The displacement of frataxin from the mitochondrial cristae correlates with abnormal respiratory supercomplexes formation and bioenergetic defects in cells of Friedreich ataxia patients.

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Title: The displacement of frataxin from the mitochondrial cristae correlates with abnormal respiratory supercomplexes formation and bioenergetic defects in cells of Friedreich ataxia patients.
Authors: Doni D; Department of Biology, University of Padova, Padova, Italy., Rigoni G; Department of Biology, University of Padova, Padova, Italy., Palumbo E; Department of Molecular Medicine, University of Padova, Padova, Italy., Baschiera E; Clinical Genetics Unit, Department of Women's and Children's Health, University of Padova, Padova, Italy.; Istituto di Ricerca Pediatrica (IRP) Città della Speranza, Padova, Italy., Peruzzo R; Department of Biology, University of Padova, Padova, Italy., De Rosa E; Department of Biology, University of Padova, Padova, Italy., Caicci F; Department of Biology, University of Padova, Padova, Italy., Passerini L; Department of Biology, University of Padova, Padova, Italy., Bettio D; Clinical Genetics Unit, Department of Women's and Children's Health, University of Padova, Padova, Italy.; Istituto di Ricerca Pediatrica (IRP) Città della Speranza, Padova, Italy., Russo A; Department of Molecular Medicine, University of Padova, Padova, Italy., Szabò I; Department of Biology, University of Padova, Padova, Italy., Soriano ME; Department of Biology, University of Padova, Padova, Italy., Salviati L; Clinical Genetics Unit, Department of Women's and Children's Health, University of Padova, Padova, Italy.; Istituto di Ricerca Pediatrica (IRP) Città della Speranza, Padova, Italy.; Myology Center, University of Padova, Padova, Italy., Costantini P; Department of Biology, University of Padova, Padova, Italy.
Source: FASEB journal : official publication of the Federation of American Societies for Experimental Biology [FASEB J] 2021 Mar; Vol. 35 (3), pp. e21362.
Publication Type: Journal Article; Research Support, Non-U.S. Gov't
Journal Info: Publisher: Federation of American Societies for Experimental Biology Country of Publication: United States NLM ID: 8804484 Publication Model: Print Cited Medium: Internet ISSN: 1530-6860 (Electronic) Linking ISSN: 08926638 NLM ISO Abbreviation: FASEB J Subsets: MEDLINE
Database: MEDLINE Ultimate
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