An analog of glibenclamide selectively enhances autophagic degradation of misfolded α1-antitrypsin Z.

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Title: An analog of glibenclamide selectively enhances autophagic degradation of misfolded α1-antitrypsin Z.
Authors: Wang Y; Department of Pediatrics, University of Pittsburgh School of Medicine, Pittsburgh, Pennsylvania, United States of America., Cobanoglu MC; Department of Computational and Systems Biology, University of Pittsburgh School of Medicine, Pittsburgh, Pennsylvania, United States of America., Li J; Department of Pediatrics, University of Pittsburgh School of Medicine, Pittsburgh, Pennsylvania, United States of America.; Department of Pediatrics, Washington University School of Medicine, St. Louis, Missouri, United States of America., Hidvegi T; Department of Pediatrics, University of Pittsburgh School of Medicine, Pittsburgh, Pennsylvania, United States of America.; Department of Pediatrics, Washington University School of Medicine, St. Louis, Missouri, United States of America., Hale P; Department of Pediatrics, University of Pittsburgh School of Medicine, Pittsburgh, Pennsylvania, United States of America.; Department of Pediatrics, Washington University School of Medicine, St. Louis, Missouri, United States of America., Ewing M; Department of Pediatrics, University of Pittsburgh School of Medicine, Pittsburgh, Pennsylvania, United States of America., Chu AS; Department of Pediatrics, University of Pittsburgh School of Medicine, Pittsburgh, Pennsylvania, United States of America., Gong Z; Department of Pediatrics, University of Pittsburgh School of Medicine, Pittsburgh, Pennsylvania, United States of America., Muzumdar R; Department of Pediatrics, University of Pittsburgh School of Medicine, Pittsburgh, Pennsylvania, United States of America., Pak SC; Department of Pediatrics, University of Pittsburgh School of Medicine, Pittsburgh, Pennsylvania, United States of America.; Department of Pediatrics, Washington University School of Medicine, St. Louis, Missouri, United States of America., Silverman GA; Department of Pediatrics, University of Pittsburgh School of Medicine, Pittsburgh, Pennsylvania, United States of America.; Department of Pediatrics, Washington University School of Medicine, St. Louis, Missouri, United States of America., Bahar I; Department of Computational and Systems Biology, University of Pittsburgh School of Medicine, Pittsburgh, Pennsylvania, United States of America., Perlmutter DH; Department of Pediatrics, University of Pittsburgh School of Medicine, Pittsburgh, Pennsylvania, United States of America.; Department of Pediatrics, Washington University School of Medicine, St. Louis, Missouri, United States of America.
Source: PloS one [PLoS One] 2019 Jan 23; Vol. 14 (1), pp. e0209748. Date of Electronic Publication: 2019 Jan 23 (Print Publication: 2019).
Publication Type: Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't
Journal Info: Publisher: Public Library of Science Country of Publication: United States NLM ID: 101285081 Publication Model: eCollection Cited Medium: Internet ISSN: 1932-6203 (Electronic) Linking ISSN: 19326203 NLM ISO Abbreviation: PLoS One Subsets: MEDLINE
Database: MEDLINE Ultimate
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ISSN:1932-6203
DOI:10.1371/journal.pone.0209748