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External validation of the DSP-risk score for prediction of clinically significant ventricular arrhythmias in primary prevention patients with desmoplakin cardiomyopathy-associated genetic variants.

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Title: External validation of the DSP-risk score for prediction of clinically significant ventricular arrhythmias in primary prevention patients with desmoplakin cardiomyopathy-associated genetic variants.
Authors: Gasperetti A; Division of Cardiology, Johns Hopkins University, Baltimore, Maryland. Electronic address: alessio.gasperetti93@gmail.com., Bauce B; Department of Cardiac, Thoracic, Vascular Sciences and Public Health, University of Padua, Padua, Italy., Protonotarios A; Inherited Cardiovascular Diseases Unit, St Bartholomew's Hospital, UCL Institute of Cardiovascular Science, London, United Kingdom., Murray B; Division of Cardiology, Johns Hopkins University, Baltimore, Maryland., Tichnell C; Division of Cardiology, Johns Hopkins University, Baltimore, Maryland., Martini M; Department of Cardiac, Thoracic, Vascular Sciences and Public Health, University of Padua, Padua, Italy., Syrris P; Inherited Cardiovascular Diseases Unit, St Bartholomew's Hospital, UCL Institute of Cardiovascular Science, London, United Kingdom., Smith E; Department of Internal Medicine, Division of Cardiovascular Medicine, University of Michigan, Ann Arbor., Ferro MD; Division of Cardiology, Cardiothoracovascular Department, Azienda Sanitaria Universitaria Giuliano Isontina and University of Trieste, Trieste, Italy., Paldino A; Division of Cardiology, Cardiothoracovascular Department, Azienda Sanitaria Universitaria Giuliano Isontina and University of Trieste, Trieste, Italy., Sinagra G; Division of Cardiology, Cardiothoracovascular Department, Azienda Sanitaria Universitaria Giuliano Isontina and University of Trieste, Trieste, Italy., Iascone M; S.S.D. Chirurgia dei Trapianti e del Trattamento Chirurgico dello Scompenso, Dipartimento Cardiovascolare, ASST Papa Giovanni XXIII, Bergamo, Italy., Iorio AM; S.S.D. Chirurgia dei Trapianti e del Trattamento Chirurgico dello Scompenso, Dipartimento Cardiovascolare, ASST Papa Giovanni XXIII, Bergamo, Italy., Scotto R; Department of Cardiology, Azienda Ospedaliera Brotzu, Piazzale Alessandro Ricchi 1, Cagliari, Italy., Iseppi M; Division of Cardiology, Santa Chiara Hospital in Trento, Trento, Italy., Calò L; Department of Cardiology, Policlinico Casilino, Rome, Italy., Crescenzi C; Department of Cardiology, Policlinico Casilino, Rome, Italy., Schiavone M; IRCCS Centro Cardiologico Monzino, Department of Cardiac Electrophysiology, Milan, Italy., Ravaro S; Istituto Auxologico Italiano, IRCCS, Center for Cardiac Arrhythmias of Genetic Origin and Laboratory of Cardiovascular Genetics, Milan, Italy; Department of Medicine and Surgery, Università Milano-Bicocca, Milan, Italy; and European Reference Network for Rare, Low Prevalence and Complex Diseases of the Heart (ERN GUARD-Heart), Amsterdam, The Netherlands., Crotti L; Istituto Auxologico Italiano, IRCCS, Center for Cardiac Arrhythmias of Genetic Origin and Laboratory of Cardiovascular Genetics, Milan, Italy; Department of Medicine and Surgery, Università Milano-Bicocca, Milan, Italy; and European Reference Network for Rare, Low Prevalence and Complex Diseases of the Heart (ERN GUARD-Heart), Amsterdam, The Netherlands., Vargas DI; Arrhythmia Section, Cardiology Department, Hospital Clínic, Universitat de Barcelona, Barcelona, Spain., Olsen PAS; ProCardio Center for Research Based Innovation, Oslo University Hospital, Rikshospitalet, Norway., Graziosi