Early laboratory indicators of acute metabolic decompensation during emergency presentations in pediatric maple syrup urine disease.

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Bibliographic Details
Title: Early laboratory indicators of acute metabolic decompensation during emergency presentations in pediatric maple syrup urine disease.
Authors: Oral-Cebeci S; Department of Pediatric Emergency, Cerrahpaşa Medical Faculty, İstanbul University-Cerrahpaşa, Istanbul, Turkey., Aktuğlu-Zeybek Ç; Department of Pediatric Nutrition and Metabolism, Cerrahpaşa Medical Faculty, İstanbul University-Cerrahpaşa, Istanbul, Turkey.; Research Laboratory of Metabolism, Cerrahpaşa Medical Faculty, İstanbul University-Cerrahpaşa, Istanbul, Turkey., Aslan B; Department of Pediatrics, Cerrahpaşa Medical Faculty, İstanbul University-Cerrahpaşa, Istanbul, Turkey., Uysal ÖY; Department of Pediatrics, Cerrahpaşa Medical Faculty, İstanbul University-Cerrahpaşa, Istanbul, Turkey., Cansever MŞ; Research Laboratory of Metabolism, Cerrahpaşa Medical Faculty, İstanbul University-Cerrahpaşa, Istanbul, Turkey.; Division of Medical Laboratory Techniques, Department of Medical Documentation and Techniques, The Vocational School of Health Services, İstanbul University-Cerrahpaşa, Istanbul, Turkey., Kıykım E; Department of Pediatric Nutrition and Metabolism, Cerrahpaşa Medical Faculty, İstanbul University-Cerrahpaşa, Istanbul, Turkey., Zubarioglu T; Department of Pediatric Nutrition and Metabolism, Cerrahpaşa Medical Faculty, İstanbul University-Cerrahpaşa, Istanbul, Turkey. tanyel.zubarioglu@iuc.edu.tr.
Source: European journal of pediatrics [Eur J Pediatr] 2026 May 19; Vol. 185 (6). Date of Electronic Publication: 2026 May 19.
Publication Type: Journal Article
Journal Info: Publisher: Springer Verlag Country of Publication: Germany NLM ID: 7603873 Publication Model: Electronic Cited Medium: Internet ISSN: 1432-1076 (Electronic) Linking ISSN: 03406199 NLM ISO Abbreviation: Eur J Pediatr Subsets: MEDLINE
Database: MEDLINE Ultimate
Description
ISSN:1432-1076
DOI:10.1007/s00431-026-07081-4