Loss or inhibition of lysosomal acid lipase in vitro leads to cholesteryl ester accumulation without affecting muscle formation or mitochondrial function.

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Title: Loss or inhibition of lysosomal acid lipase in vitro leads to cholesteryl ester accumulation without affecting muscle formation or mitochondrial function.
Authors: Akhmetshina A; Gottfried Schatz Research Center, Molecular Biology and Biochemistry, Medical University of Graz, Graz, Austria.; Division of Clinical Pharmacology, Department of Medicine, Vanderbilt University Medical Center, Nashville, TN, USA., Schooltink L; Gottfried Schatz Research Center, Molecular Biology and Biochemistry, Medical University of Graz, Graz, Austria., Amor M; Gottfried Schatz Research Center, Molecular Biology and Biochemistry, Medical University of Graz, Graz, Austria., Kuentzel KB; Gottfried Schatz Research Center, Molecular Biology and Biochemistry, Medical University of Graz, Graz, Austria., Rainer S; Gottfried Schatz Research Center, Molecular Biology and Biochemistry, Medical University of Graz, Graz, Austria., Nandy A; Division of Clinical Pharmacology, Department of Medicine, Vanderbilt University Medical Center, Nashville, TN, USA., Habisch H; Otto Loewi Research Center, Division of Medicinal Chemistry, Medical University of Graz, Graz, Austria., Madl T; Otto Loewi Research Center, Division of Medicinal Chemistry, Medical University of Graz, Graz, Austria.; BioTechMed-Graz, Graz, Austria., Rendina-Ruedy E; Division of Clinical Pharmacology, Department of Medicine, Vanderbilt University Medical Center, Nashville, TN, USA.; Molecular Physiology and Biophysics, Vanderbilt University, Nashville, TN, USA., Leithner K; BioTechMed-Graz, Graz, Austria.; Division of Pulmonology, Department of Internal Medicine, Medical University of Graz, Graz, Austria., Vujić N; Gottfried Schatz Research Center, Molecular Biology and Biochemistry, Medical University of Graz, Graz, Austria., Kratky D; Gottfried Schatz Research Center, Molecular Biology and Biochemistry, Medical University of Graz, Graz, Austria.; BioTechMed-Graz, Graz, Austria.
Source: BBA advances [BBA Adv] 2024 Dec 25; Vol. 7, pp. 100135. Date of Electronic Publication: 2024 Dec 25 (Print Publication: 2025).
Publication Type: Journal Article
Journal Info: Publisher: Elsevier B.V Country of Publication: Netherlands NLM ID: 9918227371406676 Publication Model: eCollection Cited Medium: Internet ISSN: 2667-1603 (Electronic) Linking ISSN: 26671603 NLM ISO Abbreviation: BBA Adv Subsets: PubMed not MEDLINE
Database: MEDLINE Ultimate
Description
ISSN:2667-1603
DOI:10.1016/j.bbadva.2024.100135