M; Cardiology Unit, Cardiac Thoracic and Vascular Department, IRCCS Azienda Ospedaliero-Universitaria di Bologna, Bologna, Italy, and European Reference Network for Rare, Low Prevalence and Complex Diseases of the Heart (ERN GUARD-Heart), Amsterdam, The Netherlands., Biagini E; Cardiology Unit, Cardiac Thoracic and Vascular Department, IRCCS Azienda Ospedaliero-Universitaria di Bologna, Bologna, Italy, and European Reference Network for Rare, Low Prevalence and Complex Diseases of the Heart (ERN GUARD-Heart), Amsterdam, The Netherlands., Peretto G; Division of Cardiology, San Raffaele University Hospital, Milan, Italy., Peters S; Royal Melbourne Hospital, Melbourne, Victoria, Australia., Apostu A; Department of Cardiology, University of Medicine and Pharmacy 'Carol Davila', Emergency Institute for Cardiovascular Diseases, Expert Center for Rare Genetic Cardiovascular Diseases, ERN GUARD-Heart, Bucharest, Romania., Jurçut R; Department of Cardiology, University of Medicine and Pharmacy 'Carol Davila', Emergency Institute for Cardiovascular Diseases, Expert Center for Rare Genetic Cardiovascular Diseases, ERN GUARD-Heart, Bucharest, Romania., Yap SC; Department of Cardiology, Thorax Center, Cardiovascular Institute, Erasmus MC, Rotterdam, The Netherlands., Saguner AM; Department of Cardiology, Arrhythmia Unit, University Heart Center, University Hospital Zurich, Zurich, Switzerland., Duru F; Department of Cardiology, Arrhythmia Unit, University Heart Center, University Hospital Zurich, Zurich, Switzerland., Zimmerman S; Division of Cardiology, Johns Hopkins University, Baltimore, Maryland., Chen L; State Key Laboratory of Cardiovascular Disease, National Clinical Research Center for Cardiovascular Diseases, Fuwai Hospital, National Center for Cardiovascular Diseases, Chinese Academy of Medical Sciences and Peking Union Medical College, Beijing, China., Felice T; Department of Cardiology, Mater Dei Hospital, Imsida, Malta., Raineri C; Division of Cardiology, Cardiovascular and Thoracic Department, 'Città Della Salute e Della Scienza' Hospital, Torino, Italy., Dusi V; Division of Cardiology, Cardiovascular and Thoracic Department, 'Città Della Salute e Della Scienza' Hospital, Torino, Italy., Carrillo-Mora L; Inherited Cardiac Diseases Unit (CSUR/ERN GUARD-Heart/CIBERCV), Hospital Universitario Virgen Arrixaca, Murcia, Spain; and European Reference Network for Rare, Low Prevalence and Complex Diseases of the Heart (ERN GUARD-Heart), Amsterdam, The Netherlands., Cabrera-Romero E; Inherited Cardiac Diseases Unit (CSUR/ERN GUARD-Heart/CIBERCV), Hospital Universitario Virgen Arrixaca, Murcia, Spain; and European Reference Network for Rare, Low Prevalence and Complex Diseases of the Heart (ERN GUARD-Heart), Amsterdam, The Netherlands., Gimeno JR; Inherited Cardiac Diseases Unit (CSUR/ERN GUARD-Heart/CIBERCV), Hospital Universitario Virgen Arrixaca, Murcia, Spain; and European Reference Network for Rare, Low Prevalence and Complex Diseases of the Heart (ERN GUARD-Heart), Amsterdam, The Netherlands., Fernández-Sellers C; Department of Pathology, Instituto de Medicina Legal y Ciencias Forenses de Valencia, Valencia, Spain; CAFAMUSME Research Group, Instituto de Investigación Sanitaria La Fe de Valencia, Valencia, Spain., Zorio E; CAFAMUSME Research Group, Instituto de Investigación Sanitaria La Fe de Valencia, Valencia, Spain; Department of Medicine, Faculty of Medicine and Dentistry, Universitat de València, Valencia, Spain; CIBERCV, Center for Biomedical Network Research on Cardiovascular Diseases, Madrid, Spain; Inherited Cardiac Diseases Unit, Cardiology Department, Hospital Universitario y Politécnico La Fe, Valencia, Spain., Ciabatti