View in EDS HTML Full Text PDF Full Text

Beyond Trikafta: new models to assess tissue dependent rescue of N1303K-CFTR.

Saved in:
Bibliographic Details
Title: Beyond Trikafta: new models to assess tissue dependent rescue of N1303K-CFTR.
Authors: Pranke I; INSERM, CNRS, Institut Necker Enfants Malades, Paris, France.; Université Paris-Cité, Paris, France., Capurro V; UOC Genetica Medica, IRCCS Istituto Giannina Gaslini, Genova, Italy., Chevalier B; INSERM, CNRS, Institut Necker Enfants Malades, Paris, France.; Université Paris-Cité, Paris, France., Pesce E; UOC Genetica Medica, IRCCS Istituto Giannina Gaslini, Genova, Italy., Tomati V; UOC Genetica Medica, IRCCS Istituto Giannina Gaslini, Genova, Italy., Pastorino C; UOC Genetica Medica, IRCCS Istituto Giannina Gaslini, Genova, Italy., Kelly-Aubert M; INSERM, CNRS, Institut Necker Enfants Malades, Paris, France.; Université Paris-Cité, Paris, France., Hatton A; INSERM, CNRS, Institut Necker Enfants Malades, Paris, France.; Université Paris-Cité, Paris, France., Dreano E; INSERM, CNRS, Institut Necker Enfants Malades, Paris, France.; Université Paris-Cité, Paris, France., Lena M; UOC Genetica Medica, IRCCS Istituto Giannina Gaslini, Genova, Italy.; Department of Neurosciences, Rehabilitation, Ophthalmology, Genetics, Maternal and Child Health (DINOGMI), University of Genoa, Genova, Italy., Bocciardi R; UOC Genetica Medica, IRCCS Istituto Giannina Gaslini, Genova, Italy.; Department of Neurosciences, Rehabilitation, Ophthalmology, Genetics, Maternal and Child Health (DINOGMI), University of Genoa, Genova, Italy., Zara F; UOC Genetica Medica, IRCCS Istituto Giannina Gaslini, Genova, Italy.; Department of Neurosciences, Rehabilitation, Ophthalmology, Genetics, Maternal and Child Health (DINOGMI), University of Genoa, Genova, Italy., Pantano S; UOSD CRR Fibrosi Cistica, Atri, Italy., Terlizzi V; Department of Pediatric Medicine, Meyer Children's Hospital IRCCS, Cystic Fibrosis Regional Reference Center, Florence, Italy., Lucanto C; Centro Hub Fibrosi Cistica, Azienda Ospedaliera Universitaria Policlinico G. Martino, Messina, Italy., Costa S; Department of Pediatrics, University Hospital 'G Martino', Messina, Italy., Claut L; Department of Pediatrics, Cystic Fibrosis Center, Fondazione IRCCS Ca' Granda, Ospedale Maggiore Policlinico, Milan, Italy., Daccò V; Department of Pediatrics, Cystic Fibrosis Center, Fondazione IRCCS Ca' Granda, Ospedale Maggiore Policlinico, Milan, Italy., Poli P; Department of Pediatrics, Cystic Fibrosis Regional Support Center, University of Brescia, ASST Spedali Civili Brescia, Brescia, Italy., Maschio M; Institute for Maternal and Child Health-IRCCS 'Burlo Garofolo', Trieste, Italy., Fabrizzi B; Cystic Fibrosis Regional Centre, Unit of Emerging and Immunosuppressed Infectious Diseases, Department of Gastroenterology and Transplantation, Azienda, Italy.; Ospedaliero-Universitaria 'Ospedali Riuniti', Ancona, Italy., Caporelli N; Cystic Fibrosis Regional Centre, Unit of Emerging and Immunosuppressed Infectious Diseases, Department of Gastroenterology and Transplantation, Azienda, Italy.; Ospedaliero-Universitaria 'Ospedali Riuniti', Ancona, Italy., Cipolli M; Cystic Fibrosis Center of Verona, Azienda Ospedaliera Universitaria Integrata, Verona, Italy., Volpi S; Cystic Fibrosis Center of