Demographic, clinical, and immunological features in combined immunodeficiency patients: a comparative analysis of those with and without pulmonary manifestations - a multicenter study from Iran.

Saved in:
Bibliographic Details
Title: Demographic, clinical, and immunological features in combined immunodeficiency patients: a comparative analysis of those with and without pulmonary manifestations - a multicenter study from Iran.
Authors: Khanbabaee G; Department of Pediatric Pulmonology, Mofid Children's Hospital, Shahid Beheshti University of Medical Sciences, Tehran, Iran., Pourghasem M; Pediatric Diseases Research Center, Guilan university of Medical Sciences, Rasht, Iran. Matinpourghasem@yahoo.com., Jamee M; Pediatric Nephrology Research Center, Research Institute for Children's Health, Shahid Beheshti University of Medical Sciences, Tehran, Iran., Tabatabaii SA; Department of Pediatric Pulmonology, Mofid Children's Hospital, Shahid Beheshti University of Medical Sciences, Tehran, Iran., Khalili M; Department of Radiology, Shahid Beheshti University of Medical Sciences, Tehran, Iran., Sharafian S; Immunology and Allergy Department, Mofid Children's Hospital, Shahid Beheshti University of Medical Sciences, Tehran, Iran., Mesdaghi M; Immunology and Allergy Department, Mofid Children's Hospital, Shahid Beheshti University of Medical Sciences, Tehran, Iran., Sadeghi-Shabestari M; Immunology Research Center of Tabriz, TB and lung research center of Tabriz, children hospital, Tabriz University of medical science, Tabriz, Iran., Shirvani A; Department of Medical Education, Shahid Beheshti University of Medical Sciences, Tehran, Iran., Sadr S; Department of Pediatric Pulmonology, Mofid Children's Hospital, Shahid Beheshti University of Medical Sciences, Tehran, Iran., Zahmatkesh A; Pediatric Nephrology Research Center, Research Institute for Children's Health, Shahid Beheshti University of Medical Sciences, Tehran, Iran., Delavari S; Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran., Eslami N; Immunology and Allergy Department, Mofid Children's Hospital, Shahid Beheshti University of Medical Sciences, Tehran, Iran., Farahbakhsh N; Department of Pediatric Pulmonology, Mofid Children's Hospital, Shahid Beheshti University of Medical Sciences, Tehran, Iran., Mansouri M; Immunology and Allergy Department, Mofid Children's Hospital, Shahid Beheshti University of Medical Sciences, Tehran, Iran., Tabiei E; Department of Pediatric Pulmonology, Akbar Children's Hospital, Mashhad University of Medical Sciences, Mashhad, Iran., Modarresi SZ; Children Growth Disorder Research Center, Shahid Sadoughi University of Medical Sciences, Yazd, Iran., Behbahani AT; Department of Pediatric Cardiology, Cardiovascular Research center, Rajaie cardiovascular institute, Tehran, Iran., Eslamian G; Immunology and Allergy Department, Mofid Children's Hospital, Shahid Beheshti University of Medical Sciences, Tehran, Iran., Fallahi M; Shahid fahmideh children hospital, Iran University of medical sciences, Tehran, Iran., Enayat J; Department of Pediatrics, Taleghani Children's Hospital, Golestan University of Medical Sciences, Gorgan, Iran., Fallah S; Immunology and Allergy Department, Mofid Children's Hospital, Shahid Beheshti University of Medical Sciences, Tehran, Iran., Pourghasem M; Department of Pharmacy, Pharmaceutical Sciences Branch (IAUPS), Islamic Azad University, Tehran, Iran., Aghamohammadi A; Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran., Chavoshzadeh Z; Immunology and Allergy Department, Mofid Children's Hospital, Shahid Beheshti University of Medical Sciences, Tehran, Iran. zahra_chavoshzadeh@yahoo.com.
Source: BMC pulmonary medicine [BMC Pulm Med] 2026 Jan 31; Vol. 26 (1). Date of Electronic Publication: 2026 Jan 31.
Publication Type: Journal Article; Multicenter Study; Comparative Study
Journal Info: Publisher: BioMed Central Country of Publication: England NLM ID: 100968563 Publication Model: Electronic Cited Medium: Internet ISSN: 1471-2466 (Electronic) Linking ISSN: 14712466 NLM ISO Abbreviation: BMC Pulm Med Subsets: MEDLINE
Database: MEDLINE Ultimate
FullText Text:
  Availability: 0
Header DbId: mdl
DbLabel: MEDLINE Ultimate
An: 41620725
AccessLevel: 2
PubType: Academic Journal
PubTypeId: academicJournal
PreciseRelevancyScore: 0
IllustrationInfo
Items – Name: Title
  Label: Title
  Group: Ti
  Data: Demographic, clinical, and immunological features in combined immunodeficiency patients: a comparative analysis of those with and without pulmonary manifestations - a multicenter study from Iran.