M; Department of Cardiology, Arezzo University Hospital, Arezzo, Italy., Fico V; Department of Experimental and Clinical Medicine, University of Florence, Meyer Children Hospital and Careggi University Hospital, Florence, Italy., Targetti M; Department of Experimental and Clinical Medicine, University of Florence, Meyer Children Hospital and Careggi University Hospital, Florence, Italy., Pieroni M; Department of Experimental and Clinical Medicine, University of Florence, Meyer Children Hospital and Careggi University Hospital, Florence, Italy., Cadrin-Tourigny J; Cardiovascular Genetics Center, Montreal Heart Institute, Université de Montréal, Montréal, Québec, Canada., Parikh VN; Stanford Center for Inherited Cardiovascular Disease, Division of Cardiovascular Medicine, Department of Medicine, Stanford University School of Medicine, Stanford, California., Muller S; Division of Cardiology, Johns Hopkins University, Baltimore, Maryland; Division of Cardiology, University Medical Center Utrecht, Utrecht, The Netherlands., Te Riele ASJM; Division of Cardiology, University Medical Center Utrecht, Utrecht, The Netherlands., van Tintelen P; Division of Cardiology, University Medical Center Utrecht, Utrecht, The Netherlands., Cox M; Department of Cardiology, University Medical Centre Groningen, Groningen, The Netherlands., Helms A; Department of Internal Medicine, Division of Cardiovascular Medicine, University of Michigan, Ann Arbor., Haugaa K; ProCardio Center for Research Based Innovation, Oslo University Hospital, Rikshospitalet, Norway., Pilochou K; Department of Cardiac, Thoracic, Vascular Sciences and Public Health, University of Padua, Padua, Italy., Taylor M; Department of Cardiology, University Medical Centre Groningen, Groningen, The Netherlands., Mestroni L; University of Colorado Cardiovascular Institute, University of Colorado Anschutz Medical Campus, Aurora, Colorado., Elliott P; Inherited Cardiovascular Diseases Unit, St Bartholomew's Hospital, UCL Institute of Cardiovascular Science, London, United Kingdom., Merlo M; Division of Cardiology, Cardiothoracovascular Department, Azienda Sanitaria Universitaria Giuliano Isontina and University of Trieste, Trieste, Italy., Arbelo E; Arrhythmia Section, Cardiology Department, Hospital Clínic, Universitat de Barcelona, Barcelona, Spain; Institut d'Investigació August Pi i Sunyer (IDIBAPS), Barcelona, Spain; Centro de Investigación Biomédica en Red de Enfermedades Cardiovasculares (CIBERCV), Madrid, Spain; and European Reference Network for Rare, Low Prevalence and Complex Diseases of the Heart (ERN GUARD-Heart), Amsterdam, The Netherlands., Wu KC; Division of Cardiology, Johns Hopkins University, Baltimore, Maryland., James CA; Division of Cardiology, Johns Hopkins University, Baltimore, Maryland., Calkins H; Division of Cardiology, Johns Hopkins University, Baltimore, Maryland., Carrick RT; Division of Cardiology, Johns Hopkins University, Baltimore, Maryland.
Source: Heart rhythm [Heart Rhythm] 2026 Apr 27. Date of Electronic Publication: 2026 Apr 27.
Publication Type: Journal Article
Journal Info: Publisher: Elsevier Country of Publication: United States NLM ID: 101200317 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1556-3871 (Electronic) Linking ISSN: 15475271 NLM ISO Abbreviation: Heart Rhythm Subsets: MEDLINE
Database: MEDLINE Ultimate
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PubType: Academic Journal
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  Data: External validation of the DSP-risk score for prediction of clinically significant ventricular arrhythmias in primary prevention patients with desmoplakin cardiomyopathy-associated genetic variants.
