Early laboratory indicators of acute metabolic decompensation during emergency presentations in pediatric maple syrup urine disease.

Saved in:
Bibliographic Details
Title: Early laboratory indicators of acute metabolic decompensation during emergency presentations in pediatric maple syrup urine disease.
Authors: Oral-Cebeci S; Department of Pediatric Emergency, Cerrahpaşa Medical Faculty, İstanbul University-Cerrahpaşa, Istanbul, Turkey., Aktuğlu-Zeybek Ç; Department of Pediatric Nutrition and Metabolism, Cerrahpaşa Medical Faculty, İstanbul University-Cerrahpaşa, Istanbul, Turkey.; Research Laboratory of Metabolism, Cerrahpaşa Medical Faculty, İstanbul University-Cerrahpaşa, Istanbul, Turkey., Aslan B; Department of Pediatrics, Cerrahpaşa Medical Faculty, İstanbul University-Cerrahpaşa, Istanbul, Turkey., Uysal ÖY; Department of Pediatrics, Cerrahpaşa Medical Faculty, İstanbul University-Cerrahpaşa, Istanbul, Turkey., Cansever MŞ; Research Laboratory of Metabolism, Cerrahpaşa Medical Faculty, İstanbul University-Cerrahpaşa, Istanbul, Turkey.; Division of Medical Laboratory Techniques, Department of Medical Documentation and Techniques, The Vocational School of Health Services, İstanbul University-Cerrahpaşa, Istanbul, Turkey., Kıykım E; Department of Pediatric Nutrition and Metabolism, Cerrahpaşa Medical Faculty, İstanbul University-Cerrahpaşa, Istanbul, Turkey., Zubarioglu T; Department of Pediatric Nutrition and Metabolism, Cerrahpaşa Medical Faculty, İstanbul University-Cerrahpaşa, Istanbul, Turkey. tanyel.zubarioglu@iuc.edu.tr.
Source: European journal of pediatrics [Eur J Pediatr] 2026 May 19; Vol. 185 (6). Date of Electronic Publication: 2026 May 19.
Publication Type: Journal Article
Journal Info: Publisher: Springer Verlag Country of Publication: Germany NLM ID: 7603873 Publication Model: Electronic Cited Medium: Internet ISSN: 1432-1076 (Electronic) Linking ISSN: 03406199 NLM ISO Abbreviation: Eur J Pediatr Subsets: MEDLINE
Database: MEDLINE Ultimate
FullText Text:
  Availability: 0
Header DbId: mdl
DbLabel: MEDLINE Ultimate
An: 42151652
AccessLevel: 2
PubType: Academic Journal
PubTypeId: academicJournal
PreciseRelevancyScore: 0
IllustrationInfo
Items – Name: Title
  Label: Title
  Group: Ti
  Data: Early laboratory indicators of acute metabolic decompensation during emergency presentations in pediatric maple syrup urine disease.
