date of Electronic Publication: 2025 Oct 17.
Publication Type: Journal Article; Review
Journal Info: Publisher: Taylor & Francis Country of Publication: United States NLM ID: 8109087 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1098-5549 (Electronic) Linking ISSN: 02707306 NLM ISO Abbreviation: Mol Cell Biol Subsets: MEDLINE
Database: MEDLINE Ultimate
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ISSN:1098-5549
DOI:10.1080/10985549.2025.2566671