Risk for incident comorbidities, nonhepatic cancer and mortality in acute hepatic porphyria: A matched cohort study in 1244 individuals.

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Title: Risk for incident comorbidities, nonhepatic cancer and mortality in acute hepatic porphyria: A matched cohort study in 1244 individuals.
Authors: Lissing M; Hepatology Division, Department of Upper GI Diseases, Karolinska University Hospital, Stockholm, Sweden.; Department of Medicine, Huddinge, Karolinska Institutet, Stockholm, Sweden., Vassiliou D; Department of Endocrinology, Karolinska University Hospital, Stockholm, Sweden.; Centre for Inherited Metabolic Diseases (CMMS), Porphyria Centre Sweden, Karolinska University Hospital, Stockholm, Sweden.; Department of Molecular Medicine and Surgery, Karolinska Institutet, Stockholm, Sweden., Floderus Y; Centre for Inherited Metabolic Diseases (CMMS), Porphyria Centre Sweden, Karolinska University Hospital, Stockholm, Sweden.; Department of Medical Biochemistry and Biophysics, Karolinska Institutet, Stockholm, Sweden., Harper P; Centre for Inherited Metabolic Diseases (CMMS), Porphyria Centre Sweden, Karolinska University Hospital, Stockholm, Sweden.; Department of Medical Biochemistry and Biophysics, Karolinska Institutet, Stockholm, Sweden., Yan J; Division of Biostatistics, Institute of Environmental Medicine, Karolinska Institutet, Stockholm, Sweden., Hagström H; Hepatology Division, Department of Upper GI Diseases, Karolinska University Hospital, Stockholm, Sweden.; Department of Medicine, Huddinge, Karolinska Institutet, Stockholm, Sweden., Sardh E; Department of Endocrinology, Karolinska University Hospital, Stockholm, Sweden.; Centre for Inherited Metabolic Diseases (CMMS), Porphyria Centre Sweden, Karolinska University Hospital, Stockholm, Sweden.; Department of Molecular Medicine and Surgery, Karolinska Institutet, Stockholm, Sweden., Wahlin S; Hepatology Division, Department of Upper GI Diseases, Karolinska University Hospital, Stockholm, Sweden.; Department of Medicine, Huddinge, Karolinska Institutet, Stockholm, Sweden.
Source: Journal of inherited metabolic disease [J Inherit Metab Dis] 2023 Mar; Vol. 46 (2), pp. 286-299. Date of Electronic Publication: 2022 Dec 30.
Publication Type: Journal Article; Research Support, Non-U.S. Gov't
Journal Info: Publisher: Wiley Country of Publication: United States NLM ID: 7910918 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1573-2665 (Electronic) Linking ISSN: 01418955 NLM ISO Abbreviation: J Inherit Metab Dis Subsets: MEDLINE
Database: MEDLINE Ultimate
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ISSN:1573-2665
DOI:10.1002/jimd.12583