Pulmonary function assessment in an infant with Barnes syndrome: proactive evaluation for surgical intervention.
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| Title: | Pulmonary function assessment in an infant with Barnes syndrome: proactive evaluation for surgical intervention. |
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| Authors: | Miller TL (AUTHOR), Cox T (AUTHOR), Blackson T (AUTHOR), Paul D (AUTHOR), Weiss K (AUTHOR), Shaffer TH (AUTHOR) |
| Source: | Pediatrics. Oct2006, Vol. 118 Issue 4, pe1264-7. 1p. |
| Abstract: | Our aim for this study was to report pulmonary mechanics in a neonate with a severe case of Barnes syndrome, a rare form of thoracolaryngopelvic dysplasia, and to use these data to guide ventilatory support and serve as a presurgical screening tool. A comprehensive pulmonary function evaluation was performed on a 36-day-old patient with Barnes syndrome who was being mechanically ventilated because of severe pulmonary distress secondary to thoracic dystrophy. The measurements consisted of respiratory volumes including functional residual capacity, ventilatory mechanics including compliance and resistance, and thoracoabdominal synchrony. Chest wall compliance was 64% below normal, and the thoracoabdominal motion was indicative of predominantly abdominal displacement during inspiratory breaths. The lungs were functioning at a low functional residual capacity, resulting in low lung compliance and increased pulmonary resistance. As a result of the evaluation, the patient was recommended for lateral thoracic expansion surgery and the ventilatory management was adjusted to focus on end-distending pressure support. [ABSTRACT FROM AUTHOR] |
| Copyright of Pediatrics is the property of American Academy of Pediatrics and its content may not be copied or emailed to multiple sites without the copyright holder's express written permission. Additionally, content may not be used with any artificial intelligence tools or machine learning technologies. However, users may print, download, or email articles for individual use. This abstract may be abridged. No warranty is given about the accuracy of the copy. Users should refer to the original published version of the material for the full abstract. (Copyright applies to all Abstracts.) | |
| Database: | Psychology and Behavioral Sciences Collection |
| FullText | Text: Availability: 0 |
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| Header | DbId: pbh DbLabel: Psychology and Behavioral Sciences Collection An: 106219047 AccessLevel: 6 PubType: Academic Journal PubTypeId: academicJournal PreciseRelevancyScore: 0 |
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| Items | – Name: Title Label: Title Group: Ti Data: Pulmonary function assessment in an infant with Barnes syndrome: proactive evaluation for surgical intervention. – Name: Author Label: Authors Group: Au Data: <searchLink fieldCode="AR" term="%22Miller+TL%22">Miller TL</searchLink> (AUTHOR)<br /><searchLink fieldCode="AR" term="%22Cox+T%22">Cox T</searchLink> (AUTHOR)<br /><searchLink fieldCode="AR" term="%22Blackson+T%22">Blackson T</searchLink> (AUTHOR)<br /><searchLink fieldCode="AR" term="%22Paul+D%22">Paul D</searchLink> (AUTHOR)<br /><searchLink fieldCode="AR" term="%22Weiss+K%22">Weiss K</searchLink> (AUTHOR)<br /><searchLink fieldCode="AR" term="%22Shaffer+TH%22">Shaffer TH</searchLink> (AUTHOR) – Name: TitleSource Label: Source Group: Src Data: <searchLink fieldCode="JN" term="%22Pediatrics%22">Pediatrics</searchLink>. Oct2006, Vol. 118 Issue 4, pe1264-7. 1p. – Name: Abstract Label: Abstract Group: Ab Data: Our aim for this study was to report pulmonary mechanics in a neonate with a severe case of Barnes syndrome, a rare form of thoracolaryngopelvic dysplasia, and to use these data to guide ventilatory support and serve as a presurgical screening tool. A comprehensive pulmonary function evaluation was performed on a 36-day-old patient with Barnes syndrome who was being mechanically ventilated because of severe pulmonary distress secondary to thoracic dystrophy. The measurements consisted of respiratory volumes including functional residual capacity, ventilatory mechanics including compliance and resistance, and thoracoabdominal synchrony. Chest wall compliance was 64% below normal, and the thoracoabdominal motion was indicative of predominantly abdominal displacement during inspiratory breaths. The lungs were functioning at a low functional residual capacity, resulting in low lung compliance and increased pulmonary resistance. As a result of the evaluation, the patient was recommended for lateral thoracic expansion surgery and the ventilatory management was adjusted to focus on end-distending pressure support. [ABSTRACT FROM AUTHOR] – Name: AbstractSuppliedCopyright Label: Group: Ab Data: <i>Copyright of Pediatrics is the property of American Academy of Pediatrics and its content may not be copied or emailed to multiple sites without the copyright holder's express written permission. Additionally, content may not be used with any artificial intelligence tools or machine learning technologies. However, users may print, download, or email articles for individual use. This abstract may be abridged. No warranty is given about the accuracy of the copy. Users should refer to the original published version of the material for the full abstract.</i> (Copyright applies to all Abstracts.) |
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| RecordInfo | BibRecord: BibEntity: Identifiers: – Type: doi Value: 10.1542/peds.2006-0135 Languages: – Code: eng Text: English PhysicalDescription: Pagination: PageCount: 1 StartPage: e1264 Titles: – TitleFull: Pulmonary function assessment in an infant with Barnes syndrome: proactive evaluation for surgical intervention. Type: main BibRelationships: HasContributorRelationships: – PersonEntity: Name: NameFull: Miller TL – PersonEntity: Name: NameFull: Cox T – PersonEntity: Name: NameFull: Blackson T – PersonEntity: Name: NameFull: Paul D – PersonEntity: Name: NameFull: Weiss K – PersonEntity: Name: NameFull: Shaffer TH IsPartOfRelationships: – BibEntity: Dates: – D: 01 M: 10 Text: Oct2006 Type: published Y: 2006 Identifiers: – Type: issn-print Value: 00314005 Numbering: – Type: volume Value: 118 – Type: issue Value: 4 Titles: – TitleFull: Pediatrics Type: main |
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