EEG, clinical, and MRI features of status epilepticus associated with mitochondrial diseases.

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Title: EEG, clinical, and MRI features of status epilepticus associated with mitochondrial diseases.
Authors: Damiano M; Clinical Neurophysiology Department and Neurology Department, Pitié-Salpêtrière Hospital, DMU Neurosciences, AP-HP, Sorbonne Université, Paris, France.; Reference Center for Rare Epilepsies, ERN EPiCare, Pitié-Salpêtrière Hospital, Paris, France., Lambrecq V; Clinical Neurophysiology Department and Neurology Department, Pitié-Salpêtrière Hospital, DMU Neurosciences, AP-HP, Sorbonne Université, Paris, France.; Reference Center for Rare Epilepsies, ERN EPiCare, Pitié-Salpêtrière Hospital, Paris, France., Nguyen-Michel VH; Clinical Neurophysiology Department and Neurology Department, Pitié-Salpêtrière Hospital, DMU Neurosciences, AP-HP, Sorbonne Université, Paris, France.; Reference Center for Rare Epilepsies, ERN EPiCare, Pitié-Salpêtrière Hospital, Paris, France., Marois C; Neuro-Intensive Care Department, Pitié-Salpêtrière Hospital, AP-HP, Sorbonne Université, Paris, France., Rucheton B; Metabolic Biochemistry Department, Pitié-Salpêtrière Hospital, AP-HP, Paris, France., Mochel F; Department of Medical Genetics, Reference Centers for Adult Neurometabolic Diseases and Adult Leukodystrophies, Pitié-Salpêtrière Hospital, AP-HP, Paris, France.; Paris Brain Institute - ICM, INSERM, CNRS, Sorbonne Université, 75013, Paris, France., Gourfinkel-An I; Clinical Neurophysiology Department and Neurology Department, Pitié-Salpêtrière Hospital, DMU Neurosciences, AP-HP, Sorbonne Université, Paris, France.; Reference Center for Rare Epilepsies, ERN EPiCare, Pitié-Salpêtrière Hospital, Paris, France., Demeret S; Neuro-Intensive Care Department, Pitié-Salpêtrière Hospital, AP-HP, Sorbonne Université, Paris, France., Navarro V; Clinical Neurophysiology Department and Neurology Department, Pitié-Salpêtrière Hospital, DMU Neurosciences, AP-HP, Sorbonne Université, Paris, France. vincent.navarro@aphp.fr.; Reference Center for Rare Epilepsies, ERN EPiCare, Pitié-Salpêtrière Hospital, Paris, France. vincent.navarro@aphp.fr.; Paris Brain Institute - ICM, INSERM, CNRS, Sorbonne Université, 75013, Paris, France. vincent.navarro@aphp.fr.; Epilepsy Unit, Pitié-Salpêtrière Hospital, AP-HP, 47-83 Boulevard de l'Hôpital, 75013, Paris, France. vincent.navarro@aphp.fr.
Source: Journal of neurology [J Neurol] 2026 Feb 23; Vol. 273 (2). Date of Electronic Publication: 2026 Feb 23.
Publication Type: Journal Article
Journal Info: Publisher: Springer-Verlag Country of Publication: Germany NLM ID: 0423161 Publication Model: Electronic Cited Medium: Internet ISSN: 1432-1459 (Electronic) Linking ISSN: 03405354 NLM ISO Abbreviation: J Neurol Subsets: MEDLINE
Database: MEDLINE Ultimate
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  Data: EEG, clinical, and MRI features of status epilepticus associated with mitochondrial diseases.
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  Data: <searchLink fieldCode="AU" term="%22Damiano+M%22">Damiano M</searchLink>; Clinical Neurophysiology Department and Neurology Department, Pitié-Salpêtrière Hospital, DMU Neurosciences, AP-HP, Sorbonne Université, Paris, France.; Reference Center for Rare Epilepsies, ERN EPiCare, Pitié-Salpêtrière Hospital, Paris, France.<br /><searchLink fieldCode="AU" term="%22Lambrecq+V%22">Lambrecq V</searchLink>; Clinical Neurophysiology Department and Neurology Department, Pitié-Salpêtrière Hospital, DMU Neurosciences, AP-HP, Sorbonne Université, Paris, France.; Reference Center for Rare Epilepsies, ERN EPiCare, Pitié-Salpêtrière Hospital, Paris, France.<br /><searchLink fieldCode="AU" term="%22Nguyen-Michel+VH%22">Nguyen-Michel VH</searchLink>; Clinical Neurophysiology Department and Neurology Department, Pitié-Salpêtrière Hospital, DMU Neurosciences, AP-HP, Sorbonne Université, Paris, France.; Reference Center for Rare Epilepsies, ERN EPiCare, Pitié-Salpêtrière Hospital, Paris, France.<br /><searchLink fieldCode="AU" term="%22Marois+C%22">Marois C</searchLink>; Neuro-Intensive Care Department, Pitié-Salpêtrière Hospital, AP-HP, Sorbonne Université, Paris, France.<br /><searchLink fieldCode="AU" term="%22Rucheton+B%22">Rucheton B</searchLink>; Metabolic Biochemistry Department, Pitié-Salpêtrière Hospital, AP-HP, Paris, France.<br /><searchLink fieldCode="AU" term="%22Mochel+F%22">Mochel F</searchLink>; Department of Medical Genetics, Reference Centers for Adult Neurometabolic Diseases and Adult Leukodystrophies, Pitié-Salpêtrière Hospital, AP-HP, Paris, France.; Paris Brain Institute - ICM, INSERM, CNRS, Sorbonne Université, 75013, Paris, France.<br /><searchLink fieldCode="AU" term="%22Gourfinkel-An+I%22">Gourfinkel-An I</searchLink>; Clinical Neurophysiology Department and Neurology Department, Pitié-Salpêtrière Hospital, DMU Neurosciences, AP-HP, Sorbonne Université, Paris, France.; Reference Center for Rare Epilepsies, ERN EPiCare, Pitié-Salpêtrière Hospital, Paris, France.<br /><searchLink fieldCode="AU" term="%22Demeret+S%22">Demeret S</searchLink>; Neuro-Intensive Care Department, Pitié-Salpêtrière Hospital, AP-HP, Sorbonne Université, Paris, France.<br /><searchLink fieldCode="AU" term="%22Navarro+V%22">Navarro V</searchLink>; Clinical Neurophysiology Department and Neurology Department, Pitié-Salpêtrière Hospital, DMU Neurosciences, AP-HP, Sorbonne Université, Paris, France. vincent.navarro@aphp.fr.; Reference Center for Rare Epilepsies, ERN EPiCare, Pitié-Salpêtrière Hospital, Paris, France. vincent.navarro@aphp.fr.; Paris Brain Institute - ICM, INSERM, CNRS, Sorbonne Université, 75013, Paris, France. vincent.navarro@aphp.fr.; Epilepsy Unit, Pitié-Salpêtrière Hospital, AP-HP, 47-83 Boulevard de l'Hôpital, 75013, Paris, France. vincent.navarro@aphp.fr.
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              Text: 2026 Feb 23
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