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  Data: <searchLink fieldCode="AU" term="%22Gasperetti+A%22">Gasperetti A</searchLink>; Division of Cardiology, Johns Hopkins University, Baltimore, Maryland. Electronic address: alessio.gasperetti93@gmail.com.<br /><searchLink fieldCode="AU" term="%22Bauce+B%22">Bauce B</searchLink>; Department of Cardiac, Thoracic, Vascular Sciences and Public Health, University of Padua, Padua, Italy.<br /><searchLink fieldCode="AU" term="%22Protonotarios+A%22">Protonotarios A</searchLink>; Inherited Cardiovascular Diseases Unit, St Bartholomew's Hospital, UCL Institute of Cardiovascular Science, London, United Kingdom.<br /><searchLink fieldCode="AU" term="%22Murray+B%22">Murray B</searchLink>; Division of Cardiology, Johns Hopkins University, Baltimore, Maryland.<br /><searchLink fieldCode="AU" term="%22Tichnell+C%22">Tichnell C</searchLink>; Division of Cardiology, Johns Hopkins University, Baltimore, Maryland.<br /><searchLink fieldCode="AU" term="%22Martini+M%22">Martini M</searchLink>; Department of Cardiac, Thoracic, Vascular Sciences and Public Health, University of Padua, Padua, Italy.<br /><searchLink fieldCode="AU" term="%22Syrris+P%22">Syrris P</searchLink>; Inherited Cardiovascular Diseases Unit, St Bartholomew's Hospital, UCL Institute of Cardiovascular Science, London, United Kingdom.<br /><searchLink fieldCode="AU" term="%22Smith+E%22">Smith E</searchLink>; Department of Internal Medicine, Division of Cardiovascular Medicine, University of Michigan, Ann Arbor.<br /><searchLink fieldCode="AU" term="%22Ferro+MD%22">Ferro MD</searchLink>; Division of Cardiology, Cardiothoracovascular Department, Azienda Sanitaria Universitaria Giuliano Isontina and University of Trieste, Trieste, Italy.<br /><searchLink fieldCode="AU" term="%22Paldino+A%22">Paldino A</searchLink>; Division of Cardiology, Cardiothoracovascular Department, Azienda Sanitaria Universitaria Giuliano Isontina and University of Trieste, Trieste, Italy.<br /><searchLink fieldCode="AU" term="%22Sinagra+G%22">Sinagra G</searchLink>; Division of Cardiology, Cardiothoracovascular Department, Azienda Sanitaria Universitaria Giuliano Isontina and University of Trieste, Trieste, Italy.<br /><searchLink fieldCode="AU" term="%22Iascone+M%22">Iascone M</searchLink>; S.S.D. Chirurgia dei Trapianti e del Trattamento Chirurgico dello Scompenso, Dipartimento Cardiovascolare, ASST Papa Giovanni XXIII, Bergamo, Italy.<br /><searchLink fieldCode="AU" term="%22Iorio+AM%22">Iorio AM</searchLink>; S.S.D. Chirurgia dei Trapianti e del Trattamento Chirurgico dello Scompenso, Dipartimento Cardiovascolare, ASST Papa Giovanni XXIII, Bergamo, Italy.<br /><searchLink fieldCode="AU" term="%22Scotto+R%22">Scotto R</searchLink>; Department of Cardiology, Azienda Ospedaliera Brotzu, Piazzale Alessandro Ricchi 1, Cagliari, Italy.<br /><searchLink fieldCode="AU" term="%22Iseppi+M%22">Iseppi M</searchLink>; Division of Cardiology, Santa Chiara Hospital in Trento, Trento, Italy.<br /><searchLink fieldCode="AU" term="%22Calò+L%22">Calò L</searchLink>; Department of Cardiology, Policlinico Casilino, Rome, Italy.<br /><searchLink fieldCode="AU" term="%22Crescenzi+C%22">Crescenzi C</searchLink>; Department of Cardiology, Policlinico Casilino, Rome, Italy.<br /><searchLink fieldCode="AU" term="%22Schiavone+M%22">Schiavone M</searchLink>; IRCCS Centro Cardiologico Monzino, Department of Cardiac Electrophysiology, Milan, Italy.<br /><searchLink fieldCode="AU" term="%22Ravaro+S%22">Ravaro S</searchLink>; Istituto Auxologico Italiano, IRCCS, Center for Cardiac Arrhythmias of Genetic Origin and Laboratory of Cardiovascular Genetics, Milan, Italy; Department of Medicine and Surgery, Università Milano-Bicocca, Milan, Italy; and European Reference Network for Rare, Low Prevalence and Complex Diseases of the Heart (ERN GUARD-Heart), Amsterdam, The Netherlands.