Metformin therapy to facilitate weight loss in adults with classic maple syrup urine disease.

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Title: Metformin therapy to facilitate weight loss in adults with classic maple syrup urine disease.
Authors: Rodrigues A; Clinic for Special Children, Gordonville, PA 17529, United States of America., Sweigert E; Clinic for Special Children, Gordonville, PA 17529, United States of America., Robinson D; Clinic for Special Children, Gordonville, PA 17529, United States of America., Kregel M; St. Christopher's Hospital for Children, Philadelphia, PA 19134, United States of America., Williamson J; Clinic for Special Children, Gordonville, PA 17529, United States of America., Koehler A; Clinic for Special Children, Gordonville, PA 17529, United States of America., Schreckengast S; Clinic for Special Children, Gordonville, PA 17529, United States of America., Forry C; Clinic for Special Children, Gordonville, PA 17529, United States of America., Loeven K; Clinic for Special Children, Gordonville, PA 17529, United States of America., Puffenberger E; Clinic for Special Children, Gordonville, PA 17529, United States of America., McVey A; Clinic for Special Children, Gordonville, PA 17529, United States of America., Hendrickson C; Clinic for Special Children, Gordonville, PA 17529, United States of America., Patel A; Clinic for Special Children, Gordonville, PA 17529, United States of America., Thomas A; Clinic for Special Children, Gordonville, PA 17529, United States of America., Thomas S; Clinic for Special Children, Gordonville, PA 17529, United States of America., Brigatti KW; Clinic for Special Children, Gordonville, PA 17529, United States of America., Strauss K; Clinic for Special Children, Gordonville, PA 17529, United States of America., Meier GL; Clinic for Special Children, Gordonville, PA 17529, United States of America. Electronic address: gmeier@clinicforspecialchildren.org.
Source: Molecular genetics and metabolism [Mol Genet Metab] 2026 Mar; Vol. 147 (3), pp. 109730. Date of Electronic Publication: 2026 Jan 07.
Publication Type: Journal Article
Journal Info: Publisher: Academic Press Country of Publication: United States NLM ID: 9805456 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1096-7206 (Electronic) Linking ISSN: 10967192 NLM ISO Abbreviation: Mol Genet Metab Subsets: MEDLINE
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              Text: 2026 Mar
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