Metformin therapy to facilitate weight loss in adults with classic maple syrup urine disease.
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| Title: | Metformin therapy to facilitate weight loss in adults with classic maple syrup urine disease. |
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| Authors: | Rodrigues A; Clinic for Special Children, Gordonville, PA 17529, United States of America., Sweigert E; Clinic for Special Children, Gordonville, PA 17529, United States of America., Robinson D; Clinic for Special Children, Gordonville, PA 17529, United States of America., Kregel M; St. Christopher's Hospital for Children, Philadelphia, PA 19134, United States of America., Williamson J; Clinic for Special Children, Gordonville, PA 17529, United States of America., Koehler A; Clinic for Special Children, Gordonville, PA 17529, United States of America., Schreckengast S; Clinic for Special Children, Gordonville, PA 17529, United States of America., Forry C; Clinic for Special Children, Gordonville, PA 17529, United States of America., Loeven K; Clinic for Special Children, Gordonville, PA 17529, United States of America., Puffenberger E; Clinic for Special Children, Gordonville, PA 17529, United States of America., McVey A; Clinic for Special Children, Gordonville, PA 17529, United States of America., Hendrickson C; Clinic for Special Children, Gordonville, PA 17529, United States of America., Patel A; Clinic for Special Children, Gordonville, PA 17529, United States of America., Thomas A; Clinic for Special Children, Gordonville, PA 17529, United States of America., Thomas S; Clinic for Special Children, Gordonville, PA 17529, United States of America., Brigatti KW; Clinic for Special Children, Gordonville, PA 17529, United States of America., Strauss K; Clinic for Special Children, Gordonville, PA 17529, United States of America., Meier GL; Clinic for Special Children, Gordonville, PA 17529, United States of America. Electronic address: gmeier@clinicforspecialchildren.org. |
| Source: | Molecular genetics and metabolism [Mol Genet Metab] 2026 Mar; Vol. 147 (3), pp. 109730. Date of Electronic Publication: 2026 Jan 07. |
| Publication Type: | Journal Article |
| Journal Info: | Publisher: Academic Press Country of Publication: United States NLM ID: 9805456 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1096-7206 (Electronic) Linking ISSN: 10967192 NLM ISO Abbreviation: Mol Genet Metab Subsets: MEDLINE |
| Database: | MEDLINE Ultimate |
| FullText | Text: Availability: 0 |
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| Header | DbId: mdl DbLabel: MEDLINE Ultimate An: 41564618 AccessLevel: 2 PubType: Academic Journal PubTypeId: academicJournal PreciseRelevancyScore: 0 |
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| Items | – Name: Title Label: Title Group: Ti Data: Metformin therapy to facilitate weight loss in adults with classic maple syrup urine disease. – Name: Author Label: Authors Group: Au Data: <searchLink fieldCode="AU" term="%22Rodrigues+A%22">Rodrigues A</searchLink>; Clinic for Special Children, Gordonville, PA 17529, United States of America.<br /><searchLink fieldCode="AU" term="%22Sweigert+E%22">Sweigert E</searchLink>; Clinic for Special Children, Gordonville, PA 17529, United States of America.<br /><searchLink fieldCode="AU" term="%22Robinson+D%22">Robinson D</searchLink>; Clinic for Special Children, Gordonville, PA 17529, United States of America.<br /><searchLink fieldCode="AU" term="%22Kregel+M%22">Kregel M</searchLink>; St. Christopher's Hospital for Children, Philadelphia, PA 19134, United States of America.<br /><searchLink fieldCode="AU" term="%22Williamson+J%22">Williamson J</searchLink>; Clinic for Special Children, Gordonville, PA 17529, United States of America.<br /><searchLink fieldCode="AU" term="%22Koehler+A%22">Koehler A</searchLink>; Clinic for Special Children, Gordonville, PA 17529, United States of America.<br /><searchLink fieldCode="AU" term="%22Schreckengast+S%22">Schreckengast S</searchLink>; Clinic for Special Children, Gordonville, PA 17529, United States of America.