<br /><searchLink fieldCode="AU" term="%22Crotti+L%22">Crotti L</searchLink>; Istituto Auxologico Italiano, IRCCS, Center for Cardiac Arrhythmias of Genetic Origin and Laboratory of Cardiovascular Genetics, Milan, Italy; Department of Medicine and Surgery, Università Milano-Bicocca, Milan, Italy; and European Reference Network for Rare, Low Prevalence and Complex Diseases of the Heart (ERN GUARD-Heart), Amsterdam, The Netherlands.<br /><searchLink fieldCode="AU" term="%22Vargas+DI%22">Vargas DI</searchLink>; Arrhythmia Section, Cardiology Department, Hospital Clínic, Universitat de Barcelona, Barcelona, Spain.<br /><searchLink fieldCode="AU" term="%22Olsen+PAS%22">Olsen PAS</searchLink>; ProCardio Center for Research Based Innovation, Oslo University Hospital, Rikshospitalet, Norway.<br /><searchLink fieldCode="AU" term="%22Graziosi+M%22">Graziosi M</searchLink>; Cardiology Unit, Cardiac Thoracic and Vascular Department, IRCCS Azienda Ospedaliero-Universitaria di Bologna, Bologna, Italy, and European Reference Network for Rare, Low Prevalence and Complex Diseases of the Heart (ERN GUARD-Heart), Amsterdam, The Netherlands.<br /><searchLink fieldCode="AU" term="%22Biagini+E%22">Biagini E</searchLink>; Cardiology Unit, Cardiac Thoracic and Vascular Department, IRCCS Azienda Ospedaliero-Universitaria di Bologna, Bologna, Italy, and European Reference Network for Rare, Low Prevalence and Complex Diseases of the Heart (ERN GUARD-Heart), Amsterdam, The Netherlands.<br /><searchLink fieldCode="AU" term="%22Peretto+G%22">Peretto G</searchLink>; Division of Cardiology, San Raffaele University Hospital, Milan, Italy.<br /><searchLink fieldCode="AU" term="%22Peters+S%22">Peters S</searchLink>; Royal Melbourne Hospital, Melbourne, Victoria, Australia.<br /><searchLink fieldCode="AU" term="%22Apostu+A%22">Apostu A</searchLink>; Department of Cardiology, University of Medicine and Pharmacy 'Carol Davila', Emergency Institute for Cardiovascular Diseases, Expert Center for Rare Genetic Cardiovascular Diseases, ERN GUARD-Heart, Bucharest, Romania.<br /><searchLink fieldCode="AU" term="%22Jurçut+R%22">Jurçut R</searchLink>; Department of Cardiology, University of Medicine and Pharmacy 'Carol Davila', Emergency Institute for Cardiovascular Diseases, Expert Center for Rare Genetic Cardiovascular Diseases, ERN GUARD-Heart, Bucharest, Romania.<br /><searchLink fieldCode="AU" term="%22Yap+SC%22">Yap SC</searchLink>; Department of Cardiology, Thorax Center, Cardiovascular Institute, Erasmus MC, Rotterdam, The Netherlands.<br /><searchLink fieldCode="AU" term="%22Saguner+AM%22">Saguner AM</searchLink>; Department of Cardiology, Arrhythmia Unit, University Heart Center, University Hospital Zurich, Zurich, Switzerland.<br /><searchLink fieldCode="AU" term="%22Duru+F%22">Duru F</searchLink>; Department of Cardiology, Arrhythmia Unit, University Heart Center, University Hospital Zurich, Zurich, Switzerland.<br /><searchLink fieldCode="AU" term="%22Zimmerman+S%22">Zimmerman S</searchLink>; Division of Cardiology, Johns Hopkins University, Baltimore, Maryland.<br /><searchLink fieldCode="AU" term="%22Chen+L%22">Chen L</searchLink>; State Key Laboratory of Cardiovascular Disease, National Clinical Research Center for Cardiovascular Diseases, Fuwai Hospital, National Center for Cardiovascular Diseases, Chinese Academy of Medical Sciences and Peking Union Medical College, Beijing, China.<br /><searchLink fieldCode="AU" term="%22Felice+T%22">Felice T</searchLink>; Department of Cardiology, Mater Dei Hospital, Imsida, Malta.