Verona, Azienda Ospedaliera Universitaria Integrata, Verona, Italy., Chedevergne F; Cystic Fibrosis National Pediatric Reference Center, Pneumo-Allergologie Pédiatrique, Hôpital Necker Enfants Malades, AP-HP, Paris, France., Cosson L; Centre de Ressources et de Compétence de la Mucoviscidose Enfants, Hôpital de Clocheville, Tours, France., Macey J; Centre de Ressources et de Compétence de la Mucoviscidose, CHU Pellegrin, Bordeaux, France., Ramel S; Centre de Ressources et de Compétence de la Mucoviscidose Adulte, Centre de Perharidy, Roscoff, France., Weiss L; Centre de Ressources et de Compétence de la Mucoviscidose Pédiatrique, CHU, Strasbourg, France., Grenet D; Centre de Ressources et de Compétence de la Mucoviscidose, Hôpital Foch, Suresnes, France., Le Clainche-Viala L; Centre de Ressources et de Compétence de la Mucoviscidose Pédiatrique, Hôpital Robert Debré, Paris, France., Douvry B; Centre de Ressources et de Compétence de la Mucoviscidose Mixte, CHIC, Créteil, France., Ravoninjatovo B; Centre de Ressources et de Compétence de la Mucoviscidose, American Memoral Hospital, Reims, France., Audousset C; Centre de Ressources et de Compétence de la Mucoviscidose, Institut Cœur Poumons, Lille, France., Tatopoulos A; CHU de Nancy - Hôpitaux de Brabois, Nancy, France., Richaud-Thiriez B; Centre de Ressources et de Compétence de la Mucoviscidose Adulte, Centre Hospitalier Jean Minjoz, Besancon, France., Baravalle M; Centre de Ressources et de Compétence de la Mucoviscidose Enfants, Hôpital d'Enfants de la Timone, Marseille, France., Thouvenin G; Centre de Ressources et de Compétence de la Mucoviscidose Enfants, Hôpital Trousseau, Paris, France., Labbé G; Centre de Ressources et de Compétence de la Mucoviscidose, CHU Estaing, Clermont-Ferrand, France., Mittaine M; Centre de ressources et de compétences pour la mucoviscidose, Hôpital des enfants, CHU Toulouse, Toulouse, France., Reix P; Centre de Ressources et de Compétence de la Mucoviscidose Pédiatrique, Hospices Civils de Lyon, Bron, France., Durieu I; Centre de Référence Adulte de la Mucoviscidose, Hospices Civils de Lyon, Université de Lyon, Lyon, France., Mankikian J; Centre hospitalier régional universitaire Bretonneau, Tours, France., Bui S; Université de Bordeaux, CRCM pédiatrique, center de Recherche Cardio-thoracique de Bordeaux, INSERM U1045, Bordeaux Imaging Center, Bordeaux, France., Nguyen-Khoa T; INSERM, CNRS, Institut Necker Enfants Malades, Paris, France.; Université Paris-Cité, Paris, France.; Laboratory of Biochemistry, Hôpital Universitaire Necker Enfants Malades AP-HP Centre, Paris, France., Khoukh K; Pharmacie Delpech, Paris, France., Martin C; Institut Cochin, Inserm U1016, Paris, France.; Respiratory Medicine and Cystic Fibrosis National Reference Center, Hôpital Cochin, AP-HP. Centre Université Paris Cité, Paris, France.; ERN-Lung CF network, Frankfurt, Germany., Da Silva J; Respiratory Medicine and Cystic Fibrosis National Reference Center, Hôpital Cochin, AP-HP. Centre Université Paris Cité, Paris, France.; ERN-Lung CF network, Frankfurt, Germany., De Carli P; Vaincre La Mucoviscidose, Paris, France., Castellani C; IRCCS IstitutoGianninaGaslini, CysticFibrosis Center, Genoa, Italy., Cresta F; IRCCS IstitutoGianninaGaslini, CysticFibrosis Center, Genoa, Italy., Galietta L; Telethon