A fly model of SCA36 reveals combinatorial neurotoxicity of hexanucleotide and dipeptide repeats.

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Title: A fly model of SCA36 reveals combinatorial neurotoxicity of hexanucleotide and dipeptide repeats.
Authors: Hsiao CT; Graduate Institute of Physiology, National Taiwan University, Taipei, Taiwan.; Department of Neurology, National Yang Ming Chiao Tung University School of Medicine, Taipei, Taiwan.; Department of Neurology, Neurological Institute, Taipei Veterans General Hospital, Taipei, Taiwan., Fu SJ; Graduate Institute of Physiology, National Taiwan University, Taipei, Taiwan.; Department of Neurology, Neurological Institute, Taipei Veterans General Hospital, Taipei, Taiwan.; School of Medicine, Fu‑Jen Catholic University, New Taipei City, Taiwan., Guo TN; Graduate Institute of Physiology, National Taiwan University, Taipei, Taiwan.; Department of Neurology, Neurological Institute, Taipei Veterans General Hospital, Taipei, Taiwan., Lin CC; Institute of Basic Medical Sciences, College of Medicine, National Cheng Kung University, Tainan, Taiwan., Tsao YJ; Graduate Institute of Physiology, National Taiwan University, Taipei, Taiwan.; Department of Neurology, Neurological Institute, Taipei Veterans General Hospital, Taipei, Taiwan., Chang W; Graduate Institute of Physiology, National Taiwan University, Taipei, Taiwan.; Department of Neurology, Neurological Institute, Taipei Veterans General Hospital, Taipei, Taiwan., Liao YC; Department of Neurology, National Yang Ming Chiao Tung University School of Medicine, Taipei, Taiwan.; Department of Neurology, Neurological Institute, Taipei Veterans General Hospital, Taipei, Taiwan.; Brain Research Center, National Yang Ming Chiao Tung University School of Medicine, Taipei, Taiwan., Hashimoto M; Institute of Basic Medical Sciences, College of Medicine, National Cheng Kung University, Tainan, Taiwan.; Institute of Molecular Medicine, College of Medicine, National Cheng Kung University, Tainan, Taiwan., Huang SY; Department of Medical Research, National Taiwan University Hospital, Taipei, Taiwan., Lee YC; Department of Neurology, National Yang Ming Chiao Tung University School of Medicine, Taipei, Taiwan.; Department of Neurology, Neurological Institute, Taipei Veterans General Hospital, Taipei, Taiwan.; Brain Research Center, National Yang Ming Chiao Tung University School of Medicine, Taipei, Taiwan., Yu CH; Institute of Basic Medical Sciences, College of Medicine, National Cheng Kung University, Tainan, Taiwan.; Department of Biochemistry and Molecular Biology, College of Medicine, National Cheng Kung University, Tainan, Taiwan., Chan CC; Graduate Institute of Physiology, National Taiwan University, Taipei, Taiwan.
Source: PLoS genetics [PLoS Genet] 2025 Dec 03; Vol. 21 (12), pp. e1011954. Date of Electronic Publication: 2025 Dec 03 (Print Publication: 2025).
Publication Type: Journal Article
Journal Info: Publisher: Public Library of Science Country of Publication: United States NLM ID: 101239074 Publication Model: eCollection Cited Medium: Internet ISSN: 1553-7404 (Electronic) Linking ISSN: 15537390 NLM ISO Abbreviation: PLoS Genet Subsets: MEDLINE
Database: MEDLINE Ultimate
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ISSN:1553-7404
DOI:10.1371/journal.pgen.1011954