Decreasing ganglioside synthesis delays motor and cognitive symptom onset in Spg11 knockout mice.
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| Title: | Decreasing ganglioside synthesis delays motor and cognitive symptom onset in Spg11 knockout mice. |
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| Authors: | Fortier M; Sorbonne Université, Paris Brain Institute (ICM Institut du Cerveau), INSERM U1127, CNRS UMR 7225, Assistance Publique-Hôpitaux de Paris (AP-HP), Paris, France., Cauhapé M; Sorbonne Université, Paris Brain Institute (ICM Institut du Cerveau), INSERM U1127, CNRS UMR 7225, Assistance Publique-Hôpitaux de Paris (AP-HP), Paris, France., Buono S; Dynacure SA (now Flamingo Therapeutics NV), Illkirch, France., Becker J; Dynacure SA (now Flamingo Therapeutics NV), Illkirch, France., Menuet A; Dynacure SA (now Flamingo Therapeutics NV), Illkirch, France., Branchu J; Sorbonne Université, Paris Brain Institute (ICM Institut du Cerveau), INSERM U1127, CNRS UMR 7225, Assistance Publique-Hôpitaux de Paris (AP-HP), Paris, France., Ricca I; Molecular Medicine, IRCCS Fondazione Stella Maris, 56128 Pisa, Italy., Mero S; Molecular Medicine, IRCCS Fondazione Stella Maris, 56128 Pisa, Italy., Dorgham K; Sorbonne Université, INSERM, Centre d'Immunologie et des Maladies Infectieuses-Paris (CIMI-Paris), Paris, France., El Hachimi KH; Sorbonne Université, Paris Brain Institute (ICM Institut du Cerveau), INSERM U1127, CNRS UMR 7225, Assistance Publique-Hôpitaux de Paris (AP-HP), Paris, France; EPHE, PSL Research University, Paris, France., Dobrenis K; Dominick P. Purpura Department of Neuroscience, Albert Einstein College of Medicine, Bronx, NY 10461, USA., Colsch B; Université Paris-Saclay, CEA, INRAE, Département Médicaments et Technologies pour la Santé, MetaboHUB, Gif sur Yvette, France., Samaroo D; Sorbonne Université, Paris Brain Institute (ICM Institut du Cerveau), INSERM U1127, CNRS UMR 7225, Assistance Publique-Hôpitaux de Paris (AP-HP), Paris, France., Devaux M; Sorbonne Université, Paris Brain Institute (ICM Institut du Cerveau), INSERM U1127, CNRS UMR 7225, Assistance Publique-Hôpitaux de Paris (AP-HP), Paris, France., Durr A; Sorbonne Université, Paris Brain Institute (ICM Institut du Cerveau), INSERM U1127, CNRS UMR 7225, Assistance Publique-Hôpitaux de Paris (AP-HP), Paris, France., Stevanin G; Sorbonne Université, Paris Brain Institute (ICM Institut du Cerveau), INSERM U1127, CNRS UMR 7225, Assistance Publique-Hôpitaux de Paris (AP-HP), Paris, France; EPHE, PSL Research University, Paris, France; University of Bordeaux, CNRS, INCIA, UMR 5287, NRGen Team, Bordeaux, France., Santorelli FM; Molecular Medicine, IRCCS Fondazione Stella Maris, 56128 Pisa, Italy., Colombo S; Dynacure SA (now Flamingo Therapeutics NV), Illkirch, France., Cowling B; Dynacure SA (now Flamingo Therapeutics NV), Illkirch, France., Darios F; Sorbonne Université, Paris Brain Institute (ICM Institut du Cerveau), INSERM U1127, CNRS UMR 7225, Assistance Publique-Hôpitaux de Paris (AP-HP), Paris, France. Electronic address: frederic.darios@icm-institute.org. |
| Source: | Neurobiology of disease [Neurobiol Dis] 2024 Sep; Vol. 199, pp. 106564. Date of Electronic Publication: 2024 Jun 12. |
| Publication Type: | Journal Article; Research Support, Non-U.S. Gov't |
| Journal Info: | Publisher: Academic Press Country of Publication: United States NLM ID: 9500169 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1095-953X (Electronic) Linking ISSN: 09699961 NLM ISO Abbreviation: Neurobiol Dis Subsets: MEDLINE |
| Database: | MEDLINE Ultimate |
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