Institute of Genetics and Medicine (TIGEM), Pozzuoli, Italy., Guillemaut A; Centre de ressources et de compétences pour la mucoviscidose Adultes, Centre hospitalier régional universitaire de Nancy, Vandœuvre-Lès-Nancy, France., Girodon E; INSERM, CNRS, Institut Necker Enfants Malades, Paris, France.; Université Paris-Cité, Paris, France.; Service de Médecine Génomique des Maladies de Système et d'Organe, Hôpital Cochin, Paris, France., Remus N; Centre de Ressources et de Compétence de la Mucoviscidose Mixte, CHIC, Créteil, France., Bulcaen M; Laboratory of Respiratory Diseases and Thoracic Surgery, KU Leuven, Belgium., Ensinck M; Laboratory of Respiratory Diseases and Thoracic Surgery, KU Leuven, Belgium., Zajac M; Department of Physics and Biophysics, Institute of Biology, Warsaw University of Life Sciences, Warsaw, Poland., Carlon M; Laboratory of Respiratory Diseases and Thoracic Surgery, KU Leuven, Belgium., LeBihan J; Centre de Ressources et de Compétence de la Mucoviscidose Adulte, Centre de Perharidy, Roscoff, France., Burgel PR; Université Paris-Cité, Paris, France.; Institut Cochin, Inserm U1016, Paris, France.; Respiratory Medicine and Cystic Fibrosis National Reference Center, Hôpital Cochin, AP-HP. Centre Université Paris Cité, Paris, France.; ERN-Lung CF network, Frankfurt, Germany., Sermet-Gaudelus I; INSERM, CNRS, Institut Necker Enfants Malades, Paris, France.; Université Paris-Cité, Paris, France.; Cystic Fibrosis National Pediatric Reference Center, Pneumo-Allergologie Pédiatrique, Hôpital Necker Enfants Malades, AP-HP, Paris, France.; ERN-Lung CF network, Frankfurt, Germany., Hinzpeter A; INSERM, CNRS, Institut Necker Enfants Malades, Paris, France.; Université Paris-Cité, Paris, France., Pedemonte N; UOC Genetica Medica, IRCCS Istituto Giannina Gaslini, Genova, Italy.
Source: Frontiers in pharmacology [Front Pharmacol] 2025 Oct 29; Vol. 16, pp. 1661417. Date of Electronic Publication: 2025 Oct 29 (Print Publication: 2025).
Publication Type: Journal Article
Journal Info: Publisher: Frontiers Media] Country of Publication: Switzerland NLM ID: 101548923 Publication Model: eCollection Cited Medium: Print ISSN: 1663-9812 (Print) Linking ISSN: 16639812 NLM ISO Abbreviation: Front Pharmacol Subsets: PubMed not MEDLINE
Database: MEDLINE Ultimate
Full text is not displayed to guests.
FullText Links:
  – Type: pdflink
Text:
  Availability: 1
Header DbId: mdl
DbLabel: MEDLINE Ultimate
An: 41235117
AccessLevel: 2
PubType: Academic Journal
PubTypeId: academicJournal
PreciseRelevancyScore: 0
IllustrationInfo
Items – Name: Title
  Label: Title
  Group: Ti
  Data: Beyond Trikafta: new models to assess tissue dependent rescue of N1303K-CFTR.
– Name: Author
  Label: Authors
  Group: Au
  Data: <searchLink fieldCode="AU" term="%22Pranke+I%22">Pranke I</searchLink>; INSERM, CNRS, Institut Necker Enfants Malades, Paris, France.; Université Paris-Cité, Paris, France.<br /><searchLink fieldCode="AU" term="%22Capurro+V%22">Capurro V</searchLink>; UOC Genetica Medica, IRCCS Istituto Giannina Gaslini, Genova, Italy.<br /><searchLink fieldCode="AU" term="%22Chevalier+B%22">Chevalier B</searchLink>; INSERM, CNRS, Institut Necker Enfants Malades, Paris, France.; Université Paris-Cité, Paris, France.