<br /><searchLink fieldCode="AU" term="%22Raineri+C%22">Raineri C</searchLink>; Division of Cardiology, Cardiovascular and Thoracic Department, 'Città Della Salute e Della Scienza' Hospital, Torino, Italy.<br /><searchLink fieldCode="AU" term="%22Dusi+V%22">Dusi V</searchLink>; Division of Cardiology, Cardiovascular and Thoracic Department, 'Città Della Salute e Della Scienza' Hospital, Torino, Italy.<br /><searchLink fieldCode="AU" term="%22Carrillo-Mora+L%22">Carrillo-Mora L</searchLink>; Inherited Cardiac Diseases Unit (CSUR/ERN GUARD-Heart/CIBERCV), Hospital Universitario Virgen Arrixaca, Murcia, Spain; and European Reference Network for Rare, Low Prevalence and Complex Diseases of the Heart (ERN GUARD-Heart), Amsterdam, The Netherlands.<br /><searchLink fieldCode="AU" term="%22Cabrera-Romero+E%22">Cabrera-Romero E</searchLink>; Inherited Cardiac Diseases Unit (CSUR/ERN GUARD-Heart/CIBERCV), Hospital Universitario Virgen Arrixaca, Murcia, Spain; and European Reference Network for Rare, Low Prevalence and Complex Diseases of the Heart (ERN GUARD-Heart), Amsterdam, The Netherlands.<br /><searchLink fieldCode="AU" term="%22Gimeno+JR%22">Gimeno JR</searchLink>; Inherited Cardiac Diseases Unit (CSUR/ERN GUARD-Heart/CIBERCV), Hospital Universitario Virgen Arrixaca, Murcia, Spain; and European Reference Network for Rare, Low Prevalence and Complex Diseases of the Heart (ERN GUARD-Heart), Amsterdam, The Netherlands.<br /><searchLink fieldCode="AU" term="%22Fernández-Sellers+C%22">Fernández-Sellers C</searchLink>; Department of Pathology, Instituto de Medicina Legal y Ciencias Forenses de Valencia, Valencia, Spain; CAFAMUSME Research Group, Instituto de Investigación Sanitaria La Fe de Valencia, Valencia, Spain.<br /><searchLink fieldCode="AU" term="%22Zorio+E%22">Zorio E</searchLink>; CAFAMUSME Research Group, Instituto de Investigación Sanitaria La Fe de Valencia, Valencia, Spain; Department of Medicine, Faculty of Medicine and Dentistry, Universitat de València, Valencia, Spain; CIBERCV, Center for Biomedical Network Research on Cardiovascular Diseases, Madrid, Spain; Inherited Cardiac Diseases Unit, Cardiology Department, Hospital Universitario y Politécnico La Fe, Valencia, Spain.<br /><searchLink fieldCode="AU" term="%22Ciabatti+M%22">Ciabatti M</searchLink>; Department of Cardiology, Arezzo University Hospital, Arezzo, Italy.<br /><searchLink fieldCode="AU" term="%22Fico+V%22">Fico V</searchLink>; Department of Experimental and Clinical Medicine, University of Florence, Meyer Children Hospital and Careggi University Hospital, Florence, Italy.<br /><searchLink fieldCode="AU" term="%22Targetti+M%22">Targetti M</searchLink>; Department of Experimental and Clinical Medicine, University of Florence, Meyer Children Hospital and Careggi University Hospital, Florence, Italy.<br /><searchLink fieldCode="AU" term="%22Pieroni+M%22">Pieroni M</searchLink>; Department of Experimental and Clinical Medicine, University of Florence, Meyer Children Hospital and Careggi University Hospital, Florence, Italy.<br /><searchLink fieldCode="AU" term="%22Cadrin-Tourigny+J%22">Cadrin-Tourigny J</searchLink>; Cardiovascular Genetics Center, Montreal Heart Institute, Université de Montréal, Montréal, Québec, Canada.<br /><searchLink fieldCode="AU" term="%22Parikh+VN%22">Parikh VN</searchLink>; Stanford Center for Inherited Cardiovascular Disease, Division of Cardiovascular Medicine, Department of Medicine, Stanford University School of Medicine, Stanford, California.<br /><searchLink fieldCode="AU" term="%22Muller+S%22">Muller S</searchLink>; Division of Cardiology, Johns Hopkins University, Baltimore, Maryland; Division of Cardiology, University Medical Center Utrecht, Utrecht, The Netherlands.