The displacement of frataxin from the mitochondrial cristae correlates with abnormal respiratory supercomplexes formation and bioenergetic defects in cells of Friedreich ataxia patients.
Saved in:
| Title: | The displacement of frataxin from the mitochondrial cristae correlates with abnormal respiratory supercomplexes formation and bioenergetic defects in cells of Friedreich ataxia patients. |
|---|---|
| Authors: | Doni D; Department of Biology, University of Padova, Padova, Italy., Rigoni G; Department of Biology, University of Padova, Padova, Italy., Palumbo E; Department of Molecular Medicine, University of Padova, Padova, Italy., Baschiera E; Clinical Genetics Unit, Department of Women's and Children's Health, University of Padova, Padova, Italy.; Istituto di Ricerca Pediatrica (IRP) Città della Speranza, Padova, Italy., Peruzzo R; Department of Biology, University of Padova, Padova, Italy., De Rosa E; Department of Biology, University of Padova, Padova, Italy., Caicci F; Department of Biology, University of Padova, Padova, Italy., Passerini L; Department of Biology, University of Padova, Padova, Italy., Bettio D; Clinical Genetics Unit, Department of Women's and Children's Health, University of Padova, Padova, Italy.; Istituto di Ricerca Pediatrica (IRP) Città della Speranza, Padova, Italy., Russo A; Department of Molecular Medicine, University of Padova, Padova, Italy., Szabò I; Department of Biology, University of Padova, Padova, Italy., Soriano ME; Department of Biology, University of Padova, Padova, Italy., Salviati L; Clinical Genetics Unit, Department of Women's and Children's Health, University of Padova, Padova, Italy.; Istituto di Ricerca Pediatrica (IRP) Città della Speranza, Padova, Italy.; Myology Center, University of Padova, Padova, Italy., Costantini P; Department of Biology, University of Padova, Padova, Italy. |
| Source: | FASEB journal : official publication of the Federation of American Societies for Experimental Biology [FASEB J] 2021 Mar; Vol. 35 (3), pp. e21362. |
| Publication Type: | Journal Article; Research Support, Non-U.S. Gov't |
| Journal Info: | Publisher: Federation of American Societies for Experimental Biology Country of Publication: United States NLM ID: 8804484 Publication Model: Print Cited Medium: Internet ISSN: 1530-6860 (Electronic) Linking ISSN: 08926638 NLM ISO Abbreviation: FASEB J Subsets: MEDLINE |
| Database: | MEDLINE Ultimate |
Be the first to leave a comment!