Pulmonary exacerbations in patients with genetically confirmed PCD: a prospective observational multicentre study.

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Title: Pulmonary exacerbations in patients with genetically confirmed PCD: a prospective observational multicentre study.
Authors: Anagnostopoulou P; Medical School, University of Cyprus, Nicosia, Cyprus., Kouis P; Medical School, University of Cyprus, Nicosia, Cyprus., Tural DA; School of Medicine, Hacettepe University, Ankara, Turkey., Altaraihi S; Danish PCD Centre Copenhagen, Paediatric Pulmonary Service, Copenhagen University Hospital, Copenhagen, Denmark., Basilicata S; Federico II University, Naples, Italy., Borrelli M; Federico II University, Naples, Italy., Christofidou A; Medical School, University of Cyprus, Nicosia, Cyprus., Coemert HN; Danish PCD Centre Copenhagen, Paediatric Pulmonary Service, Copenhagen University Hospital, Copenhagen, Denmark., Cutrera R; Bambino Gesù Children's Hospital, IRCCS, Rome, Italy., Emiralioglou N; School of Medicine, Hacettepe University, Ankara, Turkey., Erdem E; Marmara University School of Medicine, Istanbul, Turkey., Gokdemir Y; Marmara University School of Medicine, Istanbul, Turkey., Gracci S; University Hospital of Pisa, Pisa, Italy., Hatziagorou E; Aristotle University of Thessaloniki, Thessaloniki, Greece., Helms S; University Hospital Muenster, Muenster, Germany., Karadag B; Marmara University School of Medicine, Istanbul, Turkey., Maj D; University Hospital of Pisa, Pisa, Italy., Mall MA; Department of Pediatric Respiratory Medicine, Immunology and Critical Care Medicine, Charité-Universitätsmedizin Berlin, Berlin, Germany.; German Center for Lung Research (DZL), associated partner site, Berlin, Germany.; German Center for Child and Adolescent Health (DZKJ), partner site Berlin, Berlin, Germany.; Berlin Institute of Health at Charité - Universitätsmedizin Berlin, Berlin, Germany., Marthin JK; Danish PCD Centre Copenhagen, Paediatric Pulmonary Service, Copenhagen University Hospital, Copenhagen, Denmark., Middleton N; Cyprus University of Technology, Limassol, Cyprus., Moreno-Galdó A; Department of Pediatrics, Vall D'Hebron Hospital Universitari, Vall D'Hebron Barcelona Hospital Campus, Universitat Autònoma de Barcelona, Barcelona, Spain and CIBER of Rare Diseases (CIBERER), Instituto de Salud Carlos III (ISCIII), Madrid, Spain., Özçelik U; School of Medicine, Hacettepe University, Ankara, Turkey., Pifferi M; University Hospital of Pisa, Pisa, Italy., Raidt J; University Hospital Muenster, Muenster, Germany., Röhmel J; Department of Pediatric Respiratory Medicine, Immunology and Critical Care Medicine, Charité-Universitätsmedizin Berlin, Berlin, Germany.; German Center for Lung Research (DZL), associated partner site, Berlin, Germany.; German Center for Child and Adolescent Health (DZKJ), partner site Berlin, Berlin, Germany.; Berlin Institute of Health at Charité - Universitätsmedizin Berlin, Berlin, Germany., Rovira-Amigo S; Department of Pediatrics, Vall D'Hebron Hospital Universitari, Vall D'Hebron Barcelona Hospital Campus, Universitat Autònoma de Barcelona, Barcelona, Spain and CIBER of Rare Diseases (CIBERER), Instituto de Salud Carlos III (ISCIII), Madrid, Spain., Santamaria F; Federico II University, Naples, Italy., Tsiolakis I; Medical School, University of Cyprus, Nicosia, Cyprus., Ullmann N; Bambino Gesù Children's Hospital, IRCCS, Rome, Italy., Ziegahn N; Department of Pediatric Respiratory Medicine, Immunology and Critical Care Medicine, Charité-Universitätsmedizin Berlin, Berlin, Germany., Nielsen KG; Danish PCD Centre Copenhagen, Paediatric Pulmonary Service, Copenhagen University Hospital, Copenhagen, Denmark.; Department of Clinical Medicine, University of Copenhagen, Copenhagen, Denmark., Omran H; University Hospital Muenster, Muenster, Germany., Yiallouros P; Medical School, University of Cyprus, Nicosia, Cyprus.