– Name: Author
  Label: Authors
  Group: Au
  Data: <searchLink fieldCode="AU" term="%22Oral-Cebeci+S%22">Oral-Cebeci S</searchLink>; Department of Pediatric Emergency, Cerrahpaşa Medical Faculty, İstanbul University-Cerrahpaşa, Istanbul, Turkey.<br /><searchLink fieldCode="AU" term="%22Aktuğlu-Zeybek+Ç%22">Aktuğlu-Zeybek Ç</searchLink>; Department of Pediatric Nutrition and Metabolism, Cerrahpaşa Medical Faculty, İstanbul University-Cerrahpaşa, Istanbul, Turkey.; Research Laboratory of Metabolism, Cerrahpaşa Medical Faculty, İstanbul University-Cerrahpaşa, Istanbul, Turkey.<br /><searchLink fieldCode="AU" term="%22Aslan+B%22">Aslan B</searchLink>; Department of Pediatrics, Cerrahpaşa Medical Faculty, İstanbul University-Cerrahpaşa, Istanbul, Turkey.<br /><searchLink fieldCode="AU" term="%22Uysal+ÖY%22">Uysal ÖY</searchLink>; Department of Pediatrics, Cerrahpaşa Medical Faculty, İstanbul University-Cerrahpaşa, Istanbul, Turkey.<br /><searchLink fieldCode="AU" term="%22Cansever+MŞ%22">Cansever MŞ</searchLink>; Research Laboratory of Metabolism, Cerrahpaşa Medical Faculty, İstanbul University-Cerrahpaşa, Istanbul, Turkey.; Division of Medical Laboratory Techniques, Department of Medical Documentation and Techniques, The Vocational School of Health Services, İstanbul University-Cerrahpaşa, Istanbul, Turkey.<br /><searchLink fieldCode="AU" term="%22Kıykım+E%22">Kıykım E</searchLink>; Department of Pediatric Nutrition and Metabolism, Cerrahpaşa Medical Faculty, İstanbul University-Cerrahpaşa, Istanbul, Turkey.<br /><searchLink fieldCode="AU" term="%22Zubarioglu+T%22">Zubarioglu T</searchLink>; Department of Pediatric Nutrition and Metabolism, Cerrahpaşa Medical Faculty, İstanbul University-Cerrahpaşa, Istanbul, Turkey. tanyel.zubarioglu@iuc.edu.tr.
– Name: TitleSource
  Label: Source
  Group: Src
  Data: <searchLink fieldCode="JN" term="%227603873%22">European journal of pediatrics</searchLink> [Eur J Pediatr] 2026 May 19; Vol. 185 (6). <i>Date of Electronic Publication: </i>2026 May 19.
– Name: TypePub
  Label: Publication Type
  Group: TypPub
  Data: Journal Article
– Name: TitleSource
  Label: Journal Info
  Group: Src
  Data: <i>Publisher: </i><searchLink fieldCode="PB" term="%22Springer+Verlag%22">Springer Verlag </searchLink><i>Country of Publication: </i>Germany <i>NLM ID: </i>7603873 <i>Publication Model: </i>Electronic <i>Cited Medium: </i>Internet <i>ISSN: </i>1432-1076 (Electronic) <i>Linking ISSN: </i><searchLink fieldCode="IS" term="%2203406199%22">03406199 </searchLink><i>NLM ISO Abbreviation: </i>Eur J Pediatr <i>Subsets: </i>MEDLINE
PLink https://search.ebscohost.com/login.aspx?direct=true&site=eds-live&db=mdl&AN=42151652
RecordInfo BibRecord:
  BibEntity:
    Identifiers:
      – Type: doi
        Value: 10.1007/s00431-026-07081-4
    Languages:
      – Code: eng
        Text: English
    Titles:
      – TitleFull: Early laboratory indicators of acute metabolic decompensation during emergency presentations in pediatric maple syrup urine disease.
        Type: main
  BibRelationships:
    HasContributorRelationships:
      – PersonEntity:
          Name:
            NameFull: Oral-Cebeci S
      – PersonEntity:
          Name:
            NameFull: Aktuğlu-Zeybek Ç
      – PersonEntity:
          Name:
            NameFull: Aslan B
      – PersonEntity:
          Name:
            NameFull: Uysal ÖY
      – PersonEntity:
          Name:
            NameFull: Cansever MŞ
      – PersonEntity:
          Name:
            NameFull: Kıykım E
      – PersonEntity:
          Name:
            NameFull: Zubarioglu T
    IsPartOfRelationships:
      – BibEntity:
          Dates:
            – D: 19
              M: 05
              Text: 2026 May 19
              Type: published
              Y: 2026
          Identifiers:
            – Type: issn-electronic
              Value: 1432-1076
          Numbering:
            – Type: volume
              Value: 185
            – Type: issue
              Value: 6
          Titles:
            – TitleFull: European journal of pediatrics
              Type: main
ResultId 1