LTβR deficiency causes lymph node aplasia and impaired B cell differentiation.
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| Title: | LTβR deficiency causes lymph node aplasia and impaired B cell differentiation. |
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| Authors: | Ransmayr B; St. Anna Children's Cancer Research Institute, Vienna, Austria.; CeMM Research Center for Molecular Medicine of the Austrian Academy of Sciences, Vienna, Austria.; Ludwig Boltzmann Institute for Rare and Undiagnosed Diseases, Vienna, Austria., Bal SK; St. Anna Children's Cancer Research Institute, Vienna, Austria.; CeMM Research Center for Molecular Medicine of the Austrian Academy of Sciences, Vienna, Austria.; Ludwig Boltzmann Institute for Rare and Undiagnosed Diseases, Vienna, Austria., Thian M; St. Anna Children's Cancer Research Institute, Vienna, Austria.; CeMM Research Center for Molecular Medicine of the Austrian Academy of Sciences, Vienna, Austria.; Ludwig Boltzmann Institute for Rare and Undiagnosed Diseases, Vienna, Austria., Svaton M; St. Anna Children's Cancer Research Institute, Vienna, Austria.; CeMM Research Center for Molecular Medicine of the Austrian Academy of Sciences, Vienna, Austria., van de Wetering C; St. Anna Children's Cancer Research Institute, Vienna, Austria.; CeMM Research Center for Molecular Medicine of the Austrian Academy of Sciences, Vienna, Austria., Hafemeister C; St. Anna Children's Cancer Research Institute, Vienna, Austria., Segarra-Roca A; St. Anna Children's Cancer Research Institute, Vienna, Austria., Block J; St. Anna Children's Cancer Research Institute, Vienna, Austria.; CeMM Research Center for Molecular Medicine of the Austrian Academy of Sciences, Vienna, Austria.; Ludwig Boltzmann Institute for Rare and Undiagnosed Diseases, Vienna, Austria., Frohne A; St. Anna Children's Cancer Research Institute, Vienna, Austria., Krolo A; CeMM Research Center for Molecular Medicine of the Austrian Academy of Sciences, Vienna, Austria.; Ludwig Boltzmann Institute for Rare and Undiagnosed Diseases, Vienna, Austria., Altunbas MY; Department of Pediatrics, Division of Allergy and Immunology, Marmara University School of Medicine, Istanbul, Turkey.; Istanbul Jeffrey Modell Diagnostic Center for Primary Immunodeficiency Diseases, Istanbul, Turkey.; Işıl Berat Barlan Center for Translational Medicine, Marmara University, Istanbul, Turkey.; Marmara University, Immune Deficiency Application and Research Center, Istanbul, Turkey., Bilgic-Eltan S; Department of Pediatrics, Division of Allergy and Immunology, Marmara University School of Medicine, Istanbul, Turkey.; Istanbul Jeffrey Modell Diagnostic Center for Primary Immunodeficiency Diseases, Istanbul, Turkey.; Işıl Berat Barlan Center for Translational Medicine, Marmara University, Istanbul, Turkey.; Marmara University, Immune Deficiency Application and Research Center, Istanbul, Turkey., Kıykım A; Istanbul University-Cerrahpasa, Faculty of Medicine, Department of Pediatric Allergy and Immunology, Istanbul, Turkey., Aydiner O; Kartal Dr. Lütfi Kırdar City Hospital, Department of Radiology, Istanbul, Turkey., Kesim S; Marmara University, Faculty of Medicine, Department of Nuclear Medicine, Istanbul, Turkey., Inanir S; Marmara University, Faculty of Medicine, Department of Nuclear Medicine, Istanbul, Turkey., Karakoc-Aydiner E; Department of Pediatrics, Division of Allergy and Immunology, Marmara University School of Medicine, Istanbul, Turkey.; Istanbul Jeffrey Modell Diagnostic Center for Primary Immunodeficiency Diseases, Istanbul, Turkey.; Işıl Berat Barlan Center for Translational Medicine, Marmara University, Istanbul, Turkey.; Marmara University, Immune Deficiency Application and Research Center, Istanbul, Turkey., Ozen A; Department of Pediatrics, Division of Allergy and Immunology, Marmara University School of Medicine, Istanbul, Turkey.; Istanbul Jeffrey Modell Diagnostic Center for Primary Immunodeficiency Diseases, Istanbul, Turkey.; Işıl Berat Barlan Center for Translational Medicine, Marmara University, Istanbul, Turkey.; Marmara University, Immune Deficiency Application and Research Center, Istanbul, Turkey., Aba Ü; Can Sucak Research Laboratory for Translational Immunology, Hacettepe University, Ankara, Turkey.; Institute of Child Health, Hacettepe