Source: Frontiers in molecular biosciences [Front Mol Biosci] 2026 Jun 25; Vol. 13, pp. 1767533. Date of Electronic Publication: 2026 Jun 25 (Print Publication: 2026).
Publication Type: Journal Article
Journal Info: Publisher: Frontiers Media S.A Country of Publication: Switzerland NLM ID: 101653173 Publication Model: eCollection Cited Medium: Print ISSN: 2296-889X (Print) Linking ISSN: 2296889X NLM ISO Abbreviation: Front Mol Biosci Subsets: PubMed not MEDLINE
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  Data: Pulmonary exacerbations in patients with genetically confirmed PCD: a prospective observational multicentre study.
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  Data: <searchLink fieldCode="AU" term="%22Anagnostopoulou+P%22">Anagnostopoulou P</searchLink>; Medical School, University of Cyprus, Nicosia, Cyprus.<br /><searchLink fieldCode="AU" term="%22Kouis+P%22">Kouis P</searchLink>; Medical School, University of Cyprus, Nicosia, Cyprus.<br /><searchLink fieldCode="AU" term="%22Tural+DA%22">Tural DA</searchLink>; School of Medicine, Hacettepe University, Ankara, Turkey.<br /><searchLink fieldCode="AU" term="%22Altaraihi+S%22">Altaraihi S</searchLink>; Danish PCD Centre Copenhagen, Paediatric Pulmonary Service, Copenhagen University Hospital, Copenhagen, Denmark.<br /><searchLink fieldCode="AU" term="%22Basilicata+S%22">Basilicata S</searchLink>; Federico II University, Naples, Italy.<br /><searchLink fieldCode="AU" term="%22Borrelli+M%22">Borrelli M</searchLink>; Federico II University, Naples, Italy.<br /><searchLink fieldCode="AU" term="%22Christofidou+A%22">Christofidou A</searchLink>; Medical School, University of Cyprus, Nicosia, Cyprus.<br /><searchLink fieldCode="AU" term="%22Coemert+HN%22">Coemert HN</searchLink>; Danish PCD Centre Copenhagen, Paediatric Pulmonary Service, Copenhagen University Hospital, Copenhagen, Denmark.<br /><searchLink fieldCode="AU" term="%22Cutrera+R%22">Cutrera R</searchLink>; Bambino Gesù Children's Hospital, IRCCS, Rome, Italy.<br /><searchLink fieldCode="AU" term="%22Emiralioglou+N%22">Emiralioglou N</searchLink>; School of Medicine, Hacettepe University, Ankara, Turkey.<br /><searchLink fieldCode="AU" term="%22Erdem+E%22">Erdem E</searchLink>; Marmara University School of Medicine, Istanbul, Turkey.<br /><searchLink fieldCode="AU" term="%22Gokdemir+Y%22">Gokdemir Y</searchLink>; Marmara University School of Medicine, Istanbul, Turkey.<br /><searchLink fieldCode="AU" term="%22Gracci+S%22">Gracci S</searchLink>; University Hospital of Pisa, Pisa, Italy.<br /><searchLink fieldCode="AU" term="%22Hatziagorou+E%22">Hatziagorou E</searchLink>; Aristotle University of Thessaloniki, Thessaloniki, Greece.<br /><searchLink fieldCode="AU" term="%22Helms+S%22">Helms S</searchLink>; University Hospital Muenster, Muenster, Germany.<br /><searchLink fieldCode="AU" term="%22Karadag+B%22">Karadag B</searchLink>; Marmara University School of Medicine, Istanbul, Turkey.<br /><searchLink fieldCode="AU" term="%22Maj+D%22">Maj D</searchLink>; University Hospital of Pisa, Pisa, Italy.<br /><searchLink fieldCode="AU" term="%22Mall+MA%22">Mall MA</searchLink>; Department of Pediatric Respiratory Medicine, Immunology and Critical Care Medicine, Charité-Universitätsmedizin Berlin, Berlin, Germany.; German Center for Lung Research (DZL), associated partner site, Berlin, Germany.; German Center for Child and Adolescent Health (DZKJ), partner site Berlin, Berlin, Germany.; Berlin Institute of Health at Charité - Universitätsmedizin Berlin, Berlin, Germany.<br /><searchLink fieldCode="AU" term="%22Marthin+JK%22">Marthin JK</searchLink>; Danish PCD Centre Copenhagen, Paediatric Pulmonary Service, Copenhagen University Hospital, Copenhagen, Denmark.