<br /><searchLink fieldCode="AU" term="%22Pesce+E%22">Pesce E</searchLink>; UOC Genetica Medica, IRCCS Istituto Giannina Gaslini, Genova, Italy.<br /><searchLink fieldCode="AU" term="%22Tomati+V%22">Tomati V</searchLink>; UOC Genetica Medica, IRCCS Istituto Giannina Gaslini, Genova, Italy.<br /><searchLink fieldCode="AU" term="%22Pastorino+C%22">Pastorino C</searchLink>; UOC Genetica Medica, IRCCS Istituto Giannina Gaslini, Genova, Italy.<br /><searchLink fieldCode="AU" term="%22Kelly-Aubert+M%22">Kelly-Aubert M</searchLink>; INSERM, CNRS, Institut Necker Enfants Malades, Paris, France.; Université Paris-Cité, Paris, France.<br /><searchLink fieldCode="AU" term="%22Hatton+A%22">Hatton A</searchLink>; INSERM, CNRS, Institut Necker Enfants Malades, Paris, France.; Université Paris-Cité, Paris, France.<br /><searchLink fieldCode="AU" term="%22Dreano+E%22">Dreano E</searchLink>; INSERM, CNRS, Institut Necker Enfants Malades, Paris, France.; Université Paris-Cité, Paris, France.<br /><searchLink fieldCode="AU" term="%22Lena+M%22">Lena M</searchLink>; UOC Genetica Medica, IRCCS Istituto Giannina Gaslini, Genova, Italy.; Department of Neurosciences, Rehabilitation, Ophthalmology, Genetics, Maternal and Child Health (DINOGMI), University of Genoa, Genova, Italy.<br /><searchLink fieldCode="AU" term="%22Bocciardi+R%22">Bocciardi R</searchLink>; UOC Genetica Medica, IRCCS Istituto Giannina Gaslini, Genova, Italy.; Department of Neurosciences, Rehabilitation, Ophthalmology, Genetics, Maternal and Child Health (DINOGMI), University of Genoa, Genova, Italy.<br /><searchLink fieldCode="AU" term="%22Zara+F%22">Zara F</searchLink>; UOC Genetica Medica, IRCCS Istituto Giannina Gaslini, Genova, Italy.; Department of Neurosciences, Rehabilitation, Ophthalmology, Genetics, Maternal and Child Health (DINOGMI), University of Genoa, Genova, Italy.<br /><searchLink fieldCode="AU" term="%22Pantano+S%22">Pantano S</searchLink>; UOSD CRR Fibrosi Cistica, Atri, Italy.<br /><searchLink fieldCode="AU" term="%22Terlizzi+V%22">Terlizzi V</searchLink>; Department of Pediatric Medicine, Meyer Children's Hospital IRCCS, Cystic Fibrosis Regional Reference Center, Florence, Italy.<br /><searchLink fieldCode="AU" term="%22Lucanto+C%22">Lucanto C</searchLink>; Centro Hub Fibrosi Cistica, Azienda Ospedaliera Universitaria Policlinico G. Martino, Messina, Italy.<br /><searchLink fieldCode="AU" term="%22Costa+S%22">Costa S</searchLink>; Department of Pediatrics, University Hospital 'G Martino', Messina, Italy.<br /><searchLink fieldCode="AU" term="%22Claut+L%22">Claut L</searchLink>; Department of Pediatrics, Cystic Fibrosis Center, Fondazione IRCCS Ca' Granda, Ospedale Maggiore Policlinico, Milan, Italy.<br /><searchLink fieldCode="AU" term="%22Daccò+V%22">Daccò V</searchLink>; Department of Pediatrics, Cystic Fibrosis Center, Fondazione IRCCS Ca' Granda, Ospedale Maggiore Policlinico, Milan, Italy.<br /><searchLink fieldCode="AU" term="%22Poli+P%22">Poli P</searchLink>; Department of Pediatrics, Cystic Fibrosis Regional Support Center, University of Brescia, ASST Spedali Civili Brescia, Brescia, Italy.<br /><searchLink fieldCode="AU" term="%22Maschio+M%22">Maschio M</searchLink>; Institute for Maternal and Child Health-IRCCS 'Burlo Garofolo', Trieste, Italy.