Utilising human cellular models of primary ciliary dyskinesia: a scoping review.

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Title: Utilising human cellular models of primary ciliary dyskinesia: a scoping review.
Authors: Ong JWY; School of Clinical and Experimental Sciences, University of Southampton Faculty of Medicine, Southampton, UK.; Primary Ciliary Dyskinesia Centre, NIHR Southampton Biomedical Research Centre, University Hospital Southampton NHS Foundation Trust, Southampton, UK., Tsang W; School of Clinical and Experimental Sciences, University of Southampton Faculty of Medicine, Southampton, UK.; Primary Ciliary Dyskinesia Centre, NIHR Southampton Biomedical Research Centre, University Hospital Southampton NHS Foundation Trust, Southampton, UK., Lucas JS; School of Clinical and Experimental Sciences, University of Southampton Faculty of Medicine, Southampton, UK.; Primary Ciliary Dyskinesia Centre, NIHR Southampton Biomedical Research Centre, University Hospital Southampton NHS Foundation Trust, Southampton, UK., Jackson CL; School of Clinical and Experimental Sciences, University of Southampton Faculty of Medicine, Southampton, UK.; Primary Ciliary Dyskinesia Centre, NIHR Southampton Biomedical Research Centre, University Hospital Southampton NHS Foundation Trust, Southampton, UK., Rubbo B; School of Clinical and Experimental Sciences, University of Southampton Faculty of Medicine, Southampton, UK B.Rubbo@soton.ac.uk.; Primary Ciliary Dyskinesia Centre, NIHR Southampton Biomedical Research Centre, University Hospital Southampton NHS Foundation Trust, Southampton, UK.
Source: European respiratory review : an official journal of the European Respiratory Society [Eur Respir Rev] 2026 Jul 01; Vol. 35 (181). Date of Electronic Publication: 2026 Jul 01 (Print Publication: 2026).
Publication Type: Journal Article; Scoping Review; Review
Journal Info: Publisher: European Respiratory Society Country of Publication: England NLM ID: 9111391 Publication Model: Electronic-Print Cited Medium: Internet ISSN: 1600-0617 (Electronic) Linking ISSN: 09059180 NLM ISO Abbreviation: Eur Respir Rev Subsets: MEDLINE
Database: MEDLINE Ultimate
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  Data: <searchLink fieldCode="AU" term="%22Ong+JWY%22">Ong JWY</searchLink>; School of Clinical and Experimental Sciences, University of Southampton Faculty of Medicine, Southampton, UK.; Primary Ciliary Dyskinesia Centre, NIHR Southampton Biomedical Research Centre, University Hospital Southampton NHS Foundation Trust, Southampton, UK.<br /><searchLink fieldCode="AU" term="%22Tsang+W%22">Tsang W</searchLink>; School of Clinical and Experimental Sciences, University of Southampton Faculty of Medicine, Southampton, UK.; Primary Ciliary Dyskinesia Centre, NIHR Southampton Biomedical Research Centre, University Hospital Southampton NHS Foundation Trust, Southampton, UK.<br /><searchLink fieldCode="AU" term="%22Lucas+JS%22">Lucas JS</searchLink>; School of Clinical and Experimental Sciences, University of Southampton Faculty of Medicine, Southampton, UK.; Primary Ciliary Dyskinesia Centre, NIHR Southampton Biomedical Research Centre, University Hospital Southampton NHS Foundation Trust, Southampton, UK.<br /><searchLink fieldCode="AU" term="%22Jackson+CL%22">Jackson CL</searchLink>; School of Clinical and Experimental Sciences, University of Southampton Faculty of Medicine, Southampton, UK.; Primary Ciliary Dyskinesia Centre, NIHR Southampton Biomedical Research Centre, University Hospital Southampton NHS Foundation Trust, Southampton, UK.<br /><searchLink fieldCode="AU" term="%22Rubbo+B%22">Rubbo B</searchLink>; School of Clinical and Experimental Sciences, University of Southampton Faculty of Medicine, Southampton, UK B.Rubbo@soton.ac.uk.; Primary Ciliary Dyskinesia Centre, NIHR Southampton Biomedical Research Centre, University Hospital Southampton NHS Foundation Trust, Southampton, UK.
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  Data: <searchLink fieldCode="JN" term="%229111391%22">European respiratory review : an official journal of the European Respiratory Society</searchLink> [Eur Respir Rev] 2026 Jul 01; Vol. 35 (181). <i>Date of Electronic Publication: </i>2026 Jul 01 (<i>Print Publication: </i>2026).
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        Value: 10.1183/16000617.0193-2025
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              Text: 2026 Jul 01
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