Development and Validation of the FIP Score for the Screening of FIP1L1::PDGFRA-Associated Hypereosinophilic Syndrome.

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Title: Development and Validation of the FIP Score for the Screening of FIP1L1::PDGFRA-Associated Hypereosinophilic Syndrome.
Authors: Stammler R; National Referral Center for Hypereosinophilic Syndromes (CEREO), Suresnes, France; Department of Internal Medicine, Foch Hospital, Suresnes, France., Vallée A; Department of Epidemiology-Data-Biostatistics, Delegation of Clinical Research and Innovation (DRCI), Foch Hospital, Suresnes, France., Rohmer J; National Referral Center for Hypereosinophilic Syndromes (CEREO), Suresnes, France; Sorbonne Paris Cité University, Assistance Publique Hôpitaux de Paris, Internal Medicine Department, Bichat hospital, Paris, France., Grardel N; National Referral Center for Hypereosinophilic Syndromes (CEREO), Suresnes, France; University Hospital Center of Lille, Hematology Institute, Lille, France., Abisror N; Internal Medicine Department, Sorbonne University, Saint Antoine Hospital, Assistance Publique Hôpitaux de Paris, Paris, France., Chahla WA; National Referral Center for Hypereosinophilic Syndromes (CEREO), Suresnes, France; Pediatric Hematology Department, University Hospital Center of Lille, Lille, France., Ackermann F; National Referral Center for Hypereosinophilic Syndromes (CEREO), Suresnes, France; Department of Internal Medicine, Foch Hospital, Suresnes, France., Baudet A; Internal Medicine Department, Hospital Center of Annecy, Annecy, France., Belfeki N; Internal Medicine and Clinical Immunology Department, Sud Ile de France Group Hospital, Melun, France., Ben Abdelali R; Pole of Hematology and Oncology, CERBA Laboratory, Saint Ouen l'Aumône, France., Bidet A; Laboratory of Hematology, CHU de Bordeaux, Pessac, France., Bladé JS; Hôpital d'Instruction des Armées Saint Anne, Internal Medicine and Oncology Department, Boulevard Saint Anne, Toulon, France., Bleuse S; National Referral Center for Hypereosinophilic Syndromes (CEREO), Suresnes, France; Immunology Institute, Internal Medicine and Clinical Immunology Department, University Hospital Center of Lille, INFINITE-Institute for Translational Research in Inflammation, University of Lille, Lille, France., Bonnotte B; Service de Médecine Interne et Immunologie Clinique, Centre Hospitalo-Universitaire Dijon Bourgogne, Université de Bourgogne, Institut national de la santé et de la recherche médicale unité mixte de recherche 1098, Dijon, France., Bouderbala MA; Service d'Hématologie et Oncologie Médicale, Centre Hospitalier de Poissy Saint-Germain, Poissy, France., Cayuela JM; Laboratory of Hematology, Saint Louis Hospital, University Paris Cité, Paris, France., Chebrek S; Hematology Department, H. Duffaut Hospital Center, Avignon, France., Dion J; Internal Medicine and clinical Immunopathology Department, University Hospital Center of Toulouse, Pole Institut Universitaire du Cancer Oncopole University Hospital Center, Toulouse, France., Dossier A; Sorbonne Paris Cité University, Assistance Publique Hôpitaux de Paris, Internal Medicine Department, Bichat hospital, Paris, France., Duployez N; National Referral Center for Hypereosinophilic Syndromes (CEREO), Suresnes, France; University Hospital Center of Lille, Hematology Institute, Lille, France; University of Lille, Centre National de la Recherche Scientifique, INSERM U1277, Cancer Heterogeneity, Plasticity, and Resistance to Therapies (CANTHER), Lille, France., Faguer S; Department of Nephrology and Organ Transplantation, National Reference Center for Rare Kidney Diseases, University Hospital of Toulouse, Toulouse, France; INSERM U1297 (I2MC), F-31000 Toulouse, France., Flandrin-Gresta P; Hematology Laboratory, Nord Hospital, University Hospital Center of Saint Etienne, Saint Etienne, France., Galicier L; Internal Medicine Department, CHU La Timone, AP-HM, Marseille, France., Godon C; Hematological Cytogenetic Laboratory, University Hospital Center of Nantes, Nantes, France., Grall M; Internal Medicine Department, University Hospital Center of Rouen, Rouen, France., Jachiet V; Internal Medicine Department, Sorbonne University, Saint Antoine Hospital, Assistance Publique Hôpitaux de Paris, Paris, France., Jouvray M; Internal Medicine Department, Hospital Center of Arras, Arras, France., Latu I; Pneumology Department, H. Duffaut Hospital Center, Avignon, France., Ledoult E; National Referral Center for Hypereosinophilic Syndromes (CEREO), Suresnes, France; Immunology Institute, Internal Medicine and Clinical Immunology Department, University Hospital Center of Lille, INFINITE-Institute for Translational Research in Inflammation, University of Lille, Lille, France., Lengline E; Department of Hematology, Saint Louis Hospital, Paris, France., Leurs A; Internal Medicine Department, Alexandra Lepève Hospital Center, Dunkerque, France., Lhermitte L; University of Paris, Institut National de Recherche Médicale U1151, Laboratory of Onco-Hematology, Hôpital Necker Enfants-Malades, Paris, France., Lifermann F; Internal Medicine Department, Hospital Center of Dax, Dax, France., Limal N; Internal Medicine Department, Henri Mondor Hospital, Assistance