<br /><searchLink fieldCode="AU" term="%22Fabrizzi+B%22">Fabrizzi B</searchLink>; Cystic Fibrosis Regional Centre, Unit of Emerging and Immunosuppressed Infectious Diseases, Department of Gastroenterology and Transplantation, Azienda, Italy.; Ospedaliero-Universitaria 'Ospedali Riuniti', Ancona, Italy.<br /><searchLink fieldCode="AU" term="%22Caporelli+N%22">Caporelli N</searchLink>; Cystic Fibrosis Regional Centre, Unit of Emerging and Immunosuppressed Infectious Diseases, Department of Gastroenterology and Transplantation, Azienda, Italy.; Ospedaliero-Universitaria 'Ospedali Riuniti', Ancona, Italy.<br /><searchLink fieldCode="AU" term="%22Cipolli+M%22">Cipolli M</searchLink>; Cystic Fibrosis Center of Verona, Azienda Ospedaliera Universitaria Integrata, Verona, Italy.<br /><searchLink fieldCode="AU" term="%22Volpi+S%22">Volpi S</searchLink>; Cystic Fibrosis Center of Verona, Azienda Ospedaliera Universitaria Integrata, Verona, Italy.<br /><searchLink fieldCode="AU" term="%22Chedevergne+F%22">Chedevergne F</searchLink>; Cystic Fibrosis National Pediatric Reference Center, Pneumo-Allergologie Pédiatrique, Hôpital Necker Enfants Malades, AP-HP, Paris, France.<br /><searchLink fieldCode="AU" term="%22Cosson+L%22">Cosson L</searchLink>; Centre de Ressources et de Compétence de la Mucoviscidose Enfants, Hôpital de Clocheville, Tours, France.<br /><searchLink fieldCode="AU" term="%22Macey+J%22">Macey J</searchLink>; Centre de Ressources et de Compétence de la Mucoviscidose, CHU Pellegrin, Bordeaux, France.<br /><searchLink fieldCode="AU" term="%22Ramel+S%22">Ramel S</searchLink>; Centre de Ressources et de Compétence de la Mucoviscidose Adulte, Centre de Perharidy, Roscoff, France.<br /><searchLink fieldCode="AU" term="%22Weiss+L%22">Weiss L</searchLink>; Centre de Ressources et de Compétence de la Mucoviscidose Pédiatrique, CHU, Strasbourg, France.<br /><searchLink fieldCode="AU" term="%22Grenet+D%22">Grenet D</searchLink>; Centre de Ressources et de Compétence de la Mucoviscidose, Hôpital Foch, Suresnes, France.<br /><searchLink fieldCode="AU" term="%22Le+Clainche-Viala+L%22">Le Clainche-Viala L</searchLink>; Centre de Ressources et de Compétence de la Mucoviscidose Pédiatrique, Hôpital Robert Debré, Paris, France.<br /><searchLink fieldCode="AU" term="%22Douvry+B%22">Douvry B</searchLink>; Centre de Ressources et de Compétence de la Mucoviscidose Mixte, CHIC, Créteil, France.<br /><searchLink fieldCode="AU" term="%22Ravoninjatovo+B%22">Ravoninjatovo B</searchLink>; Centre de Ressources et de Compétence de la Mucoviscidose, American Memoral Hospital, Reims, France.<br /><searchLink fieldCode="AU" term="%22Audousset+C%22">Audousset C</searchLink>; Centre de Ressources et de Compétence de la Mucoviscidose, Institut Cœur Poumons, Lille, France.<br /><searchLink fieldCode="AU" term="%22Tatopoulos+A%22">Tatopoulos A</searchLink>; CHU de Nancy - Hôpitaux de Brabois, Nancy, France.<br /><searchLink fieldCode="AU" term="%22Richaud-Thiriez+B%22">Richaud-Thiriez B</searchLink>; Centre de Ressources et de Compétence de la Mucoviscidose Adulte, Centre Hospitalier Jean Minjoz, Besancon, France.<br /><searchLink fieldCode="AU" term="%22Baravalle+M%22">Baravalle M</searchLink>; Centre de Ressources et de Compétence de la Mucoviscidose Enfants, Hôpital d'Enfants de la Timone, Marseille, France.