Loss or inhibition of lysosomal acid lipase in vitro leads to cholesteryl ester accumulation without affecting muscle formation or mitochondrial function.

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Title: Loss or inhibition of lysosomal acid lipase in vitro leads to cholesteryl ester accumulation without affecting muscle formation or mitochondrial function.
Authors: Akhmetshina A; Gottfried Schatz Research Center, Molecular Biology and Biochemistry, Medical University of Graz, Graz, Austria.; Division of Clinical Pharmacology, Department of Medicine, Vanderbilt University Medical Center, Nashville, TN, USA., Schooltink L; Gottfried Schatz Research Center, Molecular Biology and Biochemistry, Medical University of Graz, Graz, Austria., Amor M; Gottfried Schatz Research Center, Molecular Biology and Biochemistry, Medical University of Graz, Graz, Austria., Kuentzel KB; Gottfried Schatz Research Center, Molecular Biology and Biochemistry, Medical University of Graz, Graz, Austria., Rainer S; Gottfried Schatz Research Center, Molecular Biology and Biochemistry, Medical University of Graz, Graz, Austria., Nandy A; Division of Clinical Pharmacology, Department of Medicine, Vanderbilt University Medical Center, Nashville, TN, USA., Habisch H; Otto Loewi Research Center, Division of Medicinal Chemistry, Medical University of Graz, Graz, Austria., Madl T; Otto Loewi Research Center, Division of Medicinal Chemistry, Medical University of Graz, Graz, Austria.; BioTechMed-Graz, Graz, Austria., Rendina-Ruedy E; Division of Clinical Pharmacology, Department of Medicine, Vanderbilt University Medical Center, Nashville, TN, USA.; Molecular Physiology and Biophysics, Vanderbilt University, Nashville, TN, USA., Leithner K; BioTechMed-Graz, Graz, Austria.; Division of Pulmonology, Department of Internal Medicine, Medical University of Graz, Graz, Austria., Vujić N; Gottfried Schatz Research Center, Molecular Biology and Biochemistry, Medical University of Graz, Graz, Austria., Kratky D; Gottfried Schatz Research Center, Molecular Biology and Biochemistry, Medical University of Graz, Graz, Austria.; BioTechMed-Graz, Graz, Austria.
Source: BBA advances [BBA Adv] 2024 Dec 25; Vol. 7, pp. 100135. Date of Electronic Publication: 2024 Dec 25 (Print Publication: 2025).
Publication Type: Journal Article
Journal Info: Publisher: Elsevier B.V Country of Publication: Netherlands NLM ID: 9918227371406676 Publication Model: eCollection Cited Medium: Internet ISSN: 2667-1603 (Electronic) Linking ISSN: 26671603 NLM ISO Abbreviation: BBA Adv Subsets: PubMed not MEDLINE
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  Data: Loss or inhibition of lysosomal acid lipase in vitro leads to cholesteryl ester accumulation without affecting muscle formation or mitochondrial function.
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  Data: <searchLink fieldCode="AU" term="%22Akhmetshina+A%22">Akhmetshina A</searchLink>; Gottfried Schatz Research Center, Molecular Biology and Biochemistry, Medical University of Graz, Graz, Austria.; Division of Clinical Pharmacology, Department of Medicine, Vanderbilt University Medical Center, Nashville, TN, USA.<br /><searchLink fieldCode="AU" term="%22Schooltink+L%22">Schooltink L</searchLink>; Gottfried Schatz Research Center, Molecular Biology and Biochemistry, Medical University of Graz, Graz, Austria.<br /><searchLink fieldCode="AU" term="%22Amor+M%22">Amor M</searchLink>; Gottfried Schatz Research Center, Molecular Biology and Biochemistry, Medical University of Graz, Graz, Austria.<br /><searchLink fieldCode="AU" term="%22Kuentzel+KB%22">Kuentzel KB</searchLink>; Gottfried Schatz Research Center, Molecular Biology and Biochemistry, Medical University of Graz, Graz, Austria.<br /><searchLink fieldCode="AU" term="%22Rainer+S%22">Rainer S</searchLink>; Gottfried Schatz Research Center, Molecular Biology and Biochemistry, Medical University of Graz, Graz, Austria.<br /><searchLink fieldCode="AU" term="%22Nandy+A%22">Nandy A</searchLink>; Division of Clinical Pharmacology, Department of Medicine, Vanderbilt University Medical Center, Nashville, TN, USA.<br /><searchLink fieldCode="AU" term="%22Habisch+H%22">Habisch H</searchLink>; Otto Loewi Research Center, Division of Medicinal Chemistry, Medical University of Graz, Graz, Austria.<br /><searchLink fieldCode="AU" term="%22Madl+T%22">Madl T</searchLink>; Otto Loewi Research Center, Division of Medicinal Chemistry, Medical University of Graz, Graz, Austria.; BioTechMed-Graz, Graz, Austria.<br /><searchLink fieldCode="AU" term="%22Rendina-Ruedy+E%22">Rendina-Ruedy E</searchLink>; Division of Clinical Pharmacology, Department of Medicine, Vanderbilt University Medical Center, Nashville, TN, USA.; Molecular Physiology and Biophysics, Vanderbilt University, Nashville, TN, USA.<br /><searchLink fieldCode="AU" term="%22Leithner+K%22">Leithner K</searchLink>; BioTechMed-Graz, Graz, Austria.; Division of Pulmonology, Department of Internal Medicine, Medical University of Graz, Graz, Austria.<br /><searchLink fieldCode="AU" term="%22Vujić+N%22">Vujić N</searchLink>; Gottfried Schatz Research Center, Molecular Biology and Biochemistry, Medical University of Graz, Graz, Austria.<br /><searchLink fieldCode="AU" term="%22Kratky+D%22">Kratky D</searchLink>; Gottfried Schatz Research Center, Molecular Biology and Biochemistry, Medical University of Graz, Graz, Austria.; BioTechMed-Graz, Graz, Austria.
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  Data: <searchLink fieldCode="JN" term="%229918227371406676%22">BBA advances</searchLink> [BBA Adv] 2024 Dec 25; Vol. 7, pp. 100135. <i>Date of Electronic Publication: </i>2024 Dec 25 (<i>Print Publication: </i>2025).
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  Data: <i>Publisher: </i><searchLink fieldCode="PB" term="%22Elsevier+B%2EV%22">Elsevier B.V </searchLink><i>Country of Publication: </i>Netherlands <i>NLM ID: </i>9918227371406676 <i>Publication Model: </i>eCollection <i>Cited Medium: </i>Internet <i>ISSN: </i>2667-1603 (Electronic) <i>Linking ISSN: </i><searchLink fieldCode="IS" term="%2226671603%22">26671603 </searchLink><i>NLM ISO Abbreviation: </i>BBA Adv <i>Subsets: </i>PubMed not MEDLINE
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