<br /><searchLink fieldCode="AU" term="%22Te+Riele+ASJM%22">Te Riele ASJM</searchLink>; Division of Cardiology, University Medical Center Utrecht, Utrecht, The Netherlands.<br /><searchLink fieldCode="AU" term="%22van+Tintelen+P%22">van Tintelen P</searchLink>; Division of Cardiology, University Medical Center Utrecht, Utrecht, The Netherlands.<br /><searchLink fieldCode="AU" term="%22Cox+M%22">Cox M</searchLink>; Department of Cardiology, University Medical Centre Groningen, Groningen, The Netherlands.<br /><searchLink fieldCode="AU" term="%22Helms+A%22">Helms A</searchLink>; Department of Internal Medicine, Division of Cardiovascular Medicine, University of Michigan, Ann Arbor.<br /><searchLink fieldCode="AU" term="%22Haugaa+K%22">Haugaa K</searchLink>; ProCardio Center for Research Based Innovation, Oslo University Hospital, Rikshospitalet, Norway.<br /><searchLink fieldCode="AU" term="%22Pilochou+K%22">Pilochou K</searchLink>; Department of Cardiac, Thoracic, Vascular Sciences and Public Health, University of Padua, Padua, Italy.<br /><searchLink fieldCode="AU" term="%22Taylor+M%22">Taylor M</searchLink>; Department of Cardiology, University Medical Centre Groningen, Groningen, The Netherlands.<br /><searchLink fieldCode="AU" term="%22Mestroni+L%22">Mestroni L</searchLink>; University of Colorado Cardiovascular Institute, University of Colorado Anschutz Medical Campus, Aurora, Colorado.<br /><searchLink fieldCode="AU" term="%22Elliott+P%22">Elliott P</searchLink>; Inherited Cardiovascular Diseases Unit, St Bartholomew's Hospital, UCL Institute of Cardiovascular Science, London, United Kingdom.<br /><searchLink fieldCode="AU" term="%22Merlo+M%22">Merlo M</searchLink>; Division of Cardiology, Cardiothoracovascular Department, Azienda Sanitaria Universitaria Giuliano Isontina and University of Trieste, Trieste, Italy.<br /><searchLink fieldCode="AU" term="%22Arbelo+E%22">Arbelo E</searchLink>; Arrhythmia Section, Cardiology Department, Hospital Clínic, Universitat de Barcelona, Barcelona, Spain; Institut d'Investigació August Pi i Sunyer (IDIBAPS), Barcelona, Spain; Centro de Investigación Biomédica en Red de Enfermedades Cardiovasculares (CIBERCV), Madrid, Spain; and European Reference Network for Rare, Low Prevalence and Complex Diseases of the Heart (ERN GUARD-Heart), Amsterdam, The Netherlands.<br /><searchLink fieldCode="AU" term="%22Wu+KC%22">Wu KC</searchLink>; Division of Cardiology, Johns Hopkins University, Baltimore, Maryland.<br /><searchLink fieldCode="AU" term="%22James+CA%22">James CA</searchLink>; Division of Cardiology, Johns Hopkins University, Baltimore, Maryland.<br /><searchLink fieldCode="AU" term="%22Calkins+H%22">Calkins H</searchLink>; Division of Cardiology, Johns Hopkins University, Baltimore, Maryland.<br /><searchLink fieldCode="AU" term="%22Carrick+RT%22">Carrick RT</searchLink>; Division of Cardiology, Johns Hopkins University, Baltimore, Maryland.
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      – TitleFull: External validation of the DSP-risk score for prediction of clinically significant ventricular arrhythmias in primary prevention patients with desmoplakin cardiomyopathy-associated genetic variants.
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    IsPartOfRelationships:
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          Dates:
            – D: 27
              M: 04
              Text: 2026 Apr 27
              Type: published
              Y: 2026
          Identifiers:
            – Type: issn-electronic
              Value: 1556-3871
          Titles:
            – TitleFull: Heart rhythm
              Type: main
ResultId 1