<br /><searchLink fieldCode="AU" term="%22Thouvenin+G%22">Thouvenin G</searchLink>; Centre de Ressources et de Compétence de la Mucoviscidose Enfants, Hôpital Trousseau, Paris, France.<br /><searchLink fieldCode="AU" term="%22Labbé+G%22">Labbé G</searchLink>; Centre de Ressources et de Compétence de la Mucoviscidose, CHU Estaing, Clermont-Ferrand, France.<br /><searchLink fieldCode="AU" term="%22Mittaine+M%22">Mittaine M</searchLink>; Centre de ressources et de compétences pour la mucoviscidose, Hôpital des enfants, CHU Toulouse, Toulouse, France.<br /><searchLink fieldCode="AU" term="%22Reix+P%22">Reix P</searchLink>; Centre de Ressources et de Compétence de la Mucoviscidose Pédiatrique, Hospices Civils de Lyon, Bron, France.<br /><searchLink fieldCode="AU" term="%22Durieu+I%22">Durieu I</searchLink>; Centre de Référence Adulte de la Mucoviscidose, Hospices Civils de Lyon, Université de Lyon, Lyon, France.<br /><searchLink fieldCode="AU" term="%22Mankikian+J%22">Mankikian J</searchLink>; Centre hospitalier régional universitaire Bretonneau, Tours, France.<br /><searchLink fieldCode="AU" term="%22Bui+S%22">Bui S</searchLink>; Université de Bordeaux, CRCM pédiatrique, center de Recherche Cardio-thoracique de Bordeaux, INSERM U1045, Bordeaux Imaging Center, Bordeaux, France.<br /><searchLink fieldCode="AU" term="%22Nguyen-Khoa+T%22">Nguyen-Khoa T</searchLink>; INSERM, CNRS, Institut Necker Enfants Malades, Paris, France.; Université Paris-Cité, Paris, France.; Laboratory of Biochemistry, Hôpital Universitaire Necker Enfants Malades AP-HP Centre, Paris, France.<br /><searchLink fieldCode="AU" term="%22Khoukh+K%22">Khoukh K</searchLink>; Pharmacie Delpech, Paris, France.<br /><searchLink fieldCode="AU" term="%22Martin+C%22">Martin C</searchLink>; Institut Cochin, Inserm U1016, Paris, France.; Respiratory Medicine and Cystic Fibrosis National Reference Center, Hôpital Cochin, AP-HP. Centre Université Paris Cité, Paris, France.; ERN-Lung CF network, Frankfurt, Germany.<br /><searchLink fieldCode="AU" term="%22Da+Silva+J%22">Da Silva J</searchLink>; Respiratory Medicine and Cystic Fibrosis National Reference Center, Hôpital Cochin, AP-HP. Centre Université Paris Cité, Paris, France.; ERN-Lung CF network, Frankfurt, Germany.<br /><searchLink fieldCode="AU" term="%22De+Carli+P%22">De Carli P</searchLink>; Vaincre La Mucoviscidose, Paris, France.<br /><searchLink fieldCode="AU" term="%22Castellani+C%22">Castellani C</searchLink>; IRCCS IstitutoGianninaGaslini, CysticFibrosis Center, Genoa, Italy.<br /><searchLink fieldCode="AU" term="%22Cresta+F%22">Cresta F</searchLink>; IRCCS IstitutoGianninaGaslini, CysticFibrosis Center, Genoa, Italy.<br /><searchLink fieldCode="AU" term="%22Galietta+L%22">Galietta L</searchLink>; Telethon Institute of Genetics and Medicine (TIGEM), Pozzuoli, Italy.<br /><searchLink fieldCode="AU" term="%22Guillemaut+A%22">Guillemaut A</searchLink>; Centre de ressources et de compétences pour la mucoviscidose Adultes, Centre hospitalier régional universitaire de Nancy, Vandœuvre-Lès-Nancy, France.<br /><searchLink fieldCode="AU" term="%22Girodon+E%22">Girodon E</searchLink>; INSERM, CNRS, Institut Necker Enfants Malades, Paris, France.; Université Paris-Cité, Paris, France.; Service de Médecine Génomique des Maladies de Système et d'Organe, Hôpital Cochin, Paris, France.