<br /><searchLink fieldCode="AU" term="%22Forry+C%22">Forry C</searchLink>; Clinic for Special Children, Gordonville, PA 17529, United States of America.<br /><searchLink fieldCode="AU" term="%22Loeven+K%22">Loeven K</searchLink>; Clinic for Special Children, Gordonville, PA 17529, United States of America.<br /><searchLink fieldCode="AU" term="%22Puffenberger+E%22">Puffenberger E</searchLink>; Clinic for Special Children, Gordonville, PA 17529, United States of America.<br /><searchLink fieldCode="AU" term="%22McVey+A%22">McVey A</searchLink>; Clinic for Special Children, Gordonville, PA 17529, United States of America.<br /><searchLink fieldCode="AU" term="%22Hendrickson+C%22">Hendrickson C</searchLink>; Clinic for Special Children, Gordonville, PA 17529, United States of America.<br /><searchLink fieldCode="AU" term="%22Patel+A%22">Patel A</searchLink>; Clinic for Special Children, Gordonville, PA 17529, United States of America.<br /><searchLink fieldCode="AU" term="%22Thomas+A%22">Thomas A</searchLink>; Clinic for Special Children, Gordonville, PA 17529, United States of America.<br /><searchLink fieldCode="AU" term="%22Thomas+S%22">Thomas S</searchLink>; Clinic for Special Children, Gordonville, PA 17529, United States of America.<br /><searchLink fieldCode="AU" term="%22Brigatti+KW%22">Brigatti KW</searchLink>; Clinic for Special Children, Gordonville, PA 17529, United States of America.<br /><searchLink fieldCode="AU" term="%22Strauss+K%22">Strauss K</searchLink>; Clinic for Special Children, Gordonville, PA 17529, United States of America.<br /><searchLink fieldCode="AU" term="%22Meier+GL%22">Meier GL</searchLink>; Clinic for Special Children, Gordonville, PA 17529, United States of America. Electronic address: gmeier@clinicforspecialchildren.org. – Name: TitleSource Label: Source Group: Src Data: <searchLink fieldCode="JN" term="%229805456%22">Molecular genetics and metabolism</searchLink> [Mol Genet Metab] 2026 Mar; Vol. 147 (3), pp. 109730. <i>Date of Electronic Publication: </i>2026 Jan 07. – Name: TypePub Label: Publication Type Group: TypPub Data: Journal Article – Name: TitleSource Label: Journal Info Group: Src Data: <i>Publisher: </i><searchLink fieldCode="PB" term="%22Academic+Press%22">Academic Press </searchLink><i>Country of Publication: </i>United States <i>NLM ID: </i>9805456 <i>Publication Model: </i>Print-Electronic <i>Cited Medium: </i>Internet <i>ISSN: </i>1096-7206 (Electronic) <i>Linking ISSN: </i><searchLink fieldCode="IS" term="%2210967192%22">10967192 </searchLink><i>NLM ISO Abbreviation: </i>Mol Genet Metab <i>Subsets: </i>MEDLINE |
| PLink | https://search.ebscohost.com/login.aspx?direct=true&site=eds-live&db=mdl&AN=41564618 |
| RecordInfo | BibRecord: BibEntity: Identifiers: – Type: doi Value: 10.1016/j.ymgme.2026.109730 Languages: – Code: eng Text: English PhysicalDescription: Pagination: StartPage: 109730 Titles: – TitleFull: Metformin therapy to facilitate weight loss in adults with classic maple syrup urine disease. Type: main BibRelationships: HasContributorRelationships: – PersonEntity: Name: NameFull: Rodrigues A – PersonEntity: Name: NameFull: Sweigert E – PersonEntity: Name: NameFull: Robinson D – PersonEntity: Name: NameFull: Kregel M – PersonEntity: Name: NameFull: Williamson J – PersonEntity: Name: NameFull: Koehler A – PersonEntity: Name: NameFull: Schreckengast S – PersonEntity: Name: NameFull: Forry C – PersonEntity: Name: NameFull: Loeven K – PersonEntity: Name: NameFull: Puffenberger E – PersonEntity: Name: NameFull: McVey A – PersonEntity: Name: NameFull: Hendrickson C – PersonEntity: Name: NameFull: Patel A – PersonEntity: Name: NameFull: Thomas A – PersonEntity: Name: NameFull: Thomas S – PersonEntity: Name: NameFull: Brigatti KW – PersonEntity: Name: NameFull: Strauss K – PersonEntity: Name: NameFull: Meier GL IsPartOfRelationships: – BibEntity: Dates: – D: 01 M: 03 Text: 2026 Mar Type: published Y: 2026 Identifiers: – Type: issn-electronic Value: 1096-7206 Numbering: – Type: volume Value: 147 – Type: issue Value: 3 Titles: – TitleFull: Molecular genetics and metabolism Type: main |
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