LTβR deficiency causes lymph node aplasia and impaired B cell differentiation.

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Title: LTβR deficiency causes lymph node aplasia and impaired B cell differentiation.
Authors: Ransmayr B; St. Anna Children's Cancer Research Institute, Vienna, Austria.; CeMM Research Center for Molecular Medicine of the Austrian Academy of Sciences, Vienna, Austria.; Ludwig Boltzmann Institute for Rare and Undiagnosed Diseases, Vienna, Austria., Bal SK; St. Anna Children's Cancer Research Institute, Vienna, Austria.; CeMM Research Center for Molecular Medicine of the Austrian Academy of Sciences, Vienna, Austria.; Ludwig Boltzmann Institute for Rare and Undiagnosed Diseases, Vienna, Austria., Thian M; St. Anna Children's Cancer Research Institute, Vienna, Austria.; CeMM Research Center for Molecular Medicine of the Austrian Academy of Sciences, Vienna, Austria.; Ludwig Boltzmann Institute for Rare and Undiagnosed Diseases, Vienna, Austria., Svaton M; St. Anna Children's Cancer Research Institute, Vienna, Austria.; CeMM Research Center for Molecular Medicine of the Austrian Academy of Sciences, Vienna, Austria., van de Wetering C; St. Anna Children's Cancer Research Institute, Vienna, Austria.; CeMM Research Center for Molecular Medicine of the Austrian Academy of Sciences, Vienna, Austria., Hafemeister C; St. Anna Children's Cancer Research Institute, Vienna, Austria., Segarra-Roca A; St. Anna Children's Cancer Research Institute, Vienna, Austria., Block J; St. Anna Children's Cancer Research Institute, Vienna, Austria.; CeMM Research Center for Molecular Medicine of the Austrian Academy of Sciences, Vienna, Austria.; Ludwig Boltzmann Institute for Rare and Undiagnosed Diseases, Vienna, Austria., Frohne A; St. Anna Children's Cancer Research Institute, Vienna, Austria., Krolo A; CeMM Research Center for Molecular Medicine of the Austrian Academy of Sciences, Vienna, Austria.; Ludwig Boltzmann Institute for Rare and Undiagnosed Diseases, Vienna, Austria., Altunbas MY; Department of Pediatrics, Division of Allergy and Immunology, Marmara University School of Medicine, Istanbul, Turkey.; Istanbul Jeffrey Modell Diagnostic Center for Primary Immunodeficiency Diseases, Istanbul, Turkey.; Işıl Berat Barlan Center for Translational Medicine, Marmara University, Istanbul, Turkey.; Marmara University, Immune Deficiency Application and Research Center, Istanbul, Turkey., Bilgic-Eltan S; Department of Pediatrics, Division of Allergy and Immunology, Marmara University School of Medicine, Istanbul, Turkey.; Istanbul Jeffrey Modell Diagnostic Center for Primary Immunodeficiency Diseases, Istanbul, Turkey.; Işıl Berat Barlan Center for Translational Medicine, Marmara University, Istanbul, Turkey.; Marmara University, Immune Deficiency Application and Research Center, Istanbul, Turkey., Kıykım A; Istanbul University-Cerrahpasa, Faculty of Medicine, Department of Pediatric Allergy and Immunology, Istanbul, Turkey., Aydiner O; Kartal Dr. Lütfi Kırdar City Hospital, Department of Radiology, Istanbul, Turkey., Kesim S; Marmara University, Faculty of Medicine, Department of Nuclear Medicine, Istanbul, Turkey., Inanir S; Marmara University, Faculty of Medicine, Department of Nuclear Medicine, Istanbul, Turkey., Karakoc-Aydiner E; Department of Pediatrics, Division of Allergy and Immunology, Marmara University School of Medicine, Istanbul, Turkey.; Istanbul Jeffrey Modell Diagnostic Center for Primary Immunodeficiency Diseases, Istanbul, Turkey.; Işıl Berat Barlan Center for Translational Medicine, Marmara University, Istanbul, Turkey.; Marmara University, Immune Deficiency Application and Research Center, Istanbul, Turkey., Ozen A; Department of Pediatrics, Division of Allergy and Immunology, Marmara University School of Medicine, Istanbul, Turkey.; Istanbul Jeffrey Modell Diagnostic Center for Primary Immunodeficiency Diseases, Istanbul, Turkey.; Işıl Berat