<br /><searchLink fieldCode="AU" term="%22Remus+N%22">Remus N</searchLink>; Centre de Ressources et de Compétence de la Mucoviscidose Mixte, CHIC, Créteil, France.<br /><searchLink fieldCode="AU" term="%22Bulcaen+M%22">Bulcaen M</searchLink>; Laboratory of Respiratory Diseases and Thoracic Surgery, KU Leuven, Belgium.<br /><searchLink fieldCode="AU" term="%22Ensinck+M%22">Ensinck M</searchLink>; Laboratory of Respiratory Diseases and Thoracic Surgery, KU Leuven, Belgium.<br /><searchLink fieldCode="AU" term="%22Zajac+M%22">Zajac M</searchLink>; Department of Physics and Biophysics, Institute of Biology, Warsaw University of Life Sciences, Warsaw, Poland.<br /><searchLink fieldCode="AU" term="%22Carlon+M%22">Carlon M</searchLink>; Laboratory of Respiratory Diseases and Thoracic Surgery, KU Leuven, Belgium.<br /><searchLink fieldCode="AU" term="%22LeBihan+J%22">LeBihan J</searchLink>; Centre de Ressources et de Compétence de la Mucoviscidose Adulte, Centre de Perharidy, Roscoff, France.<br /><searchLink fieldCode="AU" term="%22Burgel+PR%22">Burgel PR</searchLink>; Université Paris-Cité, Paris, France.; Institut Cochin, Inserm U1016, Paris, France.; Respiratory Medicine and Cystic Fibrosis National Reference Center, Hôpital Cochin, AP-HP. Centre Université Paris Cité, Paris, France.; ERN-Lung CF network, Frankfurt, Germany.<br /><searchLink fieldCode="AU" term="%22Sermet-Gaudelus+I%22">Sermet-Gaudelus I</searchLink>; INSERM, CNRS, Institut Necker Enfants Malades, Paris, France.; Université Paris-Cité, Paris, France.; Cystic Fibrosis National Pediatric Reference Center, Pneumo-Allergologie Pédiatrique, Hôpital Necker Enfants Malades, AP-HP, Paris, France.; ERN-Lung CF network, Frankfurt, Germany.<br /><searchLink fieldCode="AU" term="%22Hinzpeter+A%22">Hinzpeter A</searchLink>; INSERM, CNRS, Institut Necker Enfants Malades, Paris, France.; Université Paris-Cité, Paris, France.<br /><searchLink fieldCode="AU" term="%22Pedemonte+N%22">Pedemonte N</searchLink>; UOC Genetica Medica, IRCCS Istituto Giannina Gaslini, Genova, Italy.
– Name: TitleSource
  Label: Source
  Group: Src
  Data: <searchLink fieldCode="JN" term="%22101548923%22">Frontiers in pharmacology</searchLink> [Front Pharmacol] 2025 Oct 29; Vol. 16, pp. 1661417. <i>Date of Electronic Publication: </i>2025 Oct 29 (<i>Print Publication: </i>2025).
– Name: TypePub
  Label: Publication Type
  Group: TypPub
  Data: Journal Article
– Name: TitleSource
  Label: Journal Info
  Group: Src
  Data: <i>Publisher: </i><searchLink fieldCode="PB" term="%22Frontiers+Media]%22">Frontiers Media] </searchLink><i>Country of Publication: </i>Switzerland <i>NLM ID: </i>101548923 <i>Publication Model: </i>eCollection <i>Cited Medium: </i>Print <i>ISSN: </i>1663-9812 (Print) <i>Linking ISSN: </i><searchLink fieldCode="IS" term="%2216639812%22">16639812 </searchLink><i>NLM ISO Abbreviation: </i>Front Pharmacol <i>Subsets: </i>PubMed not MEDLINE
PLink https://search.ebscohost.com/login.aspx?direct=true&site=eds-live&db=mdl&AN=41235117
RecordInfo BibRecord:
  BibEntity:
    Identifiers:
      – Type: doi
        Value: 10.3389/fphar.2025.1661417
    Languages:
      – Code: eng
        Text: English
    PhysicalDescription:
      Pagination:
        StartPage: 1661417
    Titles:
      – TitleFull: Beyond Trikafta: new models to assess tissue dependent rescue of N1303K-CFTR.