– Name: Author
  Label: Authors
  Group: Au
  Data: <searchLink fieldCode="AU" term="%22Khanbabaee+G%22">Khanbabaee G</searchLink>; Department of Pediatric Pulmonology, Mofid Children's Hospital, Shahid Beheshti University of Medical Sciences, Tehran, Iran.<br /><searchLink fieldCode="AU" term="%22Pourghasem+M%22">Pourghasem M</searchLink>; Pediatric Diseases Research Center, Guilan university of Medical Sciences, Rasht, Iran. Matinpourghasem@yahoo.com.<br /><searchLink fieldCode="AU" term="%22Jamee+M%22">Jamee M</searchLink>; Pediatric Nephrology Research Center, Research Institute for Children's Health, Shahid Beheshti University of Medical Sciences, Tehran, Iran.<br /><searchLink fieldCode="AU" term="%22Tabatabaii+SA%22">Tabatabaii SA</searchLink>; Department of Pediatric Pulmonology, Mofid Children's Hospital, Shahid Beheshti University of Medical Sciences, Tehran, Iran.<br /><searchLink fieldCode="AU" term="%22Khalili+M%22">Khalili M</searchLink>; Department of Radiology, Shahid Beheshti University of Medical Sciences, Tehran, Iran.<br /><searchLink fieldCode="AU" term="%22Sharafian+S%22">Sharafian S</searchLink>; Immunology and Allergy Department, Mofid Children's Hospital, Shahid Beheshti University of Medical Sciences, Tehran, Iran.<br /><searchLink fieldCode="AU" term="%22Mesdaghi+M%22">Mesdaghi M</searchLink>; Immunology and Allergy Department, Mofid Children's Hospital, Shahid Beheshti University of Medical Sciences, Tehran, Iran.<br /><searchLink fieldCode="AU" term="%22Sadeghi-Shabestari+M%22">Sadeghi-Shabestari M</searchLink>; Immunology Research Center of Tabriz, TB and lung research center of Tabriz, children hospital, Tabriz University of medical science, Tabriz, Iran.<br /><searchLink fieldCode="AU" term="%22Shirvani+A%22">Shirvani A</searchLink>; Department of Medical Education, Shahid Beheshti University of Medical Sciences, Tehran, Iran.<br /><searchLink fieldCode="AU" term="%22Sadr+S%22">Sadr S</searchLink>; Department of Pediatric Pulmonology, Mofid Children's Hospital, Shahid Beheshti University of Medical Sciences, Tehran, Iran.<br /><searchLink fieldCode="AU" term="%22Zahmatkesh+A%22">Zahmatkesh A</searchLink>; Pediatric Nephrology Research Center, Research Institute for Children's Health, Shahid Beheshti University of Medical Sciences, Tehran, Iran.<br /><searchLink fieldCode="AU" term="%22Delavari+S%22">Delavari S</searchLink>; Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran.<br /><searchLink fieldCode="AU" term="%22Eslami+N%22">Eslami N</searchLink>; Immunology and Allergy Department, Mofid Children's Hospital, Shahid Beheshti University of Medical Sciences, Tehran, Iran.<br /><searchLink fieldCode="AU" term="%22Farahbakhsh+N%22">Farahbakhsh N</searchLink>; Department of Pediatric Pulmonology, Mofid Children's Hospital, Shahid Beheshti University of Medical Sciences, Tehran, Iran.<br /><searchLink fieldCode="AU" term="%22Mansouri+M%22">Mansouri M</searchLink>; Immunology and Allergy Department, Mofid Children's Hospital, Shahid Beheshti University of Medical Sciences, Tehran, Iran.<br /><searchLink fieldCode="AU" term="%22Tabiei+E%22">Tabiei E</searchLink>; Department of Pediatric Pulmonology, Akbar Children's Hospital, Mashhad University of Medical Sciences, Mashhad, Iran.<br /><searchLink fieldCode="AU" term="%22Modarresi+SZ%22">Modarresi SZ</searchLink>; Children Growth Disorder Research Center, Shahid Sadoughi University of Medical Sciences, Yazd, Iran.<br /><searchLink fieldCode="AU" term="%22Behbahani+AT%22">Behbahani AT</searchLink>; Department of Pediatric Cardiology, Cardiovascular Research center, Rajaie cardiovascular institute, Tehran, Iran.<br /><searchLink fieldCode="AU" term="%22Eslamian+G%22">Eslamian G</searchLink>; Immunology and Allergy Department, Mofid Children's Hospital, Shahid Beheshti University of Medical Sciences, Tehran, Iran.<br /><searchLink fieldCode="AU" term="%22Fallahi+M%22">Fallahi M</searchLink>; Shahid fahmideh children hospital, Iran University of medical sciences, Tehran, Iran.<br /><searchLink fieldCode="AU" term="%22Enayat+J%22">Enayat J</searchLink>; Department of Pediatrics, Taleghani Children's Hospital, Golestan University of Medical Sciences, Gorgan, Iran.<br /><searchLink fieldCode="AU" term="%22Fallah+S%22">Fallah S</searchLink>; Immunology and Allergy Department, Mofid Children's Hospital, Shahid Beheshti University of Medical Sciences, Tehran, Iran.<br /><searchLink fieldCode="AU" term="%22Pourghasem+M%22">Pourghasem M</searchLink>; Department of Pharmacy, Pharmaceutical Sciences Branch (IAUPS), Islamic Azad University, Tehran, Iran.<br /><searchLink fieldCode="AU" term="%22Aghamohammadi+A%22">Aghamohammadi A</searchLink>; Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran.<br /><searchLink fieldCode="AU" term="%22Chavoshzadeh+Z%22">Chavoshzadeh Z</searchLink>; Immunology and Allergy Department, Mofid Children's Hospital, Shahid Beheshti University of Medical Sciences, Tehran, Iran. zahra_chavoshzadeh@yahoo.com.
