Correction of dysregulated lipid metabolism normalizes gene expression in oligodendrocytes and prolongs lifespan in female poly-GA C9orf72 mice.

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Title: Correction of dysregulated lipid metabolism normalizes gene expression in oligodendrocytes and prolongs lifespan in female poly-GA C9orf72 mice.
Authors: Rezaei A; German Center for Neurodegenerative Diseases (DZNE), Munich, Germany.; Munich Cluster of Systems Neurology (SyNergy), Munich, Germany.; Ludwig-Maximilians-Universität (LMU) Munich, Graduate School of Systemic Neurosciences (GSN), Munich, Germany., Kocsis-Jutka V; German Center for Neurodegenerative Diseases (DZNE), Munich, Germany., Gunes ZI; Munich Cluster of Systems Neurology (SyNergy), Munich, Germany.; Ludwig-Maximilians-Universität (LMU) Munich, Graduate School of Systemic Neurosciences (GSN), Munich, Germany.; Institute of Clinical Neuroimmunology, Klinikum der Universität München, Ludwig Maximilians University Munich, Munich, Germany.; Biomedical Center, Ludwig Maximilians University Munich, Munich, Germany., Zeng Q; German Center for Neurodegenerative Diseases (DZNE), Munich, Germany.; Ludwig-Maximilians-Universität (LMU) Munich, Graduate School of Systemic Neurosciences (GSN), Munich, Germany., Kislinger G; German Center for Neurodegenerative Diseases (DZNE), Munich, Germany.; Munich Cluster of Systems Neurology (SyNergy), Munich, Germany., Bauernschmitt F; Munich Cluster of Systems Neurology (SyNergy), Munich, Germany.; Institute of Clinical Neuroimmunology, Klinikum der Universität München, Ludwig Maximilians University Munich, Munich, Germany.; Biomedical Center, Ludwig Maximilians University Munich, Munich, Germany., Isilgan HB; German Center for Neurodegenerative Diseases (DZNE), Munich, Germany., Parisi LR; Sanofi, Rare and Neurologic Diseases, Cambridge, MA, USA., Kaya T; German Center for Neurodegenerative Diseases (DZNE), Munich, Germany.; Munich Cluster of Systems Neurology (SyNergy), Munich, Germany.; Department of Neurodegenerative Diseases and Geriatric Psychiatry, University Hospital Bonn, Bonn, Germany., Franzenburg S; Institute of Clinical Molecular Biology, Kiel University, Kiel, Germany., Koppenbrink J; German Center for Neurodegenerative Diseases (DZNE), Munich, Germany., Knogler J; German Center for Neurodegenerative Diseases (DZNE), Munich, Germany., Arzberger T; Center for Neuropathology and Prion Research, University Hospital, LMU Munich, Munich, Germany.; Department of Psychiatry and Psychotherapy, University Hospital, LMU Munich, Munich, Germany., Farny D; German Center for Neurodegenerative Diseases (DZNE), Munich, Germany., Nuscher B; Chair of Metabolic Biochemistry, Biomedical Center (BMC), Faculty of Medicine, Ludwig-Maximilians-Universität Munich, Munich, Germany., Katona E; German Center for Neurodegenerative Diseases (DZNE), Munich, Germany.; Munich Cluster of Systems Neurology (SyNergy), Munich, Germany.; Ludwig-Maximilians-Universität (LMU) Munich, Graduate School of Systemic Neurosciences (GSN), Munich, Germany., Dhingra A; German Center for Neurodegenerative Diseases (DZNE), Tübingen, Germany., Yang C; German Center for Neurodegenerative Diseases (DZNE), Munich, Germany., Gouna G; German Center for Neurodegenerative Diseases (DZNE), Munich, Germany.; Ludwig-Maximilians-Universität (LMU) Munich, Graduate School of Systemic Neurosciences (GSN), Munich, Germany.; Institute of Neuronal Cell Biology, Technical University Munich, Munich, Germany., LaClair KD; German Center for Neurodegenerative Diseases (DZNE), Munich, Germany., Janjic A; Anthropology and Human Genomics, Faculty of Biology, Ludwig-Maximilians Universität München, Munich, Germany., Enard W; Anthropology and Human Genomics, Faculty of Biology, Ludwig-Maximilians Universität München, Munich, Germany., Zhou Q; German Center for Neurodegenerative Diseases (DZNE), Munich, Germany.; Munich Cluster of Systems Neurology (SyNergy), Munich, Germany., Hagan N; Sanofi, Rare and Neurologic Diseases, Cambridge, MA, USA., Ofengeim D; Sanofi, Rare and Neurologic Diseases, Cambridge, MA, USA., Beltrán E; Munich Cluster of Systems Neurology (SyNergy), Munich, Germany.; Institute of Clinical Neuroimmunology, Klinikum der Universität München, Ludwig Maximilians University Munich, Munich, Germany.; Biomedical Center, Ludwig Maximilians University Munich, Munich, Germany., Gokce O; Munich Cluster of Systems Neurology (SyNergy), Munich, Germany.; Ludwig-Maximilians-Universität (LMU) Munich, Graduate School of Systemic Neurosciences (GSN), Munich, Germany.; Department of Neurodegenerative Diseases and Geriatric Psychiatry, University Hospital Bonn, Bonn, Germany.; Institute for Stroke and Dementia Research, University Hospital of Munich, LMU Munich, Munich, Germany., Simons M; German Center for Neurodegenerative Diseases (DZNE), Munich, Germany.; Munich Cluster of Systems Neurology (SyNergy), Munich, Germany.; Ludwig-Maximilians-Universität (LMU) Munich, Graduate School of Systemic Neurosciences (GSN), Munich, Germany.; Institute of Neuronal Cell Biology, Technical University Munich, Munich, Germany., Liebscher S; Munich Cluster of Systems Neurology (SyNergy), Munich, Germany.; Ludwig-Maximilians-Universität (LMU) Munich, Graduate School of Systemic Neurosciences (GSN), Munich, Germany.; Institute of Clinical Neuroimmunology, Klinikum der Universität München, Ludwig Maximilians University Munich, Munich, Germany.; Biomedical Center, Ludwig Maximilians University Munich, Munich, Germany.; Institute of Neurobiochemistry, Medical University of Innsbruck, Innsbruck, Austria., Edbauer D; German Center for Neurodegenerative Diseases (DZNE), Munich, Germany. dieter.edbauer@dzne.de.; Munich Cluster of Systems Neurology (SyNergy), Munich, Germany. dieter.edbauer@dzne.de.; Ludwig-Maximilians-Universität (LMU) Munich, Graduate School of Systemic Neurosciences (GSN), Munich, Germany. dieter.edbauer@dzne.de.
Source: Nature communications [Nat Commun] 2025 Apr 11; Vol. 16 (1), pp. 3442. Date of Electronic Publication: 2025 Apr 11.
Publication Type: Journal Article
Journal Info: Publisher: Nature Pub. Group Country of Publication: England NLM ID: 101528555 Publication Model: Electronic Cited Medium: Internet ISSN: 2041-1723 (Electronic) Linking ISSN: 20411723 NLM ISO Abbreviation: Nat Commun Subsets: MEDLINE
Database: MEDLINE Ultimate
Description
ISSN:2041-1723
DOI:10.1038/s41467-025-58634-4