Barlan Center for Translational Medicine, Marmara University, Istanbul, Turkey.; Marmara University, Immune Deficiency Application and Research Center, Istanbul, Turkey., Aba Ü; Can Sucak Research Laboratory for Translational Immunology, Hacettepe University, Ankara, Turkey.; Institute of Child Health, Hacettepe University, Ankara, Turkey., Çomak A; Ankara Bilkent City Hospital, Children's Hospital, Department of Nuclear Medicine, Ankara, Turkey., Tuğcu GD; Ankara Bilkent City Hospital, Children's Hospital, Department of Pediatric Pulmonology, Ankara, Turkey., Pazdzior R; CeMM Research Center for Molecular Medicine of the Austrian Academy of Sciences, Vienna, Austria., Huber B; Medical University of Vienna, Department of Dermatology, Vienna, Austria., Farlik M; Medical University of Vienna, Department of Dermatology, Vienna, Austria., Kubicek S; CeMM Research Center for Molecular Medicine of the Austrian Academy of Sciences, Vienna, Austria., von Bernuth H; Department of Pediatric Respiratory Medicine, Immunology and Critical Care Medicine, Charité University Medicine, Berlin, Corporate Member of Free University and Humboldt University and Berlin Institute of Health, Berlin, Germany.; Labor Berlin Charité-Vivantes, Department of Immunology, Berlin, Germany.; Berlin Institute of International Health Global Health Center Charité - Universitätsmedizin Berlin, Berlin, Germany.; Charité - Universitätsmedizin Berlin, corporate member of Freie Universität Berlin, Humboldt-Universität zu Berlin, and Berlin Institute of Health (BIH), Berlin-Brandenburg Center for Regenerative Therapies (BCRT), Berlin, Germany., Simonitsch-Klupp I; Medical University of Vienna, Department of Pathology, Vienna, Austria., Rizzi M; Department of Rheumatology and Clinical Immunology and Center for Chronic Immunodeficiency, Medical Center University of Freiburg, Faculty of Medicine, University of Freiburg, Freiburg, Germany.; CIBSS - Centre for Integrative Biological Signalling Studies, University of Freiburg, Freiburg, Germany.; Medical University of Vienna, Center for Pathophysiology, Infectiology and Immunology, Institute of Immunology, Vienna, Austria., Halbritter F; St. Anna Children's Cancer Research Institute, Vienna, Austria., Tumanov AV; Department of Microbiology, Immunology, and Molecular Genetics, University of Texas Health Science Center at San Antonio, San Antonio, TX, USA., Kraakman MJ; St. Anna Children's Cancer Research Institute, Vienna, Austria.; CeMM Research Center for Molecular Medicine of the Austrian Academy of Sciences, Vienna, Austria.; Ludwig Boltzmann Institute for Rare and Undiagnosed Diseases, Vienna, Austria., Metin A; Ankara Bilkent City Hospital, Children's Hospital, Department of Pediatric Immunology and Allergy, Ankara, Turkey., Castanon I; St. Anna Children's Cancer Research Institute, Vienna, Austria.; CeMM Research Center for Molecular Medicine of the Austrian Academy of Sciences, Vienna, Austria., Erman B; Can Sucak Research Laboratory for Translational Immunology, Hacettepe University, Ankara, Turkey.; Institute of Child Health, Hacettepe University, Ankara, Turkey., Baris S; Department of Pediatrics, Division of Allergy and Immunology, Marmara University School of Medicine, Istanbul, Turkey.; Istanbul Jeffrey Modell Diagnostic Center for Primary Immunodeficiency Diseases, Istanbul, Turkey.; Işıl Berat Barlan Center for Translational Medicine, Marmara University, Istanbul, Turkey.; Marmara University, Immune Deficiency Application and Research Center, Istanbul, Turkey., Boztug K; St. Anna Children's Cancer Research Institute, Vienna, Austria.; CeMM Research Center for Molecular Medicine of the Austrian Academy of Sciences, Vienna, Austria.; Ludwig Boltzmann Institute for Rare and Undiagnosed Diseases, Vienna, Austria.; Medical University of Vienna, Department of Pediatrics and Adolescent Medicine, Vienna, Austria.; St. Anna Children's Hospital, Vienna, Austria.