– Name: TitleSource
  Label: Source
  Group: Src
  Data: <searchLink fieldCode="JN" term="%22100968563%22">BMC pulmonary medicine</searchLink> [BMC Pulm Med] 2026 Jan 31; Vol. 26 (1). <i>Date of Electronic Publication: </i>2026 Jan 31.
– Name: TypePub
  Label: Publication Type
  Group: TypPub
  Data: Journal Article; Multicenter Study; Comparative Study
– Name: TitleSource
  Label: Journal Info
  Group: Src
  Data: <i>Publisher: </i><searchLink fieldCode="PB" term="%22BioMed+Central%22">BioMed Central </searchLink><i>Country of Publication: </i>England <i>NLM ID: </i>100968563 <i>Publication Model: </i>Electronic <i>Cited Medium: </i>Internet <i>ISSN: </i>1471-2466 (Electronic) <i>Linking ISSN: </i><searchLink fieldCode="IS" term="%2214712466%22">14712466 </searchLink><i>NLM ISO Abbreviation: </i>BMC Pulm Med <i>Subsets: </i>MEDLINE
PLink https://search.ebscohost.com/login.aspx?direct=true&site=eds-live&db=mdl&AN=41620725
RecordInfo BibRecord:
  BibEntity:
    Identifiers:
      – Type: doi
        Value: 10.1186/s12890-026-04115-3
    Languages:
      – Code: eng
        Text: English
    Titles:
      – TitleFull: Demographic, clinical, and immunological features in combined immunodeficiency patients: a comparative analysis of those with and without pulmonary manifestations - a multicenter study from Iran.
        Type: main
  BibRelationships:
    HasContributorRelationships:
      – PersonEntity:
          Name:
            NameFull: Khanbabaee G
      – PersonEntity:
          Name:
            NameFull: Pourghasem M
      – PersonEntity:
          Name:
            NameFull: Jamee M
      – PersonEntity:
          Name:
            NameFull: Tabatabaii SA
      – PersonEntity:
          Name:
            NameFull: Khalili M
      – PersonEntity:
          Name:
            NameFull: Sharafian S
      – PersonEntity:
          Name:
            NameFull: Mesdaghi M
      – PersonEntity:
          Name:
            NameFull: Sadeghi-Shabestari M
      – PersonEntity:
          Name:
            NameFull: Shirvani A
      – PersonEntity:
          Name:
            NameFull: Sadr S
      – PersonEntity:
          Name:
            NameFull: Zahmatkesh A
      – PersonEntity:
          Name:
            NameFull: Delavari S
      – PersonEntity:
          Name:
            NameFull: Eslami N
      – PersonEntity:
          Name:
            NameFull: Farahbakhsh N
      – PersonEntity:
          Name:
            NameFull: Mansouri M
      – PersonEntity:
          Name:
            NameFull: Tabiei E
      – PersonEntity:
          Name:
            NameFull: Modarresi SZ
      – PersonEntity:
          Name:
            NameFull: Behbahani AT
      – PersonEntity:
          Name:
            NameFull: Eslamian G
      – PersonEntity:
          Name:
            NameFull: Fallahi M
      – PersonEntity:
          Name:
            NameFull: Enayat J
      – PersonEntity:
          Name:
            NameFull: Fallah S
      – PersonEntity:
          Name:
            NameFull: Pourghasem M
      – PersonEntity:
          Name:
            NameFull: Aghamohammadi A
      – PersonEntity:
          Name:
            NameFull: Chavoshzadeh Z
    IsPartOfRelationships:
      – BibEntity:
          Dates:
            – D: 31
              M: 01
              Text: 2026 Jan 31
              Type: published
              Y: 2026
          Identifiers:
            – Type: issn-electronic
              Value: 1471-2466
          Numbering:
            – Type: volume
              Value: 26
            – Type: issue
              Value: 1
          Titles:
            – TitleFull: BMC pulmonary medicine
              Type: main
ResultId 1