University, Ankara, Turkey., Çomak A; Ankara Bilkent City Hospital, Children's Hospital, Department of Nuclear Medicine, Ankara, Turkey., Tuğcu GD; Ankara Bilkent City Hospital, Children's Hospital, Department of Pediatric Pulmonology, Ankara, Turkey., Pazdzior R; CeMM Research Center for Molecular Medicine of the Austrian Academy of Sciences, Vienna, Austria., Huber B; Medical University of Vienna, Department of Dermatology, Vienna, Austria., Farlik M; Medical University of Vienna, Department of Dermatology, Vienna, Austria., Kubicek S; CeMM Research Center for Molecular Medicine of the Austrian Academy of Sciences, Vienna, Austria., von Bernuth H; Department of Pediatric Respiratory Medicine, Immunology and Critical Care Medicine, Charité University Medicine, Berlin, Corporate Member of Free University and Humboldt University and Berlin Institute of Health, Berlin, Germany.; Labor Berlin Charité-Vivantes, Department of Immunology, Berlin, Germany.; Berlin Institute of International Health Global Health Center Charité - Universitätsmedizin Berlin, Berlin, Germany.; Charité - Universitätsmedizin Berlin, corporate member of Freie Universität Berlin, Humboldt-Universität zu Berlin, and Berlin Institute of Health (BIH), Berlin-Brandenburg Center for Regenerative Therapies (BCRT), Berlin, Germany., Simonitsch-Klupp I; Medical University of Vienna, Department of Pathology, Vienna, Austria., Rizzi M; Department of Rheumatology and Clinical Immunology and Center for Chronic Immunodeficiency, Medical Center University of Freiburg, Faculty of Medicine, University of Freiburg, Freiburg, Germany.; CIBSS - Centre for Integrative Biological Signalling Studies, University of Freiburg, Freiburg, Germany.; Medical University of Vienna, Center for Pathophysiology, Infectiology and Immunology, Institute of Immunology, Vienna, Austria., Halbritter F; St. Anna Children's Cancer Research Institute, Vienna, Austria., Tumanov AV; Department of Microbiology, Immunology, and Molecular Genetics, University of Texas Health Science Center at San Antonio, San Antonio, TX, USA., Kraakman MJ; St. Anna Children's Cancer Research Institute, Vienna, Austria.; CeMM Research Center for Molecular Medicine of the Austrian Academy of Sciences, Vienna, Austria.; Ludwig Boltzmann Institute for Rare and Undiagnosed Diseases, Vienna, Austria., Metin A; Ankara Bilkent City Hospital, Children's Hospital, Department of Pediatric Immunology and Allergy, Ankara, Turkey., Castanon I; St. Anna Children's Cancer Research Institute, Vienna, Austria.; CeMM Research Center for Molecular Medicine of the Austrian Academy of Sciences, Vienna, Austria., Erman B; Can Sucak Research Laboratory for Translational Immunology, Hacettepe University, Ankara, Turkey.; Institute of Child Health, Hacettepe University, Ankara, Turkey., Baris S; Department of Pediatrics, Division of Allergy and Immunology, Marmara University School of Medicine, Istanbul, Turkey.; Istanbul Jeffrey Modell Diagnostic Center for Primary Immunodeficiency Diseases, Istanbul, Turkey.; Işıl Berat Barlan Center for Translational Medicine, Marmara University, Istanbul, Turkey.; Marmara University, Immune Deficiency Application and Research Center, Istanbul, Turkey., Boztug K; St. Anna Children's Cancer Research Institute, Vienna, Austria.; CeMM Research Center for Molecular Medicine of the Austrian Academy of Sciences, Vienna, Austria.; Ludwig Boltzmann Institute for Rare and Undiagnosed Diseases, Vienna, Austria.; Medical University of Vienna, Department of Pediatrics and Adolescent Medicine, Vienna, Austria.; St. Anna Children's Hospital, Vienna, Austria. |
| Source: | Science immunology [Sci Immunol] 2024 Nov 22; Vol. 9 (101), pp. eadq8796. Date of Electronic Publication: 2024 Nov 22. |
| Publication Type: | Journal Article; Research Support, Non-U.S. Gov't |
| Journal Info: | Publisher: American Association for the Advancement of Science Country of Publication: United States NLM ID: 101688624 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 2470-9468 (Electronic) Linking ISSN: 24709468 NLM ISO Abbreviation: Sci Immunol Subsets: MEDLINE |
| Database: | MEDLINE Ultimate |
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| ISSN: | 2470-9468 |
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| DOI: | 10.1126/sciimmunol.adq8796 |