An analog of glibenclamide selectively enhances autophagic degradation of misfolded α1-antitrypsin Z.
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| Title: | An analog of glibenclamide selectively enhances autophagic degradation of misfolded α1-antitrypsin Z. |
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| Authors: | Wang Y; Department of Pediatrics, University of Pittsburgh School of Medicine, Pittsburgh, Pennsylvania, United States of America., Cobanoglu MC; Department of Computational and Systems Biology, University of Pittsburgh School of Medicine, Pittsburgh, Pennsylvania, United States of America., Li J; Department of Pediatrics, University of Pittsburgh School of Medicine, Pittsburgh, Pennsylvania, United States of America.; Department of Pediatrics, Washington University School of Medicine, St. Louis, Missouri, United States of America., Hidvegi T; Department of Pediatrics, University of Pittsburgh School of Medicine, Pittsburgh, Pennsylvania, United States of America.; Department of Pediatrics, Washington University School of Medicine, St. Louis, Missouri, United States of America., Hale P; Department of Pediatrics, University of Pittsburgh School of Medicine, Pittsburgh, Pennsylvania, United States of America.; Department of Pediatrics, Washington University School of Medicine, St. Louis, Missouri, United States of America., Ewing M; Department of Pediatrics, University of Pittsburgh School of Medicine, Pittsburgh, Pennsylvania, United States of America., Chu AS; Department of Pediatrics, University of Pittsburgh School of Medicine, Pittsburgh, Pennsylvania, United States of America., Gong Z; Department of Pediatrics, University of Pittsburgh School of Medicine, Pittsburgh, Pennsylvania, United States of America., Muzumdar R; Department of Pediatrics, University of Pittsburgh School of Medicine, Pittsburgh, Pennsylvania, United States of America., Pak SC; Department of Pediatrics, University of Pittsburgh School of Medicine, Pittsburgh, Pennsylvania, United States of America.; Department of Pediatrics, Washington University School of Medicine, St. Louis, Missouri, United States of America., Silverman GA; Department of Pediatrics, University of Pittsburgh School of Medicine, Pittsburgh, Pennsylvania, United States of America.; Department of Pediatrics, Washington University School of Medicine, St. Louis, Missouri, United States of America., Bahar I; Department of Computational and Systems Biology, University of Pittsburgh School of Medicine, Pittsburgh, Pennsylvania, United States of America., Perlmutter DH; Department of Pediatrics, University of Pittsburgh School of Medicine, Pittsburgh, Pennsylvania, United States of America.; Department of Pediatrics, Washington University School of Medicine, St. Louis, Missouri, United States of America. |
| Source: | PloS one [PLoS One] 2019 Jan 23; Vol. 14 (1), pp. e0209748. Date of Electronic Publication: 2019 Jan 23 (Print Publication: 2019). |
| Publication Type: | Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't |
| Journal Info: | Publisher: Public Library of Science Country of Publication: United States NLM ID: 101285081 Publication Model: eCollection Cited Medium: Internet ISSN: 1932-6203 (Electronic) Linking ISSN: 19326203 NLM ISO Abbreviation: PLoS One Subsets: MEDLINE |
| Database: | MEDLINE Ultimate |
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| ISSN: | 1932-6203 |
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| DOI: | 10.1371/journal.pone.0209748 |