Publique Hôpitaux de Paris, Paris-Est Créteil University, Créteil, France., Lioger B; Internal and Polyvalent Medicine Department, Hospital Center of Blois, Blois, France., Lugosi M; Internal Medicine Department, University Grenoble Alpes, University Hospital Center Grenoble Alpes, Grenoble, France., Machelart I; Internal Medicine Department, Hospital Center of Côte Basque, Bayonne, France., Martin M; Internal Medicine Department, University Hospital Center La Milétrie, INSERM U1313, University of Poitiers, Poitiers, France., Martis N; Internal Medicine Department, Nice University Hospital Center, Nice, France., Mauvieux L; Hematology Department, University Hospital Center of Strasbourg, University of Strasbourg, CNRS UPR3572, Strasbourg, France., Melboucy-Belkhir S; Internal and Polyvalent Medicine Department, Saint Quentin Hospital Center, Saint Quentin, France., Mohr C; Hematology and Oncology Department, Hospital Group Sud Réunion, Saint Pierre, Réunion, France., Moulis G; Internal Medicine Department, University Hospital Center of Toulouse, Clinical Investigation Center 1436, PEPSS Team, Toulouse, France., Mozicconacci MJ; Paoli-Calmettes Institute, Cancerology Research Center of Marseille, Biopathology, Marseille, France., Naguib D; Laboratory of Hematology, University Hospital Center of Caen, Caen, France., Néel A; Internal Medicine Department, University Hospital Center of Nantes, Nantes, France., Nicolini FE; Cancerology and Hematology Department, Léon Bérard Center, Lyon, France., Outh R; Internal Medicine Department, Hospital Center of Perpignan, Perpignan, France., Panel K; National Referral Center for Hypereosinophilic Syndromes (CEREO), Suresnes, France., Preudhomme C; University Hospital Center of Lille, Hematology Institute, Lille, France., Puyade M; Internal Medicine Department, University Hospital Center la Milétrie, CICP-1042, Poitiers, France., Quemeneur T; Nephrology and Internal Medicine Department, Hospital Center of Valenciennes, Valenciennes, France., Queyrel Moranne V; Rheumatology Department, University Hospital Center L'Archet, Nice, France., Rey J; Department of Hematology, Institut Paoli-Calmettes, Marseille, France., Rousselot P; Hematology Department, Versailles André Mignot Hospital, University Paris-Saclay, Le Chesnay, France., Schleinitz N; Internal Medicine Department, CHU La Timone, AP-HM, Marseille, France., Slama B; Hematology Department, H. Duffaut Hospital Center, Avignon, France., Staumont-Salle D; National Referral Center for Hypereosinophilic Syndromes (CEREO), Suresnes, France; University Hospital Center of Lille, Dermatology Department, INFINITE-Institute for Translational Research in Inflammation, University of Lille, Lille, France., Taillé C; Pneumology Department and Referal Center for Rare Pulmonary Diseases, Bichat Hospital, Assistance Publique Hôpitaux de Paris, UMR 1152, Paris Cité University, Paris, France., Terriou L; National Referral Center for Hypereosinophilic Syndromes (CEREO), Suresnes, France; Immunology Institute, Internal Medicine and Clinical Immunology Department, University Hospital Center of Lille, INFINITE-Institute for Translational Research in Inflammation, University of Lille, Lille, France., Tréfond L; Internal Medicine Department, University Hospital Center of Clermont Ferrand, Gabriel Montpied Hospital, INSERM U1071, INRA USC2018, M2iSH, Clermont Auvergne University, Clermont Ferrand, France., Viallard JF; Internal Medicine Department, University Hospital Center of Bordeaux, Bordeaux, France., Kahn JE; National Referral Center for Hypereosinophilic Syndromes (CEREO), Suresnes, France; Internal Medicine Department, Ambroise Paré Hospital, AP-HP. 9, Boulogne, France; Infection and Inflammation, UMR 1173, INSERM, UVSQ/Paris Saclay University, Montigny-le-Bretonneux, France., Lefèvre G; National Referral Center for Hypereosinophilic Syndromes (CEREO), Suresnes, France; Immunology Institute, Internal Medicine and Clinical Immunology Department, University Hospital Center of Lille, INFINITE-Institute for Translational Research in Inflammation, University of Lille, Lille, France; University Lille, CHU Lille, INSERM, U1286-INFINITE-Institute for Translational Research in Inflammation, Lille, France., Groh M; National Referral Center for Hypereosinophilic Syndromes (CEREO), Suresnes, France; Department of Internal Medicine, Foch Hospital, Suresnes, France; University Lille, CHU Lille, INSERM, U1286-INFINITE-Institute for Translational Research in Inflammation, Lille, France. Electronic address: m.groh@hopital-foch.com.
Corporate Authors: COHESion, CEREO and GBMHM groups
Source: The journal of allergy and clinical immunology. In practice [J Allergy Clin Immunol Pract] 2025 Nov; Vol. 13 (11), pp. 3066-3076.e2. Date of Electronic Publication: 2025 Sep 22.
Publication Type: Journal Article; Multicenter Study; Observational Study; Validation Study; Validation Study
Journal Info: Publisher: Elsevier Inc Country of Publication: United States NLM ID: 101597220 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 2213-2201 (Electronic) NLM ISO Abbreviation: J Allergy Clin Immunol Pract Subsets: MEDLINE
Database: MEDLINE Ultimate
Description
ISSN:2213-2201
DOI:10.1016/j.jaip.2025.09.009