Pervasive nuclear envelope ruptures precede ECM signaling and disease onset without activating cGAS-STING in Lamin-cardiomyopathy mice.

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Title: Pervasive nuclear envelope ruptures precede ECM signaling and disease onset without activating cGAS-STING in Lamin-cardiomyopathy mice.
Authors: En A; Division of Molecular Cardiovascular Biology, Cincinnati Children's Hospital Medical Center, Cincinnati, OH 45229, USA; Graduate School of Nanobioscience, Yokohama City University, Yokohama, Kanagawa 236-0027, Japan., Bogireddi H; Division of Molecular Cardiovascular Biology, Cincinnati Children's Hospital Medical Center, Cincinnati, OH 45229, USA., Thomas B; Division of Molecular Cardiovascular Biology, Cincinnati Children's Hospital Medical Center, Cincinnati, OH 45229, USA., Stutzman AV; Department of Pediatrics, the University of Chicago, Chicago, IL 60637, USA., Ikegami S; Department of Pediatrics, the University of Chicago, Chicago, IL 60637, USA., LaForest B; Department of Pediatrics, the University of Chicago, Chicago, IL 60637, USA., Almakki O; Department of Pediatrics, the University of Chicago, Chicago, IL 60637, USA., Pytel P; Department of Pathology, the University of Chicago, Chicago, IL 60637, USA., Moskowitz IP; Department of Pediatrics, the University of Chicago, Chicago, IL 60637, USA; Department of Pathology, the University of Chicago, Chicago, IL 60637, USA; Department of Human Genetics, the University of Chicago, Chicago, IL 60637, USA., Ikegami K; Division of Molecular Cardiovascular Biology, Cincinnati Children's Hospital Medical Center, Cincinnati, OH 45229, USA; Department of Pediatrics, University of Cincinnati College of Medicine, Cincinnati, OH 45267, USA. Electronic address: kohta.ikegami@cchmc.org.
Source: Cell reports [Cell Rep] 2024 Jun 25; Vol. 43 (6), pp. 114284. Date of Electronic Publication: 2024 May 29.
Publication Type: Journal Article
Journal Info: Publisher: Cell Press Country of Publication: United States NLM ID: 101573691 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 2211-1247 (Electronic) NLM ISO Abbreviation: Cell Rep Subsets: MEDLINE
Database: MEDLINE Ultimate
Description
ISSN:2211-1247
DOI:10.1016/j.celrep.2024.114284