From Biogenesis to Breakdown: How Protein Biogenesis and Quality Control Failures Drive Mitochondrial Disease.
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| Title: | From Biogenesis to Breakdown: How Protein Biogenesis and Quality Control Failures Drive Mitochondrial Disease. |
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| Authors: | Leeming PJ; Department of Biochemistry and Pharmacology, The University of Melbourne, Parkville, Victoria, Australia.; The Bio21 Molecular Science and Biotechnology Institute, The University of Melbourne, Parkville, Victoria, Australia., Mercuri-Svik J; Department of Biochemistry and Pharmacology, The University of Melbourne, Parkville, Victoria, Australia.; The Bio21 Molecular Science and Biotechnology Institute, The University of Melbourne, Parkville, Victoria, Australia., Stojanovski D; Department of Biochemistry and Pharmacology, The University of Melbourne, Parkville, Victoria, Australia.; The Bio21 Molecular Science and Biotechnology Institute, The University of Melbourne, Parkville, Victoria, Australia. |
| Source: | Molecular and cellular biology [Mol Cell Biol] 2026 Jan; Vol. 46 (1), pp. 21-47. Date of Electronic Publication: 2025 Oct 17. |
| Publication Type: | Journal Article; Review |
| Journal Info: | Publisher: Taylor & Francis Country of Publication: United States NLM ID: 8109087 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1098-5549 (Electronic) Linking ISSN: 02707306 NLM ISO Abbreviation: Mol Cell Biol Subsets: MEDLINE |
| Database: | MEDLINE Ultimate |
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| FullText | Links: – Type: pdflink Text: Availability: 1 |
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| Header | DbId: mdl DbLabel: MEDLINE Ultimate An: 41105521 AccessLevel: 2 PubType: Academic Journal PubTypeId: academicJournal PreciseRelevancyScore: 0 |
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| Items | – Name: Title Label: Title Group: Ti Data: From Biogenesis to Breakdown: How Protein Biogenesis and Quality Control Failures Drive Mitochondrial Disease. – Name: Author Label: Authors Group: Au Data: <searchLink fieldCode="AU" term="%22Leeming+PJ%22">Leeming PJ</searchLink>; Department of Biochemistry and Pharmacology, The University of Melbourne, Parkville, Victoria, Australia.; The Bio21 Molecular Science and Biotechnology Institute, The University of Melbourne, Parkville, Victoria, Australia.<br /><searchLink fieldCode="AU" term="%22Mercuri-Svik+J%22">Mercuri-Svik J</searchLink>; Department of Biochemistry and Pharmacology, The University of Melbourne, Parkville, Victoria, Australia.; The Bio21 Molecular Science and Biotechnology Institute, The University of Melbourne, Parkville, Victoria, Australia.<br /><searchLink fieldCode="AU" term="%22Stojanovski+D%22">Stojanovski D</searchLink>; Department of Biochemistry and Pharmacology, The University of Melbourne, Parkville, Victoria, Australia.; The Bio21 Molecular Science and Biotechnology Institute, The University of Melbourne, Parkville, Victoria, Australia. – Name: TitleSource Label: Source Group: Src Data: <searchLink fieldCode="JN" term="%228109087%22">Molecular and cellular biology</searchLink> [Mol Cell Biol] 2026 Jan; Vol. 46 (1), pp. 21-47. <i>Date of Electronic Publication: </i>2025 Oct 17. – Name: TypePub Label: Publication Type Group: TypPub Data: Journal Article; Review – Name: TitleSource Label: Journal Info Group: Src Data: <i>Publisher: </i><searchLink fieldCode="PB" term="%22Taylor+%26+Francis%22">Taylor & Francis </searchLink><i>Country of Publication: </i>United States <i>NLM ID: </i>8109087 <i>Publication Model: </i>Print-Electronic <i>Cited Medium: </i>Internet <i>ISSN: </i>1098-5549 (Electronic) <i>Linking ISSN: </i><searchLink fieldCode="IS" term="%2202707306%22">02707306 </searchLink><i>NLM ISO Abbreviation: </i>Mol Cell Biol <i>Subsets: </i>MEDLINE |
| PLink | https://search.ebscohost.com/login.aspx?direct=true&site=eds-live&db=mdl&AN=41105521 |
| RecordInfo | BibRecord: BibEntity: Identifiers: – Type: doi Value: 10.1080/10985549.2025.2566671 Languages: – Code: eng Text: English PhysicalDescription: Pagination: StartPage: 21 Titles: – TitleFull: From Biogenesis to Breakdown: How Protein Biogenesis and Quality Control Failures Drive Mitochondrial Disease. Type: main BibRelationships: HasContributorRelationships: – PersonEntity: Name: NameFull: Leeming PJ – PersonEntity: Name: NameFull: Mercuri-Svik J – PersonEntity: Name: NameFull: Stojanovski D IsPartOfRelationships: – BibEntity: Dates: – D: 01 M: 01 Text: 2026 Jan Type: published Y: 2026 Identifiers: – Type: issn-electronic Value: 1098-5549 Numbering: – Type: volume Value: 46 – Type: issue Value: 1 Titles: – TitleFull: Molecular and cellular biology Type: main |
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