Source: Science immunology [Sci Immunol] 2024 Nov 22; Vol. 9 (101), pp. eadq8796. Date of Electronic Publication: 2024 Nov 22.
Publication Type: Journal Article; Research Support, Non-U.S. Gov't
Journal Info: Publisher: American Association for the Advancement of Science Country of Publication: United States NLM ID: 101688624 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 2470-9468 (Electronic) Linking ISSN: 24709468 NLM ISO Abbreviation: Sci Immunol Subsets: MEDLINE
Database: MEDLINE Ultimate
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  Data: LTβR deficiency causes lymph node aplasia and impaired B cell differentiation.
– Name: Author
  Label: Authors
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  Data: <searchLink fieldCode="AU" term="%22Ransmayr+B%22">Ransmayr B</searchLink>; St. Anna Children's Cancer Research Institute, Vienna, Austria.; CeMM Research Center for Molecular Medicine of the Austrian Academy of Sciences, Vienna, Austria.; Ludwig Boltzmann Institute for Rare and Undiagnosed Diseases, Vienna, Austria.<br /><searchLink fieldCode="AU" term="%22Bal+SK%22">Bal SK</searchLink>; St. Anna Children's Cancer Research Institute, Vienna, Austria.; CeMM Research Center for Molecular Medicine of the Austrian Academy of Sciences, Vienna, Austria.; Ludwig Boltzmann Institute for Rare and Undiagnosed Diseases, Vienna, Austria.<br /><searchLink fieldCode="AU" term="%22Thian+M%22">Thian M</searchLink>; St. Anna Children's Cancer Research Institute, Vienna, Austria.; CeMM Research Center for Molecular Medicine of the Austrian Academy of Sciences, Vienna, Austria.; Ludwig Boltzmann Institute for Rare and Undiagnosed Diseases, Vienna, Austria.<br /><searchLink fieldCode="AU" term="%22Svaton+M%22">Svaton M</searchLink>; St. Anna Children's Cancer Research Institute, Vienna, Austria.; CeMM Research Center for Molecular Medicine of the Austrian Academy of Sciences, Vienna, Austria.<br /><searchLink fieldCode="AU" term="%22van+de+Wetering+C%22">van de Wetering C</searchLink>; St. Anna Children's Cancer Research Institute, Vienna, Austria.; CeMM Research Center for Molecular Medicine of the Austrian Academy of Sciences, Vienna, Austria.<br /><searchLink fieldCode="AU" term="%22Hafemeister+C%22">Hafemeister C</searchLink>; St. Anna Children's Cancer Research Institute, Vienna, Austria.<br /><searchLink fieldCode="AU" term="%22Segarra-Roca+A%22">Segarra-Roca A</searchLink>; St. Anna Children's Cancer Research Institute, Vienna, Austria.<br /><searchLink fieldCode="AU" term="%22Block+J%22">Block J</searchLink>; St. Anna Children's Cancer Research Institute, Vienna, Austria.; CeMM Research Center for Molecular Medicine of the Austrian Academy of Sciences, Vienna, Austria.; Ludwig Boltzmann Institute for Rare and Undiagnosed Diseases, Vienna, Austria.<br /><searchLink fieldCode="AU" term="%22Frohne+A%22">Frohne A</searchLink>; St. Anna Children's Cancer Research Institute, Vienna, Austria.<br /><searchLink fieldCode="AU" term="%22Krolo+A%22">Krolo A</searchLink>; CeMM Research Center for Molecular Medicine of the Austrian Academy of Sciences, Vienna, Austria.; Ludwig Boltzmann Institute for Rare and Undiagnosed Diseases, Vienna, Austria.<br /><searchLink fieldCode="AU" term="%22Altunbas+MY%22">Altunbas MY</searchLink>; Department of Pediatrics, Division of Allergy and Immunology, Marmara University School of Medicine, Istanbul, Turkey.; Istanbul Jeffrey Modell Diagnostic Center for Primary Immunodeficiency Diseases, Istanbul, Turkey.; Işıl Berat Barlan Center for Translational Medicine, Marmara University, Istanbul, Turkey.; Marmara University, Immune Deficiency Application and Research Center, Istanbul, Turkey.