Genetically heterozygous - transcriptionally homozygous IRF7 deficiency underlies herpesvirus CNS infections in humans.

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Title: Genetically heterozygous - transcriptionally homozygous IRF7 deficiency underlies herpesvirus CNS infections in humans.
Authors: Werner M; Department of Biomedicine, Aarhus University, Aarhus, Denmark.; Center for Immunology of Viral Infections, Aarhus University , Aarhus, Denmark.; Department of Infectious Diseases, Aarhus University Hospital, Aarhus, Denmark., Wolff JH; Department of Biomedicine, Aarhus University, Aarhus, Denmark.; Center for Immunology of Viral Infections, Aarhus University , Aarhus, Denmark., Taft J; Department of Pediatrics, Center for Genetic Errors of Immunity, Columbia University, New York, NY, USA., Zillinger T; Department of Biomedicine, Aarhus University, Aarhus, Denmark.; Center for Immunology of Viral Infections, Aarhus University , Aarhus, Denmark.; Institute of Clinical Chemistry and Clinical Pharmacology, University Hospital Bonn , Bonn, Germany., Hinke DM; Department of Biomedicine, Aarhus University, Aarhus, Denmark.; Center for Immunology of Viral Infections, Aarhus University , Aarhus, Denmark.; Department of Infectious Diseases, Aarhus University Hospital, Aarhus, Denmark., Barfod TS; Institute for Clinical Medicine, Copenhagen University , Roskilde, Denmark.; Department of Infectious Diseases, Zealand University Hospital, Roskilde, Denmark., De Keukeleere K; Department of Biomedicine, Aarhus University, Aarhus, Denmark.; Center for Immunology of Viral Infections, Aarhus University , Aarhus, Denmark.; Department of Infectious Diseases, Aarhus University Hospital, Aarhus, Denmark., Winzig F; Department of Biomedicine, Aarhus University, Aarhus, Denmark.; Center for Immunology of Viral Infections, Aarhus University , Aarhus, Denmark.; Department of Infectious Diseases, Aarhus University Hospital, Aarhus, Denmark., Bundgaard B; Department of Biomedicine, Aarhus University, Aarhus, Denmark.; Center for Immunology of Viral Infections, Aarhus University , Aarhus, Denmark., Narita R; Department of Biomedicine, Aarhus University, Aarhus, Denmark.; Center for Immunology of Viral Infections, Aarhus University , Aarhus, Denmark., Skov TW; Department of Biomedicine, Aarhus University, Aarhus, Denmark.; Center for Immunology of Viral Infections, Aarhus University , Aarhus, Denmark., Jensen JA; Department of Biomedicine, Aarhus University, Aarhus, Denmark.; Center for Immunology of Viral Infections, Aarhus University , Aarhus, Denmark.; Department of Infectious Diseases, Aarhus University Hospital, Aarhus, Denmark., Jørgensen SE; Department of Biomedicine, Aarhus University, Aarhus, Denmark.; Center for Immunology of Viral Infections, Aarhus University , Aarhus, Denmark.; Department of Infectious Diseases, Aarhus University Hospital, Aarhus, Denmark., Jørgensen CS; State Serum Institute , Copenhagen, Denmark., Skouboe MK; Department of Biomedicine, Aarhus University, Aarhus, Denmark.; Center for Immunology of Viral Infections, Aarhus University , Aarhus, Denmark.; Department of Infectious Diseases, Aarhus University Hospital, Aarhus, Denmark., Lassaunière R; State Serum Institute , Copenhagen, Denmark., de Boer JH; University Medical Center, Utrecht , Utrecht, The Netherlands., Jakobsen MR; Department of Biomedicine, Aarhus University, Aarhus, Denmark., Mikkelsen JG; Department of Biomedicine, Aarhus University, Aarhus, Denmark.; Center for Immunology of Viral Infections, Aarhus University , Aarhus, Denmark., Bogunovic D; Department of Pediatrics, Center for Genetic Errors of Immunity, Columbia University, New York, NY, USA., Paludan SR; Department of Biomedicine, Aarhus University, Aarhus, Denmark.; Center for Immunology of Viral Infections, Aarhus University , Aarhus, Denmark.; Sahlgrenska Academy, University of Gothenburg , Gothenburg, Sweden., van der Sluis RM; Department of Biomedicine, Aarhus University, Aarhus, Denmark.; Center for Immunology of Viral Infections, Aarhus University , Aarhus, Denmark., Mogensen TH; Department of Biomedicine, Aarhus University, Aarhus, Denmark.; Center for Immunology of Viral Infections, Aarhus University , Aarhus, Denmark.; Department of Infectious Diseases, Aarhus University Hospital, Aarhus, Denmark.
Source: The Journal of experimental medicine [J Exp Med] 2026 Jan 05; Vol. 223 (1). Date of Electronic Publication: 2025 Oct 29.
Publication Type: Journal Article
Journal Info: Publisher: Rockefeller University Press Country of Publication: United States NLM ID: 2985109R Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1540-9538 (Electronic) Linking ISSN: 00221007 NLM ISO Abbreviation: J Exp Med Subsets: MEDLINE
Database: MEDLINE Ultimate
Description
ISSN:1540-9538
DOI:10.1084/jem.20250492