<br /><searchLink fieldCode="AU" term="%22Middleton+N%22">Middleton N</searchLink>; Cyprus University of Technology, Limassol, Cyprus.<br /><searchLink fieldCode="AU" term="%22Moreno-Galdó+A%22">Moreno-Galdó A</searchLink>; Department of Pediatrics, Vall D'Hebron Hospital Universitari, Vall D'Hebron Barcelona Hospital Campus, Universitat Autònoma de Barcelona, Barcelona, Spain and CIBER of Rare Diseases (CIBERER), Instituto de Salud Carlos III (ISCIII), Madrid, Spain.<br /><searchLink fieldCode="AU" term="%22Özçelik+U%22">Özçelik U</searchLink>; School of Medicine, Hacettepe University, Ankara, Turkey.<br /><searchLink fieldCode="AU" term="%22Pifferi+M%22">Pifferi M</searchLink>; University Hospital of Pisa, Pisa, Italy.<br /><searchLink fieldCode="AU" term="%22Raidt+J%22">Raidt J</searchLink>; University Hospital Muenster, Muenster, Germany.<br /><searchLink fieldCode="AU" term="%22Röhmel+J%22">Röhmel J</searchLink>; Department of Pediatric Respiratory Medicine, Immunology and Critical Care Medicine, Charité-Universitätsmedizin Berlin, Berlin, Germany.; German Center for Lung Research (DZL), associated partner site, Berlin, Germany.; German Center for Child and Adolescent Health (DZKJ), partner site Berlin, Berlin, Germany.; Berlin Institute of Health at Charité - Universitätsmedizin Berlin, Berlin, Germany.<br /><searchLink fieldCode="AU" term="%22Rovira-Amigo+S%22">Rovira-Amigo S</searchLink>; Department of Pediatrics, Vall D'Hebron Hospital Universitari, Vall D'Hebron Barcelona Hospital Campus, Universitat Autònoma de Barcelona, Barcelona, Spain and CIBER of Rare Diseases (CIBERER), Instituto de Salud Carlos III (ISCIII), Madrid, Spain.<br /><searchLink fieldCode="AU" term="%22Santamaria+F%22">Santamaria F</searchLink>; Federico II University, Naples, Italy.<br /><searchLink fieldCode="AU" term="%22Tsiolakis+I%22">Tsiolakis I</searchLink>; Medical School, University of Cyprus, Nicosia, Cyprus.<br /><searchLink fieldCode="AU" term="%22Ullmann+N%22">Ullmann N</searchLink>; Bambino Gesù Children's Hospital, IRCCS, Rome, Italy.<br /><searchLink fieldCode="AU" term="%22Ziegahn+N%22">Ziegahn N</searchLink>; Department of Pediatric Respiratory Medicine, Immunology and Critical Care Medicine, Charité-Universitätsmedizin Berlin, Berlin, Germany.<br /><searchLink fieldCode="AU" term="%22Nielsen+KG%22">Nielsen KG</searchLink>; Danish PCD Centre Copenhagen, Paediatric Pulmonary Service, Copenhagen University Hospital, Copenhagen, Denmark.; Department of Clinical Medicine, University of Copenhagen, Copenhagen, Denmark.<br /><searchLink fieldCode="AU" term="%22Omran+H%22">Omran H</searchLink>; University Hospital Muenster, Muenster, Germany.<br /><searchLink fieldCode="AU" term="%22Yiallouros+P%22">Yiallouros P</searchLink>; Medical School, University of Cyprus, Nicosia, Cyprus.
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  Data: <searchLink fieldCode="JN" term="%22101653173%22">Frontiers in molecular biosciences</searchLink> [Front Mol Biosci] 2026 Jun 25; Vol. 13, pp. 1767533. <i>Date of Electronic Publication: </i>2026 Jun 25 (<i>Print Publication: </i>2026).
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  Data: <i>Publisher: </i><searchLink fieldCode="PB" term="%22Frontiers+Media+S%2EA%22">Frontiers Media S.A </searchLink><i>Country of Publication: </i>Switzerland <i>NLM ID: </i>101653173 <i>Publication Model: </i>eCollection <i>Cited Medium: </i>Print <i>ISSN: </i>2296-889X (Print) <i>Linking ISSN: </i><searchLink fieldCode="IS" term="%222296889X%22">2296889X </searchLink><i>NLM ISO Abbreviation: </i>Front Mol Biosci <i>Subsets: </i>PubMed not MEDLINE
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