<br /><searchLink fieldCode="AU" term="%22Bilgic-Eltan+S%22">Bilgic-Eltan S</searchLink>; Department of Pediatrics, Division of Allergy and Immunology, Marmara University School of Medicine, Istanbul, Turkey.; Istanbul Jeffrey Modell Diagnostic Center for Primary Immunodeficiency Diseases, Istanbul, Turkey.; Işıl Berat Barlan Center for Translational Medicine, Marmara University, Istanbul, Turkey.; Marmara University, Immune Deficiency Application and Research Center, Istanbul, Turkey.<br /><searchLink fieldCode="AU" term="%22Kıykım+A%22">Kıykım A</searchLink>; Istanbul University-Cerrahpasa, Faculty of Medicine, Department of Pediatric Allergy and Immunology, Istanbul, Turkey.<br /><searchLink fieldCode="AU" term="%22Aydiner+O%22">Aydiner O</searchLink>; Kartal Dr. Lütfi Kırdar City Hospital, Department of Radiology, Istanbul, Turkey.<br /><searchLink fieldCode="AU" term="%22Kesim+S%22">Kesim S</searchLink>; Marmara University, Faculty of Medicine, Department of Nuclear Medicine, Istanbul, Turkey.<br /><searchLink fieldCode="AU" term="%22Inanir+S%22">Inanir S</searchLink>; Marmara University, Faculty of Medicine, Department of Nuclear Medicine, Istanbul, Turkey.<br /><searchLink fieldCode="AU" term="%22Karakoc-Aydiner+E%22">Karakoc-Aydiner E</searchLink>; Department of Pediatrics, Division of Allergy and Immunology, Marmara University School of Medicine, Istanbul, Turkey.; Istanbul Jeffrey Modell Diagnostic Center for Primary Immunodeficiency Diseases, Istanbul, Turkey.; Işıl Berat Barlan Center for Translational Medicine, Marmara University, Istanbul, Turkey.; Marmara University, Immune Deficiency Application and Research Center, Istanbul, Turkey.<br /><searchLink fieldCode="AU" term="%22Ozen+A%22">Ozen A</searchLink>; Department of Pediatrics, Division of Allergy and Immunology, Marmara University School of Medicine, Istanbul, Turkey.; Istanbul Jeffrey Modell Diagnostic Center for Primary Immunodeficiency Diseases, Istanbul, Turkey.; Işıl Berat Barlan Center for Translational Medicine, Marmara University, Istanbul, Turkey.; Marmara University, Immune Deficiency Application and Research Center, Istanbul, Turkey.<br /><searchLink fieldCode="AU" term="%22Aba+Ü%22">Aba Ü</searchLink>; Can Sucak Research Laboratory for Translational Immunology, Hacettepe University, Ankara, Turkey.; Institute of Child Health, Hacettepe University, Ankara, Turkey.<br /><searchLink fieldCode="AU" term="%22Çomak+A%22">Çomak A</searchLink>; Ankara Bilkent City Hospital, Children's Hospital, Department of Nuclear Medicine, Ankara, Turkey.<br /><searchLink fieldCode="AU" term="%22Tuğcu+GD%22">Tuğcu GD</searchLink>; Ankara Bilkent City Hospital, Children's Hospital, Department of Pediatric Pulmonology, Ankara, Turkey.<br /><searchLink fieldCode="AU" term="%22Pazdzior+R%22">Pazdzior R</searchLink>; CeMM Research Center for Molecular Medicine of the Austrian Academy of Sciences, Vienna, Austria.<br /><searchLink fieldCode="AU" term="%22Huber+B%22">Huber B</searchLink>; Medical University of Vienna, Department of Dermatology, Vienna, Austria.<br /><searchLink fieldCode="AU" term="%22Farlik+M%22">Farlik M</searchLink>; Medical University of Vienna, Department of Dermatology, Vienna, Austria.<br /><searchLink fieldCode="AU" term="%22Kubicek+S%22">Kubicek S</searchLink>; CeMM Research Center for Molecular Medicine of the Austrian Academy of Sciences, Vienna, Austria.