Juvenile asymmetric segmental spinal muscular atrophy (Hirayama's disease) Three cases without evidence of “flexion myelopathy”.
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| Title: | Juvenile asymmetric segmental spinal muscular atrophy (Hirayama's disease) Three cases without evidence of “flexion myelopathy”. |
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| Authors: | Willeit, J., Kiechl, S., Kiechl-Kohlendorfer, U., Golaszewski, S., Peer, S., Poewe, W. |
| Source: | Acta Neurologica Scandinavica. Nov2001, Vol. 104 Issue 5, p320-322. 3p. 4 Black and White Photographs. |
| Subjects: | Spinal muscular atrophy, Cervical vertebrae diseases |
| Abstract: | Compression of the cervical spinal cord during neck movements (“flexion myelopathy”) was proposed to be the main pathomechanism of juvenile asymmetric spinal muscular atrophy (JASSMA). We present 3 patients with the clinical appearance of JASSMA and typical high-intensity signals in the anterior horn cell region of the lower cervical spinal cord (T2-weighted magnetic resonance images) but without evidence of dynamic spinal cord compression. In all these patients pathomechanism distinct from mechanical damage must be assumed. [ABSTRACT FROM AUTHOR] |
| Copyright of Acta Neurologica Scandinavica is the property of Wiley-Blackwell and its content may not be copied or emailed to multiple sites without the copyright holder's express written permission. Additionally, content may not be used with any artificial intelligence tools or machine learning technologies. However, users may print, download, or email articles for individual use. This abstract may be abridged. No warranty is given about the accuracy of the copy. Users should refer to the original published version of the material for the full abstract. (Copyright applies to all Abstracts.) | |
| Database: | Psychology and Behavioral Sciences Collection |
| FullText | Links: – Type: pdflink Text: Availability: 0 |
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| Header | DbId: pbh DbLabel: Psychology and Behavioral Sciences Collection An: 5388295 AccessLevel: 6 PubType: Academic Journal PubTypeId: academicJournal PreciseRelevancyScore: 0 |
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| Items | – Name: Title Label: Title Group: Ti Data: Juvenile asymmetric segmental spinal muscular atrophy (Hirayama's disease) Three cases without evidence of “flexion myelopathy”. – Name: Author Label: Authors Group: Au Data: <searchLink fieldCode="AR" term="%22Willeit%2C+J%2E%22">Willeit, J.</searchLink><br /><searchLink fieldCode="AR" term="%22Kiechl%2C+S%2E%22">Kiechl, S.</searchLink><br /><searchLink fieldCode="AR" term="%22Kiechl-Kohlendorfer%2C+U%2E%22">Kiechl-Kohlendorfer, U.</searchLink><br /><searchLink fieldCode="AR" term="%22Golaszewski%2C+S%2E%22">Golaszewski, S.</searchLink><br /><searchLink fieldCode="AR" term="%22Peer%2C+S%2E%22">Peer, S.</searchLink><br /><searchLink fieldCode="AR" term="%22Poewe%2C+W%2E%22">Poewe, W.</searchLink> – Name: TitleSource Label: Source Group: Src Data: <searchLink fieldCode="JN" term="%22Acta+Neurologica+Scandinavica%22">Acta Neurologica Scandinavica</searchLink>. Nov2001, Vol. 104 Issue 5, p320-322. 3p. 4 Black and White Photographs. – Name: Subject Label: Subjects Group: Su Data: <searchLink fieldCode="DE" term="%22Spinal+muscular+atrophy%22">Spinal muscular atrophy</searchLink><br /><searchLink fieldCode="DE" term="%22Cervical+vertebrae+diseases%22">Cervical vertebrae diseases</searchLink> – Name: Abstract Label: Abstract Group: Ab Data: Compression of the cervical spinal cord during neck movements (“flexion myelopathy”) was proposed to be the main pathomechanism of juvenile asymmetric spinal muscular atrophy (JASSMA). We present 3 patients with the clinical appearance of JASSMA and typical high-intensity signals in the anterior horn cell region of the lower cervical spinal cord (T2-weighted magnetic resonance images) but without evidence of dynamic spinal cord compression. In all these patients pathomechanism distinct from mechanical damage must be assumed. [ABSTRACT FROM AUTHOR] – Name: AbstractSuppliedCopyright Label: Group: Ab Data: <i>Copyright of Acta Neurologica Scandinavica is the property of Wiley-Blackwell and its content may not be copied or emailed to multiple sites without the copyright holder's express written permission. Additionally, content may not be used with any artificial intelligence tools or machine learning technologies. However, users may print, download, or email articles for individual use. This abstract may be abridged. No warranty is given about the accuracy of the copy. Users should refer to the original published version of the material for the full abstract.</i> (Copyright applies to all Abstracts.) |
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| RecordInfo | BibRecord: BibEntity: Identifiers: – Type: doi Value: 10.1034/j.1600-0404.2001.00074.x Languages: – Code: eng Text: English PhysicalDescription: Pagination: PageCount: 3 StartPage: 320 Subjects: – SubjectFull: Spinal muscular atrophy Type: general – SubjectFull: Cervical vertebrae diseases Type: general Titles: – TitleFull: Juvenile asymmetric segmental spinal muscular atrophy (Hirayama's disease) Three cases without evidence of “flexion myelopathy”. Type: main BibRelationships: HasContributorRelationships: – PersonEntity: Name: NameFull: Willeit, J. – PersonEntity: Name: NameFull: Kiechl, S. – PersonEntity: Name: NameFull: Kiechl-Kohlendorfer, U. – PersonEntity: Name: NameFull: Golaszewski, S. – PersonEntity: Name: NameFull: Peer, S. – PersonEntity: Name: NameFull: Poewe, W. IsPartOfRelationships: – BibEntity: Dates: – D: 01 M: 11 Text: Nov2001 Type: published Y: 2001 Identifiers: – Type: issn-print Value: 00016314 Numbering: – Type: volume Value: 104 – Type: issue Value: 5 Titles: – TitleFull: Acta Neurologica Scandinavica Type: main |
| ResultId | 1 |