        Type: main
  BibRelationships:
    HasContributorRelationships:
      – PersonEntity:
          Name:
            NameFull: Pranke I
      – PersonEntity:
          Name:
            NameFull: Capurro V
      – PersonEntity:
          Name:
            NameFull: Chevalier B
      – PersonEntity:
          Name:
            NameFull: Pesce E
      – PersonEntity:
          Name:
            NameFull: Tomati V
      – PersonEntity:
          Name:
            NameFull: Pastorino C
      – PersonEntity:
          Name:
            NameFull: Kelly-Aubert M
      – PersonEntity:
          Name:
            NameFull: Hatton A
      – PersonEntity:
          Name:
            NameFull: Dreano E
      – PersonEntity:
          Name:
            NameFull: Lena M
      – PersonEntity:
          Name:
            NameFull: Bocciardi R
      – PersonEntity:
          Name:
            NameFull: Zara F
      – PersonEntity:
          Name:
            NameFull: Pantano S
      – PersonEntity:
          Name:
            NameFull: Terlizzi V
      – PersonEntity:
          Name:
            NameFull: Lucanto C
      – PersonEntity:
          Name:
            NameFull: Costa S
      – PersonEntity:
          Name:
            NameFull: Claut L
      – PersonEntity:
          Name:
            NameFull: Daccò V
      – PersonEntity:
          Name:
            NameFull: Poli P
      – PersonEntity:
          Name:
            NameFull: Maschio M
      – PersonEntity:
          Name:
            NameFull: Fabrizzi B
      – PersonEntity:
          Name:
            NameFull: Caporelli N
      – PersonEntity:
          Name:
            NameFull: Cipolli M
      – PersonEntity:
          Name:
            NameFull: Volpi S
      – PersonEntity:
          Name:
            NameFull: Chedevergne F
      – PersonEntity:
          Name:
            NameFull: Cosson L
      – PersonEntity:
          Name:
            NameFull: Macey J
      – PersonEntity:
          Name:
            NameFull: Ramel S
      – PersonEntity:
          Name:
            NameFull: Weiss L
      – PersonEntity:
          Name:
            NameFull: Grenet D
      – PersonEntity:
          Name:
            NameFull: Le Clainche-Viala L
      – PersonEntity:
          Name:
            NameFull: Douvry B
      – PersonEntity:
          Name:
            NameFull: Ravoninjatovo B
      – PersonEntity:
          Name:
            NameFull: Audousset C
      – PersonEntity:
          Name:
            NameFull: Tatopoulos A
      – PersonEntity:
          Name:
            NameFull: Richaud-Thiriez B
      – PersonEntity:
          Name:
            NameFull: Baravalle M
      – PersonEntity:
          Name:
            NameFull: Thouvenin G
      – PersonEntity:
          Name:
            NameFull: Labbé G
      – PersonEntity:
          Name:
            NameFull: Mittaine M
      – PersonEntity:
          Name:
            NameFull: Reix P
      – PersonEntity:
          Name:
            NameFull: Durieu I
      – PersonEntity:
          Name:
            NameFull: Mankikian J
      – PersonEntity:
          Name:
            NameFull: Bui S
      – PersonEntity:
          Name:
            NameFull: Nguyen-Khoa T
      – PersonEntity:
          Name:
            NameFull: Khoukh K
      – PersonEntity:
          Name:
            NameFull: Martin C
      – PersonEntity:
          Name:
            NameFull: Da Silva J
      – PersonEntity:
          Name:
            NameFull: De Carli P
      – PersonEntity:
          Name:
            NameFull: Castellani C
      – PersonEntity:
          Name:
            NameFull: Cresta F
      – PersonEntity:
          Name:
            NameFull: Galietta L
      – PersonEntity:
          Name:
            NameFull: Guillemaut A
      – PersonEntity:
          Name:
            NameFull: Girodon E
      – PersonEntity:
          Name:
            NameFull: Remus N
      – PersonEntity:
          Name:
            NameFull: Bulcaen M
      – PersonEntity:
          Name:
            NameFull: Ensinck M
      – PersonEntity:
          Name:
            NameFull: Zajac M
      – PersonEntity:
          Name:
            NameFull: Carlon M
      – PersonEntity:
          Name:
            NameFull: LeBihan J
      – PersonEntity:
          Name:
            NameFull: Burgel PR
      – PersonEntity:
          Name:
            NameFull: Sermet-Gaudelus I
      – PersonEntity:
          Name:
            NameFull: Hinzpeter A
      – PersonEntity:
          Name:
            NameFull: Pedemonte N
    IsPartOfRelationships:
      – BibEntity:
          Dates:
            – D: 29
              M: 10
              Text: 2025 Oct 29
              Type: published
              Y: 2025
          Identifiers:
            – Type: issn-print
              Value: 1663-9812
          Numbering:
            – Type: volume
              Value: 16
          Titles:
            – TitleFull: Frontiers in pharmacology
              Type: main
ResultId 1