<br /><searchLink fieldCode="AU" term="%22von+Bernuth+H%22">von Bernuth H</searchLink>; Department of Pediatric Respiratory Medicine, Immunology and Critical Care Medicine, Charité University Medicine, Berlin, Corporate Member of Free University and Humboldt University and Berlin Institute of Health, Berlin, Germany.; Labor Berlin Charité-Vivantes, Department of Immunology, Berlin, Germany.; Berlin Institute of International Health Global Health Center Charité - Universitätsmedizin Berlin, Berlin, Germany.; Charité - Universitätsmedizin Berlin, corporate member of Freie Universität Berlin, Humboldt-Universität zu Berlin, and Berlin Institute of Health (BIH), Berlin-Brandenburg Center for Regenerative Therapies (BCRT), Berlin, Germany.<br /><searchLink fieldCode="AU" term="%22Simonitsch-Klupp+I%22">Simonitsch-Klupp I</searchLink>; Medical University of Vienna, Department of Pathology, Vienna, Austria.<br /><searchLink fieldCode="AU" term="%22Rizzi+M%22">Rizzi M</searchLink>; Department of Rheumatology and Clinical Immunology and Center for Chronic Immunodeficiency, Medical Center University of Freiburg, Faculty of Medicine, University of Freiburg, Freiburg, Germany.; CIBSS - Centre for Integrative Biological Signalling Studies, University of Freiburg, Freiburg, Germany.; Medical University of Vienna, Center for Pathophysiology, Infectiology and Immunology, Institute of Immunology, Vienna, Austria.<br /><searchLink fieldCode="AU" term="%22Halbritter+F%22">Halbritter F</searchLink>; St. Anna Children's Cancer Research Institute, Vienna, Austria.<br /><searchLink fieldCode="AU" term="%22Tumanov+AV%22">Tumanov AV</searchLink>; Department of Microbiology, Immunology, and Molecular Genetics, University of Texas Health Science Center at San Antonio, San Antonio, TX, USA.<br /><searchLink fieldCode="AU" term="%22Kraakman+MJ%22">Kraakman MJ</searchLink>; St. Anna Children's Cancer Research Institute, Vienna, Austria.; CeMM Research Center for Molecular Medicine of the Austrian Academy of Sciences, Vienna, Austria.; Ludwig Boltzmann Institute for Rare and Undiagnosed Diseases, Vienna, Austria.<br /><searchLink fieldCode="AU" term="%22Metin+A%22">Metin A</searchLink>; Ankara Bilkent City Hospital, Children's Hospital, Department of Pediatric Immunology and Allergy, Ankara, Turkey.<br /><searchLink fieldCode="AU" term="%22Castanon+I%22">Castanon I</searchLink>; St. Anna Children's Cancer Research Institute, Vienna, Austria.; CeMM Research Center for Molecular Medicine of the Austrian Academy of Sciences, Vienna, Austria.<br /><searchLink fieldCode="AU" term="%22Erman+B%22">Erman B</searchLink>; Can Sucak Research Laboratory for Translational Immunology, Hacettepe University, Ankara, Turkey.; Institute of Child Health, Hacettepe University, Ankara, Turkey.<br /><searchLink fieldCode="AU" term="%22Baris+S%22">Baris S</searchLink>; Department of Pediatrics, Division of Allergy and Immunology, Marmara University School of Medicine, Istanbul, Turkey.; Istanbul Jeffrey Modell Diagnostic Center for Primary Immunodeficiency Diseases, Istanbul, Turkey.; Işıl Berat Barlan Center for Translational Medicine, Marmara University, Istanbul, Turkey.; Marmara University, Immune Deficiency Application and Research Center, Istanbul, Turkey.<br /><searchLink fieldCode="AU" term="%22Boztug+K%22">Boztug K</searchLink>; St. Anna Children's Cancer Research Institute, Vienna, Austria.; CeMM Research Center for Molecular Medicine of the Austrian Academy of Sciences, Vienna, Austria.; Ludwig Boltzmann Institute for Rare and Undiagnosed Diseases, Vienna, Austria.; Medical University of Vienna, Department of Pediatrics and Adolescent Medicine, Vienna, Austria.; St. Anna Children's Hospital, Vienna, Austria.
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