Sarcomas developed in patients with Lynch Syndrome are enriched in pleomorphic soft-tissue sarcomas and are sensitive to immunotherapy.

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Title: Sarcomas developed in patients with Lynch Syndrome are enriched in pleomorphic soft-tissue sarcomas and are sensitive to immunotherapy.
Authors: Poumeaud F; Department of Medical Oncology, Oncopole Claudius Regaud, Toulouse, France; Department of Digestive Medical Oncology, Toulouse University Hospital, Toulouse, France; Toulouse Cancer Research Centre, Toulouse, France., Valentin T; Department of Medical Oncology, Oncopole Claudius Regaud, Toulouse, France; Toulouse Cancer Research Centre, Toulouse, France., Fares N; Department of Digestive Medical Oncology, Toulouse University Hospital, Toulouse, France; Toulouse Cancer Research Centre, Toulouse, France., Segier B; Biostatistics & Health Date Science Unit, Oncopole Claudius Regaud IUCT-O, Toulouse, France., Watson S; Department of Medical Oncology, Institut Curie, Paris, France., Verret B; Department of Medical Oncology, Institut Gustave Roussy, Villejuif, France., Tlemsani C; Department of Medical Oncology, APHP, Paris, France., Penel N; Department of Medical Oncology, Centre Oscar Lambret, Lille, France., Lejeune S; Department of Oncogenetics, Lille University Hospital, Lille, France., Firmin N; Department of Medical Oncology, Institut du Cancer de Montpellier, Montpellier, France., Sabouret A; Department of Medical Oncology, Institut Curie, Paris, France., Thery JC; Department of Medical Oncology, Centre Henri Becquerel, Rouen, France., Bonvalot S; Biostatistics & Health Date Science Unit, Oncopole Claudius Regaud IUCT-O, Toulouse, France., Cottereau E; Department of Oncogenetics, Tours University Hospital, Tours, France., Cauchin E; Department of Medical Oncology, Institut de Cancérologie de l'Ouest, Saint-Herblain, France., Lancon A; Department of Oncogenetics, Centre Georges François Leclerc, Dijon, France., Nambot S; Department of Oncogenetics, Centre Georges François Leclerc, Dijon, France., Zattara H; Department of Oncogenetics, Marseille University Hospital, Marseille, France., Coudert M; Department of Medical Oncology, Institut de Cancérologie de l'Ouest, Saint-Herblain, France., Fourme E; Biostatistics & Health Date Science Unit, Oncopole Claudius Regaud IUCT-O, Toulouse, France., Nogues C; Department of Oncogenetics, Institut Paoli Calmettes, Marseille, France., Tougeron D; Department of Medical Oncology, Poitiers University Hospital, Poitiers, France., Prieur F; Department of Oncogenetics, Saint Etienne University Hospital, Saint Etienne, France., Collonge-Rame MA; Department of Oncogenetics, Besançon University Hospital, Besançon, France., Denis C; Department of Oncogenetics, Strasbourg University Hospital, Strasbourg, France., Laurent-Puig P; Department of Medical Oncology, Institut Gustave Roussy, Villejuif, France., Chieze-Valero S; Department of Oncogenetics, Niort Hospital Centre, Niort, France., Dreyfus H; Department of Medical Oncology, Institut Sainte Catherine, Avignon, France., Jaffrelot M; Department of Digestive Medical Oncology, Toulouse University Hospital, Toulouse, France; Department of Oncogenetics, Oncopole Claudius Regaud, Toulouse, France., Vande Perre P; Department of Oncogenetics, Oncopole Claudius Regaud, Toulouse, France., Rochaix P; Toulouse Cancer Research Centre, Toulouse, France; Department of Pathology, Toulouse University Hospital, Toulouse, France., Gomez-Mascard A; Toulouse Cancer Research Centre, Toulouse, France; Department of Pathology, Toulouse University Hospital, Toulouse, France., Rochefort P; Department of Oncogenetics, Centre Léon Bérard, Lyon, France; Groupe Génétique et Cancer, Unicancer, France., Campoy S; Department of Oncogenetics, Centre Léon Bérard, Lyon, France; Groupe Génétique et Cancer, Unicancer, France., Chibon F; Toulouse Cancer Research Centre, Toulouse, France; Department of Pathology, Toulouse University Hospital, Toulouse, France., Lasset C; Department of Oncogenetics, Centre Léon Bérard, Lyon, France; Groupe Génétique et Cancer, Unicancer, France., Selves J; Toulouse Cancer Research Centre, Toulouse, France; Department of Pathology, Toulouse University Hospital, Toulouse, France., Guimbaud R; Department of Digestive Medical Oncology, Toulouse University Hospital, Toulouse, France; Toulouse Cancer Research Centre, Toulouse, France; Department of Oncogenetics, Oncopole Claudius Regaud, Toulouse, France; Groupe Génétique et Cancer, Unicancer, France. Electronic address: guimbaud.r@chu-toulouse.fr.
Source: European journal of cancer (Oxford, England : 1990) [Eur J Cancer] 2025 Feb 05; Vol. 216, pp. 115196. Date of Electronic Publication: 2024 Dec 21.
Publication Type: Journal Article; Multicenter Study
Journal Info: Publisher: Elsevier Science Ltd Country of Publication: England NLM ID: 9005373 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1879-0852 (Electronic) Linking ISSN: 09598049 NLM ISO Abbreviation: Eur J Cancer Subsets: MEDLINE
Database: MEDLINE Ultimate
Description
ISSN:1879-0852
DOI:10.1016/j.ejca.2024.115196