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A therapy with miglustat, 2-hydroxypropyl-ß-cyclodextrin and allopregnanolone restores splenic cholesterol homeostasis in Niemann-pick disease type C1.

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Title: A therapy with miglustat, 2-hydroxypropyl-ß-cyclodextrin and allopregnanolone restores splenic cholesterol homeostasis in Niemann-pick disease type C1.
Authors: Neßlauer AM; Institute of Anatomy, Rostock University Medical Center, Gertrudenstraße 9, 18057, Rostock, Germany., Gläser A; Institute of Anatomy, Rostock University Medical Center, Gertrudenstraße 9, 18057, Rostock, Germany.; Research Group Anatomy, School of Medicine and Health Sciences, Department für Humanmedizin, Abteilung Anatomie, Carl von Ossietzky University Oldenburg, Carl-von-Ossietzky Straße 9-11, 26129, Oldenburg, Germany., Gräler M; Department of Anesthesiology and Intensive Care Medicine, Center for Sepsis Control and Care (CSCC), and the Center for Molecular Biomedicine (CMB), Jena University Hospital, Hans-Knöll-Str. 2, 07745, Jena, Germany., Engelmann R; Institute of Immunology, Rostock University Medical Center, Schillingallee 70, 18057, Rostock, Germany., Müller-Hilke B; Institute of Immunology, Rostock University Medical Center, Schillingallee 70, 18057, Rostock, Germany., Frank M; Medical Biology and Electron Microscopy Center, Rostock University Medical Center, Strempelstraße 14, 18057, Rostock, Germany., Burstein C; Institute of Clinical Chemistry and Pathobiochemistry, Rostock University Medical Center, Ernst-Heydemann-Straße 6, 18057, Rostock, Germany., Rolfs A; Centogene AG, Am Strande 7, 18055, Rostock, Germany., Neidhardt J; Human Genetics, Faculty of Medicine and Health Sciences, University of Oldenburg, Oldenburg, Germany.; Research Center for Neurosensory Science, Carl von Ossietzky University Oldenburg, Oldenburg, Germany., Wree A; Institute of Anatomy, Rostock University Medical Center, Gertrudenstraße 9, 18057, Rostock, Germany., Witt M; Institute of Anatomy, Rostock University Medical Center, Gertrudenstraße 9, 18057, Rostock, Germany., Bräuer AU; Institute of Anatomy, Rostock University Medical Center, Gertrudenstraße 9, 18057, Rostock, Germany. anja.braeuer@uni-oldenburg.de.; Research Group Anatomy, School of Medicine and Health Sciences, Department für Humanmedizin, Abteilung Anatomie, Carl von Ossietzky University Oldenburg, Carl-von-Ossietzky Straße 9-11, 26129, Oldenburg, Germany. anja.braeuer@uni-oldenburg.de.; Research Center for Neurosensory Science, Carl von Ossietzky University Oldenburg, Oldenburg, Germany. anja.braeuer@uni-oldenburg.de.
Source: Lipids in health and disease [Lipids Health Dis] 2019 Jun 28; Vol. 18 (1), pp. 146. Date of Electronic Publication: 2019 Jun 28.
Publication Type: Journal Article
Journal Info: Publisher: BioMed Central Country of Publication: England NLM ID: 101147696 Publication Model: Electronic Cited Medium: Internet ISSN: 1476-511X (Electronic) Linking ISSN: 1476511X NLM ISO Abbreviation: Lipids Health Dis Subsets: MEDLINE
Database: MEDLINE Ultimate
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  Data: <searchLink fieldCode="AU" term="%22Neßlauer+AM%22">Neßlauer AM</searchLink>; Institute of Anatomy, Rostock University Medical Center, Gertrudenstraße 9, 18057, Rostock, Germany.<br /><searchLink fieldCode="AU" term="%22Gläser+A%22">Gläser A</searchLink>; Institute of Anatomy, Rostock University Medical Center, Gertrudenstraße 9, 18057, Rostock, Germany.; Research Group Anatomy, School of Medicine and Health Sciences, Department für Humanmedizin, Abteilung Anatomie, Carl von Ossietzky University Oldenburg, Carl-von-Ossietzky Straße 9-11, 26129, Oldenburg, Germany.<br /><searchLink fieldCode="AU" term="%22Gräler+M%22">Gräler M</searchLink>; Department of Anesthesiology and Intensive Care Medicine, Center for Sepsis Control and Care (CSCC), and the Center for Molecular Biomedicine (CMB), Jena University Hospital, Hans-Knöll-Str. 2, 07745, Jena, Germany.<br /><searchLink fieldCode="AU" term="%22Engelmann+R%22">Engelmann R</searchLink>; Institute of Immunology, Rostock University Medical Center, Schillingallee 70, 18057, Rostock, Germany.<br /><searchLink fieldCode="AU" term="%22Müller-Hilke+B%22">Müller-Hilke B</searchLink>; Institute of Immunology, Rostock University Medical Center, Schillingallee 70, 18057, Rostock, Germany.<br /><searchLink fieldCode="AU" term="%22Frank+M%22">Frank M</searchLink>; Medical Biology and Electron Microscopy Center, Rostock University Medical Center, Strempelstraße 14, 18057, Rostock, Germany.<br /><searchLink fieldCode="AU" term="%22Burstein+C%22">Burstein C</searchLink>; Institute of Clinical Chemistry and Pathobiochemistry, Rostock University Medical Center, Ernst-Heydemann-Straße 6, 18057, Rostock, Germany.<br /><searchLink fieldCode="AU" term="%22Rolfs+A%22">Rolfs A</searchLink>; Centogene AG, Am Strande 7, 18055, Rostock, Germany.<br /><searchLink fieldCode="AU" term="%22Neidhardt+J%22">Neidhardt J</searchLink>; Human Genetics, Faculty of Medicine and Health Sciences, University of Oldenburg, Oldenburg, Germany.; Research Center for Neurosensory Science, Carl von Ossietzky University Oldenburg, Oldenburg, Germany.<br /><searchLink fieldCode="AU" term="%22Wree+A%22">Wree A</searchLink>; Institute of Anatomy, Rostock University Medical Center, Gertrudenstraße 9, 18057, Rostock, Germany.<br /><searchLink fieldCode="AU" term="%22Witt+M%22">Witt M</searchLink>; Institute of Anatomy, Rostock University Medical Center, Gertrudenstraße 9, 18057, Rostock, Germany.<br /><searchLink fieldCode="AU" term="%22Bräuer+AU%22">Bräuer AU</searchLink>; Institute of Anatomy, Rostock University Medical Center, Gertrudenstraße 9, 18057, Rostock, Germany. anja.braeuer@uni-oldenburg.de.; Research Group Anatomy, School of Medicine and Health Sciences, Department für Humanmedizin, Abteilung Anatomie, Carl von Ossietzky University Oldenburg, Carl-von-Ossietzky Straße 9-11, 26129, Oldenburg, Germany. anja.braeuer@uni-oldenburg.de.; Research Center for Neurosensory Science, Carl von Ossietzky University Oldenburg, Oldenburg, Germany. anja.braeuer@uni-oldenburg.de.
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